KEGG   DRUG: Aceneuramic acid
Entry
D11016                      Drug                                   
Name
Aceneuramic acid (JAN/USAN);
Acenobel (TN)
Formula
C11H19NO9
Exact mass
309.106
Mol weight
309.2699
Structure
Simcomp
Class
Unclassified
 DG03304  NPL substrate
Remark
Same as: C00270 C22382
Therapeutic category: 1900
ATC code: M09AX05
Chemical structure group: DG02580
Product (DG02580): D11016<JP>
Efficacy
Myopathy treatment
Comment
Treatment of hereditary inclusion body myopathy (HIBM)
Metabolism
Enzyme: NPL [HSA:80896]
Brite
Anatomical Therapeutic Chemical (ATC) classification [BR:br08303]
 M MUSCULO-SKELETAL SYSTEM
  M09 OTHER DRUGS FOR DISORDERS OF THE MUSCULO-SKELETAL SYSTEM
   M09A OTHER DRUGS FOR DISORDERS OF THE MUSCULO-SKELETAL SYSTEM
    M09AX Other drugs for disorders of the musculo-skeletal system
     M09AX05 Aceneuramic acid
      D11016  Aceneuramic acid (JAN/USAN) <JP>
Therapeutic category of drugs in Japan [BR:br08301]
 1  Agents affecting nervous system and sensory organs
  19  Other agents affecting nervous system and sensory organs
   190  Other agents affecting nervous system and sensory organs
    1900  Other agents affecting nervous system and sensory organs
     D11016  Aceneuramic acid (JAN/USAN)
Drug groups [BR:br08330]
 Unclassified
  DG03304  NPL substrate
   DG02580  Aceneuramic acid
    D11016  Aceneuramic acid
New drug approvals in Japan [br08318.html]
 Drugs with new active ingredients
  D11016
New drug approvals in the USA, Europe and Japan [br08328.html]
 Approval dates by FDA, EMA and PMDA
  D11016
Drug metabolizing enzymes and transporters [br08309.html]
 Drug metabolizing enzymes
  D11016
Drug groups [BR:br08330]
 Unclassified
  DG03304  NPL substrate
   DG02580  Aceneuramic acid
Other DBs
CAS: 131-48-6
PubChem: 348350488
ChEBI: 173082
PDB-CCD: SI3[PDBj]
LinkDB
KCF data

ATOM        21
            1   O1a O     4.2000  -14.8400
            2   C1b C     5.4124  -14.1400
            3   C1c C     6.6249  -14.8400
            4   C1c C     7.8373  -14.1400
            5   C1c C     9.0497  -14.8400
            6   C1c C    10.2622  -14.1400
            7   C1c C    11.4746  -14.8400
            8   C1b C    12.6870  -14.1400
            9   C5a C    13.8995  -14.8400
            10  C6a C    15.1119  -14.1400
            11  O6a O    16.3244  -14.8400
            12  O1a O     6.6249  -16.2398
            13  O1a O     7.8373  -12.7400
            14  O1a O     9.0497  -16.2399
            15  N1b N    10.2622  -12.7403
            16  O1a O    11.4746  -16.2400
            17  O5a O    13.8995  -16.2397
            18  O6a O    15.1119  -12.7400
            19  C5a C    11.4954  -12.0280
            20  C1a C    12.7015  -12.7241
            21  O5a O    11.4951  -10.6401
BOND        20
            1     1   2 1
            2     2   3 1
            3     3   4 1
            4     4   5 1
            5     5   6 1
            6     6   7 1
            7     7   8 1
            8     8   9 1
            9     9  10 1
            10   10  11 1
            11    3  12 1 #Down
            12    4  13 1 #Up
            13    5  14 1 #Up
            14    6  15 1 #Down
            15    7  16 1 #Down
            16    9  17 2
            17   10  18 2
            18   15  19 1
            19   19  20 1
            20   19  21 2

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