Atrial cardiomyopathy with heart block Cardiomyopathy, familial, with conduction disturbance
Description
Atrial standstill (AS, ATRST) is a rare cardiac arrhythmia characterized by transient or persistent absence of electrical and mechanical activity in the atria. On surface electrocardiogram, AS is distinguished by absence of the P wave, bradycardia, and junctional or ventricular escape rhythm.
Category
Cardiovascular disease
Brite
Human diseases in ICD-11 classification [BR:br08403]
11 Diseases of the circulatory system
Cardiac arrhythmia
Supraventricular rhythm disturbance
BC80 Supraventricular bradyarrhythmia
H02674 Atrial standstill
Pathway-based classification of diseases [BR:br08402]
Endocrine system
nt06325 Hormone/cytokine signaling
H02674 Atrial standstill
Disertori M, Quintarelli S, Grasso M, Pilotto A, Narula N, Favalli V, Canclini C, Diegoli M, Mazzola S, Marini M, Del Greco M, Bonmassari R, Mase M, Ravelli F, Specchia C, Arbustini E
Title
Autosomal recessive atrial dilated cardiomyopathy with standstill evolution associated with mutation of Natriuretic Peptide Precursor A.
