+H Disease
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Human Diseases in ICD-11 Classification
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A01 Certain infectious or parasitic diseases
B Gastroenteritis or colitis of infectious origin
C Bacterial intestinal infections
D 1A00 Cholera
E H00110 Cholera
D 1A01 Intestinal infection due to other Vibrio
E H00307 Vibrio parahaemolyticus infection
E H00308 Vibrio vulnificus infection
D 1A02 Intestinal infections due to Shigella
E H00299 Shigellosis
D 1A03 Intestinal infections due to Escherichia coli
E H00278 Enteropathogenic Escherichia coli (EPEC) infection
E H00280 Enterotoxigenic Escherichia coli (ETEC) infection
E H01311 Enteroinvasive Escherichia coli (EIEC) infection
E H00277 Enterohemorrhagic Escherichia coli (EHEC) infection
E H01312 Enteroaggregative Escherichia coli (EAEC) infection
D 1A04 Intestinal infections due to Clostridioides difficile
E H00338 Pseudomembranous colitis
D 1A05 Intestinal infections due to Yersinia enterocolitica
E H00298 Yersiniosis
D 1A06 Gastroenteritis due to Campylobacter
E H00321 Campylobacter infection
D 1A07 Typhoid fever
E H00111 Typhoid fever
D 1A08 Paratyphoid fever
E H00112 Paratyphoid fever
D 1A09 Infections due to other Salmonella
E H00113 Salmonellosis
D 1A0Y Other specified bacterial intestinal infections
E H01454 Colonic spirochetosis
D 1A0Z Bacterial intestinal infections, unspecified
C Bacterial foodborne intoxications
D 1A10 Foodborne staphylococcal intoxication
E H01175 Staphylococcal infection
D 1A11 Botulism
E H00339 Botulism
D 1A12 Foodborne Clostridium perfringens intoxication
E H00335 Foodborne Clostridium perfringens intoxication
D 1A13 Foodborne Bacillus cereus intoxication
E H00329 Foodborne Bacillus cereus intoxication
D 1A1Y Other specified bacterial foodborne intoxications
E H00300 Enterobacter infection
D 1A1Z Bacterial foodborne intoxications, unspecified
C Viral intestinal infections
D 1A20 Enteritis due to Adenovirus
D 1A21 Gastroenteritis due to Astrovirus
D 1A22 Gastroenteritis due to Rotavirus
E H00975 Rotaviral enteritis
D 1A23 Enteritis due to Norovirus
E H01323 Enteritis due to Norovirus
D 1A24 Intestinal infections due to Cytomegalovirus
D 1A2Y Other specified viral intestinal infections
D 1A2Z Viral intestinal infections, unspecified
E H01430 Viral gastroenteritis
C Protozoal intestinal infections
D 1A30 Infections due to Balantidium coli
E H01087 Balantidiasis
D 1A31 Giardiasis
E H00362 Giardiasis
D 1A32 Cryptosporidiosis
E H00356 Cryptosporidiosis
D 1A33 Cystoisosporiasis
E H02372 Cystoisosporiasis
D 1A34 Sarcocystosis
E H02373 Sarcocystosis
D 1A35 Blastocystosis
E H02374 Blastocystosis
D 1A36 Amoebiasis
E H00360 Amoebiasis
D 1A3Y Other specified protozoal intestinal infections
E H01089 Dientamoebiasis
D 1A3Z Protozoal intestinal infections, unspecified
C 1A40 Gastroenteritis or colitis without specification of infectious agent
B Predominantly sexually transmitted infections
C Syphilis
D 1A60 Congenital syphilis
E H00354 Syphilis
D 1A61 Early syphilis
E H00354 Syphilis
D 1A62 Late syphilis
E H00354 Syphilis
D 1A63 Latent syphilis, unspecified as early or late
D 1A6Z Syphilis, unspecified
C Gonococcal infection
D 1A70 Gonococcal genitourinary infection
E H00315 Gonococcal infection
D 1A71 Gonococcal pelviperitonitis
E H00315 Gonococcal infection
D 1A72 Gonococcal infection of other sites
E H00315 Gonococcal infection
D 1A73 Disseminated gonococcal infection
D 1A7Z Gonococcal infection, unspecified
C Sexually transmissible infections due to chlamydia
D 1A80 Chlamydial lymphogranuloma
E H00348 Lymphogranuloma venereum
D 1A81 Non-ulcerative sexually transmitted chlamydial infection
E H00347 Chlamydia infection
D 1A8Y Other specified sexually transmissible infections due to chlamydia
D 1A8Z Sexually transmissible infections due to chlamydia, unspecified
C 1A90 Chancroid
D H00305 Chancroid
C 1A91 Granuloma inguinale
D H01415 Donovanosis
C 1A92 Trichomoniasis
D H00812 Trichomoniasis
C 1A93 Sexually transmissible infestations
C 1A94 Anogenital herpes simplex infection
D H00365 Herpes simplex virus infection
C 1A95 Anogenital warts
D H01418 Condyloma acuminatum
C 1A9Y Other specified predominantly sexually transmitted infections
D H00388 Non-chlamydial non-gonococcal urethritis
C 1A9Z Predominantly sexually transmitted infections, unspecified
B Mycobacterial diseases
C Tuberculosis
D 1B10 Tuberculosis of the respiratory system
E H00342 Tuberculosis
D 1B11 Tuberculosis of the nervous system
E H00342 Tuberculosis
D 1B12 Tuberculosis of other systems and organs
E H00342 Tuberculosis
D 1B13 Miliary tuberculosis
D 1B14 Latent tuberculosis
D 1B1Y Other specified tuberculosis
D 1B1Z Tuberculosis, unspecified
C 1B20 Leprosy
D H00344 Leprosy
D H01473 Erythema nodosum leprosum
C 1B21 Infections due to non-tuberculous mycobacteria
D H01458 Nontuberculous mycobacterial infection
D H01462 Rapidly growing mycobacteria infection
D H02029 Mycobacterium avium complex (MAC) pulmonary disease
D H01042 Buruli ulcer
C 1B2Y Other specified mycobacterial diseases
C 1B2Z Mycobacterial diseases, unspecified
D H01021 Rhodococcus equi infection
D H01049 Gordonia bronchialis infection
D H01050 Tsukamurella infection
B Certain staphylococcal or streptococcal diseases
C Acute rheumatic fever
D 1B40 Acute rheumatic fever without mention of heart involvement
D 1B41 Acute rheumatic fever with heart involvement
D 1B42 Rheumatic chorea
E H01924 Sydenham chorea
C 1B50 Scarlet fever
D H01515 Scarlet fever
C 1B51 Streptococcal pharyngitis
D H00333 Streptococcal infection
D H01424 Group A streptococcal pharyngitis
C 1B53 Meningitis due to Streptococcus
D H00333 Streptococcal infection
D H01406 Streptococcus suis infection
C 1B54 Meningitis due to Staphylococcus
C 1B5Y Other specified staphylococcal or streptococcal diseases
C 1B5Z Staphylococcal or streptococcal diseases, unspecified
B Pyogenic bacterial infections of the skin or subcutaneous tissues
C 1B70 Bacterial cellulitis, erysipelas or lymphangitis
D H01517 Erysipelas
C 1B71 Necrotising fasciitis
D H01455 Necrotizing fasciitis
C 1B72 Impetigo
C 1B73 Ecthyma
C 1B74 Superficial bacterial folliculitis
C 1B75 Deep bacterial folliculitis or pyogenic abscess of the skin
C 1B7Y Other specified pyogenic bacterial infection of skin and subcutaneous tissue
D H01407 Capnocytophaga ochracea infection
B Certain zoonotic bacterial diseases
C 1B90 Rat-bite fevers
D H01314 Rat-bite fever
C 1B91 Leptospirosis
D H00355 Leptospirosis
C 1B92 Glanders
D H00316 Glanders
C 1B93 Plague
D H00297 Plague
C 1B94 Tularaemia
D H00312 Tularemia
C 1B95 Brucellosis
D H00325 Brucellosis
C 1B96 Erysipeloid
D H01315 Erysipeloid
C 1B97 Anthrax
D H00328 Anthrax
C 1B98 Cat-scratch disease
D H00326 Bartonellosis
C 1B99 Pasteurellosis
D H00306 Pasteurellosis
C 1B9A Extraintestinal yersiniosis
D H00298 Yersiniosis
C 1B9Z Unspecified zoonotic bacterial disease
B Other bacterial diseases
C 1C10 Actinomycosis
D H01325 Actinomycosis
C 1C11 Bartonellosis
D H00326 Bartonellosis
D H00327 Trench fever
C 1C12 Whooping cough
D H00319 Pertussis
C 1C13 Tetanus
D H00337 Tetanus
C 1C14 Obstetrical tetanus
C 1C15 Tetanus neonatorum
C 1C16 Gas gangrene
D H00336 Gas gangrene
C 1C17 Diphtheria
D H00343 Diphtheria
D H01051 Corynebacterium ulcerans infection
C 1C18 Brazilian purpuric fever
D H01330 Brazilian purpuric fever
C 1C19 Legionellosis
D H00311 Legionellosis
C 1C1A Listeriosis
D H00332 Listeriosis
C 1C1B Nocardiosis
D H00345 Nocardiosis
C 1C1C Meningococcal disease
D H00314 Meningococcal infection
C 1C1D Yaws
D H01318 Yaws
C 1C1E Pinta
D H01530 Pinta
C 1C1F Endemic non-venereal syphilis
D H01531 Bejel
C 1C1G Lyme borreliosis
D H00353 Lyme borreliosis
C 1C1H Necrotising ulcerative gingivitis
D H01440 Acute necrotizing ulcerative gingivitis
C 1C1J Relapsing fever
D H00427 Relapsing fever
C Other diseases due to chlamydiae
D 1C20 Chlamydial conjunctivitis
D 1C21 Chlamydial peritonitis
D 1C22 Infections due to Chlamydia psittaci
E H00350 Psittacosis
D 1C23 Trachoma
E H00349 Trachoma
D 1C2Y Other specified diseases due to chlamydiae
D 1C2Z Diseases due to chlamydiae, unspecified
C Rickettsioses
D 1C30 Typhus fever
E H00322 Epidemic typhus
E H00324 Scrub typhus
D 1C31 Spotted fever
E H00323 Spotted fever
D 1C32 Rickettsialpox
E H02379 Rickettsialpox
D 1C33 Q fever
E H00310 Q fever
D 1C3Y Other specified rickettsioses
E H01140 Sennetsu neorickettsiosis
D 1C3Z Rickettsioses, unspecified
C 1C40 Campylobacteriosis
D H00321 Campylobacter infection
C 1C41 Bacterial infection of unspecified site
D H00302 Citrobacter infection
D H00303 Serratia infection
D H01441 Pseudomonas aeruginosa infection
C 1C42 Melioidosis
D H00317 Melioidosis
C 1C43 Actinomycetoma
D H01451 Actinomycetoma
C 1C44 Non-pyogenic bacterial infections of the skin
C 1C45 Toxic shock syndrome
D H01426 Invasive streptococcal disease
C 1C4Y Other specified bacterial diseases
D H01335 Photorhabdus asymbiotica infection
D H01343 Pantoea ananatis infection
D H01446 Propionibacterium acnes infection
C 1C4Z Unspecified bacterial disease
B Human immunodeficiency virus disease
C 1C60 Human immunodeficiency virus disease associated with tuberculosis
C 1C61 Human immunodeficiency virus disease associated with malaria
C 1C62 Human immunodeficiency virus disease without mention of tuberculosis or malaria
D H01563 HIV infection
B Viral infections of the central nervous system
C 1C80 Viral encephalitis not elsewhere classified
D H02511 Jamestown Canyon encephalitis
D H02512 Cache Valley virus infection
D H02536 Infection-induced acute encephalopathy
C 1C81 Acute poliomyelitis
D H00376 Acute poliomyelitis
C 1C82 Rabies
D H00377 Rabies
D H00378 Lyssavirus infection
C 1C83 Western equine encephalitis
D H01534 Western equine encephalitis
C 1C84 Eastern equine encephalitis
D H01535 Eastern equine encephalitis
C 1C85 Japanese encephalitis
D H01533 Japanese encephalitis
C 1C86 St Louis encephalitis
D H02166 Saint Louis encephalitis
C 1C87 Rocio viral encephalitis
D H02171 Rocio viral encephalitis
C 1C88 Murray Valley encephalitis
D H01536 Murray Valley encephalitis
C 1C89 Far Eastern tick-borne encephalitis
D H00380 Tick-borne viral encephalitis
C 1C8A Central European tick-borne encephalitis
D H00380 Tick-borne viral encephalitis
C 1C8B California encephalitis
C 1C8C Venezuelan equine encephalitis
D H01547 Venezuelan equine encephalitis
C 1C8D La Crosse encephalitis
D H01537 La Crosse encephalitis
C 1C8E Viral meningitis not elsewhere classified
D H00393 Enterovirus infection
C 1C8F Lymphocytic choriomeningitis
D H01324 Lymphocytic choriomeningitis
C 1C8Y Other specified viral infections of the central nervous system
C 1C8Z Viral infections of the central nervous system, unspecified
D H00379 Mosquito-borne viral encephalitis
B Non-viral and unspecified infections of the central nervous system
C 1D00 Infectious encephalitis not elsewhere classified
D H01417 Acute encephalitis
C 1D01 Infectious meningitis not elsewhere classified
D H00304 Haemophilus influenzae infection
D H01313 Escherichia coli meningitis
D H01429 Aseptic meningitis
C 1D02 Infectious myelitis not elsewhere classified
C 1D03 Infectious abscess of the central nervous system
C 1D04 Infectious granulomas of the central nervous system
C 1D05 Infectious cysts of the central nervous system
C 1D0Y Other specified non-viral and unspecified infections of the central nervous system
C 1D0Z Non-viral and unspecified infections of the central nervous system, unspecified
B Dengue
C 1D20 Dengue without warning signs
D H00381 Dengue
C 1D21 Dengue with warning signs
D H00381 Dengue
C 1D22 Severe dengue
D H00381 Dengue
C 1D2Z Dengue fever, unspecified
D H00381 Dengue
B Certain arthropod-borne viral fevers
C 1D40 Chikungunya virus disease
D H01540 Chikungunya fever
C 1D41 Colorado tick fever
D H02165 Colorado tick fever
C 1D42 O'nyong-nyong fever
D H01545 O'nyong-nyong fever
C 1D43 Oropouche virus disease
D H02163 Oropouche fever
C 1D44 Rift Valley fever
D H01549 Rift Valley fever
C 1D45 Sandfly fever
D H02164 Sandfly fever
C 1D46 West Nile virus infection
D H01548 West Nile fever
C 1D47 Yellow fever
D H00384 Yellow fever
C 1D48 Zika virus disease
D H01553 Zika fever
C 1D49 Crimean-Congo haemorrhagic fever
D H00284 Crimean-Congo hemorrhagic fever
C 1D4A Omsk haemorrhagic fever
D H00416 Omsk hemorrhagic fever
C 1D4B Kyasanur Forest disease
D H01322 Kyasanur Forest disease
C 1D4C Alkhurma haemorrhagic fever
D H01560 Alkhumra hemorrhagic fever
C 1D4D Ross River disease
D H00397 Ross River fever
C 1D4E Severe fever with thrombocytopenia syndrome
D H01416 Severe fever with thrombocytopenia syndrome
C 1D4Y Other specified arthropod-borne viral fevers
D H00385 South American hemorrhagic fever
D H01546 Mayaro fever
D H01550 Bunyamwera fever
D H02509 Vesicular stomatitis fever
C 1D4Z Arthropod-borne viral fever, virus unspecified
D H00382 Mosquito-borne viral fever
D H00383 Arthropod-borne viral fever
B Certain zoonotic viral diseases
C 1D60 Filovirus disease
D H00283 Ebola disease
D H00405 Marburg disease
C 1D61 Arenavirus disease
D H02173 Arenaviral hemorrhagic fever
D H01541 Argentine hemorrhagic fever
D H01542 Bolivian hemorrhagic fever
D H00386 Lassa fever
D H01543 Venezuelan hemorrhagic fever
D H01544 Brazilian hemorrhagic fever
C 1D62 Hantavirus disease
D H00389 Hemorrhagic fever with renal syndrome
D H00390 Hantavirus pulmonary syndrome
C 1D63 Henipavirus encephalitis
D H00391 Henipavirus infection
D H01538 Hendra virus infection
D H01539 Nipah virus infection
C 1D64 Middle East respiratory syndrome
D H01419 Middle East respiratory syndrome
C 1D65 Severe acute respiratory syndrome
D H00402 Severe acute respiratory syndrome
C 1D6Y Other specified zoonotic viral diseases
C 1D6Z Zoonotic viral disease, virus unspecified
B Certain other viral diseases
C 1D80 Mumps
D H00396 Mumps
C 1D81 Infectious mononucleosis
D H00367 Infectious mononucleosis
C 1D82 Cytomegaloviral disease
D H00368 Cytomegalovirus infection
C 1D83 Epidemic myalgia
D H00393 Enterovirus infection
D H02413 Epidemic myalgia
C 1D84 Viral conjunctivitis
D H01320 Epidemic keratoconjunctivitis
D H00393 Enterovirus infection
D H01421 Acute hemorrhagic conjunctivitis
D H01420 Pharyngoconjunctival fever
C 1D85 Viral carditis
C 1D86 Viral haemorrhagic fever, not elsewhere classified
C Viral infection of unspecified site
D 1D90 Adenovirus infection of unspecified site
E H00371 Adenovirus infection
D 1D91 Enterovirus infection of unspecified site
E H00393 Enterovirus infection
D 1D92 Coronavirus infection, unspecified site
D 1D93 Parvovirus infection of unspecified site
D 1D9Y Other viral infections of unspecified site
D 1D9Z Unspecified viral infection of unspecified site
C 1E1Y Other specified viral diseases
C 1E1Z Unspecified viral disease
B Influenza
C 1E30 Influenza due to identified seasonal influenza virus
D H00398 Influenza
C 1E31 Influenza due to identified zoonotic or pandemic influenza virus
D H00399 Avian influenza
C 1E32 Influenza, virus not identified
B Viral hepatitis
C 1E50 Acute viral hepatitis
D H02162 Viral hepatitis
D H00411 Hepatitis A
D H00412 Hepatitis B
D H00413 Hepatitis C
D H00414 Hepatitis D
D H00415 Hepatitis E
C 1E51 Chronic viral hepatitis
D H02162 Viral hepatitis
D H00412 Hepatitis B
D H00413 Hepatitis C
D H00414 Hepatitis D
D H00415 Hepatitis E
C 1E5Z Viral hepatitis, unspecified
B Viral infections characterised by skin or mucous membrane lesions
C Infections due to poxvirus
D 1E70 Smallpox
E H00372 Smallpox
D 1E71 Monkeypox
E H00373 Mpox (Monkeypox)
D 1E72 Cowpox
E H02351 Cowpox
D 1E73 Vaccinia
E H02352 Vaccinia
D 1E74 Buffalopox
D 1E75 Orf
E H02354 Orf
D 1E76 Molluscum contagiosum
E H01052 Molluscum contagiosum
D 1E7Y Other specified infections due to poxvirus
D 1E7Z Infections due to poxvirus, unspecified
C Human papillomavirus infection of skin or mucous membrane
D 1E80 Common warts
D 1E81 Plane warts
D 1E82 Warts of lips or oral cavity
D 1E83 Wart virus proliferation in immune-deficient states
E H00842 Epidermodysplasia verruciformis
D 1E8Z Viral warts, not elsewhere classified
E H00374 Viral wart
C Varicella zoster virus infections
D 1E90 Varicella
E H00366 Varicella
D 1E91 Zoster
E H00366 Varicella
E H01624 Postherpetic neuralgia
C 1F00 Herpes simplex infections
D H00365 Herpes simplex virus infection
D H00387 B virus infection
C 1F01 Roseola infantum
D H00369 Exanthema subitum
C 1F02 Rubella
D H00395 Rubella
C 1F03 Measles
D H00394 Measles
C 1F04 Erythema infectiosum
D H00404 Erythema infectiosum
C 1F05 Picornavirus infections presenting in the skin or mucous membranes
D H00393 Enterovirus infection
D H01327 Herpangina
D H01326 Hand, foot and mouth disease
C 1F0Y Other specified viral infections characterised by skin or mucous membrane lesions
C 1F0Z Viral infections characterised by skin or mucous membrane lesions, unspecified
B Mycoses
C 1F20 Aspergillosis
D H01328 Aspergillosis
C 1F21 Basidiobolomycosis
D H01503 Zygomycosis
D H02032 Entomophthoramycosis
C 1F22 Blastomycosis
D H01501 Blastomycosis
C 1F23 Candidosis
D H00363 Candidiasis
D H01109 Chronic mucocutaneous candidiasis
C 1F24 Chromoblastomycosis
D H01520 Chromomycosis
C 1F25 Coccidioidomycosis
D H01319 Coccidioidomycosis
C 1F26 Conidiobolomycosis
D H01503 Zygomycosis
D H02032 Entomophthoramycosis
C 1F27 Cryptococcosis
D H00364 Cryptococcosis
C 1F28 Dermatophytosis
D H01316 Dermatophytosis
C 1F29 Eumycetoma
D H02385 Eumycetoma
C 1F2A Histoplasmosis
D H01062 Histoplasmosis
C 1F2B Lobomycosis
D H01518 Lobomycosis
C 1F2C Mucormycosis
D H01503 Zygomycosis
D H02033 Mucormycosis
C 1F2D Non-dermatophyte superficial dermatomycoses
D H01334 Tinea versicolor
D H02428 Trichosporonosis
C 1F2E Paracoccidioidomycosis
D H01329 Paracoccidioidomycosis
C 1F2F Phaeohyphomycosis
D H02386 Phaeohyphomycosis
C 1F2G Pneumocystosis
D H01521 Pneumocystis pneumonia
C 1F2H Scedosporiosis
D H02392 Scedosporiosis
C 1F2J Sporotrichosis
D H01499 Sporotrichosis
C 1F2K Talaromycosis
D H02393 Talaromycosis
C 1F2L Emmonsiosis
C 1F2Y Other specified mycoses
C 1F2Z Mycoses, unspecified
B Parasitic diseases
C Malaria
D 1F40 Malaria due to Plasmodium falciparum
E H00361 Malaria
D 1F41 Malaria due to Plasmodium vivax
E H00361 Malaria
D 1F42 Malaria due to Plasmodium malariae
E H00361 Malaria
D 1F43 Malaria due to Plasmodium ovale
E H00361 Malaria
D 1F44 Other parasitologically confirmed malaria
D 1F45 Malaria without parasitological confirmation
D 1F4Z Malaria, unspecified
C Nonintestinal protozoal diseases
D 1F50 Acanthamoebiasis
E H02401 Acanthamoebiasis
D 1F51 African trypanosomiasis
E H00357 African trypanosomiasis
D 1F52 Babesiosis
E H01060 Babesiosis
D 1F53 Chagas disease
E H00358 Chagas disease
D 1F54 Leishmaniasis
E H00359 Leishmaniasis
D 1F55 Naegleriasis
E H02399 Primary amoebic meningoencephalitis (PAM)
D 1F56 Rhinosporidiosis
E H02400 Rhinosporidiosis
D 1F57 Toxoplasmosis
E H00435 Toxoplasmosis
D 1F58 Microsporidiosis
E H01336 Encephalitozoon infection
D 1F5Z Unspecified protozoal disease
C Helminthiases
D Diseases due to nematodes
E 1F60 Angiostrongyliasis
F H02403 Angiostrongyliasis
E 1F61 Anisakiasis
F H01058 Anisakiasis
E 1F62 Ascariasis
F H01090 Ascariasis
E 1F63 Capillariasis
F H02404 Capillariasis
E 1F64 Dracunculiasis
F H01044 Dracunculiasis
E 1F65 Enterobiasis
F H01091 Enterobiasis
E 1F66 Filariasis
F H02028 Filariasis
F H01104 Loiasis
F H01061 Mansonelliasis
F H01086 Lymphatic filariasis
E 1F67 Gnathostomiasis
F H01057 Gnathostomiasis
E 1F68 Hookworm diseases
F H01092 Hookworm disease
E 1F69 Oesophagostomiasis
F H02405 Oesophagostomiasis
E 1F6A Onchocerciasis
F H01043 Onchocerciasis
E 1F6B Strongyloidiasis
F H01100 Strongyloidiasis
E 1F6C Syngamosis
F H02406 Syngamosis
E 1F6D Toxocariasis
F H01056 Toxocariasis
E 1F6E Trichinosis
F H01099 Trichinosis
E 1F6F Trichostrongyliasis
F H02407 Trichostrongyliasis
E 1F6G Trichuriasis
F H01046 Trichuriasis
E 1F6H Uncinariosis
E 1F6Y Other specified diseases due to nematodes
F H01137 Baylisascariasis
E 1F6Z Diseases due to nematodes, unspecified
D Diseases due to cestodes
E 1F70 Cysticercosis
F H01047 Cysticercosis
E 1F71 Diphyllobothriasis
F H01085 Diphyllobothriasis
E 1F72 Dipylidiasis
F H02408 Dipylidiasis
E 1F73 Echinococcosis
F H01153 Human echinococcosis
E 1F74 Hymenolepiasis
F H01138 Hymenolepiasis
E 1F75 Sparganosis
F H01014 Sparganosis
E 1F76 Taeniasis
F H01152 Taenia saginata infection
E 1F7Y Other specified diseases due to cestodes
E 1F7Z Diseases due to cestodes, unspecified
D Diseases due to trematodes
E 1F80 Clonorchiasis
F H01610 Clonorchiasis
E 1F81 Dicrocoeliasis
F H02409 Dicrocoeliasis
E 1F82 Fascioliasis
F H01048 Liver fluke disease
E 1F83 Fasciolopsiasis
E 1F84 Opisthorchiasis
F H01628 Opisthorchiasis
E 1F85 Paragonimiasis
F H01093 Paragonimiasis
E 1F86 Schistosomiasis
F H01045 Schistosomiasis
E 1F8Y Other specified diseases due to trematodes
F H01617 Foodborne trematodiasis
E 1F8Z Diseases due to trematodes, unspecified
D 1F90 Other and unspecified infestation by parasitic worms
D 1F91 Diphyllobothriasis and sparganosis
D 1F9Z Helminthiases, unspecified
E H01055 Giant kidney worm infection
C Infestations by ectoparasites
D 1G00 Pediculosis
E H01054 Pediculosis
D 1G01 Myiasis
E H01178 Myiasis
D 1G02 External hirudiniasis
D 1G03 Pthiriasis
E H02423 Phthiriasis
D 1G04 Scabies
E H01519 Scabies
D 1G05 Tungiasis
E H01179 Tungiasis
D 1G06 Cimicosis
E H02416 Cimicosis
D 1G07 Infestation by mites
D 1G0Y Infestation by other specified ectoparasite
D 1G0Z Infestation by unknown or unspecified ectoparasite
E H01098 Pentastomiasis
C 1G2Y Other specified parasitic diseases
C 1G2Z Unspecified parasitic diseases
B Sepsis
C 1G40 Sepsis without septic shock
C 1G41 Sepsis with septic shock
B 1G60 Certain other disorders of infectious origin
B Sequelae of infectious diseases
C 1G80 Sequelae of tuberculosis
C 1G81 Sequelae of trachoma
C 1G82 Sequelae of leprosy
C 1G83 Sequelae of poliomyelitis
C 1G84 Sequelae of viral encephalitis
C 1G85 Sequelae of diphtheria
C 1G8Y Sequelae of other specified infectious diseases
B 1H0Z Infection, unspecified
#
A02 Neoplasms
B Neoplasms of brain or central nervous system
C 2A00 Primary neoplasms of brain
D H00042 Glioma
D H01692 Subependymal giant cell astrocytoma
D H01667 Medulloblastoma
D H01007 Choroid plexus papilloma
C 2A01 Primary neoplasms of meninges
D H01556 Meningioma
C 2A02 Primary neoplasm of spinal cord, cranial nerves or remaining parts of central nervous system
D H00043 Neuroblastoma
C 2A0Z Other and unspecified neoplasms of brain or central nervous system
B Neoplasms of haematopoietic or lymphoid tissues
C Myeloproliferative neoplasms
D 2A20 Non mast cell myeloproliferative neoplasms
E H00004 Chronic myeloid leukemia
E H01605 Myelofibrosis
E H01590 Chronic eosinophilic leukemia
E H01599 Hypereosinophilic syndrome
E H00012 Polycythemia vera
D 2A21 Mastocytosis
E H01511 Mast-cell leukemia
D 2A22 Other and unspecified myeloproliferative neoplasms
C Myelodysplastic syndromes
D 2A30 Refractory anaemia
D 2A31 Refractory neutropaenia
D 2A32 Refractory thrombocytopenia
D 2A33 Refractory anaemia with ring sideroblasts
D 2A34 Refractory cytopenia with multi-lineage dysplasia
D 2A35 Refractory anaemia with excess of blasts
D 2A36 Myelodysplastic syndrome with isolated del(5q)
E H01481 Myelodysplastic syndrome
E H01484 5q- syndrome
D 2A37 Myelodysplastic syndrome, unclassifiable
E H01481 Myelodysplastic syndrome
D 2A38 Refractory cytopenia of childhood
D 2A3Y Other specified myelodysplastic syndromes
D 2A3Z Myelodysplastic syndromes, unspecified
E H01481 Myelodysplastic syndrome
C Myelodysplastic and myeloproliferative neoplasms
D 2A40 Chronic myelomonocytic leukaemia
E H02411 Chronic myelomonocytic leukemia
D 2A41 Atypical chronic myeloid leukaemia, BCR-ABL1negative
E H02412 Atypical chronic myeloid leukemia
D 2A42 Juvenile myelomonocytic leukaemia
E H02541 Juvenile myelomonocytic leukemia
D 2A43 Refractory anaemia with ring sideroblasts associated with marked thrombocytosis
D 2A44 Myeloproliferative and myelodysplastic disease, unclassifiable
D 2A4Y Other specified myelodysplastic and myeloproliferative neoplasms
D 2A4Z Myelodysplastic and myeloproliferative neoplasms, unspecified
E H02410 Myelodysplastic/myeloproliferative neoplasms
C Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1
D 2A50 Myeloid/lymphoid neoplasm associated with PDGFRA rearrangement
D 2A51 Myeloid neoplasm associated with PDGFRB rearrangement
D 2A52 Myeloid or lymphoid neoplasms with FGFR1 abnormalities
D 2A5Z Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1, unspecified
C 2A60 Acute myeloid leukaemias and related precursor neoplasms
D H00003 Acute myeloid leukemia
D H02542 Acute promyelocytic leukemia
C 2A61 Acute leukaemias of ambiguous lineage
C Precursor lymphoid neoplasms
D 2A70 Precursor B-lymphoblastic neoplasms
E H00001 B-cell acute lymphoblastic leukemia
D 2A71 Precursor T-lymphoblastic neoplasms
E H00002 T-cell acute lymphoblastic leukemia
D 2A7Z Precursor lymphoid neoplasms, unspecified
C Mature B-cell neoplasms
D 2A80 Follicular lymphoma
E H01613 Follicular lymphoma
D 2A81 Diffuse large B-cell lymphomas
E H02424 Primary central nervous system lymphoma
E H02434 Diffuse large B-cell lymphoma, not otherwise specified
D 2A82 Mature B-cell neoplasm with leukaemic behaviour
E H00005 Chronic lymphocytic leukemia
E H00006 Hairy cell leukemia
D 2A83 Plasma cell neoplasms
E H00010 Multiple myeloma
E H01461 Crow-Fukase syndrome
D 2A84 Heavy chain diseases or malignant immunoproliferative diseases
D 2A85 Other specified mature B-cell neoplasms or lymphoma
E H00011 Lymphoplasmacytic lymphoma
E H01464 Mantle cell lymphoma
E H00008 Burkitt lymphoma
D 2A86 B-cell lymphoma, mixed features
E H02664 Joint contracture, osteochondromas, and B-cell lymphoma
D 2A8Z Mature B-cell neoplasms, unspecified
C Mature T-cell or NK-cell neoplasms
D 2A90 Mature T-cell lymphoma, specified types, nodal or systemic
E H01892 Peripheral T cell lymphoma
E H00009 Adult T-cell leukemia
E H01601 Anaplastic large-cell lymphoma
D Mature T-cell or NK-cell lymphomas and lymphoproliferative disorders, primary cutaneous specified types
E 2B00 Subcutaneous panniculitis-like T-cell lymphoma
F H02661 Subcutaneous panniculitis-like T-cell lymphoma
E 2B01 Mycosis fungoides
F H01463 Mycosis fungoides
E 2B02 Sézary syndrome
E 2B03 Primary cutaneous CD-30 positive T-cell lymphoproliferative disorders
E 2B0Y Other specified primary cutaneous mature T-cell or NK-cell lymphomas and lymphoproliferative disorders
E 2B0Z Primary cutaneous T-cell lymphoma of undetermined or unspecified type
D 2B2Y Other specified mature T-cell or NK-cell neoplasms
D 2B2Z Mature T-cell or NK-cell neoplasms, unspecified
C 2B30 Hodgkin lymphoma
D H00007 Hodgkin lymphoma
C 2B31 Histiocytic or dendritic cell neoplasms
D H01512 Langerhans cell histiocytosis
D H02425 Erdheim-Chester disease
C 2B32 Immunodeficiency-associated lymphoproliferative disorders
C 2B33 Malignant haematopoietic neoplasms without further specification
D H02418 Non-Hodgkin lymphoma
C 2B3Z Neoplasms of haematopoietic or lymphoid tissues, unspecified
B Malignant neoplasms, except primary neoplasms of lymphoid, haematopoietic, central nervous system or related tissues
C Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues
D Malignant mesenchymal neoplasms
E 2B50 Chondrosarcoma, primary site
F H00053 Extraskeletal myxoid chondrosarcoma
E 2B51 Osteosarcoma, primary site
F H00036 Osteosarcoma
F H01470 Giant cell tumor of bone
F H00881 Li-Fraumeni syndrome
E 2B52 Ewing sarcoma, primary site
F H00035 Ewing sarcoma
E 2B53 Fibroblastic or myofibroblastic tumour, primary site
E 2B54 Unclassified pleomorphic sarcoma, primary site
E 2B55 Rhabdomyosarcoma, primary site
F H00037 Rhabdomyosarcoma
F H02427 Soft tissue sarcomas
E 2B56 Angiosarcoma, primary site
F H01666 Angiosarcoma
F H01557 Hepatic angiosarcoma
E 2B57 Kaposi sarcoma, primary site
F H00041 Kaposi sarcoma
E 2B58 Leiomyosarcoma, primary site
E 2B59 Liposarcoma, primary site
F H00049 Myxoid liposarcoma
E 2B5A Synovial sarcoma, primary site
F H00050 Synovial sarcoma
F H02427 Soft tissue sarcomas
E 2B5B Gastrointestinal stromal tumour, primary site
F H01591 Gastrotintestinal stromal tumor
E 2B5C Endometrial stromal sarcoma, primary site
E 2B5D Malignant mixed epithelial mesenchymal tumour, primary site
E 2B5E Malignant nerve sheath tumour of peripheral nerves or autonomic nervous system, primary site
E 2B5F Sarcoma, not elsewhere classified, primary site
E 2B5G Myosarcoma of uterus, part not specified
E 2B5H Well differentiated lipomatous tumour, primary site
E 2B5J Malignant miscellaneous tumours of bone or articular cartilage of other or unspecified sites
E 2B5K Unspecified malignant soft tissue tumours or sarcomas of bone or articular cartilage of other or unspecified sites
F H00051 Alveolar soft part sarcoma
F H00052 Clear cell sarcoma of soft tissue
F H01985 Desmoplastic small round cell tumor
E 2B5Y Other specified malignant mesenchymal neoplasms
E 2B5Z Malignant mesenchymal neoplasm of unspecified type
D Malignant neoplasms of lip, oral cavity or pharynx
E 2B60 Malignant neoplasms of lip
F H00016 Oral cancer
E 2B61 Malignant neoplasms of base of tongue
F H00016 Oral cancer
E 2B62 Malignant neoplasms of other or unspecified parts of tongue
F H00016 Oral cancer
E 2B63 Malignant neoplasms of gum
F H00016 Oral cancer
E 2B64 Malignant neoplasms of floor of mouth
F H00016 Oral cancer
E 2B65 Malignant neoplasms of palate
F H00016 Oral cancer
E 2B66 Malignant neoplasms of other or unspecified parts of mouth
F H00016 Oral cancer
E 2B67 Malignant neoplasms of parotid gland
E 2B68 Malignant neoplasms of submandibular or sublingual glands
F H01508 Salivary gland cancer
F H02420 Head and neck cancer
E 2B69 Malignant neoplasms of tonsil
F H01509 Tonsillar cancer
F H02420 Head and neck cancer
E 2B6A Malignant neoplasms of oropharynx
F H01559 Oropharyngeal cancer
F H02420 Head and neck cancer
E 2B6B Malignant neoplasms of nasopharynx
F H00054 Nasopharyngeal cancer
E 2B6C Malignant neoplasms of piriform sinus
E 2B6D Malignant neoplasms of hypopharynx
E 2B6E Malignant neoplasms of other or ill-defined sites in the lip, oral cavity or pharynx
F H02420 Head and neck cancer
E 2B6Y Other specified malignant neoplasms of lip, oral cavity or pharynx
E 2B6Z Malignant neoplasms of lip, oral cavity or pharynx, unspecified
D Malignant neoplasms of digestive organs
E 2B70 Malignant neoplasms of oesophagus
F H00017 Esophageal cancer
E 2B71 Malignant neoplasms of oesophagogastric junction
E 2B72 Malignant neoplasms of stomach
F H00018 Gastric cancer
E Malignant neoplasms of intestine
F 2B80 Malignant neoplasms of small intestine
G H00034 Carcinoid
F 2B81 Malignant neoplasms of appendix
F Malignant neoplasms of large intestine
G 2B90 Malignant neoplasms of colon
H H00020 Colorectal cancer
H H02565 Hereditary nonpolyposis colorectal cancer
H H02568 Polymerase proofreading-associated polyposis
G 2B91 Malignant neoplasms of rectosigmoid junction
H H00020 Colorectal cancer
G 2B92 Malignant neoplasms of rectum
H H00020 Colorectal cancer
G 2B93 Malignant neoplasms of large intestine, site unspecified
G 2B9Y Other specified malignant neoplasms of large intestine
H H00876 Mismatch repair deficiency
F 2C00 Malignant neoplasms of anus or anal canal
G H00044 Cancer of the anal canal
F 2C0Y Other specified malignant neoplasms of intestine
F 2C0Z Malignant neoplasms of intestine, unspecified
E 2C10 Malignant neoplasm of pancreas
F H00019 Pancreatic cancer
F H00045 Pancreatic neuroendocrine tumor
E 2C11 Malignant neoplasms of other or ill-defined digestive organs
E 2C12 Malignant neoplasms of liver or intrahepatic bile ducts
F H00048 Hepatocellular carcinoma
F H02302 Hepatoblastoma
F H00046 Cholangiocarcinoma
E 2C13 Malignant neoplasms of gallbladder
F H00047 Gallbladder cancer
E 2C14 Malignant neoplasms of proximal biliary tract, cystic duct
E 2C15 Malignant neoplasms of biliary tract, distal bile duct
E 2C16 Malignant neoplasms of ampulla of Vater
E 2C17 Malignant neoplasms of other or unspecified parts of biliary tract
E 2C18 Malignant neoplasms of perihilar bile duct
E 2C1Z Malignant neoplasms of digestive organs, unspecified
D Malignant neoplasms of middle ear, respiratory or intrathoracic organs
E 2C20 Malignant neoplasms of nasal cavity
F H00043 Neuroblastoma
E 2C21 Malignant neoplasms of middle ear
E 2C22 Malignant neoplasms of accessory sinuses
E 2C23 Malignant neoplasms of larynx
F H00055 Laryngeal cancer
F H02420 Head and neck cancer
E 2C24 Malignant neoplasms of trachea
E 2C25 Malignant neoplasms of bronchus or lung
F H00014 Non-small cell lung cancer
F H00013 Small cell lung cancer
E 2C26 Malignant neoplasms of the pleura
F H00015 Malignant pleural mesothelioma
E 2C27 Malignant neoplasms of thymus
E 2C28 Malignant neoplasms of heart, mediastinum or non-mesothelioma of pleura
E 2C29 Malignant neoplasms of other or ill-defined sites in the respiratory system or intrathoracic organs
E 2C2Y Other specified malignant neoplasms of middle ear, respiratory or intrathoracic organs
E 2C2Z Malignant neoplasms of middle ear, respiratory or intrathoracic organs, unspecified
D Malignant neoplasms of skin
E 2C30 Melanoma of skin
F H00038 Melanoma
E 2C31 Squamous cell carcinoma of skin
F H00040 Squamous cell carcinoma
F H02566 Muir-Torre syndrome
E 2C32 Basal cell carcinoma of skin
F H00039 Basal cell carcinoma
E 2C33 Adnexal carcinoma of skin
E 2C34 Cutaneous neuroendocrine carcinoma
F H01555 Merkel cell carcinoma
E 2C35 Cutaneous sarcoma
E 2C3Y Other specified malignant neoplasms of skin
E 2C3Z Malignant neoplasm of skin of unknown or unspecified type
D Malignant neoplasms of peripheral nerves or autonomic nervous system
E 2C40 Malignant neuroepitheliomatous neoplasms of peripheral nerves or autonomic nervous system
E 2C41 Malignant perineurioma
E 2C4Y Other specified malignant neoplasms of peripheral nerves and autonomic nervous system
E 2C4Z Malignant neoplasms of peripheral nerves or autonomic nervous system, unspecified
D Malignant neoplasms of retroperitoneum, peritoneum or omentum
E 2C50 Malignant neoplasms of retroperitoneum
E 2C51 Malignant neoplasms of peritoneum
F H01665 Primary peritoneal carcinoma
E 2C52 Malignant neoplasms of omentum
E 2C53 Malignant neoplasm involving overlapping sites of retroperitoneum, peritoneum or omentum
E 2C5Y Other specified malignant neoplasms of retroperitoneum, peritoneum or omentum
E 2C5Z Malignant neoplasms of retroperitoneum, peritoneum or omentum, unspecified
D Malignant neoplasms of breast
E 2C60 Carcinoma of breast, specialised type
E 2C61 Invasive carcinoma of breast
F H00031 Breast cancer
E 2C62 Inflammatory carcinoma of breast
E 2C63 Malignant phyllodes tumour of breast
E 2C64 Solid papillary carcinoma of breast with evidence of invasion
E 2C65 Hereditary breast and ovarian cancer syndrome
F H02531 Familial breast-ovarian cancer
E 2C6Y Other specified malignant neoplasms of breast
E 2C6Z Malignant neoplasms of breast, unspecified
D Malignant neoplasms of female genital organs
E 2C70 Malignant neoplasms of vulva
F H00029 Vulvar cancer
E 2C71 Malignant neoplasms of vagina
E 2C72 Malignant neoplasms of uterine ligament, parametrium, or uterine adnexa
E 2C73 Malignant neoplasms of ovary
F H00027 Ovarian cancer
E 2C74 Malignant neoplasms of fallopian tube
F H01554 Fallopian tube cancer
E 2C75 Malignant neoplasms of placenta
F H00028 Choriocarcinoma
E 2C76 Malignant neoplasms of corpus uteri
F H00026 Endometrial cancer
E 2C77 Malignant neoplasms of cervix uteri
F H00030 Cervical cancer
E 2C78 Malignant neoplasms of uterus, part not specified
E 2C79 Malignant neoplasm involving overlapping sites of female genital organs
E 2C7Y Other specified malignant neoplasms of female genital organs
E 2C7Z Malignant neoplasms of female genital organs, unspecified
D Malignant neoplasms of male genital organs
E 2C80 Malignant neoplasms of testis
F H00023 Testicular cancer
E 2C81 Malignant neoplasms of penis
F H00025 Penile cancer
E 2C82 Malignant neoplasms of prostate
F H00024 Prostate cancer
F H02530 Hereditary prostate cancer
E 2C83 Malignant neoplasms of scrotum
E 2C84 Malignant neoplasms of other specified male genital organs
E 2C8Z Malignant neoplasms of male genital organs, unspecified
D Malignant neoplasms of urinary tract
E 2C90 Malignant neoplasms of kidney, except renal pelvis
F H00021 Renal cell carcinoma
F H02301 Nephroblastoma
E 2C91 Malignant neoplasms of renal pelvis
E 2C92 Malignant neoplasms of ureter
E 2C93 Malignant neoplasms of urethra or paraurethral gland
E 2C94 Malignant neoplasms of bladder
F H00022 Bladder cancer
E 2C95 Malignant neoplasm involving overlapping sites of urinary organs
E 2C9Y Other specified malignant neoplasms of urinary tract
E 2C9Z Malignant neoplasms of urinary tract, unspecified
D Malignant neoplasms of eye or ocular adnexa
E 2D00 Malignant neoplasm of conjunctiva
E 2D01 Malignant neoplasm of cornea
E 2D02 Malignant neoplasm of retina
F H01513 Retinoblastoma
E 2D03 Malignant neoplasm of lacrimal apparatus
E 2D04 Malignant neoplasm of orbit
E 2D05 Malignant neoplasm of choroid
E 2D06 Malignant neoplasm of ciliary body
E 2D07 Malignant neoplasm of iris
E 2D0Y Other specified malignant neoplasms of eye and ocular adnexa
E 2D0Z Malignant neoplasms of eye or ocular adnexa, unspecified
D Malignant neoplasms of endocrine glands
E 2D10 Malignant neoplasms of thyroid gland
F H00032 Thyroid cancer
F H01592 Medullary thyroid cancer
E 2D11 Malignant neoplasms of adrenal gland
F H00033 Adrenal carcinoma
E 2D12 Malignant neoplasms of other endocrine glands or related structures
F H01510 Malignant paraganglioma
E 2D1Z Malignant neoplasms of endocrine glands, unspecified
D 2D3Y Other specified malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues
D 2D3Z Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic, central nervous system or related tissues, unspecified
C Malignant neoplasms of ill-defined or unspecified primary sites
D 2D40 Adenocarcinoma of unspecified site
D 2D41 Unspecified carcinoma of unspecified site
D 2D42 Malignant neoplasms of ill-defined sites
D 2D43 Malignant neoplasms of independent, multiple primary sites
D 2D4Y Other specified malignant neoplasms of unspecified primary sites
D 2D4Z Unspecified malignant neoplasms of unspecified sites
C Malignant neoplasm metastases
D 2D50 Malignant neoplasm metastasis in brain
D 2D51 Malignant neoplasm metastasis in meninges
D 2D52 Malignant neoplasm metastasis in spinal cord, cranial nerves or remaining parts of central nervous system
D Malignant neoplasm metastasis in lymph nodes
E 2D60 Malignant neoplasm metastasis in lymph node of a single region
F H02610 Head and neck squamous cell carcinoma
E 2D61 Malignant neoplasm metastases in lymph nodes of multiple regions
E 2D6Z Metastatic malignant neoplasm to unspecified lymph node
D Malignant neoplasm metastasis in thoracic or respiratory organs
E 2D70 Malignant neoplasm metastasis in lung
E 2D71 Malignant neoplasm metastasis in mediastinum
E 2D72 Malignant neoplasm metastasis in pleura
E 2D73 Malignant neoplasm metastasis in upper respiratory tract organs
E 2D7Y Malignant neoplasm metastasis in other specified thoracic organs
E 2D7Z Malignant neoplasm metastasis in thoracic or respiratory organs, unspecified
D Malignant neoplasm metastasis in digestive system
E 2D80 Malignant neoplasm metastasis in liver or intrahepatic bile duct
E 2D81 Malignant neoplasm metastasis in pancreas
E 2D82 Malignant neoplasm metastasis in extrahepatic bile ducts
E 2D83 Malignant neoplasm metastasis in ampulla of Vater
E 2D84 Malignant neoplasm metastasis in the small intestine
E 2D85 Malignant neoplasm metastasis in large intestine
E 2D86 Malignant neoplasm metastasis in anus
E 2D8Y Malignant neoplasm metastasis in other specified digestive system organ
E 2D8Z Malignant neoplasm metastasis in unspecified digestive system organ
D Malignant neoplasm metastasis in retroperitoneum or peritoneum
E 2D90 Malignant neoplasm metastasis in retroperitoneum
E 2D91 Malignant neoplasm metastasis in peritoneum
D Malignant neoplasm metastasis in other sites
E 2E00 Malignant neoplasm metastasis in kidney or renal pelvis
E 2E01 Malignant neoplasm metastasis in bladder
E 2E02 Malignant neoplasm metastasis in other or unspecified urinary system organs
E 2E03 Malignant neoplasm metastasis in bone or bone marrow
E 2E04 Malignant neoplasm metastasis in soft tissue
E 2E05 Malignant neoplasm metastasis in female reproductive system
E 2E06 Malignant neoplasm metastasis in male genital organs
E 2E07 Malignant neoplasm metastasis in adrenal gland
E 2E08 Metastatic malignant neoplasm involving skin
E 2E09 Malignant neoplasm metastasis in peripheral nervous system
E 2E0Y Malignant neoplasm metastasis in other specified sites
D 2E2Z Malignant neoplasm metastasis, unspecified
B In situ neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
C 2E60 Carcinoma in situ of oral cavity, oesophagus or stomach
C 2E61 Carcinoma in situ of other or unspecified digestive organs
C 2E62 Carcinoma in situ of middle ear or respiratory system
C 2E63 Melanoma in situ neoplasms
C 2E64 Carcinoma in situ of skin
C 2E65 Carcinoma in situ of breast
C 2E66 Carcinoma in situ of cervix uteri
C 2E67 Carcinoma in situ of other or unspecified genital organs
C 2E68 Carcinoma in situ of bladder
C 2E69 Carcinoma in situ of other or unspecified urinary organs
C 2E6A Carcinoma in situ of the eye or ocular adnexa
C 2E6B Carcinoma in situ of thyroid and other endocrine glands
D H01558 Parathyroid carcinoma
C 2E6Y Carcinoma in situ of other specified site
C 2E6Z Carcinoma in situ of unspecified site
B Benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
C Benign mesenchymal neoplasms
D 2E80 Benign lipomatous neoplasm
D 2E81 Benign vascular neoplasms
E H01471 Lymphangioma
E H01735 Lymphangiomatosis
E H01482 Infantile hemangioma
E H01875 Infantile hepatic hemangioma
D 2E82 Benign chondrogenic tumours
D 2E83 Benign osteogenic tumours
D 2E84 Benign fibrogenic or myofibrogenic tumour
D 2E85 Benign fibrohistiocytic tumour
D 2E86 Benign smooth muscle or skeletal muscle tumour
E H01640 Uterine leiomyoma
D 2E87 Benign gastrointestinal stromal tumour
D 2E88 Benign endometrial stromal nodule
D 2E89 Benign mesenchymal tumours of uncertain differentiation
D 2E8A Other mixed or unspecified benign mesenchymal tumours
D 2E8Y Other specified benign mesenchymal neoplasm
D 2E8Z Benign mesenchymal neoplasms, unspecified
E H00804 Multiple cutaneous and uterine leiomyomata
C Benign non-mesenchymal neoplasms
D 2E90 Benign neoplasm of lip, oral cavity or pharynx
D 2E91 Benign neoplasm of major salivary glands
D 2E92 Benign neoplasm of digestive organs
E H02538 Paraganglioma
E H01025 Familial adenomatous polyposis
E H00539 PTEN hamartoma tumor syndrome
E H01023 Juvenile polyposis syndrome
E H01024 Hereditary mixed polyposis syndrome
D Benign neoplasm of respiratory or intrathoracic organs
E 2F00 Benign neoplasm of middle ear or respiratory system
E 2F01 Benign neoplasm of intrathoracic organs
E 2F0Y Benign neoplasms of other specified respiratory and intrathoracic organs
E 2F0Z Benign neoplasms of unspecified respiratory and intrathoracic organs
D 2F10 Benign neoplasm of mesothelial tissue
D Benign cutaneous neoplasms
E 2F20 Benign cutaneous melanocytic neoplasms
E 2F21 Benign keratinocytic acanthomas
E 2F22 Benign neoplasms of epidermal appendages
F H00827 Brooke-Spiegler syndrome
F H00828 Familial cylindromatosis
F H00829 Multiple familial trichoepithelioma
F H00947 Pilomatricoma
E 2F23 Benign dermal fibrous or fibrohistiocytic neoplasms
F H01910 Infantile myofibromatosis
E 2F24 Benign cutaneous neoplasms of neural or nerve sheath origin
E 2F25 Cherry angioma
E 2F26 Lobular capillary haemangioma
E 2F2Y Other specified benign cutaneous neoplasms
E 2F2Z Benign cutaneous neoplasm of unspecified type
D 2F30 Benign neoplasm of breast
D 2F31 Benign non-mesenchymal neoplasms of uterus
D 2F32 Benign neoplasm of ovary
D 2F33 Benign neoplasm of other or unspecified female genital organs
D 2F34 Benign neoplasm of male genital organs
D 2F35 Benign neoplasm of urinary organs
E H01691 Renal angiomyolipoma
D 2F36 Benign neoplasm of eye or ocular adnexa
E H01149 Ring dermoid of cornea
D 2F37 Benign neoplasm of endocrine glands
E H01102 Pituitary adenomas
D 2F3Y Benign non-mesenchymal neoplasms of other specified site
D 2F3Z Benign non-mesenchymal neoplasms of unspecified site
C 2F5Y Other specified benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues
C 2F5Z Benign neoplasms, except of lymphoid, haematopoietic, central nervous system or related tissues, unspecified
B Neoplasms of uncertain behaviour, except of lymphoid, haematopoietic, central nervous system or related tissues
C 2F70 Neoplasms of uncertain behaviour of oral cavity or digestive organs
C 2F71 Neoplasms of uncertain behaviour of middle ear, respiratory or intrathoracic organs
C 2F72 Neoplasms of uncertain behaviour of skin
C 2F73 Neoplasms of uncertain behaviour of retroperitoneum
C 2F74 Neoplasms of uncertain behaviour of peritoneum
C 2F75 Neoplasms of uncertain behaviour of breast
C 2F76 Neoplasms of uncertain behaviour of female genital organs
C 2F77 Neoplasms of uncertain behaviour of male genital organs
C 2F78 Neoplasms of uncertain behaviour of urinary organs
C 2F79 Neoplasms of uncertain behaviour of eye or ocular adnexa
C 2F7A Neoplasms of uncertain behaviour of endocrine glands
D H00247 Multiple endocrine neoplasia syndrome
C 2F7B Neoplasms of uncertain behaviour of bone or articular cartilage
C 2F7C Neoplasms of uncertain behaviour of connective or other soft tissue
C 2F7Y Neoplasms of uncertain behaviour of other specified site
D H01134 Rhabdoid predisposition syndrome
D H02624 Tumor predisposition syndrome
C 2F7Z Neoplasms of uncertain behaviour of unspecified site
B Neoplasms of unknown behaviour, except of lymphoid, haematopoietic, central nervous system or related tissues
C 2F90 Neoplasms of unknown behaviour of oral cavity or digestive organs
C 2F91 Neoplasms of unknown behaviour of middle ear, respiratory or intrathoracic organs
C 2F92 Neoplasms of unknown behaviour of skin
C 2F93 Neoplasms of unknown behaviour of retroperitoneum
C 2F94 Neoplasms of unknown behaviour of peritoneum
C 2F95 Neoplasms of unknown behaviour of breast
C 2F96 Neoplasms of unknown behaviour of female genital organs
C 2F97 Neoplasms of unknown behaviour of male genital organs
C 2F98 Neoplasms of unknown behaviour of urinary organs
C 2F99 Neoplasms of unknown behaviour of eye or ocular adnexa
C 2F9A Neoplasms of unknown behaviour of endocrine glands
C 2F9B Neoplasms of unknown behaviour of bone or articular cartilage
C 2F9C Neoplasms of unknown behaviour of connective or other soft tissue
C 2F9Y Neoplasms of unknown behaviour of other specified site
C 2F9Z Neoplasms of unknown behaviour of unspecified site
#
A03 Diseases of the blood or blood-forming organs
B Anaemias or other erythrocyte disorders
C Nutritional or metabolic anaemias
D 3A00 Iron deficiency anaemia
E H01145 Atransferrinemia
E H01196 Hypochromic microcytic anemia
E H01278 Iron-refractory iron deficiency anemia
E H02206 Aceruloplasminemia
D 3A01 Megaloblastic anaemia due to vitamin B12 deficiency
E H01277 Vitamin B12 deficiency anaemia
E H01190 Transcobalamin II deficiency
D 3A02 Folate deficiency anaemia
E H01197 Dihydrofolate reductase deficiency
E H01262 Formiminotransferase deficiency
D 3A03 Other nutritional or metabolic anaemias
E H00198 Orotic aciduria
C Haemolytic anaemias
D Congenital haemolytic anaemia
E 3A10 Hereditary haemolytic anaemia
F H00668 Anemia due to disorders of glutathione metabolism
F H00231 Hereditary elliptocytosis
F H01125 Hereditary pyropoikilocytosis
F H02001 Familial pseudohyperkalemia
F H00230 Hereditary spherocytosis
F H00232 Hereditary stomatocytosis
F H00664 Anemia due to disorders of glycolytic enzymes
F H00674 Anemia due to disorders of nucleotide metabolism
F H00832 Core neuroacanthocytosis syndromes
F H01214 Rh-null hemolytic anemia (RHN)
F H01432 Choreoacanthocytosis
F H01434 Atypical hemolytic uremic syndrome
F H01720 Southeast Asian ovalocytosis
F H01978 Dehydrated hereditary stomatocytosis
F H01979 Overhydrated hereditary stomatocytosis
F H02002 Cryohydrocytosis
F H02658 X-linked congenital hemolytic anemia
E 3A1Y Other specified congenital haemolytic anaemia
D Acquired haemolytic anaemia
E 3A20 Acquired haemolytic anaemia, immune
F H01585 Autoimmune hemolytic anemia
E 3A21 Acquired haemolytic anaemia, non-immune
F H01053 Paroxysmal nocturnal hemoglobinuria
E 3A2Z Acquired haemolytic anaemia, unspecified
D 3A4Z Haemolytic anaemias, unspecified
C 3A50 Thalassaemias
D H00228 Thalassemia
C 3A51 Sickle cell disorders or other haemoglobinopathies
D H00229 Sickle cell disease
C Pure red cell aplasia
D 3A60 Congenital pure red cell aplasia
E H00237 Diamond-Blackfan anemia
D 3A61 Acquired pure red cell aplasia
E H01586 Acquired pure red cell aplasia
D 3A6Z Pure red cell aplasia, unspecified
C 3A70 Aplastic anaemia
D H01132 Aplastic anemia
D H00238 Fanconi anemia
D H00439 Shwachman-Diamond syndrome
D H00507 Dyskeratosis congenita
D H00788 Hoyeraal-Hreidarsson syndrome
D H00921 Revesz syndrome
D H02524 Ataxia-pancytopenia syndrome
D H02529 Bone marrow failure syndrome
D H02569 Pulmonary fibrosis and/or bone marrow failure, telomere-related
D H02608 Autoinflammatory-pancytopenia syndrome
C 3A71 Anaemia due to chronic disease
D H01642 Renal anemia
C 3A72 Sideroblastic anaemia
D H00982 Sideroblastic anemia
D H02670 Sideroblastic anemia with B-cell immunodeficiency, periodic fevers, and developmental delay
D H00898 Myopathy with lactic acidosis and sideroblastic anaemia
C 3A73 Congenital dyserythropoietic anaemia
D H00917 Congenital dyserythropoietic anemia
C Polycythaemia
D 3A80 Congenital polycythaemia
E H00236 Congenital polycythemia
D 3A81 Acquired polycythaemia
D 3A8Z Polycythaemia, unspecified
C 3A90 Anaemia due to acute disease
C 3A91 Congenital methaemoglobinaemia
D H00235 Methemoglobinemia
C 3A92 Hereditary methaemoglobinaemia
D H00235 Methemoglobinemia
C 3A93 Acquired methaemoglobinaemia
C 3A94 Acute posthaemorrhagic anaemia
C 3A9Y Other specified anaemias or erythrocyte disorders
C 3A9Z Anaemias or other erythrocyte disorders, unspecified
B Coagulation defects, purpura or other haemorrhagic or related conditions
C Coagulation defects
D Congenital or constitutional haemorrhagic condition
E 3B10 Hereditary factor VIII deficiency
F H00219 Hemophilia
E 3B11 Hereditary factor IX deficiency
F H00219 Hemophilia
E 3B12 Von Willebrand disease
F H00219 Hemophilia
F H02092 von Willebrand disease
E 3B13 Haemophilia C
F H00938 Factor XI deficiency
E 3B14 Other inherited coagulation factor deficiency with bleeding tendency
F H01254 Congenital prothrombin deficiency
F H00222 Afibrinogenemia
F H02257 Factor X deficiency
F H00995 Combined deficiency of vitamin K-dependent clotting factors
F H02256 Factor VII deficiency
F H00220 Factor V deficiency
F H00221 Combined deficiency of factors V and VIII
F H00945 Factor XIII deficiency
E 3B15 Inherited coagulation factor deficiency without bleeding tendency
F H00941 Factor XII deficiency
F H01078 Fletcher factor deficiency
E 3B1Z Congenital or constitutional haemorrhagic condition, unspecified
D Haemorrhagic diseases due to acquired coagulation factor defects
E 3B20 Disseminated intravascular coagulation
F H01587 Disseminated intravascular coagulation
E 3B21 Haemorrhagic disorder due to circulating anticoagulants and coagulation factors
F H01759 Autoimmune acquired factor XIII (F13) deficiency
E 3B22 Acquired haemophilia
E 3B2Y Other specified haemorrhagic diseases due to acquired coagulation factor defects
D 3B4Z Coagulation defects, unspecified
C Fibrinolytic defects
D 3B50 Inherited fibrinolytic defects
E H00983 Alpha-2-plasmin inhibitor (a2-PI) deficiency
E H01106 Plasminogen activator inhibitor type 1 deficiency
E H01206 Plasminogen deficiency
D 3B51 Acquired fibrinolytic defects
C 3B60 Non-thrombocytopenic purpura
C 3B61 Thrombophilia
D H00223 Inherited thrombophilia
D H01381 Antithrombin III deficiency
C 3B62 Qualitative platelet defects
D H01235 Bleeding disorder platelet-type
D H02097 Gray platelet syndrome
D H00224 Bernard-Soulier syndrome
D H00226 Glanzmann thrombasthenia
D H01523 Wiskott-Aldrich syndrome
D H01162 Scott syndrome
D H02093 Platelet-type von Willebrand disease
D H02259 Stormorken syndrome
C 3B63 Thrombocytosis
D H01612 Essential thrombocythemia
C 3B64 Thrombocytopenia
D H00978 Thrombocytopenia (THC)
D H00227 Congenital amegakaryocytic thrombocytopenia
D H00233 MYH9-related disease
D H00578 Epstein syndrome
D H00867 Radioulnar synostosis with amegakaryocytic thrombocytopenia
D H01740 Macrothrombocytopenia
D H01847 Thrombocytopenia-absent radius syndrome
D H02052 Sebastian syndrome
D H02053 Fechtner syndrome
D H01240 Immune thrombocytopenia
D H00225 Thrombotic thrombocytopenic purpura
C 3B65 Thrombotic microangiopathy, not elsewhere classified
C 3B6Y Other specified coagulation defects, purpura or other haemorrhagic or related conditions
C 3B6Z Coagulation defects, purpura or other haemorrhagic or related conditions, unspecified
B Diseases of spleen
C 3B80 Congenital disorders of spleen
C 3B81 Acquired disorders of spleen
C 3B8Z Diseases of spleen, unspecified
B 3C0Y Other specified diseases of the blood or blood-forming organs
B 3C0Z Diseases of the blood or blood-forming organs, unspecified
#
A04 Diseases of the immune system
B Primary immunodeficiencies
C 4A00 Primary immunodeficiencies due to disorders of innate immunity
D H01725 Primary immunodeficiency disease
D H02525 Disorders of innate immunity
D H02620 Autoinflammation with episodic fever and lymphadenopathy
D H00098 Chronic granulomatous disease
D H01094 Eosinophil peroxidase deficiency
D H02024 Neutrophil specific granule deficiency
D H02025 Myeloperoxidase deficiency
D H00104 Alternative complement pathway component defects
D H00102 Classic complement pathway component defects
D H00103 Late complement pathway defects
D H01006 Hereditary angioedema
D H00105 Mannose-binding lectin pathway component defects
D H00106 Complement regulatory protein defects
D H01136 Carboxypeptidase N deficiency
D H00089 IFN-gamma/IL-12 axis
D H00096 Defects of toll-like receptor signaling
D H00721 Pyogenic bacterial infections, recurrent, due to MYD88 deficiency
D H00090 NK cell defects
D H00097 WHIM syndrome
C 4A01 Primary immunodeficiencies due to disorders of adaptive immunity
D H01725 Primary immunodeficiency disease
D H02526 Disorders of adaptive immunity
D H00085 Agammaglobulinemias
D H02308 Immunodeficiency-centromeric instability-facial anomalies syndrome
D H00086 Hyper IgM syndromes, autosomal recessive type
D H00088 Common variable immunodeficiency
D H00093 Combined immunodeficiency
D H00091 T-B+Severe combined immunodeficiency
D H00092 T-B-Severe combined immunodeficiency
D H01128 Reticular dysgenesis
D H01244 T+B+Severe combined immunodeficiencies (SCIDs)
D H02309 Adenosine deaminase deficiency
D H02554 Omenn syndrome
D H00984 Bare lymphocyte syndrome type1
D H00985 Bare lymphocyte syndrome type2
D H00087 Other humoral immunodeficiencies
D H00924 Severe combined immunodeficiency with microcephaly, growth retardation, and sensitivity to ionizing radiation
D H01181 T-cell immunodeficiency congenital alopecia and nail dystrophy
D H01387 Activated PI3K-delta syndrome
D H02015 LIG4 syndrome
D H02133 Vici syndrome
D H02585 Roifman-Chitayat syndrome
D H01971 IPEX syndrome
D H00108 Autoimmune lymphoproliferative syndromes
D H01969 X-linked lymphoproliferative syndrome
D H01970 Lymphoproliferative syndrome
D H00109 Familial hemophagocytic lymphohistiocytosis
D H02491 Immunoskeletal dysplasia with neurodevelopmental abnormalities
D H02574 BILU syndrome
D H00064 Ataxia telangiectasia
D H00094 Immunodeficiency associated with DNA repair defects
D H00962 RIDDLE syndrome
D H01344 Nijmegen breakage syndrome
D H01346 Bloom syndrome
D H02014 Ataxia-telangiectasia-like syndrome
D H00580 Schimke immunoosseous dysplasia
D H01264 Hepatic venoocclusive disease with immunodeficiency
D H01968 Hyper-IgE syndrome
C 4A0Y Other specified primary immunodeficiencies
D H01245 Immunodeficiency without anhidrotic ectodermal dysplasia
C 4A0Z Primary immunodeficiencies, unspecified
B 4A20 Acquired immunodeficiencies
C H00406 Acquired immunodeficiency syndrome (AIDS)
B Nonorgan specific systemic autoimmune disorders
C 4A40 Lupus erythematosus
D H00080 Systemic lupus erythematosus
D H01500 Lupus nephritis
C 4A41 Idiopathic inflammatory myopathy
D H01604 Polymyositis and dermatomyositis
D H01229 Inclusion body myopathy 3
D H01505 Inclusion body myositis
D H02031 Inclusion body myopathy with Paget disease of bone and frontotemporal dementia
C 4A42 Systemic sclerosis
D H01492 Systemic sclerosis
C 4A43 Overlap or undifferentiated nonorgan specific systemic autoimmune disease
D H01761 Immunoglobulin G4-related disease
D H01502 Sjogren syndrome
D H01710 Mixed connective tissue disease
D H01693 Eosinophilic fasciitis
D H01133 Reynolds syndrome
D H01232 Syndromic multisystem autoimmune disease
D H02540 Infantile-onset multisystem autoimmune disease
C 4A44 Vasculitis
D H01698 Giant cell arteritis
D H01382 Polyarteritis nodosa
D H01718 Kawasaki disease
D H01625 Buerger disease
D H01584 IgA vasculitis
D H01767 Henoch-Schonlein purpura nephritis
D H01658 Microscopic polyangiitis
D H01655 Granulomatosis with polyangiitis
D H01468 Eosinophilic granulomatosis with polyangiitis
D H01465 Large-vessel vasculitis
C 4A45 Antiphospholipid syndrome
D H01697 Antiphospholipid syndrome
C 4A4Y Other specified nonorgan specific systemic autoimmune disorders
D H02537 Autoinflammation, immune dysregulation, and eosinophilia
D H02621 X-linked systemic autoinflammatory disease
C 4A4Z Nonorgan specific systemic autoimmune disorders, unspecified
B Autoinflammatory disorders
C 4A60 Monogenic autoinflammatory syndromes
D H02588 NLRP1-associated autoinflammation with arthritis and dyskeratosis
D H02589 Periodic fever, immunodeficiency, and thrombocytopenia syndrome
D H02591 Interleukin-18 binding protein deficiency
D H02592 Familial Behcet-like autoinflammatory syndrome
D H02593 Chronic mucocutaneous ulceration
D H02599 Inherited autoinflammatory disease
D H00288 Familial Mediterranean fever
D H00282 Cryopyrin associated periodic syndrome
D H02159 Familial cold autoinflammatory syndrome
D H02555 Muckle-Wells syndrome
D H02556 CINCA syndrome
D H00912 Tumor necrosis factor receptor-associated periodic syndrome
D H00285 Blau syndrome
D H00287 Pyogenic sterile arthritis, pyoderma gangrenosum, and acne syndrome
D H01743 Autoinflammation and PLCG2-associated antibody deficiency and immune dysregulation
D H01744 Polyglucosan body myopathy
D H02414 Autoinflammation, panniculitis, and dermatosis syndrome
D H02467 Neonatal inflammatory skin and bowel disease
D H02532 Proteasome-associated autoinflammatory syndrome
D H02561 Familial autoinflammatory syndrome with or without immunodeficiency
D H02656 X-linked multisystem autoinflammatory disease with immune dysregulation
D H02660 Autoinflammation with pulmonary and cutaneous vasculitis
D H02672 Systemic autoinflammatory disease with vasculitis
C 4A61 SAPHO syndrome
C 4A62 Behçet disease
D H01476 Behcet disease
C 4A6Y Other specified autoinflammatory disorders
D H01117 Chronic recurrent multifocal osteomyelitis
D H01275 Interleukin 1 receptor antagonist deficiency
D H01748 NLRC4 inflammasomopathy
C 4A6Z Autoinflammatory disorders, unspecified
B Allergic or hypersensitivity conditions
C 4A80 Allergic or hypersensitivity disorders involving the respiratory tract
C 4A81 Allergic or hypersensitivity disorders involving the eye
C 4A82 Allergic or hypersensitivity disorders involving skin or mucous membranes
C 4A83 Allergic or hypersensitivity disorders involving the gastrointestinal tract
D H01782 Eosinophilic gastrointestinal disorder
C 4A84 Anaphylaxis
D H01359 Anaphylaxis
C 4A85 Complex allergic or hypersensitivity conditions
C 4A8Y Allergic or hypersensitivity conditions of other specified type
C 4A8Z Allergic or hypersensitivity conditions of unspecified type
B Immune system disorders involving white cell lineages
C 4B00 Disorders of neutrophil number
D H00100 Neutropenic disorders
D H00939 Darsun syndrome
D H01218 P14 deficiency
C 4B01 Disorders of neutrophil function
C 4B02 Eosinopenia
C 4B03 Eosinophilia
C 4B04 Disorders with decreased monocyte counts
C 4B05 Disorders with increased monocyte counts
C 4B06 Acquired lymphopenia
C 4B07 Acquired lymphocytosis
C 4B0Y Other specified immune system disorders involving white cell lineages
D H00234 Pelger-Huet anomaly
D H02051 May-Hegglin anomaly
C 4B0Z Immune system disorders involving white cell lineages, unspecified
B Certain disorders involving the immune system
C 4B20 Sarcoidosis
D H01309 Sarcoidosis, early-onset
C 4B21 Polyclonal hypergammaglobulinaemia
C 4B22 Cryoglobulinaemia
C 4B23 Immune reconstitution inflammatory syndrome
C 4B24 Graft-versus-host disease
D H00084 Graft-versus-host disease
C 4B2Y Other specified disorders involving the immune system
D H01479 Castleman disease
D H02669 Inflammatory bowel disease, immunodeficiency, and encephalopathy
B 4B40 Diseases of thymus
B 4B4Y Other specified diseases of the immune system
B 4B4Z Diseases of the immune system, unspecified
#
A05 Endocrine, nutritional or metabolic diseases
B Endocrine diseases
C Disorders of the thyroid gland or thyroid hormones system
D 5A00 Hypothyroidism
E H01186 Abnormal thyroid hormone metabolism
E H00251 Thyroid dyshormonogenesis
E H00249 Thyroid hormone resistance syndrome
E H00250 Congenital nongoitrous hypothyroidism (CHNG)
E H00650 Allan-Herndon-Dudley syndrome
E H01040 Bamforth-Lazarus syndrome
D 5A01 Nontoxic goitre
D 5A02 Thyrotoxicosis
E H01269 Congenital hyperthyroidism
E H01645 Hyperthyroidism
E H00082 Graves disease
E H02402 Thyroid eye disease
D 5A03 Thyroiditis
E H01647 Subacute thyroiditis
E H00081 Hashimoto thyroiditis
D 5A04 Hypersecretion of calcitonin
D 5A05 Generalised resistance to thyroid hormone
D 5A06 Sick-euthyroid syndrome
D 5A0Y Other specified disorders of the thyroid gland or thyroid hormones system
D 5A0Z Disorders of the thyroid gland or thyroid hormones system, unspecified
C Diabetes mellitus
D 5A10 Type 1 diabetes mellitus
E H00408 Type 1 diabetes mellitus
E H01224 Ketosis-prone diabetes mellitus
D 5A11 Type 2 diabetes mellitus
E H00409 Type 2 diabetes mellitus
D 5A12 Malnutrition-related diabetes mellitus
D 5A13 Diabetes mellitus, other specified type
E H00410 Maturity onset diabetes of the young (MODY)
E H01228 Insulin-resistant diabetes mellitus with acanthosis nigricans
E H00766 Wolcott-Rallison syndrome
D 5A14 Diabetes mellitus, type unspecified
D Acute complications of diabetes mellitus
E 5A20 Diabetic hyperosmolar hyperglycaemic state
E 5A21 Hypoglycaemia in the context of diabetes mellitus
E 5A22 Diabetic acidosis
E 5A23 Diabetic coma
E 5A24 Uncontrolled or unstable diabetes mellitus
E 5A2Y Other specified acute complications of diabetes mellitus
C Other disorders of glucose regulation or pancreatic internal secretion
D 5A40 Intermediate hyperglycaemia
D 5A41 Hypoglycaemia without associated diabetes
E H01909 Hypoinsulinemic hypoglycemia with hemihypertrophy
D 5A42 Increased secretion of glucagon
D 5A43 Abnormal secretion of gastrin
E H01522 Zollinger-Ellison syndrome
D 5A44 Insulin-resistance syndromes
E H00419 Congenital generalized lipodystrophy
E H00420 Familial partial lipodystrophy
E H00719 Leprechaunism
E H00942 Rabson-Mendenhall syndrome
E H01474 Acquired generalized lipodystrophy
E H02384 Abdominal obesity-metabolic syndrome
D 5A45 Persistent hyperinsulinaemic hypoglycaemia of infancy
E H01267 Familial hyperinsulinemic hypoglycemia
D 5A4Y Other specified disorders of glucose regulation or pancreatic internal secretion
D 5A4Z Disorders of glucose regulation or pancreatic internal secretion, unspecified
C Disorders of the parathyroids or parathyroid hormone system
D 5A50 Hypoparathyroidism
E H01862 Hypoparathyroidism
E H00244 Pseudohypoparathyroidism
D 5A51 Hyperparathyroidism
E H00246 Primary hyperparathyroidism
E H01669 Secondary hyperparathyroidism
E H02026 Familial hypocalciuric hypercalcemia
E H02030 Neonatal hyperparathyroidism
D 5A5Y Other specified disorders of the parathyroids or parathyroid hormone system
D 5A5Z Disorders of the parathyroids or parathyroid hormone system, unspecified
C Disorders of the pituitary hormone system
D 5A60 Hyperfunction of pituitary gland
E H01683 Disorders of antidiuretic hormone (ADH) secretion
E H01483 Acromegaly
E H01618 Pituitary gigantism
E H01864 Excessive secretion of growth hormone
E H01388 Hyperprolactinemia
E H01682 Syndrome of inappropriate antidiuretic hormone secretion
E H01294 Nephrogenic syndrome of inappropriate antidiuresis
E H00937 Precocious puberty
E H02018 Central precocious puberty
E H01701 Pituitary TSH hypersecretion
D 5A61 Hypofunction or certain other specified disorders of pituitary gland
E H01683 Disorders of antidiuretic hormone (ADH) secretion
E H00254 Growth hormone deficiency
E H00931 Growth hormone insensitivity with immunodeficiency
E H01253 Isolated follicle-stimulating hormone deficiency
E H01274 Growth delay due to insulin-like growth factor I resistance
E H01700 Hypopituitarism
E H01907 Acid-labile subunit deficiency
E H01973 Fertile eunuch syndrome
E H02035 Isolated growth hormone deficiency
E H02036 Combined pituitary hormone deficiency
E H02037 Laron syndrome
E H02038 X-linked panhypopituitarism
E H02039 Kowarski syndrome
E H02040 Insulin-like growth factor I deficiency
E H01011 Adrenocorticotropic hormone deficiency
E H00255 Hypogonadotropic hypogonadism
E H01860 Abnormal pituitary gonadotropin secretion
E H01699 Isolated TSH deficiency
E H02034 Central hypothyroidism and testicular enlargement
E H00253 Neurohypophyseal diabetes insipidus
E H00854 Wolfram syndrome
E H00682 Woodhouse-Sakati syndrome
D 5A6Z Disorders of the pituitary hormone system, unspecified
C Disorders of the adrenal glands or adrenal hormone system
D 5A70 Cushing syndrome
E H01431 Cushing syndrome
E H00260 Pigmented micronodular adrenocortical disease
E H01820 Carney complex
E H02049 Bilateral macronodular adrenal hyperplasia
D 5A71 Adrenogenital disorders
E H01702 Glucocorticoid resistance syndrome
E H00216 Congenital adrenal hyperplasia
E H02315 Disordered steroidogenesis due to cytochrome P450 oxidoreductase
E H01111 Cortisone reductase deficiency
D 5A72 Hyperaldosteronism
E H00602 Glucocorticoid-remediable aldosteronism (GRA)
E H01603 Primary aldosteronism
E H00259 Apparent mineralocorticoid excess syndrome
D 5A73 Hypoaldosteronism
E H00258 Aldosterone synthase deficiency
D 5A74 Adrenocortical insufficiency
E H01598 Addison disease
E H00177 Neonatal adrenoleukodystrophy
E H00256 Familial glucocorticoid deficiency
E H00257 Achalasia Addisonianism Alacrima syndrome
E H02314 Adrenal insufficiency, congenital, with 46XY sex reversal, partial or complete
E H02316 Adrenal insufficiency, NR5A1 related
E H02319 IMAGE syndrome
D 5A75 Adrenomedullary hyperfunction
D 5A76 Certain specified disorders of adrenal gland
E H01163 Corticosteroid-binding globulin (CBG) deficiency
D 5A7Z Disorders of the adrenal glands or adrenal hormone system, unspecified
C Disorders of the gonadal hormone system
D 5A80 Ovarian dysfunction
E H01739 Polycystic ovary syndrome
D 5A81 Testicular dysfunction or testosterone-related disorders
E H02019 Familial male-limited precocious puberty
E H02027 Male hypogonadism
D 5A8Z Disorders of the gonadal hormone system, unspecified
C Certain disorders of puberty
D 5A90 Disorder of puberty due to oestrogen resistance
E H02061 Estrogen resistance syndrome
D 5A91 Delayed puberty
D 5A92 Peripheral precocious puberty
E H00794 Aromatase excess syndrome
E H00937 Precocious puberty
D 5A9Y Other disorders of puberty
E H02020 Aromatase deficiency
D 5A9Z Disorders of puberty, unspecified
C Polyglandular dysfunction
D 5B00 Autoimmune polyendocrinopathy
E H01972 Autoimmune polyendocrinopathy syndrome type 1
D 5B01 Polyglandular hyperfunction
D 5B0Y Other specified polyglandular dysfunction
D 5B0Z Polyglandular dysfunction, unspecified
C Endocrine disorders, not elsewhere classified
D 5B10 Carcinoid syndrome
D 5B11 Short stature, not elsewhere classified
D 5B12 Constitutional tall stature
D 5B1Y Other specified endocrine disorders, not elsewhere classified
C 5B3Y Other specified endocrine diseases
C 5B3Z Endocrine diseases, unspecified
B Nutritional disorders
C Undernutrition
D 5B50 Underweight in infants, children or adolescents
D 5B51 Wasting in infants, children or adolescents
D 5B52 Acute malnutrition in infants, children or adolescents
D 5B53 Stunting in infants, children or adolescents
D 5B54 Underweight in adults
D 5B55 Vitamin A deficiency
E H01266 Hypercarotenemia and vitamin A deficiency
D 5B56 Vitamin C deficiency
E H01580 Vitamin C deficiency
D 5B57 Vitamin D deficiency
E H01143 Vitamin D-dependent rickets
D 5B58 Vitamin E deficiency
E H00981 Ataxia with isolated vitamin E deficiency (AVED)
D 5B59 Vitamin K deficiency
D 5B5A Vitamin B1 deficiency
E H01566 Beriberi
E H01565 Wernicke encephalopathy
D 5B5B Vitamin B2 deficiency
E H02544 Riboflavin deficiency
D 5B5C Vitamin B3 deficiency
E H01582 Pellagra
D 5B5D Vitamin B6 deficiency
D 5B5E Folate deficiency
D 5B5F Vitamin B12 deficiency
D 5B5G Biotin deficiency
D 5B5H Pantothenic acid deficiency
D 5B5J Choline deficiency
D 5B5K Mineral deficiencies
E H01925 Transient neonatal zinc deficiency
D Sequelae of malnutrition or certain specified nutritional deficiencies
E 5B60 Sequelae of protein-energy malnutrition
E 5B61 Sequelae of vitamin A deficiency
E 5B62 Sequelae of vitamin C deficiency
E 5B63 Sequelae of rickets
E 5B6Y Other specified sequelae of malnutrition or certain specified nutritional deficiencies
E 5B6Z Sequelae of malnutrition or certain specified nutritional deficiencies, unspecified
D 5B70 Essential fatty acid deficiency
D 5B71 Protein deficiency
D 5B7Y Other specified undernutrition
D 5B7Z Unspecified undernutrition
C Overweight, obesity or specific nutrient excesses
D Overweight or obesity
E 5B80 Overweight or localised adiposity
E 5B81 Obesity
F H02059 Leptin deficiency
F H02060 Leptin receptor deficiency
F H02105 Prohormone convertase 1/3 deficiency
F H02106 Genetic obesity
F H02235 Morbid obesity and spermatogenic failure
D Certain specified nutrient excesses
E 5B90 Vitamin excesses
F H01266 Hypercarotenemia and vitamin A deficiency
E 5B91 Mineral excesses
E 5B9Y Other specified nutrient excesses
E 5B9Z Certain specified nutrient excesses, unspecified
D 5C1Y Other specified overweight, obesity or specific nutrient excesses
D 5C1Z Overweight, obesity or specific nutrient excesses, unspecified
C 5C3Y Other specified nutritional disorders
C 5C3Z Nutritional disorders, unspecified
B Metabolic disorders
C Inborn errors of metabolism
D 5C50 Inborn errors of amino acid or other organic acid metabolism
E H00167 Phenylketonuria
E H02419 Glycine encephalopathy with normal serum glycine
E H00163 Alkaptonuria
E H00165 Tyrosinemia
E H00171 Histidinemia
E H01233 Urocanase deficiency
E H01583 Hydroxykynureninuria
E H02545 Hypertryptophanemia
E H00188 Hyperlysinemia
E H01242 Saccharopinuria
E H02644 Alpha-aminoadipic and alpha-ketoadipic aciduria
E H02313 5-Oxoprolinase deficiency
E H01079 3-Phosphoglycerate dehydrogenase (3-PGDH) deficiency
E H01082 Phosphoserine aminotransferase deficiency
E H02116 Phosphoserine phosphatase deficiency
E H01003 Dimethylglycine dehydrogenase deficiency
E H00191 Nonketotic hyperglycinemia
E H02657 Sarcosinemia
E H02380 D-glyceric aciduria
E H00190 Hyperprolinemia
E H00187 Ornithine transcarbamylase deficiency
E H00189 Ornithinaemia
E H01398 Primary hyperammonemia (Urea cycle disorders)
E H01400 Secondary hyperammonemia
E H01028 Argininosuccinic aciduria
E H00164 Carbamoyl phosphate synthetase I deficiency
E H00186 Hyperargininemia
E H00185 Citrullinemia
E H01032 N-acetylglutamate synthase deficiency
E H01268 Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome
E H00182 Cystathioninuria
E H00183 Homocystinuria
E H00184 Hypermethioninemia
E H01237 Sulfite oxidase deficiency
E H01285 Methylcobalamin deficiency type G
E H02311 Molybdenum cofactor deficiency
E H02485 Extraoral halitosis due to MTO deficiency
E H00172 Maple syrup urine disease
E H01076 Beta-ketothiolase deficiency
E H01279 Isobutyryl-CoA dehydrogenase deficiency
E H02136 Branched-chain ketoacid dehydrogenase kinase deficiency
E H02285 Methylmalonate semialdehyde dehydrogenase deficiency
E H02546 Hypervalinemia and hyperleucine-isoleucinemia
E H01349 Methacrylic aciduria
E H00173 Isovaleric acidemia
E H00174 Methylmalonic aciduria
E H00175 Propionic acidemia
E H00180 Holocarboxylase synthetase deficiency
E H00181 3-Methylcrotonylglycinuria
E H00375 SBCAD deficiency
E H00754 3-Methylglutaconic aciduria
E H01182 Biotinidase deficiency
E H02221 Methylmalonic aciduria and homocystinuria
E H02222 Methylmalonic acidemia and hyperhomocysteinemia, cblX type
E H00074 Canavan disease
E H00178 Glutaric acidemia
E H00835 Succinic semialdehyde dehydrogenase deficiency
E H01146 Aminoacylase 1 deficiency
E H01225 D-2-hydroxyglutaric aciduria
E H01280 L-2-hydroxyglutaric aciduria
E H01283 Malonyl-CoA decarboxylase deficiency
E H02304 Combined D-2- and L-2-hydroxyglutaric aciduria
E H02109 Combined malonic and methylmalonic aciduria
E H01119 Prolidase deficiency
E H01234 Trimethylaminuria
E H00923 Congenital systemic glutamine deficiency
E H01386 Asparagine synthetase deficiency
E H02312 Glutathione synthetase deficiency
D 5C51 Inborn errors of carbohydrate metabolism
E H01065 Pentosuria
E H01135 Ribose 5-phosphate isomerase deficiency
E H01189 Transaldolase deficiency
E H02439 Short stature, developmental delay, congenital heart defect
E H02013 Glycerol kinase deficiency
E H00117 Primary hyperoxaluria
E H00069 Glycogen storage disease
E H00150 Danon disease
E H01375 Glucose 6-phosphate dehydrogenase deficiency
E H01760 Hepatic glycogen storage disease
E H01762 Muscle glycogen storage disease
E H01939 Glycogen storage disease type I
E H01940 Glycogen storage disease type II
E H01941 Glycogen storage disease type III
E H01942 Glycogen storage disease type IV
E H01943 Glycogen storage disease type V
E H01944 Glycogen storage disease type VI
E H01945 Glycogen storage disease type VII
E H01946 Glycogen storage disease type XI
E H01947 Fanconi-Bickel syndrome
E H01948 Glycogen storage disease type IX
E H01949 Glycogen storage disease type 0b
E H01950 Glycogen storage disease type 0a
E H01951 Glycogen storage disease type X
E H01952 Glycogen storage disease type XII
E H01953 Glycogen storage disease type XIII
E H01954 Glycogen storage disease type XIV
E H01955 Glycogen storage disease type XV
E H01956 Glycogen storage disease of heart
E H00070 Galactosemia
E H02008 Galactose-1P uridylyltransferase deficiency
E H02009 Galactokinase deficiency
E H02010 Galactose epimerase deficiency
E H00071 Hereditary fructose intolerance
E H00114 Fructose-1,6-bisphosphatase deficiency
E H02567 Sorbitol dehydrogenase deficiency with peripheral neuropathy
D 5C52 Inborn errors of lipid metabolism
E H01589 Systemic primary carnitine deficiency
E H01981 Carnitine palmitoyltransferase I deficiency
E H01982 Carnitine palmitoyltransferase II deficiency
E H01983 Carnitine-acylcarnitine translocase deficiency
E H02596 Disorders of carnitine transport and the carnitine cycle
E H00392 VLCAD deficiency
E H00488 MCAD deficiency
E H00489 LCHAD deficiency
E H00525 Disorders of mitochondrial fatty-acid oxidation
E H00925 2-Methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency
E H01352 Mitochondrial trifunctional protein deficiency
E H01364 3-Hydroxyacyl-CoA dehydrogenase deficiency
E H01929 2,4-Dienoyl-CoA reductase deficiency
E H01980 SCAD deficiency
E H02085 Acyl-CoA dehydrogenase 9 deficiency
E H00179 3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
E H01121 Succinyl CoA:3-oxoacid CoA transferase (SCOT) deficiency
E H01123 HMG-CoA synthase deficiency
E H00162 Sjogren-Larsson syndrome
E H02284 Leukotriene C4 synthase deficiency
E H02689 Retinal dystrophy with leukodystrophy
E H00161 Smith-Lemli-Opitz syndrome
E H00206 Mevalonate kinase deficiency
E H00617 Desmosterolosis
E H01281 Lathosterolosis
E H00151 Cerebrotendinous xanthomatosis
E H00624 Progressive familial intrahepatic cholestasis
E H00628 Congenital bile acid synthesis defect
E H02099 Alpha-methylacyl-CoA racemase deficiency
E H00152 Sitosterolemia
E H00736 Dorfman-Chanarin syndrome
E H01297 Neutral lipid storage disease with myopathy
E H00654 Barth syndrome
E H02527 Lipid storage myopathy due to FLAD1 deficiency
E H02711 Acetyl-CoA carboxylase-alpha deficiency
D 5C53 Inborn errors of energy metabolism
E H01427 Mitochondrial disease
E H01096 Pyruvate kinase deficiency
E H00072 Pyruvate dehydrogenase complex deficiency
E H01996 Pyruvate dehydrogenase phosphatase deficiency
E H01997 Pyruvate dehydrogenase E1-alpha deficiency
E H01998 Pyruvate dehydrogenase E1-beta deficiency
E H01999 Pyruvate dehydrogenase E2 deficiency
E H02000 Dihydrolipoamide dehydrogenase deficiency
E H02003 Pyruvate dehydrogenase E3-binding protein deficiency
E H00073 Pyruvate carboxylase deficiency
E H02197 Mitochondrial pyruvate carrier deficiency
E H02438 Hyperglycinemia, lactic acidosis, and seizures
E H02520 Phosphoenolpyruvate carboxykinase deficiency
E H01022 Diseases of the tricarboxylic acid cycle
E H02004 Fumarase deficiency
E H02006 Alpha-ketoglutarate dehydrogenase complex deficiency
E H02113 Infantile cerebellar-retinal degeneration
E H02562 Yoon-Bellen neurodevelopmental syndrome
E H00469 Mitochondrial DNA depletion syndrome
E H01389 Alpers syndrome
E H01390 Mitochondrial neurogastrointestinal encephalomyopathy
E H01384 Mitochondrial recessive ataxia syndrome
E H00999 Coenzyme Q10 deficiency
E H00871 Leukoencephalopathy with brain stem and spinal cord involvement and lactate elevation
E H01367 Infantile liver failure
E H01354 Leigh syndrome
E H01369 ATP synthase deficiency
E H00473 Mitochondrial complex I deficiency
E H00891 Combined oxidative phosphorylation deficiency
E H00920 Exocrine pancreatic insufficiency, dyserythropoietic anemia, and calvarial hyperostosis
E H01201 Jensen syndrome
E H01368 Cytochrome c oxidase (COX) deficiency
E H01894 Multiple mitochondrial dysfunctions syndrome
E H02005 Mitochondrial complex II deficiency
E H02007 GRACILE syndrome
E H02086 Mitochondrial complex III deficiency
E H01305 Global cerebral hypomyelination
E H01348 Mitochondrial phosphate carrier deficiency
E H00834 Guanidinoacetate methyltransferase deficiency
E H00849 Cerebral creatine deficiency syndrome
E H02181 Idiopathic hyperCKemia
E H02196 X-linked creatine deficiency syndrome
E H01248 Monocarboxylate transporter 1 deficiency
E H01900 Encephalopathy due to defective mitochondrial and peroxisomal fission
E H02518 Neonatal severe encephalopathy with lactic acidosis and brain abnormalities
E H02643 Lipoyltransferase 1 deficiency
D 5C54 Inborn errors of glycosylation or other specified protein modification
E H01486 Multiple congenital anomalies-hypotonia-seizures syndrome
E H01487 CHIME syndrome
E H00118 Congenital disorders of glycosylation type I
E H00119 Congenital disorders of glycosylation type II
E H01188 Tn syndrome
E H01193 Familial tumoral calcinosis
E H00996 Amish infantile epilepsy syndrome
E H01127 PIGM-congenital disorder of glycosylation
E H01489 Inherited glycosylphosphatidylinositol deficiencies
E H02451 Congenital disorder of glycosylation with defective fucosylation
E H02690 Structural heart defects and renal anomalies syndrome
D 5C55 Inborn errors of purine, pyrimidine or nucleotide metabolism
E H00192 Xanthinuria
E H00194 Lesch-Nyhan syndrome
E H00195 Adenine phosphoribosyltransferase deficiency
E H00196 Phosphoribosylpyrophosphate synthetase superactivity
E H00197 Adenylosuccinate lyase deficiency
E H00964 Thiopurine S-methyltransferase deficiency (TPMT deficiency)
E H00966 AICA-ribosiduria
E H02011 Familial juvenile hyperuricemic nephropathy
E H02237 AMP deaminase deficiency
E H00193 Dihydropyrimidine dehydrogenase deficiency
E H00199 Dihydropyrimidinase deficiency
E H00200 Beta-ureidopropionase deficiency
E H00290 Aicardi-Goutieres syndrome
E H00878 Cystic leukoencephalopathy without megalencephaly
E H02433 Hypomyelination with brainstem and spinal cord involvement and leg spasticity
D 5C56 Lysosomal diseases
E H01425 Lysosomal storage disease
E H00423 Sphingolipidosis
E H00124 GM2 gangliosidoses
E H00281 GM1 gangliosidosis
E H00426 Gangliosidosis
E H02016 Tay-Sachs disease
E H02017 Sandhoff disease
E H00125 Fabry disease
E H00127 Metachromatic leukodystrophy
E H00272 Multiple sulfatase deficiency
E H00126 Gaucher disease
E H00136 Niemann-Pick disease type C
E H00137 Niemann-Pick disease type A/B
E H00138 Farber lipogranulomatosis
E H00148 Lysosomal acid lipase deficiency
E H00424 Defects in the degradation of sphingomyelin
E H01239 Combined SAP deficiency
E H02468 Early childhood-onset progressive leukodystrophy
E H00149 Neuronal ceroid lipofuscinosis
E H02275 Batten disease
E H02276 Kufs disease
E H02277 Santavuori-Haltia disease
E H02278 Jansky-Bielschowsky disease
E H02279 Cathepsin D deficiency
E H00422 Glycoproteinoses
E H00143 Mucolipidosis II
E H00144 Mucolipidosis IV
E H02130 Mucolipidosis III
E H00139 alpha-Mannosidosis
E H00140 beta-Mannosidosis
E H00141 Fucosidosis
E H00142 Sialidosis
E H00145 Aspartylglucosaminuria
E H00146 Alpha-N-acetylgalactosaminidase deficiency
E H00276 Galactosialidosis
E H00421 Mucopolysaccharidosis
E H00128 Mucopolysaccharidosis type I
E H00129 Mucopolysaccharidosis type II
E H00123 Mucopolysaccharidosis type IV
E H00131 Mucopolysaccharidosis type VI
E H00130 Mucopolysaccharidosis type III
E H00132 Mucopolysaccharidosis type VII
E H00133 Mucopolysaccharidosis type IX
E H02205 Mucopolysaccharidosis-plus syndrome
E H02729 Ain-Naz type of dysostosis multiplex
E H00147 Sialuria
E H00273 Pycnodysostosis
E H00274 Papillon-Lefevre syndrome
E H00425 Lysosomal cysteine protease deficiencies
E H02128 Defects in lysosomal trafficking
D 5C57 Peroxisomal diseases
E H00177 Neonatal adrenoleukodystrophy
E H00205 Peroxisome biogenesis disorder
E H00207 Rhizomelic chondrodysplasia punctata
E H01342 Zellweger syndrome
E H02100 Peroxisomal fatty acyl-CoA reductase 1 disorder
E H00075 Refsum disease
E H00176 Adrenoleukodystrophy
E H00407 Peroxisomal beta-oxidation enzyme deficiency
E H00874 Leukoencephalopathy with dystonia and motor neuropathy
E H02096 Peroxisomal acyl-CoA oxidase deficiency
E H02098 D-bifunctional protein deficiency
E H02099 Alpha-methylacyl-CoA racemase deficiency
E H00203 Acatalasemia
D 5C58 Inborn errors of porphyrin or heme metabolism
E H02025 Myeloperoxidase deficiency
E H00208 Hyperbilirubinemia
E H02054 Crigler-Najjar syndrome
E H02055 Gilbert syndrome
E H02056 Dubin-Johnson syndrome
E H00624 Progressive familial intrahepatic cholestasis
E H02192 Benign recurrent intrahepatic cholestasis
E H00950 Arthrogryposis, renal dysfunction, and cholestasis
E H01936 Hyperbiliverdinemia
E H02057 Rotor syndrome
E H01763 Porphyria
E H00202 Hepatic porphyria
E H00201 Erythropoietic porphyria
D 5C59 Inborn errors of neurotransmitter metabolism
E H01005 Dopamine beta-hydroxylase deficiency
E H01161 Aromatic L-amino acid decarboxylase deficiency
E H02597 Sepiapterin reductase deficiency
E H00548 Brunner syndrome
E H01257 GABA-transaminase deficiency
E H02432 Butyrylcholinesterase deficiency
D 5C5A Alpha-1-antitrypsin deficiency
E H01103 Alpha-1-antitrypsin deficiency
D 5C5Y Other specified inborn errors of metabolism
E H00967 Adiponectin deficiency
E H01567 Thiamine pyrophosphokinase deficiency
E H02441 HUPRA syndrome
E H02727 Triokinase and FMN cyclase deficiency syndrome
D 5C5Z Inborn errors of metabolism, unspecified
C Disorders of metabolite absorption or transport
D 5C60 Disorders of amino acid absorption or transport
E H00692 Lowe syndrome
E H00275 Cystinosis
E H00901 Cystinuria
E H00843 Hartnup disorder
E H00899 Lysinuric protein intolerance
E H00905 Iminoglycinuria
E H00911 Dicarboxylic aminoaciduria
E H01304 Hyperglycinuria
D 5C61 Disorders of carbohydrate absorption or transport
E H00115 Congenital sucrase-isomaltase deficiency
E H02090 Trehalase deficiency
E H00836 GLUT1 deficiency syndrome
E H01126 Familial renal glucosuria
E H02575 Lactose intolerance, adult type
E H00116 Congenital lactase deficiency
E H01261 Congenital glucose-galactose malabsorption
D 5C62 Disorders of lipid absorption or transport
E H02330 Pancreatic lipase deficiency
D 5C63 Disorders of vitamin or non-protein cofactor absorption or transport
E H01252 Hereditary folate malabsorption
E H01262 Formiminotransferase deficiency
E H01295 Neurodegeneration due to cerebral folate transport deficiency
E H00214 Hypophosphatemic rickets
E H02139 Autosomal recessive hypophosphatemic rickets
E H02141 Autosomal dominant hypophosphatemic rickets
E H02142 X-linked recessive hypophosphatemic rickets
E H02143 X-linked dominant hypophosphatemic rickets
E H01124 Pyridoxamine-5'-phosphate oxidase (PNPO) deficiency
E H01183 Thiamine-responsive megaloblastic anemia
E H01231 Biotin-thiamine-responsive basal ganglia disease
E H02662 Sulfide quinone oxidoreductase deficiency
E H02671 Sodium-dependent multivitamin transporter deficiency
E H02699 Folate-responsive megaloblastic anemia
D 5C64 Disorders of mineral absorption or transport
E H00210 Wilson disease
E H00209 Menkes syndrome
E H00833 Neurodegeneration with brain iron accumulation
E H02207 Kufor-Rakeb syndrome
E H02208 Pantothenate kinase-associated neurodegeneration
E H02209 HARP syndrome
E H00211 Hemochromatosis
E H00212 Acrodermatitis enteropathica
E H02550 Birk-Landau-Perez syndrome
E H00213 Hypophosphatasia
E H01113 Acid phosphatase deficiency
E H02138 Hereditary hypophophatemic rickets with hypercalciuria
E H00240 Gitelman syndrome
E H01210 Hypomagnesemia
E H00245 Calcium sensing receptor (CASR) related disease
E H01371 Hypercalcemia infantile
E H01938 Hypermanganesemia with dystonia
D 5C6Y Other specified disorders of metabolite absorption or transport
D 5C6Z Disorders of metabolite absorption or transport, unspecified
C Disorders of fluid, electrolyte or acid-base balance
D 5C70 Volume depletion
D 5C71 Hyperosmolality or hypernatraemia
D 5C72 Hypo-osmolality or hyponatraemia
D 5C73 Acidosis
D 5C74 Alkalosis
D 5C75 Mixed disorder of acid-base balance
D 5C76 Hyperkalaemia
D 5C77 Hypokalaemia
D 5C78 Fluid overload
D 5C7Y Other specified disorders of fluid, electrolyte or acid-base balance
D 5C7Z Disorders of fluid, electrolyte or acid-base balance, unspecified
C Disorders of lipoprotein metabolism or certain specified lipidaemias
D 5C80 Hyperlipoproteinaemia
E H01101 Combined lipase deficiency
E H01635 Hyperlipidemia
E H00155 Familial hypercholesterolemia
E H01383 Hyperlipoproteinemia type IIa
E H01918 Familial autosomal recessive hypercholesterolemia
E H00154 Hyperlipoproteinemia, type I
E H00157 Hyperlipoproteinemia, type V
E H01637 Hypertriglyceridemia
E H01784 Primary hyperchylomicronemia
E H02731 Transient infantile hypertriglyceridemia
E H00153 Familial combined hyperlipidemia
E H00156 Hyperlipoproteinemia, type III
E H01199 Hyperalphalipoproteinemia
E H01108 CD36 deficiency
E H02329 Hepatic lipase deficiency
D 5C81 Hypolipoproteinaemia
E H00159 Tangier disease
E H00930 Hypoalphalipoproteinemia
E H00160 Abetalipoproteinemia
E H00927 Chylomicron retention disease
E H01270 Familial hypobetalipoproteinemia
E H00158 Lecithin:cholesterol acyltransferase deficiency
D 5C8Y Other specified disorders of lipoprotein metabolism or lipidaemias
D 5C8Z Unspecified disorders of lipoprotein metabolism or lipidaemias
C 5C90 Metabolic or transporter liver disease
C Other metabolic disorders
D 5D00 Amyloidosis
E H01185 Cerebral amyloid angiopathy
E H01217 Primary localized cutaneous amyloidosis
E H02499 AL amyloidosis
E H00845 Familial amyloidosis
E H02484 X-linked reticulate pigmentary disorder with systemic manifestations
E H02322 Amyloidosis, Finnish type
D 5D01 Tumour lysis syndrome
D 5D0Y Other specified metabolic disorders
C 5D2Z Metabolic disorders, unspecified
B Postprocedural endocrine or metabolic disorders
C 5D40 Postprocedural hypothyroidism
C 5D41 Postprocedural hypoinsulinaemia
C 5D42 Postprocedural hypoparathyroidism
C 5D43 Postprocedural hypopituitarism
C 5D44 Postprocedural ovarian failure
C 5D45 Postprocedural testicular hypofunction
C 5D46 Postprocedural adrenocortical hypofunction
#
A06 Mental, behavioural or neurodevelopmental disorders
B Neurodevelopmental disorders
C 6A00 Disorders of intellectual development
D H00480 X-linked intellectual developmental disorder
D H00658 X-linked syndromic intellectual developmental disorder
D H00768 Autosomal recessive intellectual developmental disorder
D H00773 Autosomal dominant intellectual developmental disorder
D H01306 FRA12A mental retardation
D H01911 Syndromic autosomal recessive mental retardation
C 6A01 Developmental speech or language disorders
D H00902 Speech-language disorder 1
C 6A02 Autism spectrum disorder
D H02111 Autism
D H01882 Asperger syndrome
D H02371 Intellectual developmental disorder with autism and speech delay
D H02507 Pilarowski-Bjornsson syndrome
C 6A03 Developmental learning disorder
C 6A04 Developmental motor coordination disorder
C 6A05 Attention deficit hyperactivity disorder
D H01895 Attention deficit hyperactivity disorder (ADHD)
C 6A06 Stereotyped movement disorder
C 6A0Y Other specified neurodevelopmental disorders
D H02387 Snijders Blok-Fisher syndrome
D H02490 Gabriele-de Vries syndrome
D H02510 Jaberi-Elahi syndrome
D H02521 Diets-Jongmans syndrome
D H02571 Neurodevelopmental disorder with hypotonia and variable intellectual and behavioral abnormalities
D H02692 Usmani-Riazuddin syndrome
D H02705 Neurodevelopmental disorder with glutamatergic synapse dysfunction
C 6A0Z Neurodevelopmental disorders, unspecified
B Schizophrenia or other primary psychotic disorders
C 6A20 Schizophrenia
D H01649 Schizophrenia
C 6A21 Schizoaffective disorder
C 6A22 Schizotypal disorder
C 6A23 Acute and transient psychotic disorder
C 6A24 Delusional disorder
C 6A25 Symptomatic manifestations of primary psychotic disorders
C 6A2Y Other specified primary psychotic disorder
C 6A2Z Schizophrenia or other primary psychotic disorders, unspecified
B Catatonia
C 6A40 Catatonia associated with another mental disorder
C 6A41 Catatonia induced by substances or medications
C 6A4Z Catatonia, unspecified
B Mood disorders
C Bipolar or related disorders
D 6A60 Bipolar type I disorder
E H01653 Bipolar disorder
D 6A61 Bipolar type II disorder
E H01653 Bipolar disorder
D 6A62 Cyclothymic disorder
D 6A6Y Other specified bipolar or related disorders
D 6A6Z Bipolar or related disorders, unspecified
C Depressive disorders
D 6A70 Single episode depressive disorder
E H01646 Major depressive disorder
D 6A71 Recurrent depressive disorder
E H01646 Major depressive disorder
D 6A72 Dysthymic disorder
D 6A73 Mixed depressive and anxiety disorder
D 6A7Y Other specified depressive disorders
D 6A7Z Depressive disorders, unspecified
C 6A80 Symptomatic and course presentations for mood episodes in mood disorders
C 6A8Y Other specified mood disorders
C 6A8Z Mood disorders, unspecified
B Anxiety or fear-related disorders
C 6B00 Generalised anxiety disorder
D H01662 Generalized anxiety disorder
C 6B01 Panic disorder
D H01664 Panic disorder
C 6B02 Agoraphobia
C 6B03 Specific phobia
C 6B04 Social anxiety disorder
D H01670 Social anxiety disorder
C 6B05 Separation anxiety disorder
C 6B06 Selective mutism
C 6B0Y Other specified anxiety or fear-related disorders
C 6B0Z Anxiety or fear-related disorders, unspecified
B Obsessive-compulsive or related disorders
C 6B20 Obsessive-compulsive disorder
D H01450 Obsessive-compulsive disorder
C 6B21 Body dysmorphic disorder
D H01447 Body dysmorphic disorder
C 6B22 Olfactory reference disorder
C 6B23 Hypochondriasis
C 6B24 Hoarding disorder
D H01448 Hoarding disorder
C 6B25 Body-focused repetitive behaviour disorders
D H00864 Trichotillomania
D H01449 Excoriation disorder
C 6B2Y Other specified obsessive-compulsive or related disorders
C 6B2Z Obsessive-compulsive or related disorders, unspecified
D H01453 Obsessive-Compulsive and Related Disorder
B Disorders specifically associated with stress
C 6B40 Post traumatic stress disorder
C 6B41 Complex post traumatic stress disorder
C 6B42 Prolonged grief disorder
C 6B43 Adjustment disorder
C 6B44 Reactive attachment disorder
C 6B45 Disinhibited social engagement disorder
C 6B4Y Other specified disorders specifically associated with stress
C 6B4Z Disorders specifically associated with stress, unspecified
B Dissociative disorders
C 6B60 Dissociative neurological symptom disorder
C 6B61 Dissociative amnesia
C 6B62 Trance disorder
C 6B63 Possession trance disorder
C 6B64 Dissociative identity disorder
C 6B65 Partial dissociative identity disorder
C 6B66 Depersonalization-derealization disorder
C 6B6Y Other specified dissociative disorders
C 6B6Z Dissociative disorders, unspecified
B Feeding or eating disorders
C 6B80 Anorexia Nervosa
C 6B81 Bulimia Nervosa
C 6B82 Binge eating disorder
C 6B83 Avoidant-restrictive food intake disorder
C 6B84 Pica
C 6B85 Rumination-regurgitation disorder
C 6B8Y Other specified feeding or eating disorders
D H01703 Eating Disorders
C 6B8Z Feeding or eating disorders, unspecified
B Elimination disorders
C 6C00 Enuresis
C 6C01 Encopresis
C 6C0Z Elimination disorders, unspecified
B Disorders of bodily distress or bodily experience
C 6C20 Bodily distress disorder
C 6C21 Body integrity dysphoria
C 6C2Y Other specified disorders of bodily distress or bodily experience
C 6C2Z Disorders of bodily distress or bodily experience, unspecified
B Disorders due to substance use or addictive behaviours
C Disorders due to substance use
D 6C40 Disorders due to use of alcohol
E H01611 Alcohol dependence
E H01071 Acute alcohol sensitivity
D 6C41 Disorders due to use of cannabis
D 6C42 Disorders due to use of synthetic cannabinoids
D 6C43 Disorders due to use of opioids
D 6C44 Disorders due to use of sedatives, hypnotics or anxiolytics
D 6C45 Disorders due to use of cocaine
D 6C46 Disorders due to use of stimulants including amphetamines, methamphetamine or methcathinone
D 6C47 Disorders due to use of synthetic cathinones
D 6C48 Disorders due to use of caffeine
D 6C49 Disorders due to use of hallucinogens
D 6C4A Disorders due to use of nicotine
D 6C4B Disorders due to use of volatile inhalants
D 6C4C Disorders due to use of MDMA or related drugs, including MDA
D 6C4D Disorders due to use of dissociative drugs including ketamine and phencyclidine [PCP]
D 6C4E Disorders due to use of other specified psychoactive substances, including medications
D 6C4F Disorders due to use of multiple specified psychoactive substances, including medications
D 6C4G Disorders due to use of unknown or unspecified psychoactive substances
D 6C4H Disorders due to use of non-psychoactive substances
D 6C4Y Other specified disorders due to substance use
D 6C4Z Disorders due to substance use, unspecified
C Disorders due to addictive behaviours
D 6C50 Gambling disorder
D 6C51 Gaming disorder
D 6C5Y Other specified disorders due to addictive behaviours
D 6C5Z Disorders due to addictive behaviours, unspecified
B Impulse control disorders
C 6C70 Pyromania
C 6C71 Kleptomania
C 6C72 Compulsive sexual behaviour disorder
C 6C73 Intermittent explosive disorder
C 6C7Y Other specified impulse control disorders
C 6C7Z Impulse control disorders, unspecified
B Disruptive behaviour or dissocial disorders
C 6C90 Oppositional defiant disorder
C 6C91 Conduct-dissocial disorder
C 6C9Y Other specified disruptive behaviour or dissocial disorders
C 6C9Z Disruptive behaviour or dissocial disorders, unspecified
B Personality disorders and related traits
C 6D10 Personality disorder
C 6D11 Prominent personality traits or patterns
B Paraphilic disorders
C 6D30 Exhibitionistic disorder
C 6D31 Voyeuristic disorder
C 6D32 Pedophilic disorder
C 6D33 Coercive sexual sadism disorder
C 6D34 Frotteuristic disorder
C 6D35 Other paraphilic disorder involving non-consenting individuals
C 6D36 Paraphilic disorder involving solitary behaviour or consenting individuals
C 6D3Z Paraphilic disorders, unspecified
B Factitious disorders
C 6D50 Factitious disorder imposed on self
C 6D51 Factitious disorder imposed on another
C 6D5Z Factitious disorders, unspecified
B Neurocognitive disorders
C 6D70 Delirium
C 6D71 Mild neurocognitive disorder
C 6D72 Amnestic disorder
C Dementia
D 6D80 Dementia due to Alzheimer disease
D 6D81 Dementia due to cerebrovascular disease
D 6D82 Dementia due to Lewy body disease
D 6D83 Frontotemporal dementia
D 6D84 Dementia due to psychoactive substances including medications
D 6D85 Dementia due to diseases classified elsewhere
D 6D86 Behavioural or psychological disturbances in dementia
D 6D8Y Dementia, other specified cause
D 6D8Z Dementia, unknown or unspecified cause
C 6E0Y Other specified neurocognitive disorders
C 6E0Z Neurocognitive disorders, unspecified
B Mental or behavioural disorders associated with pregnancy, childbirth or the puerperium
C 6E20 Mental or behavioural disorders associated with pregnancy, childbirth or the puerperium, without psychotic symptoms
C 6E21 Mental or behavioural disorders associated with pregnancy, childbirth or the puerperium, with psychotic symptoms
C 6E2Z Mental or behavioural disorders associated with pregnancy, childbirth or the puerperium, unspecified
B 6E40 Psychological or behavioural factors affecting disorders or diseases classified elsewhere
B Secondary mental or behavioural syndromes associated with disorders or diseases classified elsewhere
C 6E60 Secondary neurodevelopmental syndrome
C 6E61 Secondary psychotic syndrome
C 6E62 Secondary mood syndrome
C 6E63 Secondary anxiety syndrome
C 6E64 Secondary obsessive-compulsive or related syndrome
C 6E65 Secondary dissociative syndrome
C 6E66 Secondary impulse control syndrome
C 6E67 Secondary neurocognitive syndrome
C 6E68 Secondary personality change
C 6E69 Secondary catatonia syndrome
C 6E6Y Other specified secondary mental or behavioural syndrome
C 6E6Z Secondary mental or behavioural syndrome, unspecified
B 6E8Y Other specified mental, behavioural or neurodevelopmental disorders
B 6E8Z Mental, behavioural or neurodevelopmental disorders, unspecified
#
A07 Sleep-wake disorders
B Insomnia disorders
C 7A00 Chronic insomnia
D H01609 Insomnia
C 7A01 Short-term insomnia
D H01609 Insomnia
C 7A0Z Insomnia disorders, unspecified
B Hypersomnolence disorders
C 7A20 Narcolepsy
D H01293 Narcolepsy
C 7A21 Idiopathic hypersomnia
C 7A22 Kleine-Levin syndrome
C 7A23 Hypersomnia due to a medical condition
C 7A24 Hypersomnia due to a medication or substance
C 7A25 Hypersomnia associated with a mental disorder
C 7A26 Insufficient sleep syndrome
C 7A2Y Other specified hypersomnolence disorders
C 7A2Z Hypersomnolence disorders, unspecified
B Sleep-related breathing disorders
C 7A40 Central sleep apnoeas
C 7A41 Obstructive sleep apnoea
C 7A42 Sleep-related hypoventilation or hypoxemia disorders
D H01727 Primary alveolar hypoventilation syndrome
D H01729 Premature ventricular complexes
D H01715 Obesity hypoventilation syndrome
D H00916 Congenital central hypoventilation syndrome
C 7A4Y Other specified sleep-related breathing disorders
C 7A4Z Sleep-related breathing disorders, unspecified
B Circadian rhythm sleep-wake disorders
C 7A60 Delayed sleep-wake phase disorder
D H00689 Delayed sleep phase disorder
C 7A61 Advanced sleep-wake phase disorder
D H00688 Familial advanced sleep phase syndrome
C 7A62 Irregular sleep-wake rhythm disorder
C 7A63 Non-24 hour sleep-wake rhythm disorder
C 7A64 Circadian rhythm sleep-wake disorder, shift work type
C 7A65 Circadian rhythm sleep-wake disorder, jet lag type
C 7A6Z Circadian rhythm sleep-wake disorders, unspecified
B Sleep-related movement disorders
C 7A80 Restless legs syndrome
D H01597 Restless legs syndrome
C 7A81 Periodic limb movement disorder
C 7A82 Sleep-related leg cramps
C 7A83 Sleep-related bruxism
C 7A84 Sleep-related rhythmic movement disorder
C 7A85 Benign sleep myoclonus of infancy
C 7A86 Propriospinal myoclonus at sleep onset
C 7A87 Sleep-related movement disorder due to a medical condition
C 7A88 Sleep-related movement disorder due to a medication or substance
C 7A8Y Other specified sleep-related movement disorders
C 7A8Z Sleep-related movement disorders, unspecified
B Parasomnia disorders
C 7B00 Disorders of arousal from non-REM sleep
C 7B01 Parasomnias related to REM sleep
C 7B02 Other parasomnias
C 7B0Y Other specified parasomnia disorders
C 7B0Z Parasomnia disorders, unspecified
B 7B2Y Other specified sleep-wake disorders
B 7B2Z Sleep-wake disorders, unspecified
#
A08 Diseases of the nervous system
B Movement disorders
C 8A00 Parkinsonism
D H01600 Parkinsonian syndrome
D H00057 Parkinson disease
D H00077 Progressive supranuclear palsy
D H00879 Perry syndrome
D H01574 Familial idiopathic basal ganglia calcification
C 8A01 Choreiform disorders
D H00860 Benign hereditary chorea
D H00059 Huntington disease
D H01243 Huntington disease-like syndrome
D H00060 Dentatorubropallidoluysian atrophy (DRPLA)
D H00655 McLeod syndrome
D H00832 Core neuroacanthocytosis syndromes
D H01779 Neuroferritinopathy
D H02367 Chorea, childhood-onset, with psychomotor retardation
C 8A02 Dystonic disorders
D H00831 Primary dystonia
D H01255 Juvenile-onset dystonia
D H01608 Cervical dystonia
D H02706 Early-onset dystonia and/or spastic paraplegia
D H02557 Dopa-responsive dystonia
D H00989 Mohr-Tranebjaerg syndrome
D H02676 Infantile-onset parkinsonism-dystonia
C 8A03 Ataxic disorders
D H01616 Spinocerebellar degeneration
D H00067 Friedreich ataxia
D H00749 Episodic ataxias
D H00063 Spinocerebellar ataxia (SCA)
D H01478 Machado-Joseph disease
D H01891 Autosomal recessive spinocerebellar ataxias
D H02573 Autosomal recessive spinocerebellar ataxias with axonal neuropathy
D H00848 Ataxia with ocular apraxia
D H01036 Posterior column ataxia with retinitis pigmentosa
D H01038 Cerebellar ataxia cayman type
D H01170 Autosomal recessive spastic ataxia of Charlevoix-Saguenay
D H01204 Cerebellar ataxia, mental retardation (MR), and dysequilibrium syndrome (CAMRQ)
D H01432 Choreoacanthocytosis
D H02101 Autosomal dominant sensory ataxia
D H02140 Boucher-Neuhauser syndrome
D H02144 Gordon Holmes syndrome
D H02273 Nonprogressive cerebellar ataxia with mental retardation
D H02552 Ataxia, intention tremor, and hypotonia syndrome
C 8A04 Disorders associated with tremor
D H01577 Essential tremor
C 8A05 Tic disorders
D H00862 Tourette syndrome
C 8A06 Myoclonic disorders
C 8A07 Certain specified movement disorder
D H01287 Congenital mirror movements
D H01528 Neuroleptic malignant syndrome
C 8A0Y Other specified movement disorders
D H01570 Autosomal dominant striatal degeneration
C 8A0Z Movement disorders, unspecified
B Disorders with neurocognitive impairment as a major feature
C 8A20 Alzheimer disease
D H00056 Alzheimer disease
C 8A21 Progressive focal atrophies
C 8A22 Lewy body disease
D H00066 Lewy body dementia (LBD)
C 8A23 Frontotemporal lobar degeneration
D H00078 Frontotemporal lobar degeneration
C 8A2Y Other specified disorders with neurocognitive impairment as a major feature
D H00290 Aicardi-Goutieres syndrome
C 8A2Z Disorders with neurocognitive impairment as a major feature, unspecified
B Multiple sclerosis or other white matter disorders
C 8A40 Multiple sclerosis
D H01490 Multiple sclerosis
C 8A41 Isolated demyelinating syndromes of the central nervous system
C 8A42 Acute disseminated encephalomyelitis
C 8A43 Neuromyelitis optica
D H01491 Neuromyelitis optica
C 8A44 Leukodystrophies
D H02598 Progressive leukoencephalopathy
D H00176 Adrenoleukodystrophy
D H00065 Alexander disease
D H00438 Nasu-Hakola disease
D H00679 Hypomyelinating leukodystrophy
D H00869 Leukoencephalopathy with vanishing white matter
D H00875 Megaloencephalic leukoencephalopathy with subcortical cysts
D H01230 Adult-onset autosomal dominant leukodystrophy
D H01807 Hereditary diffuse leukoencephalopathy with spheroids
D H02200 Leukoencephalopathy, progressive, with ovarian failure
D H02377 Leukodystrophy and acquired microcephaly with or without dystonia
D H00135 Krabbe disease
C 8A45 Secondary white matter disorders
D H01724 HTLV1-associated myelopathy
D H01696 Subacute sclerosing panencephalitis
D H00370 Progressive multifocal leukoencephalopathy
C 8A46 Central demyelination of corpus callosum
C 8A4Y Other specified multiple sclerosis or other white matter disorders
D H02457 Developmental delay, leukoencephalopathy, and neurologic decompensation
C 8A4Z Multiple sclerosis or other white matter disorders, unspecified
B Epilepsy or seizures
C 8A60 Epilepsy due to structural or metabolic conditions or diseases
D H01826 Mesial temporal lobe epilepsy with hippocampal sclerosis
C 8A61 Genetic or presumed genetic syndromes primarily expressed as epilepsy
D H00577 Symptomatic generalized epilepsies
D H00808 Idiopathic generalized epilepsies
D H01247 Pyridoxine-dependent epilepsy
D H01819 Early myoclonic encephalopathy
D H02250 Early-onset vitamin B6-dependent epilepsy
D H02696 Early-onset epilepsy
D H00806 Benign familial neonatal seizure
D H01818 Dravet syndrome
D H01815 Malignant migrating partial seizures in infancy
D H01775 PCDH19-related epilepsy syndrome
D H02212 Familial infantile myoclonic epilepsy
D H02215 Childhood absence epilepsy
D H01823 Myoclonic-astatic epilepsy
D H01822 Epilepsy with myoclonic absence
D H01258 Generalized epilepsy and paroxysmal dyskinesia
D H02361 Myoclonic-atonic epilepsy
D H02564 Generalized epilepsy with febrile seizures plus
D H02217 Juvenile myoclonic epilepsy
D H02216 Juvenile absence epilepsy
D H02213 Familial adult myoclonic epilepsy
D H00809 Familial epilepsy temporal lobe (ETL)
D H00810 Progressive myoclonic epilepsy
D H01212 Familial encephalopathy with neuroserpin inclusion bodies
D H01994 Myoclonic epilepsy of Lafora
D H01995 Unverricht-Lundborg disease
D H00807 Nocturnal frontal lobe epilepsy
D H00836 GLUT1 deficiency syndrome
D H02214 Familial focal epilepsy with variable foci
C 8A62 Epileptic encephalopathies
D H01460 West syndrome
D H01813 Lennox-Gastaut syndrome
D H01514 Landau-Kleffner syndrome
D H00606 Early infantile epileptic encephalopathy
D H01808 Hemiconvulsion-hemiplegia-epilepsy syndrome
D H01812 Rasmussen encephalitis
D H01827 Rolandic epilepsy, mental retardation, and speech dyspraxia
D H01829 Acute encephalitis with refractory repetitive partial seizures
D H02150 Infantile or early childhood epileptic encephalopathy
D H02360 Epileptic encephalopathy, childhood-onset
D H02472 Early-onset progressive encephalopathy
C 8A63 Seizure due to acute causes
D H00783 Febrile seizures
C 8A64 Single seizure due to remote causes
C 8A65 Single unprovoked seizure
C 8A66 Status epilepticus
C 8A67 Acute repetitive seizures
C 8A68 Types of seizures
C 8A6Y Other specified epilepsy or seizures
C 8A6Z Epilepsy or seizures, unspecified
B Headache disorders
C 8A80 Migraine
D H00775 Hemiplegic migraine
D H02362 Benign familial infantile seizure
C 8A81 Tension-type headache
C 8A82 Trigeminal autonomic cephalalgias
D H01588 Cluster headache
C 8A83 Other primary headache disorder
C 8A84 Secondary headache
C 8A85 Painful cranial neuropathies or other facial pains
C 8A8Y Other specified headache disorders
C 8A8Z Headache disorders, unspecified
B Cerebrovascular diseases
C Intracranial haemorrhage
D 8B00 Intracerebral haemorrhage
D 8B01 Subarachnoid haemorrhage
D 8B02 Nontraumatic subdural haemorrhage
D 8B03 Nontraumatic epidural haemorrhage
D 8B0Z Intracranial haemorrhage, unspecified
C Cerebral ischaemia
D 8B10 Transient ischaemic attack
D 8B11 Cerebral ischaemic stroke
D 8B1Y Other specified cerebral ischaemia
D 8B1Z Cerebral ischaemia, unspecified
C 8B20 Stroke not known if ischaemic or haemorrhagic
C 8B21 Cerebrovascular disease with no acute cerebral symptom
C 8B22 Certain specified cerebrovascular diseases
D H01184 Familial dementia
D H00534 Cerebral cavernous malformation
D H01396 Moyamoya disease
D H00536 Cerebral autosomal dominant arteriopathy with subcortical infarcts and leucoencephalopathy (CADASIL)
D H01757 Cerebral autosomal recessive arteriopathy with subcortical infarcts and leukoencephalopathy
D H00877 Brain small vessel disease
D H02718 Autosomal dominant pontine microangiopathy and leukoencephalopathy
C 8B23 Cerebrovascular abnormalities
C 8B24 Hypoxic-ischaemic encephalopathy
C 8B25 Late effects of cerebrovascular disease
C 8B26 Vascular syndromes of brain in cerebrovascular diseases
D H01120 Proliferative vasculopathy and hydranencephaly-hydrocephaly syndrome
C 8B2Z Cerebrovascular diseases, unspecified
B Spinal cord disorders excluding trauma
C 8B40 Cauda equina syndrome
C 8B41 Myelitis
D H01863 Atopic myelitis
C 8B42 Myelopathy
C 8B43 Non-compressive vascular myelopathies
C 8B44 Degenerative myelopathic disorders
D H00266 Hereditary spastic paraplegia
D H01351 Spastic ataxia
D H02114 Spastic paraplegia, optic atrophy, and neuropathy
D H02293 Spastic paraplegia-psychomotor retardation-seizures syndrome
D H02178 MASA syndrome
D H01172 Infantile-onset ascending hereditary spastic paralysis
C 8B4Y Other specified spinal cord disorders excluding trauma
C 8B4Z Spinal cord disorders excluding trauma, unspecified
B Motor neuron diseases or related disorders
C 8B60 Motor neuron disease
D H00058 Amyotrophic lateral sclerosis (ALS)
D H00970 Juvenile primary lateral sclerosis
D H02342 Frontotemporal dementia and amyotrophic lateral sclerosis
D H00841 Infantile progressive bulbar palsy
C 8B61 Spinal muscular atrophy
D H00455 Spinal muscular atrophy
D H00062 Spinal and bulbar muscular atrophy (SBMA)
D H00524 Scapuloperoneal spinal muscular atrophy
D H00856 Distal hereditary motor neuropathies
D H02238 Spinal muscular atrophy with congenital bone fractures
C 8B62 Post polio progressive muscular atrophy
C 8B6Y Other specified motor neuron diseases or related disorders
C 8B6Z Motor neuron diseases or related disorders, unspecified
B Disorders of nerve root, plexus or peripheral nerves
C Disorders of cranial nerves
D 8B80 Disorders of olfactory nerve
D 8B81 Disorders of vestibulocochlear nerve
D 8B82 Disorders of trigeminal nerve
D 8B83 Disorders of spinal accessory nerve
D 8B84 Disorders of hypoglossal nerve
D 8B85 Disorders of multiple cranial nerves
D 8B86 Disorders of vagus nerve
D 8B87 Disorders of glossopharyngeal nerve
D 8B88 Disorders of facial nerve
D 8B8Y Other specified disorders of cranial nerves
E H02594 Congenital facial palsy with ptosis and velopharyngeal dysfunction
D 8B8Z Disorders of cranial nerves, unspecified
C Nerve root or plexus disorders
D 8B90 Nerve root and plexus compressions
D 8B91 Brachial plexus disorders
D 8B92 Lumbosacral plexus disorders
D 8B93 Radiculopathy
D 8B94 Diabetic radiculoplexoneuropathy
D 8B95 Secondary brachial plexus lesion due to certain specified disorders
D 8B9Y Other specified nerve root or plexus disorders
D 8B9Z Nerve root or plexus disorders, unspecified
C Polyneuropathy
D 8C00 Idiopathic progressive neuropathy
D 8C01 Inflammatory polyneuropathy
E H01436 Guillain-Barre syndrome
E H01689 Fisher syndrome
E H01842 Bickerstaff brainstem encephalitis
E H01527 Chronic inflammatory demyelinating polyradiculoneuropathy
D 8C03 Other secondary polyneuropathy
E H01459 Diabetic neuropathy
E H02559 Microvascular complications of diabetes
D 8C0Y Other specified polyneuropathy
D 8C0Z Polyneuropathy, unspecified
C Mononeuropathy
D 8C10 Mononeuropathies of upper limb
E H00798 Familial carpal tunnel syndrome
D 8C11 Mononeuropathies of lower limb
D 8C12 Certain specified mononeuropathies
D 8C1Y Mononeuropathy of other specified site
D 8C1Z Mononeuropathy of unspecified site
C Hereditary neuropathy
D 8C20 Hereditary motor and sensory neuropathy
E H00264 Charcot-Marie-Tooth disease
E H02357 Congenital hypomyelinating neuropathy
E H01131 Hereditary neuralgic amyotrophy
E H01155 Roussy-Levy syndrome
E H01296 Hereditary neuropathy with liability to pressure palsies
E H02344 Cowchock syndrome
E H02345 Autosomal recessive peripheral neuropathy (PNRIID)
E H02359 Dejerine-Sottas disease
E H02649 Autosomal dominant slowed nerve conduction velocity
D 8C21 Hereditary sensory or autonomic neuropathy
E H00265 Hereditary sensory and autonomic neuropathy
E H02580 Hereditary sensory neuropathy with spastic paraplegia
E H01987 Familial dysautonomia
E H01836 Congenital pain insensitivity with anhidrosis
E H00774 Congenital insensitivity to pain
E H00935 Cold-induced sweating syndrome
D 8C2Y Other specified hereditary neuropathy
E H01259 Giant axonal neuropathy
D 8C2Z Hereditary neuropathy, unspecified
C 8C4Y Other specified disorders of nerve root, plexus or peripheral nerves
C 8C4Z Disorders of nerve root, plexus or peripheral nerves, unspecified
B Diseases of neuromuscular junction or muscle
C Myasthenia gravis or certain specified neuromuscular junction disorders
D 8C60 Myasthenia gravis
E H01594 Myasthenia gravis
D 8C61 Congenital myasthenic syndromes
E H00770 Congenital myasthenic syndrome
D 8C62 Lambert-Eaton syndrome
E H01596 Lambert-Eaton myasthenic syndrome
D 8C6Y Other specified myasthenia gravis and neuromuscular junction disorders
D 8C6Z Unspecified myasthenia gravis or neuromuscular junction disorders
C Primary disorders of muscles
D 8C70 Muscular dystrophy
E H00562 Dystrophinopathies
E H01964 Becker muscular dystrophy
E H01963 Duchenne muscular dystrophy
E H00563 Emery-Dreifuss muscular dystrophy
E H00591 Facioscapulohumeral muscular dystrophy
E H00565 Sarcoglycanopathies
E H00593 Limb-girdle muscular dystrophy
E H00567 Limb-girdle muscular dystrophy 1C
E H00592 Calpainopathy
E H01959 Muscular dystrophy-dystroglycanopathy type C
E H01962 Congenital muscular dystrophy type 1D
E H01974 Limb-girdle muscular dystrophy 2B
E H00656 Scapuloperoneal myopathy
E H00120 Muscular dystrophy-dystroglycanopathy type A
E H00590 Congenital muscular dystrophies (CMD/MDC)
E H01284 Marinesco-Sjogren syndrome
E H01340 Bethlem myopathy
E H01341 Collagen VI myopathy
E H01778 Ullrich disease
E H01957 Fukuyama congenital muscular dystrophy
E H01958 Merosin-deficient congenital muscular dystrophy
E H01960 Muscular dystrophy-dystroglycanopathy type B
E H01961 Congenital muscular dystrophy type 1C
E H02307 Muscular dystrophy-dystroglycanopathy
E H00697 X-linked myopathy with postural muscle atrophy
E H02721 Scapulohumeroperoneal myopathy
D 8C71 Myotonic disorders
E H00568 Myotonic dystrophy
E H01777 Schwartz-Jampel syndrome
E H00705 Myotonia congenita
E H00744 Potassium-aggravated myotonia
E H01804 Isaacs syndrome
E H02390 Autosomal recessive neuromyotonia and axonal neuropathy
E H01780 Non-dystrophic myotonia
E H02179 Rippling muscle disease
D 8C72 Congenital myopathies
E H01810 Congenital myopathy
E H00698 Nemaline myopathy
E H00702 Cap myopathy
E H00700 Centronuclear myopathy
E H00699 Central core disease
E H00703 Myosin storage myopathy
E H01291 Spheroid body myopathy
E H01310 Multi-minicore disease
E H01338 Myosclerosis
E H02678 External ophthalmoplegia with rib and vertebral anomalies
E H00701 Congenital fiber type disproportion
E H00657 Reducing body myopathy
E H01781 Autophagic vacuolar myopathy
E H02084 Native American myopathy
E H02258 Tubular aggregate myopathy
E H02320 Vacuolar myopathy with CASQ1 aggregates
E H02321 Early-onset myopathy, areflexia, respiratory distress, and dysphagia
D 8C73 Mitochondrial myopathies
E H01363 NARP syndrome
E H00068 Leber hereditary optic atrophy
E H01200 Fatal infantile cardioencephalomyopathy
E H01347 MELAS syndrome
E H01356 Myoclonic Epilepsy and Ragged-Red Fiber Disease
E H01365 Leber hereditary optic neuropathy and dystonia
E H02201 Mitochondrial myopathy with lactic acidosis
E H02447 Myopathy with extrapyramidal signs
E H02448 Harel-Yoon syndrome
E H02684 Mitochondrial progressive myopathy with congenital cataract and developmental delay
E H02701 Recurrent metabolic crises with variable encephalomyopathic features and neurologic regression
E H02704 Mitochondrial myopathy and ataxia
D 8C74 Periodic paralyses or disorders of muscle membrane excitability
E H00743 Paramyotonia congenita
E H00215 Periodic paralysis
E H00746 Hypokalemic periodic paralysis
E H00745 Hyperkalemic periodic paralysis
E H00747 Thyrotoxic hypokalemic periodic paralysis
E H00748 Andersen-Tawil syndrome
D 8C75 Distal myopathies
E H00566 Distal myopathy with anterior tibial onset
E H00594 Distal myopathy
E H00596 Nonaka myopathy (NM)
E H01965 Miyoshi muscular dystrophy
E H01975 Welander distal myopathy
E H01976 Tibial muscular dystrophy
E H01977 Laing distal myopathy
E H02182 Distal myopathy, Tateyama type
E H02586 Distal myopathy with rimmed vacuoles
D 8C76 Myofibrillar myopathy
E H00595 Myofibrillar myopathies
D 8C77 Ocular myopathy
D 8C78 Malignant hyperthermia or hyperpyrexia
E H02646 Malignant hyperthermia
D 8C7Y Other specified primary disorders of muscles
E H01129 Brody myopathy
D 8C7Z Primary disorders of muscles, unspecified
C Secondary myopathies
D 8C80 Drug-induced myopathy
D 8C81 Autoimmune myopathy
D 8C82 Myopathy in certain specified infectious or parasitic disease
D 8C83 Myopathy in certain specified endocrine disease
D 8C84 Secondary rhabdomyolysis
D 8C8Y Other specified secondary myopathies
D 8C8Z Secondary myopathies, unspecified
C 8D0Y Other specified diseases of neuromuscular junction or muscle
C 8D0Z Diseases of neuromuscular junction or muscle, unspecified
B Cerebral palsy
C 8D20 Spastic cerebral palsy
D H01097 Spastic quadriplegic cerebral palsy
C 8D21 Dyskinetic cerebral palsy
C 8D22 Ataxic cerebral palsy
C 8D23 Worster-Drought syndrome
D H01837 Congenital suprabulbar paresis
C 8D2Y Other specified cerebral palsy
C 8D2Z Cerebral palsy, unspecified
B Nutritional or toxic disorders of the nervous system
C 8D40 Neurological disorders due to nutrient deficiency
C 8D41 Neurological disorders due to an excess of micro or macro nutrients
C 8D42 Neurological disorders due to overweight or obesity in adults or children
C 8D43 Neurological disorders due to toxicity
D H01578 Subacute myelo-optico-neuropathy (SMON)
C 8D44 Alcohol-related neurological disorders
C 8D4Y Other specified nutritional or toxic disorders of the nervous system
C 8D4Z Nutritional or toxic disorders of the nervous system, unspecified
B Disorders of cerebrospinal fluid pressure or flow
C 8D60 Increased intracranial pressure
C 8D61 Intracranial hypotension
C 8D62 Cerebrospinal fluid rhinorrhoea
C 8D63 Cerebrospinal fluid otorrhoea
C 8D64 Hydrocephalus
D H01676 Normal pressure hydrocephalus
C 8D65 Cerebrospinal fluid fistula
C 8D66 Syringomyelia or syringobulbia
D H01675 Syringomyelia
C 8D67 Intracranial arachnoid cyst
C 8D68 Porencephalic cyst
C 8D6Y Other specified disorders of cerebrospinal fluid pressure or flow
C 8D6Z Disorders of cerebrospinal fluid pressure or flow, unspecified
B Disorders of autonomic nervous system
C 8D80 Congenital malformations of the autonomic nervous system
C 8D81 Inherited autonomic nervous system disorders
C 8D82 Autoimmune disorders involving the autonomic nervous system
C 8D83 Autonomic nervous system disorder due to infection
C 8D84 Pure autonomic nervous system failure
C 8D85 Autonomic nervous system disorder due to substances
C 8D86 Autonomic nervous system hyperactivity
C 8D87 Autonomic nervous system disorder due to certain specified neurodegenerative disorder
D H01614 Multiple system atrophy
D H01177 Infantile bilateral striatal necrosis
C 8D88 Autonomic neuropathies
C 8D89 Disorders of orthostatic tolerance
D H01031 Orthostatic intolerance
C 8D8A Focal or segmental autonomic disorders
C 8D8B Disorders affecting autonomic synaptic neurotransmission
C 8D8C Autonomic dysreflexia
C 8D8D Hypoglycaemia unawareness
C 8D8Y Other specified disorders of autonomic nervous system
C 8D8Z Disorders of autonomic nervous system, unspecified
B Human prion diseases
C 8E00 Sporadic Creutzfeldt-Jakob Disease
D H00061 Prion disease
C 8E01 Acquired prion disease
D H00061 Prion disease
C 8E02 Genetic prion diseases
D H00061 Prion disease
C 8E03 Variably protease sensitive prionopathy
D H00061 Prion disease
C 8E0Y Other specified human prion diseases
D H00061 Prion disease
C 8E0Z Human prion diseases, unspecified
B Disorders of consciousness
C 8E20 Persistent vegetative state
C 8E21 Permanent vegetative state
C 8E22 Minimally conscious state
C 8E2Y Other specified disorders of consciousness
C 8E2Z Disorders of consciousness, unspecified
B Other disorders of the nervous system
C 8E40 Disorders of the meninges excluding infection
D H01668 Neoplastic meningitis
C 8E41 Pachymeningitis
C 8E42 Superficial siderosis of the nervous system
D H01846 Superficial siderosis
C 8E43 Pain disorders
D H01638 Neuropathic pain
D H00772 Paroxysmal extreme pain disorder
D H01391 Familial episodic pain syndrome
C 8E44 Post anoxic brain damage
C 8E45 Locked-in syndrome
C 8E46 Reye syndrome
C 8E47 Encephalopathy, not elsewhere classified
D H01841 Acute encephalopathy with biphasic seizures and late reduced diffusion
D H02261 PEBAT
D H02262 PEBEL
C 8E48 Encephalitis, not elsewhere classified
C 8E49 Postviral fatigue syndrome
C 8E4A Paraneoplastic or autoimmune disorders of the nervous system
D H01452 Pediatric autoimmune neuropsychiatric disorders associated with streptococcal infection
C 8E4Y Other specified disorders of the nervous system
D H02473 Leukoencephalopathy, brain calcifications, and cysts
D H02476 Childhood-onset neurodegeneration with brain atrophy
D H02489 Mild encephalopathy with reversible myelin vacuolization
D H02572 Neurodegeneration, childhood-onset, stress-induced, with variable ataxia and seizures
B Postprocedural disorders of the nervous system
C 8E60 Post ventricular shunting leak
C 8E61 Post radiation injury of the nervous system
C 8E62 Postprocedural meningitis
C 8E63 Post pump encephalopathy
C 8E64 Multifocal cerebral infarctions
C 8E66 Intracranial hypotension due to lumbar puncture
B 8E7Y Other specified diseases of the nervous system
B 8E7Z Diseases of the nervous system, unspecified
#
A09 Diseases of the visual system
B Disorders of the ocular adnexa or orbit
C Disorders of eyelid or peri-ocular area
D 9A00 Congenital malposition of eyelids
D 9A01 Infectious disorders of eyelid
E H01644 Blepharitis
D 9A02 Inflammatory disorders of eyelid
E H01644 Blepharitis
D 9A03 Acquired malposition of eyelid
D 9A04 Acquired disorders of eyelashes
D 9A05 Movement disorders of eyelid
D 9A06 Certain specified disorders of eyelid
D 9A0Y Other specified disorders of eyelid or peri-ocular area
D 9A0Z Disorders of eyelid or peri-ocular area, unspecified
C Disorders of lacrimal apparatus
D 9A10 Disorders of lacrimal gland
D 9A11 Disorders of lacrimal drainage system
D 9A1Y Other specified disorders of lacrimal apparatus
D 9A1Z Disorders of lacrimal apparatus, unspecified
C Disorders of orbit
D 9A20 Displacement of eyeball
D 9A21 Orbital infection
D 9A22 Orbital inflammation
D 9A23 Orbital cyst
D 9A24 Bony deformity of orbit
D 9A25 Soft tissue deformity of orbit
D 9A26 Combined bony and soft tissue deformity of orbit
D 9A2Y Other specified disorders of orbit
D 9A2Z Disorders of orbit, unspecified
C 9A4Y Other specified disorders of the ocular adnexa or orbit
C 9A4Z Disorders of the ocular adnexa or orbit, unspecified
B Disorders of the eyeball anterior segment
C Disorders of conjunctiva
D 9A60 Conjunctivitis
E H01366 Bacterial conjunctivitis
D 9A61 Certain specified disorders of conjunctiva
D 9A62 Mucous membrane pemphigoid with ocular involvement
D 9A6Y Other specified disorders of conjunctiva
D 9A6Z Disorders of conjunctiva, unspecified
C Disorders of the cornea
D 9A70 Hereditary corneal dystrophies
E H00960 Fuchs corneal dystrophy
E H00963 Congenital hereditary endothelial dystrophy
E H00726 Meesmann corneal dystrophy
E H00951 Reis-Bucklers corneal dystrophy
E H00952 Thiel-Behnke dystrophies
E H00953 Gelatinous drop-like corneal dystrophy
E H00954 Macular corneal dystrophy
E H00955 Granular corneal dystrophies
E H00956 Lattice corneal dystrophies
E H00957 Fleck corneal dystrophy
E H00958 Congenital stromal corneal dystrophy
E H00959 Schnyder corneal dystrophy
E H01221 Epithelial basement membrane corneal dystrophy
D 9A71 Infectious keratitis
D 9A72 Traumatic keratitis
D 9A73 Exposure keratitis
D 9A74 Neurotrophic keratitis
D 9A75 Autoimmune keratitis
D 9A76 Corneal ulcer
D 9A77 Corneal scars or opacities
D 9A78 Certain specified disorders of cornea
E H00789 Keratoconus
E H02426 EDICT syndrome
D 9A79 Keratoconjunctivitis sicca
E H01641 Dry eye disease
D 9A7Y Other specified disorders of the cornea
E H01273 Autosomal dominant keratitis
D 9A7Z Disorders of the cornea, unspecified
C Disorders of the anterior chamber
D 9A80 Hyphaema
D 9A81 Parasites in the anterior chamber of the eye
D 9A82 Cyst in the anterior chamber of the eye
D 9A83 Flat anterior chamber hypotony of eye
D 9A8Y Other specified disorders of the anterior chamber
D 9A8Z Disorders of the anterior chamber, unspecified
C Disorders of the anterior uvea
D 9A90 Degeneration of iris or ciliary body
D 9A91 Cyst of iris or ciliary body
D 9A92 Persistent pupillary membranes
D 9A93 Adhesions or disruptions of iris or ciliary body
D 9A94 Certain specified disorders of iris or ciliary body
D 9A96 Anterior uveitis
D 9A9Y Other specified disorders of the anterior uvea
D 9A9Z Disorders of the anterior uvea, unspecified
C Functional disorders of the pupil
D 9B00 Disorders of the afferent pupillary system
D 9B01 Disorders of the efferent pupillary system
D 9B02 Light-near dissociations
D 9B0Y Other specified functional disorders of the pupil
D 9B0Z Functional disorders of the pupil, unspecified
C Disorders of lens
D 9B10 Cataract
E H01202 Cataract
E H02204 Hereditary hyperferritinaemia-cataract syndrome
D 9B11 Certain specified disorders of lens
D 9B1Z Disorders of lens, unspecified
C 9B3Y Other specified disorders of the eyeball anterior segment
C 9B3Z Disorders of the eyeball anterior segment, unspecified
B Disorders of the eyeball posterior segment
C Disorders of sclera
D 9B50 Episcleritis
D 9B51 Scleritis
D 9B52 Scleral staphyloma
D 9B5Y Other specified disorders of sclera
D 9B5Z Disorders of sclera, unspecified
C Disorders of the choroid
D 9B60 Choroidal degeneration
D 9B61 Choroidal dystrophy
E H00732 Sorsby fundus dystrophy
E H01116 Choroideremia
E H01768 Central areolar choroidal dystrophy
E H01880 Autosomal recessive microcephaly and chorioretinopathy
E H02107 Bietti crystalline corneoretinal dystrophy
D 9B62 Chorioretinal scars
D 9B63 Choroidal haemorrhage or rupture
D 9B64 Choroidal detachment
D 9B65 Choroiditis
D 9B66 Intermediate choroiditis
D 9B6Y Other specified disorders of the choroid
D 9B6Z Disorders of the choroid, unspecified
C Disorders of the retina
D 9B70 Inherited retinal dystrophies
E H00481 Cone-rod dystrophy and cone dystrophy
E H00527 Retinitis pigmentosa
E H00814 Vitelliform macular dystrophy
E H00819 Stargardt disease
E H00825 Familial flecked retina syndrome
E H00837 Leber congenital amaurosis
E H00971 Achromatopsia
E H00974 Blue cone monochromacy
E H01009 Newfoundland rod-cone dystrophy
E H01130 Late-onset retinal degeneration
E H01770 Macular dystrophy
E H01890 Pattern dystrophies of the retinal pigment epithelium
E H02075 Enhanced S-cone syndrome
E H02077 Snowflake vitreoretinal degeneration
E H02078 Autosomal dominant vitreoretinochoroidopathy
E H02108 Basal laminar drusen
E H02110 Doyne honeycomb retinal dystrophy
E H02288 Retinal dystrophy with inner retinal dysfunction and ganglion cell abnormalities
E H02289 Retinal dystrophy with or without extraocular anomalies
E H02290 Retinal dystrophy and iris coloboma with or without congenital cataract
E H02291 Retinal dystrophy, iris coloboma, and comedogenic acne syndrome
E H02341 Goldmann-Favre syndrome
E H02440 Fleck retina, familial benign
D 9B71 Retinopathy
E H01457 Diabetic retinopathy
E H02559 Microvascular complications of diabetes
D 9B72 Inflammatory diseases of the retina
D 9B73 Retinal detachments or breaks
E H01766 Juvenile retinoschisis
D 9B74 Retinal vascular occlusions
D 9B75 Macular disorders
E H00821 Age-related macular degeneration
E H01480 Idiopathic macular hole
E H01010 Occult macular dystrophy
E H01651 Macular edema
D 9B76 Degenerative high myopia
D 9B77 Eales disease
D 9B78 Certain specified retinal disorders
E H01000 Retinal vasculopathy with cerebral leukodystrophy
E H02251 Cerebroretinal microangiopathy with calcifications and cysts
E H01798 Autosomal dominant neovascular inflammatory vitreoretinopathy
E H01180 Sveinsson chorioretinal atrophy (SCRA)
D 9B7Y Other specified disorders of the retina
E H00690 Aland Island eye disease
E H01088 Pigmented paravenous chorioretinal atrophy
E H02469 Cone-rod synaptic disorder
E H02642 Retinal arterial macroaneurysm with supravalvular pulmonic stenosis
D 9B7Z Disorders of the retina, unspecified
C Disorders of the vitreous body
D 9B80 Inherited vitreoretinal disorders
E H00805 Vitreoretinal degeneration
E H02073 Wagner syndrome
D 9B81 Posterior vitreous detachment
D 9B82 Vitreous prolapse
D 9B83 Vitreous haemorrhage
D 9B84 Vitreous opacities, membranes or strands
D 9B8Y Other specified disorders of the vitreous body
D 9B8Z Disorders of the vitreous body, unspecified
C 9C0Y Other specified disorders of the eyeball posterior segment
C 9C0Z Disorders of the eyeball posterior segment, unspecified
B Disorders of the eyeball affecting both anterior and posterior segments
C 9C20 Panuveitis
C 9C21 Endophthalmitis
C 9C22 Eyeball deformity
C 9C2Y Other specified disorders of the eyeball affecting both anterior and posterior segments
C 9C2Z Disorders of the eyeball affecting both anterior and posterior segments, unspecified
B Disorders of the visual pathways or centres
C 9C40 Disorder of the optic nerve
D H01719 Optic neuropathy
D H01717 Optic neuritis
D H00068 Leber hereditary optic atrophy
D H01020 Optic atrophy
D H01365 Leber hereditary optic neuropathy and dystonia
D H01378 Bosch-Boonstra optic atrophy syndrome
C 9C41 Disorder of optic chiasm
C 9C42 Disorder of post chiasmal visual pathways
C 9C43 Disorder of visual cortex
C 9C44 Disorder of higher visual centres
C 9C4Y Other specified disorders of the visual pathways or centres
C 9C4Z Disorders of the visual pathways or centres, unspecified
B Glaucoma or glaucoma suspect
C 9C60 Glaucoma suspect
C 9C61 Glaucoma
D H00612 Primary open angle glaucoma
D H01203 Primary congenital glaucoma
C 9C6Y Other specified glaucoma or glaucoma suspect
C 9C6Z Glaucoma or glaucoma suspect, unspecified
B Strabismus or ocular motility disorders
C 9C80 Non paralytic strabismus
C 9C81 Ocular motor nerve palsies
C 9C82 Disorders of extraocular muscles
D H01118 Progressive external ophthalmoplegia
D H01355 Kearns-Sayre syndrome
D H01395 Autosomal recessive progressive external ophthalmoplegia
D H00704 Oculopharyngeal muscular dystrophy
D H02513 Oculopharyngodistal myopathy
D H00633 Duane retraction syndrome
D H00838 Congenital fibrosis of the extraocular muscles
D H02151 Hereditary congenital facial paresis
D H02693 Congenital cranial dysinnervation disorder with absent corneal reflex and developmental delay
C 9C83 Disorders of binocular movement
D H02450 Horizontal gaze palsy with progressive scoliosis
C 9C84 Nystagmus
D H00776 Congenital motor nystagmus (CMN)
C 9C85 Certain specified irregular eye movements
C 9C8Y Other specified strabismus or ocular motility disorders
C 9C8Z Strabismus or ocular motility disorders, unspecified
B Disorders of refraction or accommodation
C 9D00 Disorders of refraction
D H02041 Myopia
C 9D01 Disorders of accommodation
C 9D0Y Other specified disorders of refraction or accommodation
C 9D0Z Disorders of refraction or accommodation, unspecified
B Postprocedural disorders of eye or ocular adnexa
C 9D20 Bullous aphakic keratopathy following cataract surgery
C 9D21 Cataract lens fragments in eye following cataract surgery
C 9D22 Chorioretinal scars after surgery for detachment
C 9D23 Conjunctival blebitis after glaucoma surgery
C 9D24 Complications with glaucoma drainage devices
C 9D25 Glaucoma due to ocular surgery or laser
B Impairment of visual functions
C 9D41 Impairment of visual field
C 9D42 Patterns of visual field impairment
C 9D43 Impairment of contrast vision
C 9D44 Impairment of colour vision
D H00971 Achromatopsia
D H00976 Colorblindness
C 9D45 Impairment of light sensitivity
D H00787 Congenital stationary night blindness
C 9D46 Impairment of binocular functions
C Subjective visual experiences
D 9D50 Visual discomfort
D 9D51 Transient visual loss
D 9D52 Hemifield losses
D 9D53 Entoptic phenomena
D 9D54 Visual illusions
D 9D55 Nonorganic visual loss
D 9D56 Visual release hallucinations
D 9D5Y Other specified subjective visual experiences
D 9D5Z Subjective visual experiences, unspecified
C 9D7Y Other specified impairment of visual functions
D H00973 Bradyopsia
C 9D7Z Impairment of visual functions, unspecified
B Vision impairment
C 9D90 Vision impairment including blindness
C 9D92 Specific vision dysfunctions
C 9D93 Complex vision-related dysfunctions
C 9D94 Impairment of presenting visual acuity
C 9D95 Impairment of best corrected visual acuity
C 9D96 Impairment of uncorrected visual acuity
C 9D9Y Other specified vision impairment
C 9D9Z Vision impairment, unspecified
B 9E1Y Other specified diseases of the visual system
C H00169 Ocular albinism
B 9E1Z Diseases of the visual system, unspecified
#
A10 Diseases of the ear or mastoid process
B Diseases of external ear
C Infectious diseases of external ear
D AA00 Abscess of external ear
D AA01 Cellulitis of external ear
D AA02 Malignant otitis externa
D AA03 Otomycosis
D AA04 Perichondritis of external ear
D AA0Y Other specified infectious diseases of external ear
D AA0Z Infectious diseases of external ear, unspecified
C Otitis externa
D Noninfectious inflammation of external ear
E AA10 Seborrhoeic otitis externa
E AA11 Acute noninfectious otitis externa
E AA12 Chondrodermatitis nodularis
E AA13 Chronic otitis externa
E AA1Y Other specified noninfectious inflammation of external ear
E AA1Z Noninfectious inflammation of external ear, unspecified
D AA3Y Other specified otitis externa
D AA3Z Otitis externa, unspecified
C Noninflammatory disorders of the external ear
D AA40 Acquired deformity of external auditory canal
D AA41 Acquired deformity of pinna
D AA42 Impacted cerumen
D AA4Y Other specified noninflammatory disorders of the external ear
D AA4Z Noninflammatory disorders of the external ear, unspecified
C AA6Z Diseases of external ear, unspecified
B Diseases of middle ear or mastoid
C Otitis media
D Nonsuppurative otitis media
E AA80 Acute serous or mucoid otitis media
E AA81 Acute nonserous nonsuppurative otitis media
E AA82 Chronic serous or mucoid otitis media
E AA83 Noninfected otitis media with effusion
E AA8Z Nonsuppurative otitis media, unspecified
D Suppurative otitis media
E AA90 Acute suppurative otitis media
E AA91 Chronic suppurative otitis media
E AA9Y Other specified suppurative otitis media
E AA9Z Suppurative otitis media, unspecified
D AB00 Acute otitis media
D AB01 Chronic otitis media
D AB0Y Other specified otitis media
D AB0Z Otitis media, unspecified
C AB10 Disorders of Eustachian tube
C AB11 Mastoiditis or related conditions
C AB12 Cholesteatoma of middle ear
C AB13 Perforation of tympanic membrane
C AB14 Acute myringitis
C AB15 Chronic myringitis
C AB16 Tympanosclerosis
C AB17 Adhesive middle ear disease
C AB18 Discontinuity or dislocation of ear ossicles
C AB19 Acquired abnormalities of ear ossicles not related to discontinuity or dislocation
C AB1A Polyp of middle ear
C AB1B Middle ear cicatrix
C AB1Y Other specified diseases of middle ear or mastoid
C AB1Z Diseases of middle ear or mastoid, unspecified
B Diseases of inner ear
C AB30 Acute vestibular syndrome
C AB31 Episodic vestibular syndrome
D H01495 Meniere disease
D H01706 Delayed endolymphatic hydrops
C AB32 Chronic vestibular syndrome
C AB33 Otosclerosis
C AB34 Disorders of vestibular function
C AB35 Labyrinthine fistula
C AB36 Labyrinthine dysfunction
C AB37 Noise effects on inner ear
C AB3Y Other specified diseases of inner ear
C AB3Z Diseases of inner ear, unspecified
B Disorders with hearing impairment
C AB50 Congenital hearing impairment
D H00604 Deafness, autosomal dominant
D H00605 Deafness, autosomal recessive
D H01209 Deafness, X-linked
D H02336 Deafness, Y-linked
D H02636 Sinoatrial node dysfunction and deafness
C AB51 Acquired hearing impairment
D H01704 Sudden sensorineural hearing loss
D H01705 Bilateral sudden sensorineural hearing loss
C AB52 Deafness not otherwise specified
C AB53 Ototoxic hearing loss
C AB54 Presbycusis
C AB55 Sudden idiopathic hearing loss
C AB56 Hereditary hearing loss
C AB57 Auditory synaptopathy or neuropathy
D H02339 Auditory neuropathy
C AB5Y Other specified disorders with hearing impairment
C AB5Z Disorders with hearing impairment, unspecified
B Disorders of ear, not elsewhere classified
C AB70 Otalgia or effusion of ear
C AB71 Degenerative or vascular disorders of ear
C AB72 Disorders of acoustic nerve
C AB73 Atrophy ear
C AB7Y Other specified disorders of ear, not elsewhere classified
B Postprocedural disorders of ear or mastoid process
C AB90 Recurrent cholesteatoma of postmastoidectomy cavity
C AB91 Mucosal cyst of postmastoidectomy cavity
C AB92 Granulation of postmastoidectomy cavity
C AB93 Chronic inflammation of postmastoidectomy cavity
B AC0Y Other specified diseases of the ear or mastoid process
B AC0Z Diseases of the ear or mastoid process, unspecified
#
A11 Diseases of the circulatory system
B Hypertensive diseases
C BA00 Essential hypertension
D H01633 High blood pressure
C BA01 Hypertensive heart disease
C BA02 Hypertensive renal disease
C BA03 Hypertensive crisis
C BA04 Secondary hypertension
D H00242 Liddle syndrome
D H00603 Hypertension exacerbated in pregnancy
B Hypotension
C BA20 Idiopathic hypotension
C BA21 Orthostatic hypotension
C BA2Y Other specified hypotension
C BA2Z Hypotension, unspecified
B Ischaemic heart diseases
C Acute ischaemic heart disease
D BA40 Angina pectoris
E H01632 Angina pectoris
D BA41 Acute myocardial infarction
E H01730 Myocardial infarction
D BA42 Subsequent myocardial infarction
D BA43 Coronary thrombosis not resulting in myocardial infarction
D BA4Z Acute ischaemic heart disease, unspecified
C Chronic ischaemic heart disease
D BA50 Old myocardial infarction
D BA51 Ischaemic cardiomyopathy
D BA52 Coronary atherosclerosis
D BA5Y Other specified chronic ischaemic heart disease
D BA5Z Chronic ischaemic heart disease, unspecified
C BA60 Certain current complications following acute myocardial infarction
C BA6Z Ischaemic heart diseases, unspecified
B Diseases of coronary artery
C BA81 Coronary artery aneurysm
C BA82 Coronary artery dissection
C BA83 Coronary artery fistula, acquired
C BA84 Chronic total occlusion of coronary artery
C BA85 Coronary vasospastic disease
C BA86 Coronary microvascular disease
C BA8Y Other specified diseases of coronary artery
C BA8Z Diseases of coronary artery, unspecified
D H01742 Coronary artery disease
B Pulmonary heart disease or diseases of pulmonary circulation
C BB00 Pulmonary thromboembolism
C BB01 Pulmonary hypertension
D H01619 Primary pulmonary hypertension
D H01621 Pulmonary arterial hypertension
D H01866 Pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis
D H01622 Chronic thromboembolic pulmonary hypertension
C BB02 Certain specified diseases of pulmonary vessels
C BB03 Acquired pulmonary venous abnormality
C BB0Y Other specified pulmonary heart disease or diseases of pulmonary circulation
C BB0Z Pulmonary heart disease or diseases of pulmonary circulation, unspecified
B Pericarditis
C BB20 Acute pericarditis
C BB21 Chronic rheumatic pericarditis
C BB22 Constrictive pericarditis
C BB23 Cardiac tamponade
C BB24 Haemopericardium
C BB25 Pericardial effusion
C BB2Y Other specified pericarditis
C BB2Z Pericarditis, unspecified
B Acute or subacute endocarditis
C BB40 Acute or subacute infectious endocarditis
C BB41 Myoendocarditis
C BB42 Periendocarditis
C BB4Y Other specified acute or subacute endocarditis
C BB4Z Acute or subacute endocarditis, unspecified
B Heart valve diseases
C Mitral valve disease
D BB60 Mitral valve stenosis
D BB61 Mitral valve insufficiency
D BB62 Mitral valve prolapse
E H01868 Mitral valve prolapse
D BB63 Mitral valve stenosis with insufficiency
D BB64 Mitral valvar abscess
D BB65 Mitral valve rupture
D BB6Y Other specified mitral valve disease
D BB6Z Mitral valve disease, unspecified
C Aortic valve disease
D BB70 Aortic valve stenosis
D BB71 Aortic valve insufficiency
D BB72 Aortic valve stenosis with insufficiency
D BB73 Aortic valvar abscess
D BB74 Aortic valvar prolapse
D BB7Y Other specified aortic valve disease
D BB7Z Aortic valve disease, unspecified
C Tricuspid valve disease
D BB80 Tricuspid valve stenosis
D BB81 Tricuspid valve insufficiency
D BB82 Tricuspid valve stenosis with insufficiency
D BB83 Tricuspid valvular abscess
D BB84 Tricuspid valve rupture
D BB8Y Other specified tricuspid valve disease
D BB8Z Tricuspid valve disease, unspecified
C Pulmonary valve disease
D BB90 Pulmonary valve stenosis
D BB91 Pulmonary valve insufficiency
D BB92 Pulmonary valve stenosis with insufficiency
D BB93 Pulmonary valvar abscess
D BB9Y Other specified pulmonary valve disease
D BB9Z Pulmonary valve disease, unspecified
C BC00 Multiple valve disease
C BC01 Prosthetic valve disease
C BC02 Acquired abnormality of congenitally malformed valve
C BC0Z Heart valve diseases, unspecified
D H00334 Bacterial endocarditis
B BC20 Chronic rheumatic heart diseases, not elsewhere classified
B Diseases of the myocardium or cardiac chambers
C BC40 Acquired atrial abnormality
C BC41 Acquired ventricular abnormality
C BC42 Myocarditis
D H00295 Viral myocarditis
C BC43 Cardiomyopathy
D H00294 Dilated cardiomyopathy
D H02697 Long-Olsen-Distelmaier syndrome
D H00292 Hypertrophic cardiomyopathy
D H01219 Restrictive cardiomyopathy
D H00293 Arrhythmogenic right ventricular cardiomyopathy
D H00669 Naxos disease
D H02094 Carvajal syndrome
D H02498 Diabetic cardiomyopathy
D H02683 Arrhythmogenic cardiomyopathy with variable ectodermal abnormalities
C BC44 Noncompaction cardiomyopathy
D H01216 Left ventricular noncompaction
C BC45 Cardiomegaly
C BC46 Intracardiac thrombosis
C BC4Y Other specified diseases of the myocardium or cardiac chambers
C BC4Z Diseases of the myocardium or cardiac chambers, unspecified
B Cardiac arrhythmia
C BC60 Atrial premature depolarization
C BC61 Junctional premature depolarization
C BC62 Accessory pathway
C BC63 Conduction disorders
D H01263 Progressive cardiac conduction defect (PCCD)
D H02125 Cardiac conduction disease with or without dilated cardiomyopathy
C BC64 Sudden arrhythmic death syndrome
C BC65 Cardiac arrhythmia associated with genetic disorder
D H00720 Long QT syndrome
D H00748 Andersen-Tawil syndrome
D H02091 Jervell and Lange-Nielsen syndrome
D H00728 Brugada syndrome
D H00725 Short QT syndrome
D H00730 Familial idiopathic ventricular fibrillation
D H01019 Catecholaminergic polymorphic ventricular tachycardia
D H02122 Chronic atrial and intestinal dysrhythmia
C Ventricular rhythm disturbance
D BC70 Ventricular premature depolarization
D BC71 Ventricular tachyarrhythmia
E H02269 Familial ventricular tachycardia
D BC7Y Other specified ventricular rhythm disturbance
D BC7Z Ventricular rhythm disturbance, unspecified
C Supraventricular rhythm disturbance
D BC80 Supraventricular bradyarrhythmia
E H02636 Sinoatrial node dysfunction and deafness
E H00729 Sick sinus syndrome
E H02674 Atrial standstill
D BC81 Supraventricular tachyarrhythmia
E H00731 Atrial fibrillation
E H01154 Wolff-Parkinson-White (WPW) syndrome
D BC8Y Other specified supraventricular rhythm disturbance
D BC8Z Supraventricular rhythm disturbance, unspecified
C BC90 Rhythm disturbance at level of atrioventricular junction
C BC91 Pacemaker or implantable cardioverter defibrillator battery at end of battery life
C BC9Y Other specified cardiac arrhythmia
C BC9Z Cardiac arrhythmia, unspecified
B Heart failure
C BD10 Congestive heart failure
C BD11 Left ventricular failure
C BD12 High output syndromes
C BD13 Right ventricular failure
C BD14 Biventricular failure
C BD1Y Other specified heart failure
D H01631 Acute heart failure
C BD1Z Heart failure, unspecified
B Diseases of arteries or arterioles
C BD30 Acute arterial occlusion
C Chronic arterial occlusive disease
D BD40 Atherosclerotic chronic arterial occlusive disease
E H01626 Arteriosclerosis obliterans
E H01629 Chronic arterial occlusive disease
E H02505 Atherosclerosis
D BD41 Non-atherosclerotic chronic arterial occlusive disease
E H01629 Chronic arterial occlusive disease
E H02719 Multifocal fibromuscular dysplasia
D BD42 Raynaud phenomenon
E H01620 Raynaud syndrome
E H01629 Chronic arterial occlusive disease
D BD4Y Other specified chronic arterial occlusive disease
D BD4Z Chronic arterial occlusive disease, unspecified
C BD50 Aortic aneurysm or dissection
D H00801 Familial thoracic aortic aneurysm and dissection
C BD51 Arterial aneurysm or dissection, excluding aorta
C BD52 Certain specified disorders of arteries or arterioles
D H00824 Calcification of joints and arteries
D H01002 Generalized arterial calcification of infancy
C BD53 Secondary disorders of arteries and arterioles
C BD54 Diabetic foot ulcer
C BD55 Asymptomatic stenosis of intracranial or extracranial artery
C BD56 Asymptomatic occlusion of intracranial or extracranial artery
C BD5Y Other specified diseases of arteries or arterioles
C BD5Z Diseases of arteries or arterioles, unspecified
B Diseases of veins
C BD70 Superficial thrombophlebitis
C BD71 Deep vein thrombosis
D H01723 Deep vein thrombosis
C BD72 Venous thromboembolism
C BD73 Acquired systemic vein abnormality
C BD74 Chronic peripheral venous insufficiency of lower extremities
C BD75 Venous varicosities of sites other than lower extremity
C BD7Y Other specified diseases of veins
C BD7Z Diseases of veins, unspecified
B Disorders of lymphatic vessels or lymph nodes
C BD90 Lymphadenitis
D H01397 Tick-borne lymphadenopathy
C BD91 Lymphangitis
C BD92 Lymphangiectasia
C BD93 Lymphoedema
D H00535 Lymphatic malformation
D H01017 Choanal atresia and lymphedema
D H02167 Lymphedema-distichiasis syndrome
D H02168 Hypotrichosis-lymphedema-telangiectasia syndrome
D H02169 Hennekam lymphangiectasia-lymphedema syndrome
C BD9Y Other specified disorders of lymphatic vessels or lymph nodes
C BD9Z Disorders of lymphatic vessels or lymph nodes, unspecified
B Postprocedural disorders of circulatory system
C BE10 Postcardiotomy syndrome
C BE11 Other functional disturbances following cardiac surgery
C BE12 Postprocedural valve disorders
C BE13 Postprocedural true or false aortic aneurysm
C BE14 Postprocedural disorder of circulatory system following repair of congenital heart or great vessel anomaly
C BE15 Postprocedural pulmonary arterial tree disorder
C BE16 Postprocedural pulmonary venous disorder
C BE17 Postprocedural residual or recurrent interatrial communication
C BE19 Postprocedural ventricular abnormality
C BE1A Cardiac transplant associated coronary allograft vasculopathy
C BE1B Lymphoedema due to surgery or radiotherapy
C BE1C Inferior caval vein obstruction due to foreign body
C BE1D Superior caval vein obstruction due to foreign body
C BE1E Postprocedural right atrial complication
C BE1F Postprocedural left atrial complication
B BE2Y Other specified diseases of the circulatory system
B BE2Z Diseases of the circulatory system, unspecified
#
A12 Diseases of the respiratory system
B Upper respiratory tract disorders
C CA00 Acute nasopharyngitis
D H02442 Common cold
C CA01 Acute sinusitis
C CA02 Acute pharyngitis
C CA03 Acute tonsillitis
C CA04 Acute laryngopharyngitis
C CA05 Acute laryngitis or tracheitis
C CA06 Acute obstructive laryngitis or epiglottitis
C CA07 Acute upper respiratory infections of multiple and unspecified sites
C CA08 Vasomotor or allergic rhinitis
D H01360 Allergic rhinitis
C CA09 Chronic rhinitis, nasopharyngitis or pharyngitis
C CA0A Chronic rhinosinusitis
D H01765 Eosinophilic sinusitis
C CA0B Silent sinus syndrome
C CA0C Cyst or mucocele of nose or nasal sinus
C CA0D Deviated nasal septum
C CA0E Hypertrophy of nasal turbinates
C CA0F Chronic diseases of tonsils or adenoids
C CA0G Chronic laryngitis or laryngotracheitis
C CA0H Diseases of vocal cords or larynx, not elsewhere classified
C CA0J Nasal polyp
C CA0K Abscess of upper respiratory tract
C CA0Y Other specified upper respiratory tract disorders
C CA0Z Upper respiratory tract disorders, unspecified
B Certain lower respiratory tract diseases
C CA20 Bronchitis
C CA21 Emphysema
C CA22 Chronic obstructive pulmonary disease
D H01714 Chronic obstructive pulmonary disease (COPD)
D H01873 Obliterative bronchiolitis
C CA23 Asthma
D H00079 Asthma
D H01191 Asthma with nasal polyps and aspirin intolerance
C CA24 Bronchiectasis
D H00892 Bronchiectasis with or without elevated sweat chloride
C CA25 Cystic fibrosis
D H00218 Cystic fibrosis
C CA26 Chronic bronchiolitis
D H01873 Obliterative bronchiolitis
D H01713 Diffuse panbronchiolitis
C CA27 Tracheobronchitis
C CA2Y Other specified lower respiratory tract disease
C CA2Z Lower respiratory tract disease, unspecified
B Lung infections
C CA40 Pneumonia
D H00351 Chlamydial pneumonia
D H00304 Haemophilus influenzae infection
D H00301 Klebsiella infection
D H00341 Mycoplasma pneumonia
D H01441 Pseudomonas aeruginosa infection
D H00333 Streptococcal infection
D H01321 Pneumococcal disease
D H00401 Respiratory syncytial virus infection
D H00400 Parainfluenza infection
D H01063 Human metapneumovirus infection
D H01521 Pneumocystis pneumonia
C CA41 Acute bronchiolitis
D H00401 Respiratory syncytial virus infection
C CA42 Acute bronchitis
D H00341 Mycoplasma pneumonia
D H00401 Respiratory syncytial virus infection
D H00400 Parainfluenza infection
D H00304 Haemophilus influenzae infection
C CA43 Abscess of lung or mediastinum
C CA44 Pyothorax
C CA45 Respiratory infections, not elsewhere classified
C CA4Y Other specified lung infections
C CA4Z Lung infections, unspecified
B Lung diseases due to external agents
C CA60 Pneumoconiosis
C Pneumonitis
D CA70 Hypersensitivity pneumonitis due to organic dust
E H00346 Extrinsic allergic alveolitis
E H01411 Saccharomonospora viridis infection
D CA71 Pneumonitis due to solids and liquids
D CA72 Mendelson syndrome
D CA7Y Other specified pneumonitis
D CA7Z Pneumonitis, unspecified
C CA80 Airway disease due to specific organic dust
C CA81 Respiratory conditions due to inhalation of chemicals, gases, fumes or vapours
C CA82 Respiratory conditions due to other external agents
C CA8Y Other specified lung diseases due to external agents
C CA8Z Lung diseases due to external agents, unspecified
B Respiratory diseases principally affecting the lung interstitium
C CB00 Acute respiratory distress syndrome
C CB01 Pulmonary oedema
C CB02 Pulmonary eosinophilia
C CB03 Idiopathic interstitial pneumonitis
D H01716 Idiopathic interstitial pneumonias
D H01299 Idiopathic pulmonary fibrosis
C CB04 Primary interstitial lung diseases specific to infancy or childhood
D H00830 Alveolar capillary dysplasia with misalignment of pulmonary veins
D H00217 Pulmonary alveolar proteinosis
D H01122 Congenital pulmonary alveolar proteinosis
D H02124 Interstitial lung and liver disease
D H00913 Brain-lung-thyroid syndrome
C CB05 Interstitial lung diseases associated with systemic diseases
D H02466 Rajab interstitial lung disease with brain calcification
C CB06 Pulmonary alveolar microlithiasis
D H01298 Pulmonary alveolar microlithiasis
C CB07 Lymphangioleiomyomatosis
D H00896 Lymphangioleiomyomatosis
C CB0Y Other specified respiratory diseases principally affecting the lung interstitium
C CB0Z Respiratory diseases principally affecting the lung interstitium, unspecified
B Pleural, diaphragm or mediastinal disorders
C CB20 Pleural plaque
C CB21 Pneumothorax
D H01110 Pneumothorax
C CB22 Diseases of mediastinum, not elsewhere classified
C CB23 Disorders of diaphragm
C CB24 Chylous effusion
C CB25 Fibrothorax
C CB26 Haemothorax
C CB27 Pleural effusion
C CB2Y Other specified pleural, diaphragm or mediastinal disorders
C CB2Z Pleural, diaphragm or mediastinal disorders, unspecified
B CB40 Certain diseases of the respiratory system
B CB41 Respiratory failure
B Postprocedural disorders of the respiratory system
C CB60 Tracheostomy malfunction
C CB61 Chronic pulmonary insufficiency following surgery
C CB62 Postprocedural subglottic stenosis
C CB63 Postprocedural stenosis of the trachea
C CB64 Transfusion related acute lung injury
B CB7Z Diseases of the respiratory system, unspecified
#
A13 Diseases of the digestive system
B Diseases or disorders of orofacial complex
C DA00 Disorders of lips
C DA01 Disorders of oral mucosa
D H02648 Acantholytic blistering of the oral and laryngeal mucosa
C DA02 Miscellaneous specified disorders of lips or oral mucosa
D H00724 White sponge nevus
C DA03 Diseases of tongue
C DA04 Diseases of salivary glands
C DA05 Cysts of oral or facial-neck region
C DA06 Certain specified diseases of jaws
C DA07 Disorders of tooth development or eruption
D H00680 Primary failure of tooth eruption
C DA08 Diseases of hard tissues of teeth
D H01331 Dental caries
C DA09 Diseases of pulp or periapical tissues
C DA0A Certain specified disorders of teeth or supporting structures
C DA0B Gingival diseases
C DA0C Periodontal disease
D H01408 Periodontal disease
D H02050 Prepubertal periodontitis
D H01317 Aggressive periodontitis
C DA0D Certain specified disorders of gingiva or edentulous alveolar ridge
D H01250 Hereditary gingival fibromatosis
C DA0E Dentofacial anomalies
C DA0F Sensory disturbances affecting orofacial complex
C DA0Y Other specified diseases or disorders of orofacial complex
C DA0Z Diseases or disorders of orofacial complex, unspecified
D H01407 Capnocytophaga ochracea infection
B Diseases of oesophagus
C DA20 Acquired anatomical alterations of the oesophagus
C DA21 Motility disorders of oesophagus
C DA22 Gastro-oesophageal reflux disease
D H01602 Gastroesophageal reflux disease
C DA23 Columnar metaplastic epithelium of the oesophagus
D H01901 Barrett esophagus
C DA24 Oesophagitis
D H01361 Eosinophilic esophagitis
C DA25 Oesophageal ulcer
C DA26 Vascular disorders of the oesophagus
C DA2Y Other specified diseases of oesophagus
C DA2Z Diseases of oesophagus, unspecified
B Diseases of the stomach or the duodenum
C Diseases of stomach
D DA40 Acquired anatomical alterations of the stomach
D DA41 Gastroduodenal motor or secretory disorders
D DA42 Gastritis
D DA43 Vascular disorders of the stomach
D DA44 Gastric polyp
D DA4Y Other specified diseases of stomach
C Diseases of duodenum
D DA50 Acquired anatomical alterations of the duodenum
D DA51 Duodenitis
E H00320 Helicobacter pylori infection
D DA52 Vascular disorders of the duodenum
D DA53 Duodenal polyp
D DA5Y Other specified diseases of duodenum
C Ulcer of stomach or duodenum
D DA60 Gastric ulcer
E H01634 Peptic ulcer
E H00320 Helicobacter pylori infection
E H02504 Gastrointestinal ulceration, recurrent, with dysfunctional platelets
D DA61 Peptic ulcer, site unspecified
E H01634 Peptic ulcer
D DA62 Anastomotic ulcer
E H01634 Peptic ulcer
E H00320 Helicobacter pylori infection
D DA63 Duodenal ulcer
E H01634 Peptic ulcer
E H00320 Helicobacter pylori infection
C DA7Z Diseases of the stomach or the duodenum, unspecified
B Diseases of small intestine
C DA90 Nonstructural developmental anomalies of small intestine
D H01805 Tricho-hepato-enteric syndrome
D H01276 Chronic idiopathic intestinal pseudo-obstruction
D H02553 Visceral myopathy
C DA91 Obstruction of small intestine
C DA92 Other acquired anatomical alterations of small intestine
C DA93 Motility disorders of small intestine
C DA94 Noninfectious enteritis or ulcer of small intestine
D H01853 Chronic nonspecific multiple ulcers of the small intestine
C DA95 Coeliac disease
D H02123 Celiac disease
C DA96 Intestinal malabsorption or protein-losing enteropathy
D H00352 Whipple disease
D H00988 Enterokinase deficiency
D H01016 Primary bile acid malabsorption
D H01935 Familial hypercholanemia
C DA97 Certain vascular disorders of small intestine
C DA98 Polyps of small intestine
C DA9Y Other specified diseases of small intestine
C DA9Z Diseases of small intestine, unspecified
B Diseases of appendix
C DB10 Appendicitis
C DB11 Certain specified diseases of appendix
C DB1Y Other specified diseases of appendix
C DB1Z Diseases of appendix, unspecified
B Diseases of large intestine
C DB30 Obstruction of large intestine
C DB31 Other acquired anatomical alterations of large intestine
C DB32 Motility disorders of large intestine
D H01871 Isolated hypoganglionosis
C DB33 Certain noninfectious colitis or proctitis
C DB34 Certain vascular disorders of large intestine
C DB35 Polyp of large intestine
C DB36 Certain infections of the large intestine
C DB3Y Other specified diseases of large intestine
C DB3Z Diseases of large intestine, unspecified
B Diseases of anal canal
C Acquired anatomical alterations of the anal canal
D DB50 Fissure or fistula of anal regions
D DB51 Stenosis of anal canal
D DB52 Ulcer of anus
D DB53 Anal prolapse
D DB5Y Other specified acquired anatomical alterations of the anal canal
D DB5Z Acquired anatomical alterations of the anal canal, unspecified
C Haemorrhoids or perianal venous conditions
D DB60 Haemorrhoids
D DB61 Perianal venous thrombosis
D DB62 Residual haemorrhoidal skin tags
D DB6Y Other specified haemorrhoids or perianal venous conditions
D DB6Z Haemorrhoids or perianal venous conditions, unspecified
C DB70 Infections of the anal region
C DB71 Anal polyp
C DB72 Certain specified diseases of anal canal
C DB7Y Other specified diseases of anal canal
C DB7Z Diseases of anal canal, unspecified
B Diseases of liver
C DB90 Infectious liver disease
C DB91 Acute or subacute hepatic failure
D H01712 Fulminant hepatic failure
C DB92 Non-alcoholic fatty liver disease
D H01333 Non-alcoholic fatty liver disease
C DB93 Hepatic fibrosis or cirrhosis
D H02194 North American Indian childhood cirrhosis
D H02225 Familial cirrhosis
C DB94 Alcoholic liver disease
D H02516 Alcoholic liver disease
C DB95 Drug-induced or toxic liver disease
C DB96 Autoimmune liver disease
D H01685 Autoimmune hepatitis
D H01467 Primary biliary cholangitis
D H01684 Primary sclerosing cholangitis
D H00742 Neonatal ichthyosis-sclerosing cholangitis (NISCH) syndrome
C DB97 Certain specified inflammatory liver diseases
C DB98 Vascular disorders of the liver
D H01687 Extrahepatic portal vein obstruction
D H01433 Budd-Chiari syndrome
D H01686 Idiopathic portal hypertension
C DB99 Certain specified diseases of liver
D H00545 Polycystic liver disease
D H01506 Hepatic encephalopathy
C DB9Z Diseases of liver, unspecified
B Diseases of gallbladder or biliary tract
C DC10 Acquired anatomical alterations of gallbladder or bile ducts
C DC11 Cholelithiasis
D H01213 Gallbladder disease
D H01679 Intrahepatic lithiasis
C DC12 Cholecystitis
D H01213 Gallbladder disease
C DC13 Cholangitis
C DC14 Certain specified biliary diseases
C DC1Y Other specified diseases of gallbladder or biliary tract
C DC1Z Diseases of gallbladder or biliary tract, unspecified
B Diseases of pancreas
C DC30 Cystic diseases of the pancreas
C DC31 Acute pancreatitis
D H01681 Acute pancreatitis
C DC32 Chronic pancreatitis
D H01680 Chronic pancreatitis
D H00933 Hereditary pancreatitis
D H00932 Tropical calcific pancreatitis
C DC33 Autoimmune pancreatitis
C DC34 Obstructive pancreatitis
C DC35 Certain specified diseases of pancreas
C DC3Y Other specified diseases of pancreas
C DC3Z Diseases of pancreas, unspecified
B Diseases of peritoneum
C DC50 Peritonitis
C DC51 Certain specified disorders of peritoneum or retroperitoneum
C DC5Z Diseases of peritoneum, unspecified
B Diverticular disease of intestine
C Diverticular disease of small intestine
D DC70 Diverticulitis of small intestine
D DC71 Diverticulosis of small intestine
D DC72 Diverticulum of small intestine
C Diverticular disease of large intestine
D DC80 Diverticulitis of large intestine
D DC81 Diverticulosis of large intestine
D DC82 Diverticulum of large intestine
C Diverticular disease of intestine of overlapping sites
D DC90 Diverticular disease of small and large intestine
C Diverticular disease of unspecified part of intestine
D DD00 Diverticulitis of unspecified part of intestine
D DD01 Diverticulosis of unspecified part of intestine
D DD02 Diverticulum of unspecified part of intestine
C DD1Z Diverticular disease of intestine, unspecified
B Ischaemic vascular disorders of intestine
C DD30 Acute vascular disorders of intestine
C DD31 Chronic vascular disorders of intestine
C DD3Y Other specified ischaemic vascular disorders of intestine
C DD3Z Ischaemic vascular disorders of intestine, unspecified
B Hernias
C DD50 Non-abdominal wall hernia
C DD51 Inguinal hernia
C DD52 Femoral hernia
C DD53 Umbilical hernia
C DD54 Paraumbilical hernia
C DD55 Epigastric hernia
C DD56 Incisional hernia
C DD57 Parastomal hernia
C DD5Y Other specified hernias
C DD5Z Hernias, unspecified
B Inflammatory bowel diseases
C DD70 Crohn disease
D H00286 Crohn disease
D H01227 Inflammatory bowel disease (IBD)
C DD71 Ulcerative colitis
D H01227 Inflammatory bowel disease (IBD)
D H01466 Ulcerative colitis
C DD72 Indeterminate colitis
D H01227 Inflammatory bowel disease (IBD)
C DD7Y Other specified inflammatory bowel diseases
C DD7Z Inflammatory bowel diseases, unspecified
B Functional gastrointestinal disorders
C DD90 Functional oesophageal or gastroduodenal disorders
C DD91 Irritable bowel syndrome or certain specified functional bowel disorders
D H01615 Irritable bowel syndrome
C DD92 Functional anorectal disorders
C DD93 Functional digestive disorders of infants, toddlers or children
C DD94 Functional gallbladder disorder
C DD95 Functional sphincter of Oddi disorder
C DD9Y Other specified functional gastrointestinal disorders
C DD9Z Functional gastrointestinal disorders, unspecified
B Postprocedural disorders of digestive system
C DE10 Vomiting following gastrointestinal surgery
C DE11 Dumping syndrome
C DE12 Malfunction or complication of external stoma of digestive organs
C DE13 Postsurgical malabsorption, not elsewhere classified
B DE2Y Other specified diseases of the digestive system
B DE2Z Diseases of the digestive system, unspecified
#
A14 Diseases of the skin
B Certain skin disorders attributable to infection or infestation
C Certain skin disorders attributable to viral infection
D Viral exanthems
E EA00 Viral exanthem due to unknown or unspecified agent
E EA0Y Viral exanthem due to other specified virus
D Certain dermatoses with suspected viral aetiology
E EA10 Pityriasis rosea
F H01660 Pityriasis rosea
E EA11 Papular purpuric gloves and socks syndrome
E EA12 Infantile papular acrodermatitis
D Dermatoses from distant or systemic viral infection
E EA20 Necrolytic acral erythema
D EA3Z Unspecified skin disorder attributable to viral infection
C Certain skin disorders attributable to bacterial infection
D Predominantly tropical or subtropical bacterial infections affecting skin
E EA40 Tropical phagedaenic ulcer
D EA50 Toxin-mediated cutaneous reactions to distant or systemic bacterial infection
D EA51 Skin complications of BCG immunisation
D EA5Y Cutaneous involvement by other specified bacterial infection
D EA5Z Cutaneous involvement by unspecified bacterial infection
C EA60 Certain skin disorders attributable to fungal infection
C EA6Y Cutaneous involvement by other specified infection or infestation
B Inflammatory dermatoses
C Dermatitis and eczema
D EA80 Atopic eczema
E H01358 Atopic dermatitis
D EA81 Seborrhoeic dermatitis and related conditions
E H00795 Seborrhea-like dermatitis with psoriasiform element
E H01652 Seborrheic dermatitis
D EA82 Nummular dermatitis
D EA83 Lichen simplex or lichenification
D EA84 Asteatotic eczema
D EA85 Dermatitis or eczema of hands and feet
D EA86 Dermatitis and eczema of lower legs
D EA87 Dermatitis or eczema of anogenital region
D EA88 Miscellaneous specified eczematous dermatoses
D EA89 Generalised eczematous dermatitis of unspecified type
D EA8Y Other specified eczematous dermatosis
D EA8Z Dermatitis or eczema, unspecified
C Papulosquamous dermatoses
D EA90 Psoriasis
E H01656 Psoriasis
E H01663 Pustular psoriasis
D EA91 Lichen planus
E H01654 Lichen planus
D EA92 Lichenoid dermatoses
D EA93 Pityriasis lichenoides
D EA94 Pityriasis rubra pilaris
E H01659 Pityriasis rubra pilaris
D EA95 Small plaque parapsoriasis
C Urticaria, angioedema and other urticarial disorders
D EB00 Spontaneous urticaria
D EB01 Inducible urticaria and angioedema
E H01799 Vibratory urticaria
D EB02 Cholinergic urticaria and related conditions
D EB03 Syndromes with urticarial reactions or angioedema
D EB04 Idiopathic angioedema
D EB05 Urticaria of unspecified type
D EB0Y Other specified urticarial disorders
C Inflammatory erythemas and other reactive inflammatory dermatoses
D EB10 Diffuse inflammatory erythemas
D EB11 Annular erythema
D EB12 Erythema multiforme
E H01695 Erythema multiforme
D EB13 Stevens-Johnson syndrome or toxic epidermal necrolysis
E H01694 Stevens-Johnson syndrome
D Neutrophilic dermatoses
E EB20 Acute febrile neutrophilic dermatosis
F H02590 Acute febrile neutrophilic dermatosis
E EB21 Pyoderma gangrenosum
E EB2Y Other specified neutrophilic dermatoses
D EB30 Eosinophilic cellulitis
D EB31 Erythema nodosum
E H01473 Erythema nodosum leprosum
C Immunobullous diseases of the skin
D EB40 Pemphigus
E H01648 Pemphigus
D EB41 Pemphigoid
E H01650 Pemphigoid
D EB42 Linear IgA bullous dermatosis
D EB43 Epidermolysis bullosa acquisita
D EB44 Dermatitis herpetiformis
E H01362 Dermatitis herpetiformis
D EB4Y Other specified immunobullous disorder
C Cutaneous lupus erythematosus
D EB50 Subacute cutaneous lupus erythematosus
E H01595 Cutaneous lupus erythematosus
D EB51 Chronic cutaneous lupus erythematosus
E H01595 Cutaneous lupus erythematosus
D EB5Z Cutaneous lupus erythematosus of unspecified type
C Scarring or sclerosing inflammatory dermatoses
D EB60 Lichen sclerosus
E H01690 Lichen sclerosus et atrophicus
D EB61 Morphoea
E H01493 Localized Scleroderma
C EB7Y Other specified inflammatory dermatoses
B Metabolic and nutritional disorders affecting the skin
C EB90 Dermatoses resulting from disturbed metabolic processes
D H01661 Xanthoma
C EB9Y Other specified metabolic and nutritional disorders affecting the skin
B Genetic and developmental disorders affecting the skin
C Genetic syndromes affecting the skin
D EC10 Genetic syndromes with poikiloderma
E H00793 Poikiloderma with neutropenia
E H01906 Poikiloderma, hereditary fibrosing, with tendon contractures, myopathy, and pulmonary fibrosis
D EC1Y Other specified genetic syndromes affecting the skin
C EC20 Genetic disorders of keratinisation
D H01771 Congenital ichthyosis
D H00735 Ichthyosis vulgaris
D H00134 X-linked ichthyosis
D H00733 Harlequin ichthyosis
D H00734 Autosomal recessive congenital ichthyosis
D H00691 Bullous congenital ichthyosiform erythroderma (BCIE)
D H00693 Ichthyosis bullosa of Siemens
D H00707 Ichthyosis hystrix, Curth-Macklin type
D H02265 Annular epidermolytic ichthyosis
D H00710 Erythrokeratodermia variabilis
D H00738 Ichthyosis with confetti
D H00790 Keratosis linearis with ichthyosis congenita and sclerosing keratoderma
D H02449 Autosomal dominant lamellar ichthyosis
D H00737 Peeling skin syndrome
D H00715 Darier disease
D H00844 Familial benign chronic pemphigus
D H00716 Palmoplantar keratoderma with deafness
D H00274 Papillon-Lefevre syndrome
D H00695 Mal de Meleda
D H00714 Vohwinkel syndrome
D H00722 Epidermolytic palmoplantar keratoderma
D H00723 Non-epidermolytic palmoplantar keratoderma
D H02264 Palmoplantar keratoderma, Nagashima type
D H02266 Palmoplantar keratoderma, Bothnian type
D H02517 Olmsted syndrome
D H00717 Striate palmoplantar keratoderma
D H02263 Focal nonepidermolytic palmoplantar keratoderma
D H02702 Tylosis with esophageal cancer
D H00755 Acrokeratosis verruciformis
D H01394 Cole disease
C EC21 Genetic defects of hair or hair growth
D H00667 Woolly hair
D H00670 Monilethrix
D H01796 Uncombable hair syndrome
D H00820 Bjornstad syndrome
D H00866 Trichothiodystrophy
D H00893 Cardiomyopathy, dilated, with woolly hair and keratoderma
D H00780 Atrichia with papular lesions
D H00784 Localized autosomal recessive hypotrichosis
D H00786 Hypotrichosis
D H00858 Marie-Unna hereditary hypotrichosis
D H00782 Hypotrichosis and recurrent skin vesicles
C EC22 Genetic defects of nails or nail growth
D H00683 Anonychia congenita
D H01307 Nonsyndromic congenital nail disorder
C EC23 Genetic disorders of skin pigmentation
D H00884 Familial progressive hyperpigmentation
D H00944 Dowling-Degos disease
D H02188 Watson syndrome
D H00166 Hermansky-Pudlak syndrome
D H00168 Oculocutaneous albinism
D H02021 Chediak-Higashi syndrome
D H00170 Piebaldism
D H00759 Waardenburg syndrome
D H00885 Hypomelanosis of Ito
D H01187 Tietz syndrome
D H02022 Griscelli syndrome
D H00880 Dyschromatosis symmetrica hereditaria
D H02350 Dyschromatosis universalis hereditaria
D H02665 Reticulate acropigmentation of Kitamura
C Genetically-determined epidermolysis bullosa
D EC30 Epidermolysis bullosa simplex
E H00584 Epidermolysis bullosa simplex
E H00585 Epidermolysis bullosa, hemidesmosomal
E H00644 Ectodermal dysplasia/skin fragility syndrome
D EC31 Junctional epidermolysis bullosa
E H00586 Epidermolysis bullosa, junctional
D EC32 Dystrophic epidermolysis bullosa
E H00587 Epidermolysis bullosa, dystrophica
E H00763 Transient bullous dermolysis of the newborn
D EC33 Syndromic epidermolysis bullosa
E H00588 Kindler syndrome
D EC3Z Epidermolysis bullosa
E H00813 Laryngo onycho cutaneous syndrome
E H01737 Epidermolysis bullosa
C Genetic disorders affecting dermal collagen, elastin or other matrix proteins
D EC40 Pseudoxanthoma elasticum
E H00560 Pseudoxanthoma elasticum
D EC4Y Other specified genetic disorders affecting dermal matrix proteins
C Specified developmental anomalies affecting the skin
D EC50 Developmental anomalies of the umbilicus
D EC5Y Other specified developmental anomalies affecting the skin
C EC7Y Other specified genetic and developmental disorders affecting the skin
B Sensory and psychological disorders affecting the skin
C Disturbances of cutaneous sensation
D EC90 Pruritus
D EC91 Prurigo
D EC92 Mucocutaneous or cutaneous pain syndromes
D EC9Y Other specified disturbances of cutaneous sensation
C Psychological or psychiatric conditions affecting the skin
D Self-inflicted skin disorders
E ED00 Artefactual skin disorder
E ED01 Simulated skin disease
E ED02 Painful bruising syndrome
E ED0Y Other specified self-inflicted skin disorders
D ED2Y Other specified psychological or psychiatric conditions affecting the skin
C Neurological conditions affecting the skin
D ED30 Neuropathic skin damage
D ED31 Burning feet syndrome
D ED3Y Cutaneous involvement in other specified neurological condition
B Skin disorders involving specific cutaneous structures
C Disorders of the epidermis and epidermal appendages
D Disorders of epidermal keratinisation
E ED50 Ichthyoses
E ED51 Diffuse epidermal hyperkeratosis and acanthosis
E ED52 Porokeratoses
F H00791 Disseminated superficial actinic porokeratosis (DSAP)
F H01933 Porokeratosis
E ED53 Skin peeling
E ED54 Xerosis cutis or asteatosis
E ED55 Palmoplantar keratodermas
F H01673 Palmoplantar keratoderma
F H02318 Palmoplantar hyperkeratosis with squamous cell carcinoma of skin and sex reversal
E ED56 Keratosis pilaris
F H00750 Keratosis pilaris atrophicans
E ED5Y Other specified disorders of epidermal keratinisation
D Disorders of skin colour
E ED60 Acquired hypermelanosis
E ED61 Acquired melanotic macules or lentigines
E ED62 Endogenous non-melanin pigmentation
E ED63 Acquired hypomelanotic disorders
F H01372 Vitiligo
F H01504 Vogt-Koyanagi-Harada syndrome
E ED64 Abnormal skin pigmentation
E ED6Y Other specified disorders of skin pigmentation
D Disorders of hair
E ED70 Alopecia or hair loss
F H01158 Alopecia universalis
E ED71 Hypertrichosis
E ED72 Hirsutism and syndromes with hirsutism
E ED73 Acquired disorders of the hair shaft
E ED7Y Other specified disorders of hair
D Disorders of the hair follicle
E Acne and related disorders
F ED80 Acne
G H01445 Acne vulgaris
F ED81 Acneform inflammatory disorders
E ED90 Rosacea and related disorders
E ED91 Disorders of the sebaceous gland
E ED92 Disorders involving the apocrine follicular unit
F H00681 Acne inversa
E ED9Y Other specified disorders involving the hair follicle
F H00672 Pseudofolliculitis barbae
D Disorders of eccrine sweat glands or sweating
E EE00 Hyperhidrosis
E EE01 Hypohidrosis
F H01848 Acquired idiopathic generalized anhidrosis
F H02281 Isolated anhidrosis with normal sweat glands
E EE02 Miliaria
E EE0Y Other specified disorders of eccrine sweat glands or sweating
D Disorders of the nail or perionychium
E EE10 Acquired deformities of the nail plate
E EE11 Acquired abnormalities of nail colour
E EE12 Infections of the nail or perionychium
E EE13 Certain disorders affecting the nails or perionychium
E EE1Y Other specified disorders of the nail or perionychium
E EE1Z Disorders of the nail or perionychium, unspecified
D Disorders of epidermal integrity
E EE20 Acute cutaneous distension syndrome
E EE21 Epidermal fragility
C Disorders of the dermis and subcutis
D Disorders of cutaneous connective tissue
E EE40 Atrophy or degeneration of dermal or subcutaneous connective tissue
E EE41 Abnormalities of dermal elastin
F H00557 Cutis laxa
E Poikiloderma
F EE50 Acquired poikiloderma
E Fibromatoses and keloids
F EE60 Keloid or hypertrophic scars
F EE61 Superficial fibromatoses
F EE6Y Other specified fibromatous disorders of skin and soft tissue
G H00663 Restrictive dermopathy
G H01173 Stiff skin syndrome
E EE70 Perforating dermatoses
E EE7Y Other specified disorders of cutaneous connective tissue
D Histiocytic-granulomatous disorders of the skin
E EE80 Necrobiotic granulomatous skin disorders
E EE81 Dermal dendrocyte, Class IIa histiocytoses
E EE8Y Other specified histiocytic and granulomatous disorders of the skin
D Benign dermal lymphocytic or lymphoplasmacytic infiltrations or proliferations
E EE90 Benign lymphocytic infiltration of the skin
E EE91 Lymphocytoma cutis
D Disorders of subcutaneous fat
E EF00 Panniculitis
E EF01 Lipoatrophy or lipodystrophy
F H01475 Lipodystrophy
E EF02 Certain noninflammatory disorders of subcutaneous fat
E EF0Y Other specified disorders of subcutaneous fat
C Disorders of cutaneous blood and lymphatic vessels
D Malformations involving cutaneous blood vessels
E EF20 Acquired malformations of cutaneous blood vessels
E EF2Z Cutaneous vascular malformation, unspecified
D Purpura or bruising
E EF30 Purpura or bruising due to disorders of coagulation
E EF31 Traumatic purpura
E EF3Y Other specified purpura
E EF3Z Purpura of unspecified aetiology
D EF40 Vasculitis or capillaritis involving the skin
D Dermatoses attributable to hyperviscosity or microvascular occlusion
E EF50 Livedoid vasculopathy
E EF5Y Other specified dermatoses attributable to hyperviscosity or microvascular occlusion
D Dermatoses resulting from vascular insufficiency
E EF60 Ischaemic ulceration of skin
E Dermatoses due to venous disease
F EF70 Lower limb venous eczema
F EF7Y Other specified dermatoses due to venous disease
F EF7Z Dermatoses due to venous disease, unspecified
E EF9Y Other specified dermatoses resulting from vascular insufficiency
D Functional vascular disorders of the skin
E EG00 Vasodilatation of extremities
F H00771 Inherited erythromelalgia
E EG01 Vasoconstriction of extremities
E EG02 Flushing disorders
B Skin disorders involving certain specific body regions
C Skin disorders involving the head and neck
D EG30 Skin disorders localised to the scalp
E H01446 Propionibacterium acnes infection
D Disorders of the external ear involving the skin
E Inflammatory disorders of the external ear
F EG40 Contact dermatitis of external ear
F EG4Y Other specified inflammatory disorder of external ear
F EG4Z Inflammatory disorder of external ear, unspecified
C Skin disorders involving the genital and perianal regions
D Dermatoses of the anus, perianal area or perineum
E EG60 Anal pruritus
E EG61 Infections of the anus or perianal skin
E EG62 Inflammatory dermatoses of the perianal area
E EG63 Sacrococcygeal pilonidal disease
D EG7Y Other specified skin disorders involving the genital and perianal regions
C EG9Y Skin disorders involving other specific body regions
C EG9Z Skin disorders involving certain specific body regions, unspecified
B Skin disorders associated with pregnancy, the neonatal period and infancy
C Skin disorders specific to the perinatal or neonatal period
D Neonatal skin infection
E EH10 Neonatal viral infections involving the skin
E EH11 Neonatal pyogenic skin infections
E EH12 Neonatal fungal infections involving the skin
E EH1Z Neonatal skin infection, unspecified
D EH3Y Other specified skin disorders specific to the perinatal or neonatal period
C EH40 Dermatoses of infancy
B Adverse cutaneous reactions to medication
C Drug eruptions
D EH60 Exanthematic drug eruption
D EH61 Drug-induced urticaria, angioedema and anaphylaxis
D EH62 Lichenoid drug eruption
D EH63 Stevens-Johnson syndrome and toxic epidermal necrolysis due to drug
D EH64 Drug-induced erythroderma
D EH65 DRESS syndrome
D EH66 Fixed drug eruption
D EH67 Acne or acneform reactions attributable to drugs
D EH6Y Drug eruption of other specified type
D EH6Z Drug eruption of unspecified type
C EH70 Pigmentary abnormalities of skin due to drug
C EH71 Dermatoses precipitated by drug therapy
C EH72 Drug-induced hair abnormalities
C EH73 Drug-induced nail abnormalities
C EH74 Drug-induced oral conditions
C EH75 Photosensitivity due to drug
C EH76 Dermatoses associated with specific classes of medication
C EH77 Localised adverse cutaneous reactions to administration of drug
C EH78 Adverse cutaneous reactions to herbal, homoeopathic or other alternative therapies
C EH7Y Other specified adverse cutaneous reactions to medication
C EH7Z Unspecified adverse cutaneous reactions to medication
B Skin disorders provoked by external factors
C EH90 Pressure ulceration
C EH92 Dermatoses provoked by friction or mechanical stress
C EH93 Dermatoses due to foreign bodies
C EH94 Scar of skin, not elsewhere classified
C Dermatoses provoked or exacerbated by exposure to cold
D EJ0Y Other specified dermatoses provoked or exacerbated by exposure to cold
C Dermatoses provoked by heat or electricity
D EJ10 Erythema ab igne
D EJ1Y Other specified dermatoses provoked by heat or electricity
C Dermatoses provoked by light or UV radiation
D Chronic effects of ultraviolet radiation on the skin
E EJ20 Photoaging of the skin
E EJ2Y Other specified chronic effects of ultraviolet radiation on the skin
D EJ30 Autoimmune or other photodermatoses
D Acute effects of ultraviolet radiation on normal skin
E EJ40 Sunburn
E EJ41 Burn from exposure to artificial source of ultraviolet radiation
E EJ4Z Acute effects of ultraviolet radiation on normal skin, unspecified
D EJ6Y Other specified dermatoses provoked by light or UV radiation
E H02131 UV-sensitive syndrome
C Dermatoses due to ionizing radiation
D EJ71 Chronic effects of ionizing radiation on the skin
D EJ7Z Dermatoses due to ionizing radiation, unspecified
C EK00 Allergic contact dermatitis
D H01357 Allergic contact dermatitis
C EK01 Photo-allergic contact dermatitis
C EK02 Irritant contact dermatitis
C EK10 Allergic contact urticaria
C EK11 Protein contact dermatitis
C EK12 Allergic contact sensitisation
C Phototoxic reactions to skin contact with photoactive agents
D EK20 Phototoxic reaction to fragrance or cosmetics
D EK2Y Phototoxic reaction to skin contact with other specified photoactive agent
D EK2Z Phototoxic dermatitis, unspecified
C EK50 Cutaneous reactions to venomous or noxious animals
C EK5Y Other specified skin disorders provoked by external factors
B Benign proliferations, neoplasms and cysts of the skin
C EK70 Cutaneous cysts
C EK71 Skin tags or polyps
B Disorders of the skin of uncertain or unpredictable malignant potential
C EK90 Actinic keratosis and other discrete epidermal dysplasias
D H02429 Actinic keratosis
C EK91 Dermatoses which may presage cutaneous lymphoma
C EK92 Histiocytoses of uncertain malignant potential
D H01168 Sea-blue histiocyte disease
B Cutaneous markers of internal disorders
C Cutaneous markers of internal malignancy
D EL10 Paraneoplastic syndromes involving skin
D EL1Y Other specified cutaneous markers of internal malignancy
C EL3Y Other specified cutaneous markers of internal disorders
B Postprocedural disorders of the skin
C EL50 Unsatisfactory surgical scar of skin
C EL51 Cutaneous flap necrosis
C EL52 Myocutaneous flap necrosis
C EL53 Skin graft failure
C EL54 Composite graft failure
C Adverse cutaneous effects of therapeutic ionizing irradiation
D EL60 Acute radiodermatitis following radiotherapy
D EL61 Chronic radiodermatitis following radiotherapy
D EL63 Radionecrosis of skin due to therapeutic ionizing irradiation
C Complications of cutaneous cosmetic procedures
D EL73 Unsatisfactory outcome from cutaneous cosmetic surgical procedure
C EL80 Adverse cutaneous effects of diagnostic procedures
B EM0Y Other specified diseases of the skin
B EM0Z Skin disease of unspecified nature
#
A15 Diseases of the musculoskeletal system or connective tissue
B Arthropathies
C Osteoarthritis
D FA00 Osteoarthritis of hip
D FA01 Osteoarthritis of knee
D FA02 Osteoarthritis of wrist or hand
D FA03 Osteoarthritis of other specified joint
D FA04 Oligoosteoarthritis
D FA05 Polyosteoarthritis
D FA0Z Osteoarthritis, unspecified
C Infection related arthropathies
D FA10 Direct infections of joint
E H01442 Septic arthritis
D FA11 Reactive arthropathies
D FA12 Postinfectious arthropathies
D FA13 Infectious spondyloarthritis
D FA1Y Other specified infection related arthropathies
D FA1Z Infection related arthropathies, unspecified
C Inflammatory arthropathies
D FA20 Rheumatoid arthritis
E H00630 Rheumatoid arthritis
D FA21 Psoriatic arthritis
D FA22 Polymyalgia rheumatica
E H01606 Polymyalgia rheumatica
D FA23 Adult-onset Still disease
E H01516 Adult onset Still disease
D FA24 Juvenile idiopathic arthritis
E H01672 Juvenile idiopathic arthritis
D FA25 Gout
E H01532 Gout
D FA26 Certain specified crystal arthropathies
E H01236 Familial articular chondrocalcinosis
D FA27 Certain specified inflammatory arthropathies
E H01507 Seronegative arthritis
D FA2Z Inflammatory arthropathies, unspecified
C Certain specified joint disorders or deformities of limbs
D FA30 Acquired deformities of fingers or toes
D FA31 Other acquired deformities of limbs
D FA32 Disorders of patella
D FA33 Internal derangement of knee
D FA34 Certain specified joint derangements
D FA35 Wear of articular bearing surface of joint prosthesis
D FA36 Effusion of joint
D FA37 Certain joint disorders, not elsewhere classified
D FA38 Arthropathy in diseases classified elsewhere
D FA3Z Unspecified joint disorders and deformities of limbs
C FA5Y Other specified arthropathies
C FA5Z Arthropathies, unspecified
B Conditions associated with the spine
C Structural disorders of spine
D FA70 Spinal deformities
D FA71 Torticollis
D FA72 Disorders of vertebra
E H01708 Diffuse idiopathic skeletal hyperostosis
D FA7Y Other specified structural disorders of spine
D FA7Z Structural disorders of spine, unspecified
C Degenerative condition of spine
D FA80 Intervertebral disc degeneration
E H02539 Intervertebral disc disease
D FA81 Spondylolysis
D FA82 Spinal stenosis
E H01711 Spinal stenosis
D FA83 Ossification of spinal ligaments
E H00431 Ossification of the posterior longitudinal ligament of spine
E H01707 Ossified ligamentum flavum
D FA84 Spondylolisthesis
D FA85 Spinal endplate defects
D FA8Y Other specified degenerative condition of spine
D FA8Z Degenerative condition of spine, unspecified
C Inflammation of spine
D FA90 Infection of vertebra
D FA91 Infection of intervertebral disc
D FA92 Inflammatory spondyloarthritis
E H01674 Ankylosing spondylitis
D FA9Y Other specified inflammation of spine
D FA9Z Inflammation of spine, unspecified
C Spondylopathies
D FB00 Ankylosis of spinal joint
D FB0Y Other specified spondylopathies
D FB0Z Spondylopathies, unspecified
C FB10 Spinal instabilities
C FB1Y Other specified conditions associated with the spine
C FB1Z Conditions associated with the spine, unspecified
B Soft tissue disorders
C Disorders of muscles
D FB30 Infectious myositis
D FB31 Calcification or ossification of muscle
E H00441 Progressive osseous heteroplasia
E H00430 Fibrodysplasia ossificans progressiva
D FB32 Certain specified disorders of muscle
E H02452 Muscle hypertrophy
D FB33 Secondary disorders of muscle
D FB3Z Disorders of muscles, unspecified
C Disorders of synovium or tendon
D FB40 Tenosynovitis
D FB41 Spontaneous rupture of synovium or tendon
D FB42 Certain specified disorders of synovium or tendon
D FB43 Secondary disorders of synovium or tendon
D FB4Y Other specified disorders of synovium or tendon
D FB4Z Disorders of synovium or tendon, unspecified
C Miscellaneous specified soft tissue disorders
D FB50 Bursitis
D FB51 Fibroblastic disorders
D FB52 Soft tissue disorders in diseases classified elsewhere
D FB53 Shoulder lesions
D FB54 Enthesopathies of lower limb
D FB55 Certain specified enthesopathies
D FB56 Specified soft tissue disorders, not elsewhere classified
C FB6Z Soft tissue disorders, unspecified
B Osteopathies or chondropathies
C FB80 Certain specified disorders of bone density or structure
D H00501 Fibrous dysplasia, polyostotic
D H01774 Hyperostosis corticalis generalisata
D H02609 Craniodiaphyseal dysplasia
C FB81 Osteonecrosis
D H01709 Glucocorticoid-induced osteonecrosis
C FB82 Chondropathies
D H00448 Familial osteochondritis dissecans
D H01526 Legg-Calve-Perthes Disease
D H01529 Avascular necrosis of femoral head
D H01758 Relapsing polychondritis
C FB83 Low bone mass disorders
D H01593 Osteoporosis
C FB84 Osteomyelitis or osteitis
C FB85 Paget disease of bone
D H00437 Paget disease of bone
C FB86 Disorders associated with bone growth
D H00457 Primary hypertrophic osteoarthropathy
D H00472 Torg syndrome
D H00614 Hyaline fibromatosis syndrome
D H00623 Hajdu-Cheney syndrome
D H01865 Multicentric carpotarsal osteolysis syndrome
D H02042 Familial expansile osteolysis
D H02089 Winchester syndrome
C FB8Y Other specified osteopathies or chondropathies
C FB8Z Osteopathies or chondropathies, unspecified
B FC00 Certain specified acquired deformities of musculoskeletal system or connective tissue, not elsewhere classified
B FC01 Postprocedural disorders of the musculoskeletal system
B FC0Y Other specified diseases of the musculoskeletal system or connective tissue
B FC0Z Diseases of the musculoskeletal system or connective tissue, unspecified
#
A16 Diseases of the genitourinary system
B Diseases of the female genital system
C Inflammatory disorders of the female genital tract
D GA00 Vulvitis
D GA01 Inflammatory disorders of the uterus, except cervix
D GA02 Vaginitis
D GA03 Diseases of Bartholin gland
D GA04 Cervicitis
D GA05 Female pelvic inflammatory diseases
D GA06 Pelvic peritoneal adhesions of unknown or combined origin
D GA07 Salpingitis and oophoritis
D GA0Z Inflammatory disorders of the female genital tract, unspecified
C GA10 Endometriosis
D H01639 Endometriosis
C GA11 Adenomyosis
C Noninflammatory disorders of female genital tract
D GA12 Dyspareunia
D GA13 Acquired abnormalities of vulva or perineum
D GA14 Acquired abnormalities of vagina
D GA15 Acquired abnormalities of cervix uteri
D GA16 Acquired abnormalities of uterus, except cervix
D GA17 Acquired abnormalities of fallopian tube
D GA18 Acquired abnormalities of ovary
D GA19 Acquired abnormalities of broad ligament
D GA1Y Other specified noninflammatory disorders of female genital tract
D GA1Z Noninflammatory disorders of female genital tract, unspecified
C Abnormal uterine or vaginal bleeding
D GA20 Menstrual cycle bleeding disorders
D GA21 Nonmenstrual bleeding disorders
D GA22 Excessive menstruation with irregular cycle
D GA23 Anovulatory bleeding
D GA2Y Other specified abnormal uterine or vaginal bleeding
D GA2Z Abnormal uterine or vaginal bleeding, unspecified
C GA30 Menopausal or certain specified perimenopausal disorders
D H00627 Premature ovarian failure
C GA31 Female infertility
D H01897 Oocyte/zygote/embryo maturation arrest
D H02335 Preimplantation embryonic lethality
C GA32 Complications associated with medically assisted reproduction
D H01039 Ovarian hyperstimulation syndrome
C GA33 Recurrent pregnancy loss
C GA34 Female pelvic pain associated with genital organs or menstrual cycle
C Dermatoses of female genitalia
D GA40 Inflammatory dermatoses of the vulva
D GA41 Ulcerative or erosive disorders of the vulva
D GA42 Sensory disturbance of the vulva
D GA43 Miscellaneous dermatoses of female genitalia
D GA4Y Other specified dermatoses of female genitalia
C GA6Y Other specified diseases of the female genital system
C GA6Z Diseases of the female genital system, unspecified
B Diseases of the male genital system
C Dermatoses of male genitalia
D GA80 Ulcerative disorders of the penis or scrotum
D GA81 Miscellaneous dermatoses of male genitalia
C Diseases of prostate
D GA90 Hyperplasia of prostate
D GA91 Inflammatory and other diseases of prostate
C GB00 Hydrocele or spermatocele
C GB01 Torsion of testis, epididymis or appendices
C GB02 Orchitis or epididymitis
C GB03 Atrophy of testis
C GB04 Male infertility
D H00890 Azoospermia
D H01208 Globozoospermia
D H01282 Spermatogenic failure
D H02534 Y-linked spermatogenic failure
C GB05 Redundant prepuce, phimosis or paraphimosis
C GB06 Certain specified disorders of penis
C GB07 Inflammatory disorders of male genital organs, not elsewhere classified
C GB08 Vascular disorders of male genital organs
C GB0Y Other specified diseases of the male genital system
C GB0Z Diseases of the male genital system, unspecified
B Disorders of breast
C GB20 Benign breast disease
C GB21 Inflammatory disorders of breast
C GB22 Hypertrophy of breast
C GB23 Certain specified disorders of breast
C GB2Z Disorders of breast, unspecified
B Diseases of the urinary system
C Glomerular diseases
D GB40 Nephritic syndrome
E H01688 Rapidly progressive glomerulonephritis
D GB41 Nephrotic syndrome
E H00576 Pierson syndrome
E H01657 Nephrotic syndrome
E H01722 Galloway-Mowat syndrome
D GB42 Persistent proteinuria or albuminuria
D GB4Y Other specified glomerular diseases
E H00582 Benign familial hematuria
D GB4Z Glomerular diseases, unspecified
C Renal tubulo-interstitial diseases
D GB50 Acute tubulo-interstitial nephritis
D GB51 Acute pyelonephritis
D GB52 Acute tubular necrosis
D GB53 Acute renal papillary necrosis
D GB54 Tubulo-interstitial nephritis, not specified as acute or chronic
D GB55 Chronic tubulo-interstitial nephritis
E H02577 Karyomegalic interstitial nephritis
D GB56 Obstructive or reflux nephropathy
E H01037 Vesicoureteral reflux
D GB57 Nephrocalcinosis
D GB58 Pyonephrosis
D GB59 Renal or perinephric abscess
D GB5Y Other specified renal tubulo-interstitial diseases
D GB5Z Renal tubulo-interstitial diseases, unspecified
C Kidney failure
D GB60 Acute kidney failure
D GB61 Chronic kidney disease
E H01456 Diabetic nephropathy
E H02559 Microvascular complications of diabetes
D GB6Z Kidney failure, unspecified
C Urolithiasis
D GB70 Calculus of upper urinary tract
E H02145 Calcium oxalate nephrolithiasis
E H02626 Kalamiella piersonii infection
D GB71 Calculus of lower urinary tract
D GB7Z Urolithiasis, unspecified
C Cystic or dysplastic kidney disease
D GB80 Nonfamilial nongenetic cystic kidney disease
D GB81 Autosomal dominant polycystic kidney disease
E H00542 Polycystic kidney disease
D GB82 Autosomal dominant tubulointerstitial disease
E H00541 Autosomal dominant tubulointerstitial kidney disease
E H02012 Medullary cystic kidney disease
D GB83 Nephronophthisis
E H00537 Nephronophthisis
E H00538 Senior-Loken syndrome
D GB8Y Other specified cystic or dysplastic kidney disease
E H00542 Polycystic kidney disease
D GB8Z Cystic or dysplastic kidney disease, unspecified
C GB90 Certain specified disorders of kidney or ureter
D H01198 Fanconi renotubular syndrome
D H00239 Bartter syndrome
D H00241 Combined proximal and distal renal tubular acidosis (RTA type 3)
D H00243 Hyperkalemic distal renal tubular acidosis (RTA type 4)
D H00428 Distal renal tubular acidosis (RTA type 1)
D H00429 Proximal renal tubular acidosis (RTA type 2)
D H02310 Renal tubular acidosis
D H00888 Nephrolithiasis/osteoporosis, hypophosphatemic
D H00252 Congenital nephrogenic diabetes insipidus
D H00694 Dent disease
D H00948 Renal hypouricemia
D H02147 X-linked recessive nephrolithiasis with renal failure
D H02148 Low molecular weight proteinuria with hypercalciuria and nephrocalcinosis
D H02149 X-linked hypercalciuric nephrolithiasis
C Certain specified diseases of urinary system
D GC00 Cystitis
E H01551 Interstitial cystitis
D GC01 Other disorders of bladder
D GC02 Urethritis and urethral syndrome
D GC03 Urethral stricture
D GC04 Fistula of the genitourinary tract
D GC05 Prolapsed urethral mucosa
D GC06 Urethral diverticulum
D GC07 Urethral caruncle
D GC08 Urinary tract infection, site not specified
E H01176 Uncomplicated urinary tract infection
E H00279 Uropathogenic Escherichia coli (UPEC) infection
E H01339 Asymptomatic bacteriuria
D GC0Y Other diseases of urinary system
C GC2Z Diseases of the urinary system, unspecified
B Other conditions of the genitourinary system
C Female pelvic floor dysfunction
D GC40 Pelvic organ prolapse
D GC41 Anorectal dysfunction associated with pelvic organ prolapse
D GC42 Sexual dysfunction associated with pelvic organ prolapse
D GC4Z Female pelvic floor dysfunction, unspecified
C GC50 Functional bladder disorders, not otherwise specified
C GC51 Female Genital Mutilation
B Postprocedural disorders of genitourinary system
C GC70 Postoperative adhesions of vagina
C GC71 Prolapse of vaginal vault after hysterectomy
C GC72 Postprocedural urethral stricture
C GC73 Postprocedural pelvic peritoneal adhesions
C GC74 Malfunction or complication of external stoma of urinary tract
C GC75 Malfunction of the afferent segment of a continent urinary pouch
C GC76 Malfunction of the efferent segment of a continent urinary pouch
C GC77 Postprocedural nonmenstrual uterine bleeding
C GC78 Postprocedural acute female pelvic inflammatory disease
C GC79 Disorders of breast reduction
C GC7A Disorders of breast augmentation
C GC7B Postinterventional ischemia or infarction of kidney
B GC8Y Other specified diseases of the genitourinary system
B GC8Z Diseases of the genitourinary system, unspecified
#
A17 Conditions related to sexual health
B Sexual dysfunctions
C HA00 Hypoactive sexual desire dysfunction
C HA01 Sexual arousal dysfunctions
C HA02 Orgasmic dysfunctions
C HA03 Ejaculatory dysfunctions
C HA0Y Other specified sexual dysfunctions
C HA0Z Sexual dysfunctions, unspecified
B Sexual pain disorders
C HA20 Sexual pain-penetration disorder
C HA2Y Other specified sexual pain disorders
C HA2Z Sexual pain disorders, unspecified
B HA40 Aetiological considerations in sexual dysfunctions and sexual pain disorders
B Gender incongruence
C HA60 Gender incongruence of adolescence or adulthood
C HA61 Gender incongruence of childhood
C HA6Z Gender incongruence, unspecified
B HA8Y Other specified conditions related to sexual health
B HA8Z Conditions related to sexual health, unspecified
#
A18 Pregnancy, childbirth or the puerperium
B Abortive outcome of pregnancy
C JA00 Abortion
C JA01 Ectopic pregnancy
C JA02 Molar pregnancy
D H00289 Recurrent hydatidiform moles
C JA03 Missed abortion
C JA04 Blighted ovum or nonhydatidiform mole
C JA05 Complications following abortion, ectopic or molar pregnancy
C JA0Z Abortive outcome of pregnancy, unspecified
B Oedema, proteinuria, or hypertensive disorders in pregnancy, childbirth, or the puerperium
C JA20 Pre-existing hypertension complicating pregnancy, childbirth or the puerperium
C JA21 Pre-eclampsia superimposed on chronic hypertension
C JA22 Gestational oedema or proteinuria without hypertension
C JA23 Gestational hypertension
C JA24 Pre-eclampsia
C JA25 Eclampsia
C JA2Z Oedema, proteinuria, or hypertensive disorders in pregnancy, childbirth, or the puerperium, unspecified
B Obstetric haemorrhage
C JA40 Haemorrhage in early pregnancy
C JA41 Antepartum haemorrhage
C JA42 Intrapartum haemorrhage
C JA43 Postpartum haemorrhage
C JA4Z Obstetric haemorrhage, unspecified
B Certain specified maternal disorders predominantly related to pregnancy
C JA60 Excessive vomiting in pregnancy
C JA61 Venous complications in pregnancy
C JA62 Infections of genitourinary tract in pregnancy
C JA63 Diabetes mellitus in pregnancy
C JA64 Malnutrition in pregnancy
C JA65 Maternal care for other conditions predominantly related to pregnancy
D H02193 Intrahepatic cholestasis of pregnancy
C JA66 Clinical findings on antenatal screening of mother
C JA67 Complications of anaesthesia during pregnancy
C JA6Z Maternal disorders predominantly related to pregnancy, unspecified
B Maternal care related to the fetus, amniotic cavity or possible delivery problems
C JA80 Maternal care related to multiple gestation
C JA81 Maternal care related to complications specific to multiple gestation
C JA82 Maternal care for known or suspected malpresentation of fetus
C JA83 Maternal care for known or suspected disproportion
C JA84 Maternal care for known or suspected abnormality of pelvic organs
C JA85 Maternal care for known or suspected fetal abnormality or damage
C JA86 Maternal care for other known or suspected fetal problems
C JA87 Maternal care related to polyhydramnios
C JA88 Maternal care related to certain specified disorders of amniotic fluid or membranes
C JA89 Maternal care related to premature rupture of membranes
C JA8A Maternal care related to placental disorders
C JA8B Maternal care related to placenta praevia or low lying placenta
C JA8C Maternal care related to premature separation of placenta
C JA8D Maternal care related to false labour
C JA8E Maternal care related to prolonged pregnancy
C JA8Y Maternal care related to other specified fetus, amniotic cavity or possible delivery problems
C JA8Z Maternal care related to unspecified fetus, amniotic cavity or possible delivery problems
B Complications of labour or delivery
C JB00 Preterm labour or delivery
C JB01 Failed induction of labour
C JB02 Abnormalities of forces of labour
C JB03 Long labour
C JB04 Obstructed labour due to malposition or malpresentation of fetus
C JB05 Obstructed labour due to maternal pelvic abnormality
C JB06 Obstructed labour due to other causes
C JB07 Labour or delivery complicated by fetal distress
C JB08 Labour or delivery complicated by umbilical cord complications
C JB09 Perineal laceration during delivery
C JB0A Certain specified obstetric trauma
C JB0B Retained placenta or membranes, without haemorrhage
C JB0C Complications of anaesthesia during labour or delivery
C JB0D Certain specified complications of labour or delivery, not elsewhere classified
C JB0Y Other specified complications of labour or delivery
C JB0Z Complications of labour or delivery, unspecified
B Delivery
C JB20 Single spontaneous delivery
C JB21 Single delivery by forceps or vacuum extractor
C JB22 Single delivery by caesarean section
C JB23 Other assisted single delivery
C JB24 Multiple delivery
C JB2Z Delivery, unspecified
B Complications predominantly related to the puerperium
C JB40 Infections in the puerperium
C JB41 Venous complications in the puerperium
C JB42 Obstetric embolism
C JB43 Complications of anaesthesia during the puerperium
C JB44 Certain specified complications of the puerperium
C JB45 Infections of breast associated with childbirth
C JB46 Certain specified disorders of breast or lactation associated with childbirth
D H01607 Galactorrhea
C JB4Z Complications predominantly related to the puerperium, unspecified
B Certain obstetric conditions, not elsewhere classified
C JB60 Obstetric death of unspecified cause
C JB61 Death from any obstetric cause occurring more than 42 days but less than one year after delivery
C JB62 Death from sequelae of obstetric causes
C JB63 Maternal infectious diseases classifiable elsewhere but complicating pregnancy, childbirth or the puerperium
C JB64 Certain maternal diseases classifiable elsewhere but complicating pregnancy, childbirth or the puerperium
C JB65 Sequelae of complication of pregnancy, childbirth or the puerperium
C JB6Y Other specified obstetric conditions, not elsewhere classified
C JB6Z Unspecified obstetric condition
#
A19 Certain conditions originating in the perinatal period
B Fetus or newborn affected by maternal factors or by complications of pregnancy, labour or delivery
C KA00 Fetus or newborn affected by maternal conditions that may be unrelated to present pregnancy
C KA01 Fetus or newborn affected by maternal complications of pregnancy
C KA02 Fetus or newborn affected by complications of placenta
C KA03 Fetus or newborn affected by complications of umbilical cord
C KA04 Fetus or newborn affected by other abnormalities of membranes
C KA05 Fetus or newborn affected by certain complications of labour or delivery
C KA06 Fetus or newborn affected by noxious influences transmitted via placenta or breast milk
C KA07 Neonatal dermatoses due to maternal antibodies
C KA0Z Fetus or newborn affected by unspecified maternal factors or by complications of pregnancy, labour or delivery
B Disorders of newborn related to length of gestation or fetal growth
C KA20 Disorders of newborn related to slow fetal growth or fetal malnutrition
C KA21 Disorders of newborn related to short gestation or low birth weight, not elsewhere classified
C KA22 Disorders of newborn related to long gestation or high birth weight
C KA2Y Other specified disorders of newborn related to length of gestation or fetal growth
C KA2Z Disorders of newborn related to length of gestation or fetal growth, unspecified
B Birth injury
C KA40 Birth injury to central nervous system
C KA41 Birth injury to eye
C KA42 Birth injury to scalp
C KA43 Birth injury to skin or soft tissues
C KA44 Birth injury to peripheral nervous system
C KA45 Birth injury to skeleton
C KA46 Birth injury to other organs
C KA4Z Birth injury, unspecified
B Infections of the fetus or newborn
C KA60 Sepsis of fetus or newborn
C KA61 Other bacterial infections of the fetus or newborn
C KA62 Viral infection in the fetus or newborn
C KA63 Fungal infection of fetus or newborn
C KA64 Parasitic diseases in the fetus or newborn
C KA65 Neonatal infections of certain specified sites
C KA6Y Other specified infections of the fetus or newborn
C KA6Z Infections of the fetus or newborn, unspecified
B Haemorrhagic or haematological disorders of fetus or newborn
C KA80 Fetal blood loss
C KA81 Umbilical haemorrhage of newborn
C KA82 Intracranial nontraumatic haemorrhage of fetus or newborn
C KA83 Certain specified neonatal haemorrhages
C KA84 Haemolytic disease of fetus or newborn
C KA85 Hydrops fetalis due to haemolytic disease
C KA86 Neonatal kernicterus
C KA87 Neonatal hyperbilirubinaemia
D H02152 Transient familial neonatal hyperbilirubinemia
C KA88 Disseminated intravascular coagulation of fetus or newborn
C KA89 Transient neonatal thrombocytopaenia
C KA8A Polycythaemia neonatorum
C KA8B Anaemia of prematurity
C KA8C Congenital hypoplastic anaemia
C KA8D Transient neonatal neutropaenia
C KA8E Alloimmune neonatal neutropaenia
C KA8F Neonatal vitamin K deficiency
C KA8Y Other specified haemorrhagic or haematological disorders of fetus or newborn
C KA8Z Haemorrhagic or haematological disorders of fetus or newborn, unspecified
B Neurological disorders specific to the perinatal or neonatal period
C KB00 Neonatal cerebral ischaemia
C KB01 Periventricular cysts of newborn
C KB02 Neonatal cerebral leukomalacia
C KB03 Neonatal encephalopathy
D H01211 MECP2-related severe neonatal encephalopathy
C KB04 Hypoxic ischaemic encephalopathy of newborn
C KB05 Neonatal hydrocephalus
C KB06 Neonatal seizures
C KB07 Compression of brain in neonate
C KB08 Disorders of muscle tone of newborn
C KB0Y Other specified neurological disorders specific to the perinatal or neonatal period
C KB0Z Neurological disorders specific to the perinatal or neonatal period, unspecified
B Respiratory disorders specific to the perinatal or neonatal period
C KB20 Intrauterine hypoxia
C KB21 Birth asphyxia
C KB22 Metabolic acidaemia in newborn
C KB23 Respiratory distress of newborn
C KB24 Congenital pneumonia
C KB25 Neonatal tracheitis
C KB26 Neonatal aspiration syndromes
C KB27 Pulmonary air leak or related conditions originating in the perinatal period
C KB28 Pulmonary haemorrhage originating in the perinatal period
C KB29 Chronic respiratory disease originating in the perinatal period
C KB2A Apnoea of newborn
C KB2B Primary atelectasis of newborn
C KB2C Cyanotic attacks of newborn
C KB2D Respiratory failure of newborn
C KB2E Respiratory arrest of newborn
C KB2F Congenital lung or lobar atelectasis
C KB2G Tracheal haemorrhage of newborn due to airway trauma
C KB2H Acquired vocal cord paralysis in newborn
C KB2J Airway obstruction in the neonate due to airway abnormality
C KB2K Pulmonary cysts in newborn
C KB2Y Other specified respiratory disorders specific to the perinatal or neonatal period
C KB2Z Respiratory disorders specific to the perinatal or neonatal period, unspecified
B Cardiovascular disorders present in the perinatal or neonatal period
C KB40 Neonatal cardiac failure
C KB41 Cardiac arrhythmias in the neonate
C KB42 Persistent pulmonary hypertension of the newborn
C KB44 Transient myocardial ischaemia of newborn
C KB45 Neonatal hypertension
C KB46 Neonatal hypotension
C KB47 Benign or innocent cardiac murmurs in newborn
C KB48 Patent arterial duct of prematurity
C KB4Y Other specified cardiovascular disorders present in the perinatal or neonatal period
C KB4Z Cardiovascular disorders present in the perinatal or neonatal period, unspecified
B Transitory endocrine or metabolic disorders specific to fetus or newborn
C KB60 Transitory disorders of carbohydrate metabolism specific to fetus or newborn
D H00513 Transient neonatal diabetes mellitus
D H00512 Permanent neonatal diabetes mellitus
D H01377 Mitchell-Riley syndrome
C KB61 Transitory neonatal disorders of calcium or magnesium metabolism
C KB62 Transitory neonatal disorders of thyroid function
C KB63 Certain specified transitory neonatal electrolyte or metabolic disturbances
C KB64 Transitory neonatal hypoparathyroidism
C KB6Z Transitory endocrine or metabolic disorders specific to fetus or newborn, unspecified
B Digestive system disorders of fetus or newborn
C KB80 Gastro-oesophageal reflux disease in newborn
C KB81 Oesophagitis in newborn
C KB82 Prenatal gastric perforation
C KB83 Postnatal gastric perforation
C KB84 Postnatal isolated ileal perforation
C KB85 Prenatal intrauterine intestinal perforation
C KB86 Postnatal intestinal perforation
C KB87 Intestinal obstruction of newborn
C KB88 Necrotising enterocolitis of newborn
C KB89 Neonatal malabsorption syndromes
D H01469 Short bowel syndrome
D H01477 Congenital short bowel syndrome
C KB8A Neonatal haematemesis or melaena due to swallowed maternal blood
C KB8B Neonatal peritonitis
C KB8C Noninfectious neonatal diarrhoea
D H01174 Congenital diarrhea
C KB8Y Other specified digestive system disorders of fetus or newborn
D H02730 Severe congenital liver disease
C KB8Z Digestive system disorders of fetus or newborn, unspecified
B Genitourinary system disorders specific to the perinatal or neonatal period
C KC00 Congenital hydrocele
C KC01 Congenital renal failure
C KC0Y Other specified genitourinary system disorders specific to the perinatal or neonatal period
C KC0Z Genitourinary system disorders specific to the perinatal or neonatal period, unspecified
B Disorders involving the integument of fetus or newborn
C KC20 Conditions involving the umbilical cord
C KC21 Inflammatory dermatoses of the newborn
C KC22 Neonatal disorders of subcutaneous fat
C KC23 Neonatal disorders of the oral mucosa
C KC24 Neonatal nutritional disorders affecting the skin
C Skin disorders associated with prematurity
D KC30 Skin fragility of prematurity
D KC31 Congenital erosive or vesicular dermatosis healing with reticulated supple scarring
D KC3Y Other specified skin disorders associated with prematurity
C KC40 Miscellaneous skin disorders in the neonate
C KC41 Miscellaneous specified conditions of integument specific to fetus or newborn
C Iatrogenic injuries involving the skin of the neonate
D Postnatal iatrogenic skin injury
E KC50 Neonatal phototherapy burn
E KC5Y Other specified postnatal iatrogenic skin injury
E KC5Z Postnatal iatrogenic skin injury, unspecified
D KC7Y Other specified iatrogenic injuries involving the skin of the neonate
C KC9Z Disorders involving the integument of fetus or newborn, unspecified
B Disturbances of temperature regulation of newborn
C KD10 Environmental hyperthermia of newborn
C KD11 Fever of newborn
C KD12 Hypothermia of newborn
C KD1Y Other specified disturbances of temperature regulation of newborn
C KD1Z Disturbances of temperature regulation of newborn, unspecified
B Certain disorders originating in the perinatal period
C KD30 Birth depression
C KD31 Wide cranial sutures of newborn
C KD32 Feeding problems of newborn
C KD33 Jittery baby, not elsewhere classified
C KD34 Reactions or intoxications due to drugs administered to fetus or newborn
C KD35 Neonatal withdrawal syndrome from maternal use of drugs of addiction
C KD36 Withdrawal symptoms from therapeutic use of drugs in newborn
C KD37 Exposure to tobacco smoke in the perinatal period
C KD38 Meconium staining
C KD39 Complications of intrauterine procedures, not elsewhere classified
C KD3A Termination of pregnancy, affecting surviving fetus or newborn
C KD3B Fetal death, cause not specified
C KD3C Vomiting in newborn
C KD3Y Other specified disorders originating in the perinatal period
B KD5Z Conditions originating in the perinatal or neonatal period, unspecified
#
A20 Developmental anomalies
B Structural developmental anomalies primarily affecting one body system
C Structural developmental anomalies of the nervous system
D LA00 Anencephaly or similar anomalies
E H02120 Anencephaly
D LA01 Cephalocele
D LA02 Spina bifida
E H00262 Neural tube defects, folate-sensitive
E H02563 Neural tube defects
D LA03 Arnold-Chiari malformation type II
E H01561 Chiari malformation
D LA04 Congenital hydrocephalus
E H01677 Congenital hydrocephalus
E H02458 Hydrocephalus due to congenital stenosis of aqueduct of Sylvius
D LA05 Cerebral structural developmental anomalies
E H00269 Primary microcephaly
E H01833 Hemimegalencephaly
E H02446 Autosomal recessive macrocephaly/megalencephaly syndrome
E H00267 Holoprosencephaly
E H00263 Acrocallosal syndrome
E H01835 Neuronal migration disorder
E H00271 Polymicrogyria
E H01251 Focal cortical dysplasia of Taylor
E H01881 Complex cortical dysplasia with other brain malformations
E H00270 Periventricular nodular heterotopia
E H00839 Porencephaly
E H01160 Schizencephaly
E H01870 Microhydranencephaly
E H02501 Occipital cortical malformation
D LA06 Cerebellar structural developmental anomalies
E H01678 Dandy-Walker syndrome
D LA07 Structural developmental anomalies of the neurenteric canal, spinal cord or vertebral column
E H01675 Syringomyelia
E H01561 Chiari malformation
E H01893 Lateral meningocele syndrome
D LA0Y Other specified structural developmental anomalies of the nervous system
E H02494 Alkuraya-Kucinskas syndrome
D LA0Z Structural developmental anomalies of the nervous system, unspecified
C Structural developmental anomalies of the eye, eyelid or lacrimal apparatus
D LA10 Structural developmental anomalies of ocular globes
E H01027 Microphthalmia
E H02172 Nanophthalmos
D LA11 Structural developmental anomalies of the anterior segment of eye
E H01114 Ocular coloboma
E H01029 Cornea plana congenita
E H02104 Megalocornea
E H00620 Axenfeld-Rieger syndrome
E H01159 Anterior segment dysgenesis
E H00635 Aniridia
E H00961 Posterior polymorphous corneal dystrophy
E H01075 Peters anomaly
D LA12 Structural developmental anomalies of lens or zonula
E H00676 Congenital primary aphakia
E H00662 Ectopia lentis
D LA13 Structural developmental anomalies of the posterior segment of eye
E H02112 Persistent hyperplastic primary vitreous
E H00589 Familial exudative vitreoretinopathy
E H02475 Retinoschisis
E H02203 Optic nerve hypoplasia
E H02270 Cavitary optic disc anomalies
E H01256 Foveal hypoplasia
E H02231 Optic disc anomalies with retinal and/or macular dystrophy
D LA14 Structural developmental anomalies of eyelid, lacrimal apparatus or orbit
E H00677 Aplasia of lacrimal and salivary glands
E H02514 Lacrimal duct defect
D LA1Y Other specified structural developmental anomalies of the eye, eyelid or lacrimal apparatus
D LA1Z Structural developmental anomalies of the eye, eyelid or lacrimal apparatus, unspecified
C Structural developmental anomalies of the ear
D LA20 Structural anomaly of eustachian apparatus
D LA21 Minor anomalies of pinnae
D LA22 Structural developmental anomalies of ear causing hearing impairment
E H02115 Congenital aural atresia
D LA23 Otocephaly
E H02118 Agnathia-otocephaly complex
D LA24 Accessory auricle
D LA2Y Other specified structural developmental anomalies of the ear
D LA2Z Structural developmental anomalies of the ear, unspecified
C Structural developmental anomalies of the face, mouth or teeth
D LA30 Structural developmental anomalies of teeth and periodontal tissues
E H00625 Tooth agenesis
E H00652 Solitary median maxillary central incisor syndrome
E H00615 Amelogenesis imperfecta
E H00618 Amelogenesis imperfecta hypoplastic-hypomaturation with taurodontism
E H01015 Jalili syndrome
E H02348 Dentin dysplasia
E H00432 Hereditary dentine disorders
D LA31 Structural developmental anomalies of mouth or tongue
D Clefts of lip, alveolus or palate
E LA40 Cleft lip
F H00516 Cleft lip and/or cleft palate
E LA41 Cleft lip and alveolus
F H00516 Cleft lip and/or cleft palate
E LA42 Cleft palate
F H00516 Cleft lip and/or cleft palate
F H00909 Cleft palate with ankyloglossia
E LA4Y Other specified clefts of lip, alveolus or palate
E LA4Z Clefts of lip, alveolus or palate, unspecified
D LA50 Congenital velopharyngeal incompetence
D LA51 Facial clefts
E H02202 Oblique facial cleft
D LA52 Facial asymmetry
D LA53 Macrocheilia
D LA54 Microcheilia
D LA55 Compression facies
D LA56 Pierre Robin syndrome
D LA5Y Other specified structural developmental anomalies of the face
D LA5Z Structural developmental anomalies of the face, unspecified
C Structural developmental anomalies of the neck
D LA60 Webbed neck
D LA61 Congenital sternomastoid tumour
D LA62 Congenital torticollis
D LA6Y Other specified structural developmental anomalies of the neck
D LA6Z Structural developmental anomalies of the neck, unspecified
C Structural developmental anomalies of the respiratory system
D LA70 Structural developmental anomalies of the nose or cavum
E H01017 Choanal atresia and lymphedema
D LA71 Structural developmental anomalies of larynx
D LA72 Laryngotracheooesophageal cleft
D LA73 Structural developmental anomalies of trachea
E H02600 Congenital tracheal stenosis
D LA74 Structural developmental anomalies of bronchi
D LA75 Structural developmental anomalies of lungs
E H00564 Primary ciliary dyskinesia
D LA76 Structural developmental anomalies of pleura
D LA77 Congenital cyst of mediastinum
D LA7Y Other specified structural developmental anomalies of the respiratory system
D LA7Z Structural developmental anomalies of the respiratory system, unspecified
C Structural developmental anomalies of the circulatory system
D Structural developmental anomaly of heart or great vessels
E LA80 Anomalous position-orientation of heart
E LA81 Abnormal ventricular relationships
E LA82 Total mirror imagery
E LA83 Right isomerism
E LA84 Left isomerism
F H01764 Polysplenia syndrome
E LA85 Congenital anomaly of an atrioventricular or ventriculo-arterial connection
F H01786 Congenitally corrected transposition of the great arteries
F H00550 Complete transposition of the great arteries
F H00918 Double-outlet right ventricle
F H01736 Persistent truncus arteriosus
E LA86 Congenital anomaly of mediastinal vein
F H02605 Congenital pulmonary venous stenosis
E LA87 Congenital anomaly of an atrioventricular valve or atrioventricular septum
F H02230 X-linked cardiac valvular dysplasia
F H02602 Congenital tricuspid valve stenosis
F H01783 Ebstein anomaly
F H02603 Congenital mitral valve stenosis
F H00547 Atrioventricular septal defect
E LA88 Congenital anomaly of a ventricle or the ventricular septum
F H00549 Tetralogy of Fallot
F H01803 Pulmonary atresia with ventricular septal defect
F H01926 Ventricular septal defect
E LA89 Functionally univentricular heart
F H01787 Univentricular heart
F H01785 Tricuspid atresia
F H01272 Hypoplastic left heart syndrome
F H02375 Cardiac valvular dysplasia
E LA8A Congenital anomaly of a ventriculo-arterial valve or adjacent regions
F H01802 Pulmonary atresia with intact ventricular septum
F H00554 Aortic valve disease
F H00553 Congenital supravalvular aortic stenosis
E LA8B Congenital anomaly of great arteries including arterial duct
F H01630 Patent ductus arteriosus
F H02601 Pulmonary arterial sling
E LA8C Congenital anomaly of coronary artery
E LA8D Congenital pericardial anomaly
E LA8E Congenital anomaly of atrial septum
F H00546 Atrial septal defect
E LA8F Congenital anomaly of right atrium
E LA8G Congenital anomaly of left atrium
E LA8Y Other specified structural developmental anomaly of heart or great vessels
F H00632 Heterotaxy
F H02199 Congenital heart defects, multiple type
E LA8Z Structural developmental anomaly of heart or great vessels, unspecified
D LA90 Structural developmental anomalies of the peripheral vascular system
E H00533 Hereditary hemorrhagic telangiectasia
E H00531 Venous malformations
E H01849 Peripheral arteriovenous malformation
E H02043 Capillary malformation-arteriovenous malformation
D LA9Y Other specified structural developmental anomalies of the circulatory system
D LA9Z Structural developmental anomalies of the circulatory system, unspecified
C Structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord
D LB00 Structural developmental anomalies of diaphragm
E H01241 Congenital diaphragmatic hernia
D LB01 Omphalocele
D LB02 Gastroschisis
D LB03 Structural developmental anomalies of umbilical cord
D LB0Y Other specified structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord
D LB0Z Structural developmental anomalies of the diaphragm, abdominal wall or umbilical cord, unspecified
C Structural developmental anomalies of the digestive tract
D LB10 Structural developmental anomalies of salivary glands or ducts
D LB11 Congenital diverticulum of pharynx
D LB12 Structural developmental anomalies of oesophagus
D LB13 Structural developmental anomalies of stomach
D LB14 Structural developmental anomalies of duodenum
D LB15 Structural developmental anomalies of small intestine
D LB16 Structural developmental anomalies of large intestine
E H00910 Hirschsprung disease
E H01871 Isolated hypoganglionosis
D LB17 Structural developmental anomalies of anal canal
E H01858 Persistent cloaca
E H01856 Cloacal exstrophy
D LB18 Congenital anomalies of intestinal fixation
D LB1Y Other specified structural developmental anomalies of the digestive tract
E H02331 Gastrointestinal defects and immunodeficiency syndrome
D LB1Z Structural developmental anomalies of the digestive tract, unspecified
C Structural developmental anomalies of the liver, biliary tract, pancreas or spleen
D LB20 Structural developmental anomalies of gallbladder, bile ducts or liver
E H01855 Biliary atresia
E H00551 Alagille syndrome
D LB21 Structural developmental anomalies of pancreas
E H00861 Pancreatic agenesis
D LB22 Structural developmental anomalies of spleen
E H01435 Congenital asplenia
D LB2Y Other specified structural developmental anomalies of the liver, biliary tract, pancreas or spleen
D LB2Z Structural developmental anomalies of the liver, biliary tract, pancreas or spleen, unspecified
C Structural developmental anomalies of the urinary system
D LB30 Structural developmental anomalies of kidneys
E H01867 Congenital anomalies of kidney and urinary tract
E H00822 Renal hypodysplasia and aplasia
E H00575 Renal tubular dysgenesis
D LB31 Structural developmental anomalies of urinary tract
E H01867 Congenital anomalies of kidney and urinary tract
E H02495 Congenital megabladder
D LB3Y Other specified structural developmental anomalies of the urinary system
D LB3Z Structural developmental anomalies of the urinary system, unspecified
C Structural developmental anomalies of the female genital system
D LB40 Structural developmental anomalies of vulva
D LB41 Structural developmental anomalies of clitoris
D LB42 Structural developmental anomalies of vagina
D LB43 Structural developmental anomalies of cervix uteri
D LB44 Structural developmental anomalies of uterus, except cervix
E H00600 Mullerian agenesis
D LB45 Structural developmental anomalies of ovaries, fallopian tubes or broad ligaments
E H00599 Ovarian dysgenesis
D LB4Y Other specified structural developmental anomalies of the female genital system
D LB4Z Structural developmental anomalies of the female genital system, unspecified
C Structural developmental anomalies of the male genital system
D LB50 Micropenis or penis agenesis
D LB51 Anorchia or microorchidia
D LB52 Cryptorchidism
E H02176 Cryptorchidism
D LB53 Hypospadias
E H02175 Hypospadias
D LB54 Congenital chordee
D LB55 Epispadias
D LB56 Bifid scrotum
D LB57 Agenesis of vas deferens
E H01033 Congenital bilateral absence of vas deferens
D LB58 Polyorchidism
D LB59 Hypoplasia of testis or scrotum
D LB5Y Other specified structural developmental anomalies of the male genital system
D LB5Z Structural developmental anomalies of the male genital system, unspecified
C Structural developmental anomalies of the breast
D LB60 Breast aplasia
D LB61 Absent nipple
D LB62 Supernumerary breasts
D LB63 Accessory nipple
D LB6Y Other specified structural developmental anomalies of the breast
D LB6Z Structural developmental anomalies of the breast, unspecified
C Structural developmental anomalies of the skeleton
D LB70 Structural developmental anomalies of cranium
E H02160 Craniosynostoses
E H01207 Trigonocephaly
E H00475 Enlarged parietal foramina/cranium bifidum
E H01105 Cranio-lenticulo-sutural dysplasia
D LB71 Structural developmental anomalies of facial bones
D LB72 Structural developmental anomalies of shoulder girdle
D LB73 Structural developmental anomalies of spine or bony thorax
E H01851 Congenital scoliosis associated with rib anomalies
E H00852 Klippel-Feil syndrome
D LB74 Structural developmental anomalies of pelvic girdle
E H01817 Beukes hip dysplasia
D LB75 Brachydactyly
E H00482 Brachydactyly
D LB76 Triphalangeal thumb
D LB77 Hyperphalangy
D LB78 Polydactyly
E H01226 Polysyndactyly
E H01852 Postaxial polydactyly
E H02332 Preaxial polydactyly
D LB79 Syndactyly
E H01095 Syndactyly
E H00459 Synpolydactyly
E H01854 Metacarpal 4-5 fusion
D Congenital deformities of fingers or toes
E LB80 Congenital deformities of fingers
F H01246 Isolated congenital nail clubbing
E LB81 Congenital deformities of toes
E LB8Z Congenital deformities of fingers or toes, unspecified
D LB90 Joint formation defects
E H00484 Multiple synostosis syndrome
E H00851 Proximal symphalangism
D LB91 Congenital shoulder dislocation
D LB92 Congenital elbow dislocation
D LB93 Congenital knee dislocation
D LB94 Congenital patella dislocation
D LB95 Patella aplasia or hypoplasia
D LB96 Congenital bowing of long bones
D LB97 Limb overgrowth
E H02647 Macrodactyly
D LB98 Congenital deformities of feet
E H00903 Congenital clubfoot
E H00929 Congenital vertical talus
D LB99 Reduction defects of upper limb
E H00471 Split-hand/foot malformation
D LB9A Reduction defects of lower limb
E H00471 Split-hand/foot malformation
D LB9B Reduction defects of upper and lower limbs
E H00629 Acheiropodia
E H00636 Tetra-amelia syndrome
D LB9Y Other specified structural developmental anomalies of the skeleton
E H00873 Cousin syndrome
D LB9Z Structural developmental anomalies of the skeleton, unspecified
E H00762 Spondyloepiphyseal dysplasia with congenital joint dislocations
C Structural developmental anomalies of the skin
D Developmental hamartomata of the epidermis and epidermal appendages
E LC00 Keratinocytic epidermal hamartoma
F H02627 Epidermal nevus
E LC01 Pilosebaceous hamartoma
E LC02 Complex epidermal hamartoma
F H02716 Becker nevus syndrome
E LC0Y Other specified developmental hamartomata of the epidermis and epidermal appendages
D Developmental anomalies of skin pigmentation
E LC10 Dermal melanocytosis
E LC1Y Other specified developmental anomalies of skin pigmentation
D Hamartomata derived from dermal connective tissue
E LC20 Connective tissue hamartoma
E LC2Y Other specified hamartomata derived from dermal connective tissue
D Developmental defects of hair or nails
E LC30 Developmental defects of hair or hair growth
E LC31 Developmental defects of the nail apparatus
D LC40 Dermoid cyst
D Developmental anomalies of cutaneous vasculature
E LC50 Developmental capillary vascular malformations of the skin
E LC51 Developmental venous malformations involving the skin
F H02044 Cutaneous and mucosal venous malformation
E LC52 Complex or combined developmental vascular malformations involving the skin
E LC5Y Other specified developmental anomalies of cutaneous vasculature
E LC5Z Developmental anomalies of cutaneous vasculature, unspecified
D Congenital anomalies of skin development
E LC60 Aplasia cutis congenita
F H01896 Aplasia cutis congenita
D LC7Y Other specified structural developmental anomalies of the skin
E H02295 Adermatoglyphia
D LC7Z Structural developmental anomalies of the skin, unspecified
C Structural developmental anomalies of the adrenal glands
D LC80 Congenital adrenal hypoplasia
E H01772 Adrenal hypoplasia, congenital
D LC8Y Other specified structural developmental anomalies of the adrenal glands
D LC8Z Structural developmental anomalies of the adrenal glands, unspecified
C LD0Y Other specified structural developmental anomalies primarily affecting one body system
C LD0Z Structural developmental anomalies primarily affecting one body system, unspecified
B Multiple developmental anomalies or syndromes
C LD20 Syndromes with central nervous system anomalies as a major feature
D H00530 Joubert syndrome and related disorders
D H00897 Pontocerebellar hypoplasia
D H01001 COACH syndrome
D H01811 Arima syndrome
D H02272 CAPOS syndrome
D H02431 Cerebellar hypoplasia, epilepsy, and global developmental delay
D H02464 Poretti-Boltshauser syndrome
D H00268 Lissencephaly
D H00792 Warburg micro syndrome
D H02117 Neu-Laxova syndrome
D H00616 Bowen-Conradi syndrome
D H00840 Pseudo-TORCH syndrome
D H00990 Microcephaly, Amish type
D H00991 Microcephalic osteodysplastic primordial dwarfism, type II (MOPD II)
D H00993 Microcephalic osteodysplastic primordial dwarfism, type I (MOPD I)
D H01872 Microcephaly-capillary malformation syndrome
D H01876 Microcephaly with or without chorioretinopathy, lymphedema, or mental retardation
D H01921 MICPCH syndrome
D H02132 Microcephaly syndrome
D H02282 Spastic tetraplegia, thin corpus callosum, and progressive microcephaly
D H02461 Neurodevelopmental disorder with microcephaly
D H02492 Microcephaly, growth restriction, and increased sister chromatid exchange
D H02668 Heyn-Sproul-Jackson syndrome
D H02707 Khan-Khan-Katsanis syndrome
D H02708 Baralle-Macken syndrome
D H02709 Neurodevelopmental disorder with aminoacyl-tRNA synthetase defect
D H02726 Kaya-Barakat-Masson syndrome
D H00544 Septo-optic dysplasia
D H00816 Agenesis of the corpus callosum with peripheral neuropathy
D H01034 L1 syndrome
D H01035 Corpus callosum, agenesis of, with mental retardation, ocular coloboma and micrognathia
D H01776 Aicardi syndrome
D H01789 You-Hoover-Fong syndrome
D H01919 Proud syndrome
D H01937 Multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, and hydranencephaly
D H02366 Cerebellar ataxia, neuropathy, and vestibular areflexia syndrome
D H02396 Corpus callosum agenesis with facial anomalies and cerebellar ataxia
D H02487 Diencephalic-mesencephalic junction dysplasia syndrome
D H02519 Mega-corpus-callosum syndrome with cerebellar hypoplasia and cortical malformations
D H02606 Pachygyria, microcephaly, developmental delay, and dysmorphic facies, with or without seizures
D H02645 Cerebellar atrophy with seizures and variable developmental delay
D H02652 Macrocephaly, acquired, with impaired intellectual development
D H02653 Faundes-Banka syndrome
D H02675 Ichthyotic keratoderma, spasticity, hypomyelination, and dysmorphic facial features
D H02680 Neurodegeneration with developmental delay, early respiratory failure, myoclonic seizures, and brain abnormalities
D H02695 Fibrosis, neurodegeneration, and cerebral angiomatosis
D H02723 Macrocephaly/autism syndrome
C LD21 Syndromes with eye anomalies as a major feature
D H01904 Microphthalmia with linear skin defects syndrome
D H02134 Microphthalmia with limb anomalies
D H02170 Microphthalmia, syndromic
D H00673 Weill-Marchesani syndrome
D H00826 Blepharophimosis-ptosis-epicanthus inversus syndrome
D H01012 Oculo-auricular syndrome
D H02045 Norrie disease
D H02292 Retinal dystrophy, juvenile cataracts, and short stature syndrome
D H02422 Retinitis pigmentosa with skeletal anomalies
D H02445 Microcornea, myopic chorioretinal atrophy, and telecanthus
D H02655 Retinal dystrophy and microvillus inclusion disease
C LD22 Syndromes with dental anomalies as a major feature
C LD23 Syndromes with vascular anomalies as a major feature
D H00579 Hereditary angiopathy with nephropathy, aneurysms, and muscle cramps (HANAC)
D H01809 Sturge-Weber syndrome
D H02088 Primary intraosseous vascular malformation
C LD24 Syndromes with skeletal anomalies as a major feature
D H00520 Type II collagenopathies
D H00505 FGFR3-related short limb skeletal dysplasia
D H01749 Achondroplasia
D H02069 SADDAN
D H02068 Hypochondroplasia
D H01750 Thanatophoric dysplasia
D H00515 Atelosteogenesis type II
D H02063 Diastrophic dysplasia
D H00207 Rhizomelic chondrodysplasia punctata
D H00447 HEM skeletal dysplasia
D H00496 Congenital hemidysplasia with ichthyosiform nevus and limb defects (CHILD)
D H01194 X-linked chondrodysplasia punctata
D H00436 Osteopetrosis
D H00452 Buschke-Ollendorff syndrome
D H00434 Camurati-Engelmann disease
D H00444 Osteopathia striata with cranial sclerosis
D H00450 Worth type autosomal dominant osteosclerosis
D H00486 Sclerosteosis
D H00490 Diaphyseal dysplasia with anemia
D H00491 Craniometaphyseal dysplasia
D H00508 Blomstrand syndrome
D H00613 Infantile cortical hyperostosis
D H00968 Raine syndrome
D H01832 Lenz-Majewski syndrome
D H02631 Melorheostosis
D H00122 Multiple exostoses
D H00493 Heparan sulfate proteoglycan gene defects
D H00497 Cherubism
D H02127 Yunis-Varon syndrome
D H00443 Osteoglophonic dysplasia
D H00498 Gnathodiaphyseal dysplasia
D H00521 Cleidocranial dysplasia
D H01018 Metachondromatosis
D H02558 Craniotubular dysplasia, Ikegawa type
D H00445 Osteoarthritis with mild chondrodysplasia
D H00474 Schneckenbecken dysplasia
D H00483 Angel shaped phalangoepiphyseal dysplasia
D H00499 Spondylocarpotarsal synostosis syndrome
D H00519 Spondyloepiphyseal dysplasia congenita
D H00757 Dyggve-Melchior-Clausen disease
D H00758 Progressive pseudorheumatoid dysplasia
D H00760 Spondyloepiphyseal dysplasia tarda
D H00761 SEMD, Pakistani type
D H00765 Spondyloepiphyseal dysplasia, Kimberley type
D H00767 SEMD, Matrilin type
D H00777 SEMD, short limb-hand type
D H00863 Spondylo-megaepiphyseal-metaphyseal dysplasia
D H01494 SEMD with joint laxity type
D H01575 Roifman syndrome
D H01576 Spondyloenchondrodysplasia with immune dysregulation (SPENCDI)
D H01967 Anauxetic dysplasia
D H02070 Kniest dysplasia
D H02071 Czech dysplasia
D H02079 Oto-spondylo-megaepiphyseal dysplasia
D H02080 Fibrochondrogenesis
D H02155 Dyssegmental dysplasia
D H02183 Parastremmatic dwarfism
D H02184 Metatropic dysplasia
D H02186 Spondyloepiphyseal dysplasia, Maroteaux type
D H02187 Spondyloepimetaphyseal dysplasia
D H02462 Spondyloepiphyseal dysplasia
D H02497 Smith-McCort dysplasia
D H01821 Spondylometaphyseal dysplasia with cone-rod dystrophy
D H01825 Spondylometaphyseal dysplasia, Sedaghatian type
D H01830 Spondylometaphyseal dysplasia, Megarbane-Dagher-Melki type
D H02185 Spondylometaphyseal dysplasia
D H02732 Rhizomelic skeletal dysplasia with or without Pelger-Huet anomaly
D H00678 Achondrogenesis type IA
D H02065 Achondrogenesis type IB
D H02066 Achondrogenesis type II
D H00522 Brachyolmia
D H01828 Opsismodysplasia
D H01844 Diaphanospondylodysostosis
D H00495 Eiken dysplasia
D H00477 Pseudoachondroplasia
D H00476 Multiple epiphyseal dysplasia
D H02436 Al-Gazali syndrome
D H00479 Metaphyseal dysplasias
D H00518 Metaphyseal dysplasia without hypotrichosis
D H00675 Acrocapitofemoral dysplasia
D H00900 Geleophysic dysplasia
D H02062 Familial digital arthropathy-brachydactyly
D H02228 Acromicric dysplasia
D H02229 Terminal osseous dysplasia
D H00466 Grebe dysplasia
D H00468 Acromesomelic dysplasia, Demirhan type
D H00470 Acromesomelic dysplasia, Maroteaux type
D H02543 Acromesomelic dysplasia
D H00485 Robinow syndrome
D H00492 SHOX-related short stature
D H02154 Omodysplasia
D H00511 Short rib-polydactyly syndrome
D H00751 Asphyxiating thoracic dystrophy
D H02157 Short-rib thoracic dysplasia
D H00462 Stuve-Wiedemann syndrome
D H02629 Bent bone dysplasia syndrome
D H00509 3M syndrome
D H00619 Kenny-Caffey syndrome
D H00622 Hypoparathyroidism-retardation-dysmorphism syndrome
D H00992 Seckel syndrome
D H02223 Osteocraniostenosis
D H00494 Desbuquois syndrome
D H01498 Multiple joint dislocations, short stature, craniofacial dysmorphism, and congenital heart defects
D H02048 Larsen syndrome
D H02064 Atelosteogenesis type I and III
D H02067 Boomerang dysplasia
D H00458 Syndromic craniosynostoses
D H01756 Pfeiffer syndrome
D H01754 Crouzon syndrome
D H01755 Apert syndrome
D H01008 C syndrome
D H01753 Antley-Bixler syndrome
D H01888 Carpenter syndrome
D H01988 Jackson-Weiss syndrome
D H01989 Beare-Stevenson syndrome
D H01990 Muenke syndrome
D H01991 Saethre-Chotzen syndrome
D H01992 Craniofrontonasal syndrome
D H01993 Baller-Gerold syndrome
D H02047 Bohring-Opitz syndrome
D H02254 Craniosynostosis and dental anomalies
D H02637 Brachycephaly, trichomegaly, and developmental delay
D H00517 Spondylocostal dysostosis
D H01843 Cerebrocostomandibular syndrome
D H00464 Nail-patella syndrome
D H00461 Ischiocoxopodopatellar syndrome
D H01889 Meier-Gorlin syndrome
D H00506 Osteogenesis imperfecta
D H00451 Osteoporosis-pseudoglioma syndrome
D H00514 Bruck syndrome
D H01496 Spondyloocular syndrome
D H01571 Singleton-Merten syndrome
D H01572 Cole-Carpenter syndrome
D H02395 Calvarial doughnut lesions with bone fragility
D H00969 Skeletal defects, genital hypoplasia, and mental retardation
D H02233 Alazami syndrome
D H02280 Complex lethal osteochondrodysplasia
D H02300 Steel syndrome
D H02306 Chondrodysplasia with joint dislocations, GPAPP type
D H02349 Odontochondrodysplasia
D H02415 Craniofacial dysmorphism, skeletal anomalies, and mental retardation syndrome
D H02551 Skeletal dysplasia with joint laxity and advanced bone age
C LD25 Syndromes with face or limb anomalies as a major feature
D H00454 Oral-facial-digital syndrome
D H00456 Fronto-otopalatodigital syndromes
D H01816 Frank-ter Haar syndrome
D H02227 Frontometaphyseal dysplasia
D H01376 Acrofacial dysostosis
D H02158 Weyers acrofacial dysostosis
D H00528 Frontonasal dysplasia
D H00850 Frontorhiny
D H01884 Auriculocondylar syndrome
D H02210 Acromelic frontonasal dysostosis
D H02234 Hamamy syndrome
D H02640 Vertebral hypersegmentation and orofacial anomalies
C LD26 Syndromes with limb anomalies as a major feature
D H00467 Fibular hypoplasia and complex brachydactyly
D H00853 Cenani-Lenz syndactyly syndrome
D H00855 Triphalangeal thumb-polysyndactyly syndrome
D H00859 Guttmacher syndrome
D H00870 Brachydactyly-syndactyly syndrome
D H02161 Greig cephalopolysyndactyly syndrome
D H02333 Laurin-Sandrow syndrome
D H00778 Tarsal-carpal coalition syndrome
D H00986 Multiple pterygium syndrome
D H00935 Cold-induced sweating syndrome
D H01392 Arthrogryposis, mental retardation, and seizures
D H01886 Van den Ende-Gupta syndrome
D H02299 Arthrogryposis multiplex congenita
D H02358 Arthrogryposis multiplex congenita, neurogenic, with myelin defect
D H00811 Distal arthrogryposis
D H00865 Lethal congenital contractural syndrome
D H00872 Trismus-pseudocamptodactyly syndrome
D H01931 Lethal-type popliteal pterygium syndrome
D H02268 Wieacker-Wolff syndrome
D H00532 Parkes Weber syndrome
D H01788 Klippel-Trenaunay-Weber syndrome
D H01497 Temtamy preaxial brachydactyly syndrome
D H00846 Fuhrmann syndrome
D H00847 Al-Awadi/Raas-Rothschild syndrome
D H02717 Contractures, pterygia, and spondylocarpostarsal fusion syndrome
C LD27 Syndromes with skin or mucosal anomalies as a major feature
D H00651 Hypohidrotic ectodermal dysplasia
D H00645 Incontinentia pigmenti
D H01874 Cronkhite-Canada syndrome
D H02456 Ectodermal dysplasia
D H00648 Ectodermal dysplasia, Clouston type
D H00095 Ectodermal dysplasia and immunodeficiency
D H00204 Heimler syndrome
D H00449 Oculodentodigital dysplasia
D H00487 Tricho-dento-osseous syndrome
D H00503 Ellis-van Creveld syndrome
D H00529 Cranioectodermal dysplasia
D H00540 Osteoporosis, lymphedema, anhydrotic ectodermal dysplasia with immunodeficiency (OLEDAID)
D H00571 Johanson-Blizzard syndrome
D H00638 Ectrodactyly-ectodermal dysplasia-cleft lip/palate syndrome
D H00639 Ectodermal dysplasia, ectrodactyly, and macular dystrophy
D H00640 Limb-mammary syndrome
D H00641 ADULT syndrome
D H00642 Lacrimo-auriculo-dento-digital syndrome
D H00643 Tooth and nail syndrome
D H00646 Odontoonychodermal dysplasia
D H00647 Ectodermal dysplasia-syndactyly syndrome
D H00649 Ectodermal dysplasia, hair-nail type
D H00708 Naegeli-Franceschetti-Jadassohn syndrome
D H00752 Ankyloblepharon-ectodermal defects-cleft lip/palate (AEC) syndrome and Rapp-Hodgkin syndrome
D H00781 Schopf-Schulz-Passarge syndrome
D H00796 Dermatopathia pigmentosa reticularis
D H00857 Oligodontia-colorectal cancer syndrome
D H00922 Schinzel-Giedion midface retraction syndrome
D H00949 Focal dermal hypoplasia
D H00977 Trichorhinophalangeal syndrome
D H01271 Hypoparathyroidism with sensorineural deafness and renal dysplasia
D H01403 Coffin-Siris syndrome
D H01905 Trichomegaly
D H01966 Cartilage-hair hypoplasia
D H02058 Kohlschutter-Tonz syndrome
D H02081 Marshall syndrome
D H02083 Focal facial dermal dysplasia
D H02218 DOORS syndrome
D H02219 DDOD syndrome
D H02296 Basan syndrome
D H02303 Alopecia-mental retardation syndrome
D H02417 Gingival fibromatosis with hypertrichosis
D H02474 Blepharocheilodontic syndrome
D H02691 Scalp-ear-nipple syndrome
D H01428 Xeroderma pigmentosum
D H00671 Netherton syndrome
D H00712 KID/HID syndrome
D H00739 Ichthyosis with hypotrichosis
D H00740 Ichthyosis follicularis, alopecia, and photophobia syndrome
D H00741 Ichthyosis prematurity syndrome
D H00799 CEDNIK syndrome
D H01934 Barber-Say syndrome
D H00818 Birt-Hogg-Dube syndrome
D H01986 Legius syndrome
D H02189 Neurofibromatosis-Noonan syndrome
D H01741 Autoinflammation lipodystrophy and dermatosis syndrome
D H00665 Mandibuloacral dysplasia
D H02236 Keppen-Lubinsky syndrome
D H00684 Pachyonychia congenita
D H00696 Haim-Munk syndrome
D H00785 Congenital hypotrichosis with juvenile macular dystrophy
D H00815 H syndrome
D H00883 Lipoid proteinosis
D H02486 HELIX syndrome
D H02713 Inflammatory poikiloderma with hair abnormalities and acral keratoses
C LD28 Syndromes with connective tissue involvement as a major feature
D H00660 Congenital contractural arachnodactyly
D H00653 Marfan syndrome
D H00800 Loeys-Dietz syndrome
D H00659 Shprintzen-Goldberg syndrome
D H00661 MASS phenotype
D H01385 Rienhoff syndrome
D H02720 Meester-Loeys syndrome
D H00802 Ehlers-Danlos syndrome
D H01902 Brittle cornea syndrome
D H02239 Ehlers-Danlos syndrome, spondylodysplastic type
D H02240 Ehlers-Danlos syndrome periodontal type
D H02241 Ehlers-Danlos syndrome cardiac valvular type
D H02242 Ehlers-Danlos syndrome vascular type
D H02243 Ehlers-Danlos syndrome arthrochalasia type
D H02244 Ehlers-Danlos syndrome dermatosparaxis type
D H02245 Ehlers-Danlos syndrome kyphoscoliosis type
D H02246 Ehlers-Danlos syndrome musculocontractural type
D H02247 Ehlers-Danlos syndrome myopathic type
D H02724 Combined osteogenesis imperfecta and Ehlers-Danlos syndrome
D H00904 Cutis laxa with severe pulmonary, gastrointestinal, and urinary abnormalities
D H00906 Macrocephaly, alopecia, cutis laxa, and scoliosis
D H01859 Occipital horn syndrome
D H00919 Arterial tortuosity syndrome
D H02224 Grange syndrome
D H02502 Joint laxity, short stature, and myopia
D H02654 Boudin-Mortier syndrome
D H02703 VISS syndrome
C LD29 Syndromes with obesity as a major feature
D H01915 Borjeson-Forssman-Lehmann syndrome
D H02195 MEHMO syndrome
D H02267 Wilson-Turner syndrome
C LD2A Malformative disorders of sex development
D H00607 46,XY gonadal dysgenesis
D H00608 46,XY disorder of sex development due to testosterone secretion defect
D H02177 Androgen insensitivity syndrome
D H00442 Campomelic dysplasia
D H00598 46,XX testicular disorder of sex development
D H00609 Persistent Mullerian duct syndrome
D H02317 SERKAL syndrome
D H02318 Palmoplantar hyperkeratosis with squamous cell carcinoma of skin and sex reversal
C LD2B Syndromes with premature ageing appearance as a major feature
D H00076 Cockayne syndrome
D H00558 Geroderma osteodysplasticum
D H00601 Hutchinson-Gilford progeria syndrome
D H01733 Werner syndrome
D H01734 Rothmund-Thomson syndrome
D H01883 Nestor-Guillermo progeria syndrome
D H02323 Ruijs-Aalfs syndrome
D H02480 Fontaine progeroid syndrome
D H02570 Cerebro-oculo-facio-skeletal syndrome
D H02677 Progeroid laminopathy
C LD2C Overgrowth syndromes
D H00713 Beckwith-Wiedemann syndrome
D H00718 Sotos syndrome
D H00980 Nevo syndrome
D H01215 Simpson-Golabi-Behmel syndrome
D H01308 Macrocephaly macrosomia facial dysmorphism syndrome
D H01412 Perlman syndrome
D H01751 Weaver syndrome
D H01806 Tenorio syndrome
D H01834 Marshall-Smith syndrome
D H01885 Megalencephaly-polymicrogyria-polydactyly-hydrocephalus syndrome
D H01909 Hypoinsulinemic hypoglycemia with hemihypertrophy
D H01912 Congenital lipomatous overgrowth, vascular malformations, and epidermal nevi
D H02119 Proteus syndrome
D H02153 Megalencephaly-capillary malformation syndrome
D H02294 Tatton-Brown-Rahman syndrome
D H02297 CLAPO syndrome
D H02298 Macrocephaly, dysmorphic facies, and psychomotor retardation
D H02347 Thauvin-Robinet-Faivre syndrome
D H02444 Luscan-Lumish syndrome
D H02477 Cohen-Gibson syndrome
D H02522 Imagawa-Matsumoto syndrome
D H02679 Miura-type epiphyseal chondrodysplasia
C LD2D Phakomatoses or hamartoneoplastic syndromes
D H00666 Peutz-Jeghers syndrome
D H01437 Neurofibromatosis type 1
D H01438 Neurofibromatosis type 2
D H00915 Tuberous sclerosis complex
D H00895 Basal cell nevus syndrome
D H00559 von Hippel-Lindau syndrome
D H01222 Cowden syndrome
D H02576 Familial cutaneous telangiectasia and cancer syndrome
D H02628 Schimmelpenning-Feuerstein-Mims syndrome
D H02722 Nevus comedonicus
C LD2E Syndromes with structural anomalies due to inborn errors of metabolism
C LD2F Syndromes with multiple structural anomalies, without predominant body system involvement
D H00979 Sacral defect with anterior meningocele
D H02129 Prune belly syndrome
D H01195 VACTERL/VATER association
D H00261 Meckel syndrome
D H01738 Noonan syndrome
D H00610 Treacher Collins syndrome
D H01838 Mandibulofacial dysostosis with microcephaly
D H02126 Mandibulofacial dysostosis with alopecia
D H02211 Acrodysostosis
D H02673 Craniofacial microsomia
D H00433 Holt-Oram syndrome
D H00453 Branchio-oto-renal syndrome
D H00460 Hand-foot-genital syndrome
D H00463 Currarino syndrome
D H00500 Keutel syndrome
D H00502 Pallister-Hall syndrome
D H00504 Rubinstein-Taybi syndrome
D H00510 Feingold syndrome
D H00523 Noonan syndrome and related disorders
D H00555 Char syndrome
D H00556 CHARGE syndrome
D H00569 Aarskog-Scott syndrome
D H00570 Kabuki syndrome
D H00572 Roberts-SC phocomelia syndrome
D H00573 Townes-Brocks syndrome
D H00574 Coffin-Lowry syndrome
D H00583 Opitz-GBBB syndrome
D H00611 Popliteal pterygium syndrome (PPS)
D H00631 Cornelia de Lange syndrome
D H00634 Duane-radial ray syndrome
D H00637 Ulnar-mammary syndrome
D H00685 Bifid nose with or without anorectal and renal anomalies
D H00686 Manitoba oculotrichoanal syndrome
D H00709 Birk Barel mental retardation syndrome (BBMRS)
D H00711 Russell-Silver syndrome
D H00753 Urofacial syndrome
D H00756 Pitt-Hopkins syndrome
D H00797 Martsolf syndrome
D H00817 Branchiooculofacial syndrome
D H00868 Stapes ankylosis with broad thumb and toes
D H00886 Donnai-Barrow syndrome
D H00889 Lujan-Fryns syndrome
D H00894 FG syndrome
D H00907 Kleefstra syndrome
D H00908 Mowat-Wilson syndrome
D H00914 Warsaw breakage syndrome
D H00926 Growth retardation, developmental delay, coarse facies, and early death
D H00934 Caudal duplication anomaly
D H00936 Goldberg-Shprintzen megacolon syndrome
D H00943 TARP syndrome
D H00965 RAPADILINO syndrome
D H00972 Endocrine-cerebro-osteodysplasia syndrome
D H00987 Fetal akinesia deformation sequence
D H00997 CATSHL syndrome
D H01026 Renal coloboma syndrome
D H01030 Congenital arthrogryposis with anterior horn cell disease
D H01156 STAR syndrome
D H01220 Congenital cataracts, facial dysmorphism, and neuropathy
D H01265 Hydrolethalus syndrome
D H01289 Mulibrey nanism
D H01292 Nance-Horan syndrome
D H01370 SHORT syndrome
D H01393 Van Maldergem syndrome
D H01402 Nicolaides-Baraitser syndrome
D H01413 Adams-Oliver syndrome
D H01568 3C syndrome
D H01569 CHOPS syndrome
D H01573 Zimmermann-Laband syndrome
D H01745 Cardiofaciocutaneous syndrome
D H01747 Costello syndrome
D H01793 Young-Simpson syndrome
D H01794 Genitopatellar syndrome
D H01795 Blepharophimosis-mental retardation syndrome
D H01797 Webb-Dattani syndrome
D H01814 Stromme syndrome
D H01839 Burn-McKeown syndrome
D H01840 Moebius syndrome
D H01845 Catel-Manzke syndrome
D H01869 Megacystis microcolon intestinal hypoperistalsis syndrome
D H01878 Al-Raqad syndrome
D H01879 Wiedemann-Steiner syndrome
D H01887 3MC syndrome
D H01908 Carey-Fineman-Ziter syndrome
D H01917 CK syndrome
D H01923 Microcephaly, short stature, and impaired glucose metabolism
D H01927 Van der Woude syndrome
D H01930 Au-Kline syndrome
D H01932 Ablepharon-macrostomia syndrome
D H01984 Leopard syndrome
D H02023 Baraitser-Winter syndrome
D H02046 OFC syndrome
D H02072 Stickler syndrome
D H02074 Knobloch syndrome
D H02082 Floating-Harbor syndrome
D H02087 Vertebral, cardiac, renal, and limb defects syndrome
D H02102 Myhre syndrome
D H02180 McKusick-Kaufman syndrome
D H02190 CBL syndrome
D H02191 Noonan-like syndrome with loose anagen hair
D H02198 Pancreatic agenesis and congenital heart disease
D H02232 CAGSSS syndrome
D H02248 MEND syndrome
D H02249 Primrose syndrome
D H02253 Beaulieu-Boycott-Innes syndrome
D H02255 FDLAB syndrome
D H02260 Chondrodysplasia Chassaing-Lacombe type
D H02271 Cerebellofaciodental syndrome
D H02274 Cerebellar atrophy, visual impairment, and psychomotor retardation
D H02283 IVIC syndrome
D H02324 Sacral agenesis with vertebral anomalies
D H02327 KBG syndrome
D H02328 Sifrim-Hitz-Weiss syndrome
D H02334 Pierpont syndrome
D H02364 Heart and brain malformation syndrome
D H02368 Developmental delay with short stature, dysmorphic facial features, and sparse hair
D H02369 IMAGE-I syndrome
D H02370 FILS syndrome
D H02376 Global developmental delay, absent or hypoplastic corpus callosum, and dysmorphic facies
D H02381 Cleft palate, psychomotor retardation, and distinctive facial features
D H02382 Bainbridge-Ropers syndrome
D H02383 Midface hypoplasia, hearing impairment, elliptocytosis, and nephrocalcinosis
D H02391 Infantile-onset multisystem neurologic, endocrine, and pancreatic disease
D H02394 Cleft palate, cardiac defects, and mental retardation
D H02453 Congenital heart defects and ectodermal dysplasia
D H02454 Congenital heart defects, dysmorphic facial features, and intellectual developmental disorder
D H02455 Congenital heart defects, hamartomas of tongue, and polysyndactyly
D H02478 CATIFA syndrome
D H02479 Nivelon-Nivelon-Mabille syndrome
D H02481 Syndromic disorder with short stature
D H02482 ROSAH syndrome
D H02483 Basel-Vanagaite-Smirin-Yosef syndrome
D H02493 Al Kaissi syndrome
D H02496 Cerebellar, ocular, craniofacial, and genital syndrome
D H02500 Congenital interstitial lung disease with nephrotic syndrome and epidermolysis bullosa
D H02503 Richieri-Costa-Pereira syndrome
D H02506 Cardioacrofacial dysplasia
D H02508 Agenesis of corpus callosum, cardiac, ocular, and genital syndrome
D H02533 Kaufman oculocerebrofacial syndrome
D H02581 Juberg-Hayward syndrome
D H02595 Oculoskeletodental syndrome
D H02607 Short stature and microcephaly with genital anomalies
D H02619 Hypotonia, ataxia, developmental delay, and tooth enamel defect syndrome
D H02625 Primordial dwarfism-immunodeficiency-lipodystrophy syndrome
D H02641 Arthrogryposis, cleft palate, craniosynostosis, and impaired intellectual development
D H02650 Menke-Hennekam syndrome
D H02694 Alazami-Yuan syndrome
D H02725 Heart-hand syndrome
D H01824 CODAS syndrome
D H01850 Hartsfield syndrome
D H01857 Filippi syndrome
D H02343 EVEN-plus syndrome
D H02465 Weiss-Kruszka syndrome
D H02547 BRENS syndrome
D H02548 CIMDAG syndrome
D H02549 Cerebellar ataxia, brain abnormalities, and cardiac conduction defects
D H02578 Short stature, microcephaly, and endocrine dysfunction
D H02638 Zaki syndrome
D H02639 Atelis syndrome
D H02663 Braddock-Carey syndrome
D H02667 Takenouchi-Kosaki syndrome
D H02710 Yuksel-Vogel-Bauer syndrome
D H02733 Growth restriction, hypoplastic kidneys, alopecia, and distinctive facies
C LD2G Conjoined twins
C LD2H Syndromic genetic deafness
D H00687 Fraser syndrome
D H02356 PCWH syndrome
D H00779 Usher syndrome
D H00446 Craniofacial-deafness-hand syndrome
D H00581 Alport syndrome
D H00706 Bart-Pumphrey syndrome
D H00727 Athabascan brainstem dysgenesis syndrome
D H00803 Seizures-sensorineural deafness-ataxia-mental retardation-electrolyte imbalance (SESAME)
D H00823 ABCD syndrome
D H00946 Arts syndrome
D H01286 Microtia hearing impairment and cleft palate
D H01903 Brown-Vialetto-Van Laere syndrome
D H02095 Perrault syndrome
D H02135 Cone-rod dystrophy and hearing loss
D H02220 MEDNIK syndrome
D H02226 Cardiospondylocarpofacial syndrome
D H02286 Congenital deafness with inner ear agenesis, microtia, and microdontia
D H02287 Deafness, dystonia, and cerebral hypomyelination
D H02326 Keipert syndrome
D H02355 Deafness and myopia
D H02430 Ataxia, combined cerebellar and peripheral, with hearing loss and diabetes mellitus
D H02435 Deafness-infertility syndrome
D H02634 Deafness, cataract, impaired intellectual development, and polyneuropathy
D H02687 Congenital deafness and adult-onset progressive leukoencephalopathy
C LD2Y Other specified multiple developmental anomalies or syndromes
D H00417 Alstrom syndrome
D H00418 Bardet-Biedl syndrome
D H01623 MDPL syndrome
D H02488 Cardiac-urogenital syndrome
D H02523 Genitourinary and/or brain malformation syndrome
D H02630 Chitayat syndrome
C LD2Z Multiple developmental anomalies or syndromes, unspecified
D H00493 Heparan sulfate proteoglycan gene defects
B Chromosomal anomalies, excluding gene mutations
C LD40 Complete trisomies of the autosomes
D H01552 Down syndrome
D H01562 Patau syndrome
D H01564 Edwards syndrome
C LD41 Duplications of the autosomes
D H02604 Chromosome 1q21.1 duplication syndrome
D H01790 Emanuel syndrome
C LD42 Polyploidies
C LD43 Complete monosomies of the autosomes
C LD44 Deletions of the autosomes
D H01831 Ring chromosome 20 syndrome
D H01792 1p36 deletion syndrome
D H02471 Brain malformations with urinary tract defects
D H00561 Brachydactyly-mental retardation syndrome
D H02146 Glass syndrome
D H01773 4p deletion syndrome
D H01223 Mental retardation-stereotypic movements-epilepsy and/or cerebral malformations
D H00764 Chromosome 5p deletion syndrome
D H01439 Williams-Beuren syndrome
D H01800 Verheij syndrome
D H02103 DeSanto-Shinawi syndrome
D H02156 Lamb-Shaffer syndrome
D H01861 Chromosome 15q24 microdeletion syndrome
D H01877 Chromosome 15q13.3 microdeletion syndrome
D H02121 Koolen-De Vries syndrome
D H01791 Smith-Magenis syndrome
D H01004 Velocardiofacial syndrome
D H01524 DiGeorge syndrome
D H01525 22q11.2 deletion syndrome
D H01238 Phelan-McDermid syndrome
C LD45 Uniparental disomies
D H01801 Kagami-Ogata syndrome
C LD46 Imprinting errors
C LD47 Balanced rearrangements or structural rearrangements
C Sex chromosome anomalies
D LD50 Number anomalies of chromosome X
D LD51 Structural anomalies of chromosome X, excluding Turner syndrome
E H00552 Chromosome Xp21 deletion syndrome
E H00994 Familial skewed X-chromosome inactivation
D LD52 Number anomalies of chromosome Y
D LD53 Structural anomalies of chromosome Y
D LD54 Male with sex chromosome mosaicism
D LD55 Fragile X chromosome
E H00465 Fragile X syndrome
E H01731 Fragile X tremor/ataxia syndrome
D LD56 Chimaera 46, XX, 46, XY
D LD5Y Other specified sex chromosome anomalies
D LD5Z Sex chromosome anomalies, unspecified
C LD7Y Other specified chromosomal anomalies, excluding gene mutations
D H01288 Mosaic variegated aneuploidy syndrome
C LD7Z Chromosomal anomalies, excluding gene mutations, unspecified
B LD90 Conditions with disorders of intellectual development as a relevant clinical feature
C H01732 Angelman syndrome
C H00478 Prader-Willi syndrome
C H00440 Rett syndrome
C H00597 Snyder-Robinson syndrome
C H00769 Hyperekplexia
C H00940 Cohen syndrome
C H01752 ATR-X syndrome
C H01769 ZTTK syndrome
C H01913 Renpenning syndrome
C H01914 Christianson syndrome
C H01916 Stocco dos Santos X-linked mental retardation syndrome
C H01920 Partington syndrome
C H01922 Infantile hypotonia with psychomotor retardation and characteristic facies
C H02137 Laurence-Moon syndrome
C H02252 PEHO syndrome
C H02305 RERE-related neurodevelopmental syndrome
C H02325 Schaaf-Yang syndrome
C H02337 Skraban-Deardorff syndrome
C H02338 PEHO-like syndrome
C H02346 Intellectual developmental disorder with short stature
C H02353 Hyperekplexia and epilepsy
C H02363 Ververi-Brady syndrome
C H02365 Helsmoortel-van der Aa syndrome
C H02378 Hypotonia, ataxia, and delayed development syndrome
C H02397 Neurodevelopmental disorder with movement abnormalities or hypotonia
C H02437 Growth retardation, impaired intellectual development, hypotonia, and hepatopathy
C H02459 Syndromic neurodevelopmental disorder
C H02460 Neurodevelopmental disorder with dysmorphic facies and skeletal anomalies
C H02461 Neurodevelopmental disorder with microcephaly
C H02463 Syndromic intellectual developmental disorder
C H02470 Neurodevelopmental disorder with structural brain abnormalities
C H02515 Li-Ghorbani-Weisz-Hubshman syndrome
C H02528 Hao-Fountain syndrome
C H02535 Neurodevelopmental disorder with dysmorphic facies
C H02560 White-Kernohan syndrome
C H02582 Mullegama-Klein-Martinez syndrome
C H02583 X-linked intellectual disability-hypotonic facies syndrome
C H02584 Ferguson-Bonni neurodevelopmental syndrome
C H02587 Luo-Schoch-Yamamoto syndrome
C H02611 Turnpenny-Fry syndrome
C H02612 Radio-Tartaglia syndrome
C H02613 Brunet-Wagner neurodevelopmental syndrome
C H02614 Snijders Blok-Campeau syndrome
C H02615 Parenti-Mignot neurodevelopmental syndrome
C H02616 Neurodevelopmental disorder with macrocephaly
C H02617 Bryant-Li-Bhoj neurodevelopmental syndrome
C H02618 Developmental delay with variable intellectual disability and dysmorphic facies
C H02622 Shukla-Vernon syndrome
C H02623 Kury-Isidor syndrome
C H02632 PP2A-related neurodevelopmental disorder
C H02633 Beck-Fahrner syndrome
C H02635 Poirier-Bienvenu neurodevelopmental syndrome
C H02651 Lessel-Kreienkamp syndrome
C H02659 Dentici-Novelli neurodevelopmental syndrome
C H02666 Chilton-Okur-Chung neurodevelopmental syndrome
C H02682 Nizon-Isidor syndrome
C H02685 Developmental delay with neuropsychiatric disorders
C H02686 Developmental delay with dysmorphic facies and dental anomalies
C H02688 Dworschak-Punetha neurodevelopmental syndrome
C H02698 Trichohepatoneurodevelopmental syndrome
C H02700 Intellectual developmental disorder with impaired language and dysmorphic facies
C H02712 Li-Campeau syndrome
C H02714 Tessadori-Bicknell-van Haaften neurodevelopmental syndrome
C H02715 Neurodevelopmental disorder with defects of ubiquitin-proteasome system
C H02728 Marbach-Schaaf neurodevelopmental syndrome
C H02734 Hengel-Maroofian-Schols syndrome
B LD9Y Other specified developmental anomalies
B LD9Z Developmental anomalies, unspecified
#
A21 Symptoms, signs or clinical findings, not elsewhere classified
B Symptoms, signs or clinical findings of blood, blood-forming organs, or the immune system
C Symptoms of blood, blood-forming organs, or the immune system
D MA00 Symptom or complaint of the blood
D MA01 Enlarged lymph nodes
D MA0Y Other specified symptoms of blood, blood-forming organs, or the immune system
C Clinical findings in blood, blood-forming organs, or the immune system
D MA10 Abnormal serum enzyme levels
D MA11 Clinical findings of hormones in blood, blood-forming organs, or the immune system
D MA12 Clinical findings of drugs, medicaments and biological substances in blood, blood-forming organs, or the immune system
D MA13 Clinical findings of substances chiefly nonmedicinal as to source in blood, blood-forming organs, or the immune system
D MA14 Immunological findings in blood, blood-forming organs, or the immune system
D MA15 Microbiological findings in blood, blood-forming organs, or the immune system
D MA16 Cytological findings in blood, blood-forming organs, or the immune system
D MA17 Histological findings in blood, blood-forming organs, or the immune system
D MA18 Certain clinical findings of blood chemistry
D MA19 Certain abnormalities of plasma proteins
D MA1A Elevated erythrocyte sedimentation rate or abnormality of plasma viscosity
D MA1Y Other specified clinical findings in blood, blood-forming organs, or the immune system
C MA3Y Other specified symptoms, signs or clinical findings of blood, blood-forming organs, or the immune system
B Symptoms, signs or clinical findings of endocrine, nutritional or metabolic diseases
C Results of function studies of the endocrine, nutritional or metabolic diseases
D MA50 Abnormal results of thyroid function studies
D MA51 Abnormal results of other endocrine function studies
C MA6Y Other specified symptoms, signs or clinical findings of endocrine, nutritional or metabolic diseases
B Symptoms, signs or clinical findings of speech or voice
C Symptoms or signs involving speech or voice
D MA80 Speech disturbances
D MA81 Speech dysfluency
D MA82 Voice disturbances
D MA8Y Other specified symptoms or signs involving speech or voice
C MB0Y Other specified symptoms, signs or clinical findings of speech or voice
B Mental or behavioural symptoms, signs or clinical findings
C MB20 Symptoms, signs or clinical findings involving consciousness
C MB21 Symptoms, signs or clinical findings involving cognition
C MB22 Symptoms or signs involving motivation or energy
C MB23 Symptoms or signs involving appearance or behaviour
C MB24 Symptoms or signs involving mood or affect
C MB25 Symptoms or signs involving form of thought
C MB26 Symptoms or signs involving content of thought
C MB27 Symptoms or signs involving perceptual disturbance
C MB28 Symptoms or signs related to personality features
C MB29 Symptoms or signs involving eating and related behaviour
C MB2A Symptoms or signs involving elimination
C MB2Y Other specified mental or behavioural symptoms, signs or clinical findings
B Symptoms, signs or clinical findings of the nervous system
C Symptoms or signs involving the nervous system
D MB40 Sensation disturbance
D MB41 Disturbances of smell and taste
D MB42 Phonophobia
D MB43 Dyssomnia
D MB44 Abnormalities of gait and mobility
D MB45 Lack of coordination
D MB46 Abnormal involuntary movements
D MB47 Abnormality of tonus and reflex
E H02388 Infantile-onset limb and orofacial dyskinesia
E H02389 Familial dyskinesia with facial myokymia
D MB48 Dizziness and giddiness
D MB49 Aura
D MB4A Apraxia
D MB4B Symbolic dysfunctions
E H01899 Dyslexia
D MB4C Gerstmann syndrome
D MB4D Headache, not elsewhere classified
D Paralytic symptoms
E MB50 Tetraplegia
E MB51 Diplegia of upper extremities
E MB52 Diplegia of lower extremities
E MB53 Hemiplegia
F H00998 Alternating hemiplegia of childhood
E MB54 Monoplegia of upper extremity
E MB55 Monoplegia of lower extremity
E MB56 Paraplegia
E MB57 Functional level of injury of spinal cord
E MB5Y Other specified paralytic symptoms
E MB5Z Paralytic symptoms, unspecified
D MB60 Sleeptalking
D MB6Y Other specified symptoms or signs involving the nervous system
C Clinical findings in the nervous system
D MB70 Clinical findings in cerebrospinal fluid
D MB71 Clinical findings on diagnostic imaging of central nervous system
D MB72 Results of function studies of the nervous system
D MB7Y Other specified clinical findings in the nervous system
C MB9Y Other specified symptoms, signs or clinical findings of the nervous system
B Symptoms, signs or clinical findings of the visual system
C Symptoms or signs involving the visual system
D MC10 Eye appearance abnormal
D MC11 Eye sensation abnormal
D MC12 Chronic enlargement of lacrimal gland
D MC13 Epiphora
D MC14 Eye discharge
D MC15 Red eye
D MC16 Pallor conjunctiva
D MC17 Icteric sclera
D MC18 Ocular pain
D MC19 Quadrantanopia
D MC1A Visual floaters
D MC1B Symptom or complaint of the eyelid
D MC1C Symptom or complaint of glasses
D MC1D Symptom or complaint of contact lens
D MC1Y Other specified symptoms or signs involving the visual system
C MC20 Clinical findings of the visual system
C MC21 Impairment of electrophysiological functions
C MC2Y Other specified symptoms, signs or clinical findings of the visual system
B Symptoms, signs or clinical findings of ear or mastoid process
C Symptoms or signs involving the ear or mastoid process
D MC40 Plugged feeling ear
D MC41 Tinnitus
D MC4Y Other specified symptoms or signs involving the ear or mastoid process
C MC6Y Other specified symptoms, signs or clinical findings of ear or mastoid process
B Symptoms, signs or clinical findings of the circulatory system
C Symptoms or signs involving the circulatory system
D MC80 Abnormal blood-pressure reading, without diagnosis
D MC81 Abnormalities of heart beat
D MC82 Cardiac arrest
D MC83 Cardiac murmurs and other cardiac sounds
D MC84 Cardiovascular pain
D MC85 Gangrene
D MC86 Precordial pain
D MC87 Pressure or tightness of heart
D MC88 Prominent veins
D MC8Y Other specified symptoms or signs involving the circulatory system
C MC90 Clinical findings on diagnostic imaging of heart or coronary circulation
C MC91 Results of function studies of the circulatory system
C MC9Y Other specified symptoms, signs or clinical findings of the circulatory system
B Symptoms, signs or clinical findings of the respiratory system
C Symptoms or signs involving the respiratory system
D MD10 Abnormal sputum
D MD11 Abnormalities of breathing
D MD12 Cough
D Haemorrhage from respiratory passages
E MD20 Epistaxis
E MD21 Haemorrhage from throat
E MD22 Haemoptysis
E MD23 Haemorrhage from other sites in respiratory passages
E MD24 Acute idiopathic pulmonary haemorrhage in infants over 28 days of age
E MD2Z Haemorrhage from respiratory passages, unspecified
D MD30 Pain in throat or chest
D MD31 Pleurisy
D MD32 Rales
D MD33 Respiratory arrest
D MD34 Symptom or complaint of the nose
D MD35 Symptom or complaint of the sinus
D MD36 Symptom or complaint of the throat
D MD3Y Other specified symptoms or signs involving the respiratory system
C Clinical findings in the respiratory system
D MD40 Clinical findings in specimens from respiratory organs and thorax
D MD41 Clinical findings on diagnostic imaging of lung
D MD42 Results of function studies of the respiratory system
D MD4Y Other specified clinical findings in the respiratory system
C MD6Y Other specified symptoms, signs or clinical findings of the respiratory system
B Symptoms, signs or clinical findings of the digestive system or abdomen
C Symptoms or signs involving the digestive system or abdomen
D MD80 Symptoms or signs of the orofacial complex
D MD81 Abdominal or pelvic pain
D MD82 Intra-abdominal or pelvic swelling, mass or lump
D Symptoms related to the upper gastrointestinal tract
E MD90 Nausea or vomiting
E MD91 Belching
E MD92 Dyspepsia
E MD93 Dysphagia
E MD94 Halitosis
E MD95 Heartburn
E MD9Y Other specified symptoms related to the upper gastrointestinal tract
D Symptoms related to the lower gastrointestinal tract or abdomen
E ME00 Abdominal compartment syndrome
E ME01 Abdominal distension
E ME02 Abdominal rigidity
E ME03 Abnormal bowel sounds
E ME04 Ascites
E ME05 Change in bowel habit
E ME06 Chronic enteritis of uncertain aetiology
E ME07 Faecal incontinence
E ME08 Flatulence and related conditions
E ME09 Rectal tenesmus
E ME0A Visible peristalsis
E ME0B Problems with defaecation, not otherwise specified
E ME0Y Other specified symptoms related to the lower gastrointestinal tract or abdomen
D ME10 Abnormalities related to hepatobiliary system
D ME1Y Other specified symptoms or signs involving the digestive system or abdomen
C Clinical findings in the digestive system
D ME20 Clinical findings in specimens from digestive organs or abdominal cavity
D ME21 Clinical findings on diagnostic imaging of liver or biliary tract
D ME22 Clinical findings on diagnostic imaging of digestive tract
D ME23 Results of function studies of the digestive system
D ME24 Clinical manifestations of the digestive system
D ME2Y Other specified clinical findings in the digestive system
C ME4Y Other specified symptoms, signs or clinical findings of the digestive system or abdomen
B Symptoms, signs or clinical findings involving the skin
C Symptoms or signs involving the skin
D ME60 Skin lesion of uncertain or unspecified nature
D ME61 Subcutaneous swelling, mass or lump of uncertain or unspecified nature
D ME62 Acute skin eruption of uncertain or unspecified nature
D ME63 Chronic skin disorder of uncertain or unspecified nature
D ME64 Non-specific cutaneous vascular signs
D ME65 Disturbances of skin sensation of unspecified aetiology
D ME66 Miscellaneous non-specific skin-related symptoms and signs
D ME67 Skin disorder of uncertain or unspecified nature
D ME6Y Other specified symptoms or signs involving the skin
B Symptoms, signs or clinical findings of the musculoskeletal system
C Symptoms or signs of the musculoskeletal system
D ME80 Clicking hip
D ME81 Musculoskeletal chest pain
D ME82 Pain in joint
D ME83 Rheumatism, unspecified
D ME84 Spinal pain
D ME85 Stiffness of joint
D ME86 Symptom or complaint of a body part
D ME8Y Other specified symptoms or signs of the musculoskeletal system
C Clinical findings in the musculoskeletal system
D ME90 Clinical findings on diagnostic imaging of skull and head
D ME91 Clinical findings on diagnostic imaging of limbs
D ME92 Clinical findings on diagnostic imaging of other parts of musculoskeletal system
D ME93 Biomechanical lesions, not elsewhere classified
D ME9Y Other specified clinical findings in the musculoskeletal system
C MF1Y Other specified symptoms, signs or clinical findings of the musculoskeletal system
B Symptoms, signs or clinical findings of the genitourinary system
C Symptoms, signs or clinical findings involving the female genital system
D MF30 Breast lump or mass female
D MF31 Breast or lactation symptom or complaint
D MF32 Menopausal symptom or complaint
D MF33 Premenstrual symptom or complaint
D MF34 Pregnancy symptom or complaint
D MF35 Postpartum symptom or complaint
D MF36 Other symptom or complaint of vagina
D MF37 Symptom or complaint of female nipple
D MF38 Symptom or complaint of female pelvis
D MF39 Symptom or complaint of the vulva
D MF3A Vaginal discharge
E H01380 Bacterial vaginosis
D MF3Y Other specified symptoms, signs or clinical findings involving the female genital system
C Symptoms, signs or clinical findings involving the male genital system
D MF40 Problems of male genital organs
D MF41 Symptom or complaint of male sexual function
D MF42 Retractile testis migrans
D MF4Y Other specified symptoms, signs or clinical findings involving the male genital system
C Symptoms, signs or clinical findings involving the urinary system
D MF50 Abnormal micturition
D MF51 Anuria or oliguria
D MF52 Bladder pain
D MF53 Extrarenal uraemia
D MF54 Macroscopic changes of size of the kidney
D MF55 Polyuria
D MF56 Renal colic
D MF57 Symptom or complaint of bladder
D MF58 Urethral discharge
D MF59 Urinary symptom or complaint
D MF5Y Other specified symptoms, signs or clinical findings involving the urinary system
C Clinical findings in specimens from female genital organs
D MF60 Abnormal level of enzymes in specimens from female genital organs
D MF61 Abnormal level of hormones in specimens from female genital organs
D MF62 Abnormal level of drugs, medicaments and biological substances in specimens from female genital organs
D MF63 Abnormal level of substances chiefly nonmedicinal as to source in specimens from female genital organs
D MF64 Abnormal immunological findings in specimens from female genital organs
D MF65 Abnormal microbiological findings in specimens from female genital organs
D MF66 Abnormal cytological findings in specimens from female genital organs
D MF67 Abnormal histological findings in specimens from female genital organs
D MF68 Abnormal chromosomal findings in specimens from female genital organs
D MF6Y Other specified clinical findings in specimens from female genital organs
D MF6Z Clinical findings in specimens from female genital organs, unspecified
C Clinical findings in specimens from male genital organs
D MF70 Abnormal level of enzymes in specimens from male genital organs
D MF71 Abnormal level of hormones in specimens from male genital organs
D MF72 Abnormal level of drugs, medicaments and biological substances in specimens from male genital organs
D MF73 Abnormal level of substances chiefly nonmedicinal as to source in specimens from male genital organs
D MF74 Abnormal immunological findings in specimens from male genital organs
D MF75 Abnormal microbiological findings in specimens from male genital organs
D MF76 Abnormal cytological findings in specimens from male genital organs
D MF77 Abnormal histological findings in specimens from male genital organs
D MF78 Abnormal chromosomal findings in specimens from male genital organs
D MF7Y Other specified clinical findings in specimens from male genital organs
D MF7Z Clinical findings in specimens from male genital organs, unspecified
C Clinical findings in specimens from the urinary system
D MF80 Diffuse mesangial sclerosis
D MF81 Fibronectin glomerulopathy
E H01260 Glomerulopathy with fibronectin deposits
D MF82 Lipoprotein glomerulopathy
E H00887 Lipoprotein glomerulopathy
D MF83 Diabetic glomerular changes
D MF84 Pauci-immune proliferative glomerulonephritis
D MF85 Anti-glomerular basement membrane antibody mediated disease
E H01721 Anti-glomerular basement membrane (GBM) disease
D MF8Y Other specified clinical findings in specimens from the urinary system
E H00626 Focal segmental glomerulosclerosis
E H01581 IgA nephropathy
E H01726 Membranoproliferative glomerulonephritis
E H01767 Henoch-Schonlein purpura nephritis
E H02579 C3 glomerulopathy
D MF8Z Clinical findings in specimens from the urinary system, unspecified
C Clinical findings on examination of urine, without diagnosis
D MF90 Acetonuria
D MF91 Bilirubinuria
D MF92 Chyluria
D MF93 Glycosuria
D MF94 Haemoglobinuria
D MF95 Myoglobinuria
E H01290 Acute recurrent myoglobinuria
D MF96 Proteinuria
D MF97 Pyuria
D MF98 Abnormal levels of serum electrolytes in the urine
E H02340 Absorptive hypercalciuria
D MF99 Elevated urine levels of drugs, medicaments and biological substances
D MF9A Abnormal urine levels of substances chiefly nonmedicinal as to source
D MF9B Abnormal findings on microbiological examination of urine
D MF9C Abnormal findings on cytological and histological examination of urine
D MF9Y Other specified clinical findings on examination of urine, without diagnosis
C MG00 Clinical findings on diagnostic imaging of breast
C MG01 Clinical findings on diagnostic imaging of urinary organs
C MG02 Results of kidney function studies
C MG0Y Other specified symptoms, signs or clinical findings of the genitourinary system
B General symptoms, signs or clinical findings
C General symptoms
D MG20 Cachexia
D MG21 Chills
D MG22 Fatigue
D MG23 Fear of death or dying
D MG24 Fear of disease
D MG25 Feeling ill
D MG26 Fever of other or unknown origin
D MG27 Haemorrhage, not elsewhere classified
D MG28 Hypothermia, not associated with low environmental temperature
D MG29 Oedema
D MG2A Ageing associated decline in intrinsic capacity
D Pain
E MG30 Chronic pain
F H01636 Fibromyalgia
E MG31 Acute pain
E MG3Z Pain, unspecified
D MG40 Shock
D MG41 Sleep disturbance, not elsewhere classified
D MG42 Somnolence, not elsewhere classified
D MG43 Symptoms and signs concerning food and fluid intake
D MG44 Symptoms peculiar to infancy
E H02681 Short stature with nonspecific skeletal abnormalities
D MG45 Syncope and collapse
D MG46 Systemic inflammatory response syndrome of noninfectious origin
D MG47 Toxicosis not further specified
D MG48 Unknown and unspecified causes of morbidity
D MG49 Hangover
D MG4A Multi organ failure
D MG4Y Other specified general symptoms
C Finding of microorganism resistant to antimicrobial drugs
D MG50 Finding of gram negative bacteria resistant to antimicrobial drugs
E H00309 Multidrug-resistant Acinetobacter infection
E H01422 Carbapenem-resistant bacterial infection
E H00313 Multidrug-resistant Pseudomonas aeruginosa infection
D MG51 Finding of gram positive bacteria resistant to antimicrobial drugs
E H00330 Methicillin-resistant Staphylococcal aureus (MRSA) infection
E H00331 Vancomycin-resistant Staphylococcal aureus (VRSA) infection
E H01423 Penicillin-resistant Streptococcus pneumoniae infection
E H00340 Vancomycin-resistant enterococci infection
E H01401 Methicillin-resistant Staphylococcus epidermidis (MRSE) infection
D MG52 Finding of bacteria, neither gram negative nor positive, resistant to antimicrobial drugs
E H01472 Multidrug-resistant tuberculosis
D MG53 Finding of virus resistant to antimicrobial drugs
D MG54 Finding of fungus resistant to antimicrobial drugs
D MG55 Finding of parasite resistant to antimicrobial drugs
D MG56 Finding of microorganism resistant to other multiple antimicrobial drugs
D MG5Y Finding of other microorganism resistant to antimicrobial drugs
D MG5Z Finding of microorganism resistant to antimicrobial drugs, unspecified
C Clinical findings in specimens from other specified organs, systems and tissues
D MG60 Abnormal level of enzymes in specimens from other organs, systems and tissues
D MG61 Abnormal level of hormones in specimens from other organs, systems and tissues
D MG62 Abnormal level of drugs, medicaments and biological substances in specimens from other organs, systems and tissues
D MG63 Abnormal level of substances chiefly nonmedicinal as to source in specimens from other organs, systems and tissues
D MG64 Abnormal immunological findings in specimens from other organs, systems and tissues
D MG65 Abnormal microbiological findings in specimens from other organs, systems and tissues
D MG66 Abnormal cytological findings in specimens from other organs, systems and tissues
D MG67 Abnormal histological findings in specimens from other organs, systems and tissues
D MG6Y Other specified clinical findings in specimens from other specified organs, systems and tissues
C Abnormal results, not elsewhere classified
D MG70 Abnormal diagnostic imaging results not elsewhere classified
D MG71 Abnormal laboratory results, not elsewhere classified
D MG72 Abnormal results of function studies of other organs and systems
D MG7Y Other specified abnormal results, not elsewhere classified
D MG7Z Abnormal results, not elsewhere classified, unspecified
C MG9Y Other specified general symptoms, signs or clinical findings
B Ill-defined and unknown causes of mortality
C MH10 Brain death
C MH11 Sudden infant death syndrome
D H02174 Sudden infant death with dysgenesis of the testes syndrome
C MH12 Other sudden death, cause unknown
C MH13 Unattended death
C MH14 Other ill-defined and unspecified causes of mortality
C MH15 Sudden unexpected death in epilepsy
B MH2Y Other specified symptoms, signs or clinical findings, not elsewhere classified
#
A22 Injury, poisoning or certain other consequences of external causes
B Injuries to the head
C NA00 Superficial injury of head
C NA01 Open wound of head
C NA02 Fracture of skull or facial bones
C NA03 Dislocation or strain or sprain of joints or ligaments of head
C NA04 Injury of cranial nerves
C NA05 Injury of blood vessels of head
C NA06 Injury of eye or orbit
C NA07 Intracranial injury
C NA08 Crushing injury of head
C NA09 Traumatic amputation of part of head
C NA0A Certain specified injuries of head
C NA0B Injury of the auricle
C NA0C Injury of middle or inner ear
C NA0D Injury of teeth or supporting structures
C NA0Z Injuries to the head, unspecified
B Injuries to the neck
C NA20 Superficial injury of neck
C NA21 Open wound of neck
C NA22 Fracture of neck
C NA23 Dislocation or strain or sprain of joints or ligaments at neck level
C Injury of nerves or spinal cord at neck level
D Injury of spinal cord at neck level
E NA30 Concussion or oedema of cervical spinal cord
E NA31 Certain specified injuries of cervical spinal cord
E NA3Z Injury of cervical spinal cord, unspecified
D Injury of nerves at neck level
E NA40 Injury of nerve root of cervical spine
E NA41 Injury of brachial plexus
E NA42 Injury of peripheral nerves of neck
E NA43 Injury of cervical sympathetic nerves
E NA44 Injury of phrenic nerve
E NA4Y Injury of other specified nerves at neck level
E NA4Z Injury of nerves at neck level, unspecified
C NA60 Injury of blood vessels at neck level
C NA61 Injury of muscle, fascia or tendon at neck level
C NA62 Crushing injury of neck
C NA63 Traumatic amputation at neck level
C NA64 Multiple injuries of neck
C NA6Y Other specified injuries to the neck
C NA6Z Injuries to the neck, unspecified
B Injuries to the thorax
C NA80 Superficial injury of thorax
C NA81 Open wound of thorax
C NA82 Fracture of rib, sternum or thoracic spine
C NA83 Dislocation or strain or sprain of joints or ligaments of thorax
C Injury of nerves or spinal cord at thorax level
D Injury of spinal cord at thorax level
E NA90 Concussion or oedema of thoracic spinal cord
E NA91 Certain specified injuries of thoracic spinal cord
E NA9Z Injury of thoracic spinal cord, unspecified
D Injury of nerves at thorax level
E NB00 Injury of nerve root of thoracic spine
E NB01 Injury of peripheral nerves of thorax
E NB02 Injury of thoracic sympathetic nerves
E NB0Y Injury of other specified nerves at thorax level
D NB2Y Other specified injury of nerves or spinal cord at thorax level
D NB2Z Injury of nerves or spinal cord at thorax level, unspecified
C NB30 Injury of blood vessels of thorax
C NB31 Injury of heart
C NB32 Injury of other or unspecified intrathoracic organs
C NB33 Crushing injury of thorax or traumatic amputation of part of thorax
C NB34 Injury of muscle, fascia or tendon at thorax level
C NB35 Multiple injuries of thorax
C NB3Y Other specified injuries to the thorax
C NB3Z Injuries to the thorax, unspecified
B Injuries to the abdomen, lower back, lumbar spine or pelvis
C NB50 Superficial injury of abdomen, lower back or pelvis
C NB51 Open wound of abdomen, lower back or pelvis
C NB52 Fracture of lumbar spine or pelvis
C NB53 Dislocation or strain or sprain of joints or ligaments of lumbar spine or pelvis
C Injury of nerves or lumbar spinal cord at abdomen, lower back or pelvis level
D Injury of spinal cord at abdomen, lower back or pelvis level
E NB60 Concussion or oedema of lumbar spinal cord
E NB61 Concussion or oedema of sacral spinal cord
E NB62 Certain specified injuries of lumbar spinal cord
E NB63 Certain specified injuries of sacral spinal cord
E NB6Z Injury of spinal cord at abdomen, lower back or pelvis level, unspecified
D Injury of nerves at abdomen, lower back or pelvis level
E NB70 Injury of nerve root of lumbar spine
E NB71 Injury of nerve root of sacral spine
E NB72 Injury of cauda equina
E NB73 Injury of lumbosacral plexus
E NB74 Injury of lumbar, sacral or pelvic sympathetic nerves
E NB75 Injury of peripheral nerve of abdomen, lower back or pelvis
E NB7Y Other specified injury of nerves at abdomen, lower back or pelvis level
E NB7Z Injury of nerves at abdomen, lower back or pelvis level, unspecified
C NB90 Injury of blood vessels at abdomen, lower back or pelvis level
C NB91 Injury of intra-abdominal organs
C NB92 Injury of urinary or pelvic organs
C NB93 Crushing injury or traumatic amputation of part of abdomen, lower back or pelvis
C NB94 Injury of muscle, fascia or tendon of abdomen, lower back or pelvis
C NB95 Injury of intra-abdominal organ with pelvic organ
C NB96 Other multiple injuries of abdomen, lower back or pelvis
C NB97 Certain specified injuries of abdomen, lower back or pelvis
C NB98 Injury to female genital organ without further specification
C NB99 Injury to male genital organ without further specification
C NB9Y Other specified injuries to the abdomen, lower back, lumbar spine or pelvis
C NB9Z Injuries to the abdomen, lower back, lumbar spine or pelvis, unspecified
B Injuries to the shoulder or upper arm
C NC10 Superficial injury of shoulder or upper arm
C NC11 Open wound of shoulder or upper arm
C NC12 Fracture of shoulder or upper arm
C NC13 Dislocation or strain or sprain of joints or ligaments of shoulder girdle
C NC14 Injury of nerves at shoulder or upper arm level
C NC15 Injury of blood vessels at shoulder or upper arm level
C NC16 Injury of muscle, fascia, tendon or bursa at shoulder or upper arm level
C NC17 Crushing injury of shoulder or upper arm
C NC18 Traumatic amputation of shoulder or upper arm
C NC19 Multiple injuries of shoulder or upper arm
C NC1Y Other specified injuries to the shoulder or upper arm
C NC1Z Injuries to the shoulder or upper arm, unspecified
B Injuries to the elbow or forearm
C NC30 Superficial injury of forearm
C NC31 Open wound of forearm
C NC32 Fracture of forearm
C NC33 Dislocation or strain or sprain of joints or ligaments of elbow
C NC34 Injury of nerves at forearm level
C NC35 Injury of blood vessels at forearm level
C NC36 Injury of muscle, fascia, tendon or bursa at forearm level
C NC37 Crushing injury of forearm
C NC38 Traumatic amputation of forearm
C NC39 Multiple injuries of forearm
C NC3Y Other specified injuries to the elbow or forearm
C NC3Z Injuries to the elbow or forearm, unspecified
B Injuries to the wrist or hand
C NC50 Injury to fingernail
C NC51 Superficial injury of wrist or hand
C NC52 Open wound of wrist or hand
C NC53 Fracture at wrist or hand level
C NC54 Dislocation or strain or sprain of joints or ligaments at wrist or hand level
C NC55 Injury of nerves at wrist or hand level
C NC56 Injury of blood vessels at wrist or hand level
C NC57 Injury of muscle, fascia or tendon at wrist or hand level
C NC58 Crushing injury of wrist or hand
C NC59 Traumatic amputation of wrist or hand
C NC5A Multiple injuries of wrist or hand
C NC5Y Other specified injuries to the wrist or hand
C NC5Z Injuries to the wrist or hand, unspecified
B Injuries to the hip or thigh
C NC70 Superficial injury of hip or thigh
C NC71 Open wound of hip or thigh
C NC72 Fracture of femur
C NC73 Dislocation or strain or sprain of joint or ligaments of hip
C NC74 Injury of nerves at hip or thigh level
C NC75 Injury of blood vessels at hip or thigh level
C NC76 Injury of muscle, fascia, tendon or bursa at hip or thigh level
C NC77 Crushing injury of hip or thigh
C NC78 Traumatic amputation of hip or thigh
C NC79 Multiple injuries of hip or thigh
C NC7Y Other specified injuries to the hip or thigh
C NC7Z Injuries to the hip or thigh, unspecified
B Injuries to the knee or lower leg
C NC90 Superficial injury of knee or lower leg
C NC91 Open wound of knee or lower leg
C NC92 Fracture of lower leg, including ankle
C NC93 Dislocation or strain or sprain of joints or ligaments of knee
C NC94 Injury of nerves at lower leg level
C NC95 Injury of blood vessels at lower leg level
C NC96 Injury of muscle, fascia, tendon or bursa at lower leg level
C NC97 Crushing injury of lower leg
C NC98 Traumatic amputation of lower leg
C NC99 Multiple injuries of lower leg
C NC9Y Other specified injuries to the knee or lower leg
C NC9Z Injuries to the knee or lower leg, unspecified
B Injuries to the ankle or foot
C ND10 Injury to toenail
C ND11 Superficial injury of ankle or foot
C ND12 Open wound of ankle or foot
C ND13 Fracture of foot, except ankle
C ND14 Dislocation or strain or sprain of joints or ligaments at ankle or foot level
C ND15 Injury of nerves at ankle or foot level
C ND16 Injury of blood vessels at ankle or foot level
C ND17 Injury of muscle, fascia or tendon at ankle or foot level
C ND18 Crushing injury of ankle or foot
C ND19 Traumatic amputation of ankle or foot
C ND1A Multiple injuries of ankle or foot
C ND1Y Other specified injuries to the ankle or foot
C ND1Z Injuries to the ankle or foot, unspecified
B Injuries involving multiple body regions
C ND30 Superficial injuries involving multiple body regions
C ND31 Open wounds involving multiple body regions
C ND32 Fractures involving multiple body regions
C ND33 Dislocations, strains or sprains involving multiple body regions
C ND34 Crushing injuries involving multiple body regions
C ND35 Traumatic amputations involving multiple body regions
C ND36 Other injuries involving multiple body regions, not elsewhere classified
C ND37 Unspecified multiple injuries
B Injuries to unspecified part of trunk, limb or body region
C ND50 Fracture of spine, level unspecified
C ND51 Other injuries of spine or trunk, level unspecified
C ND52 Fracture of arm, level unspecified
C ND53 Other injuries of arm, level unspecified
C ND54 Fracture of leg, level unspecified
C ND55 Other injuries of leg, level unspecified
C ND56 Injury of unspecified body region
C ND57 Secondary effect of trauma
C ND5Y Other specified injuries to unspecified part of trunk, limb or body region
C ND5Z Injuries to unspecified part of trunk, limb or body region, unspecified
B Effects of foreign body entering through natural orifice
C ND70 Foreign body on external eye
C ND71 Foreign body in ear
C ND72 Foreign body in respiratory tract
C ND73 Foreign body in alimentary tract
C ND74 Foreign body in genitourinary tract
C ND7Z Effects of foreign body entering through natural orifice, unspecified
B Burns
C Burns of external body surface, specified by site
D ND90 Burn of head or neck except face
D ND91 Burn of face except eye or ocular adnexa
D ND92 Burn of trunk except perineum or genitalia
D ND93 Burn of perineum or genitalia
D ND94 Burn of shoulder or arm, except wrist or hand
D ND95 Burn of wrist or hand
D ND96 Burn of hip or leg, except ankle or foot
D ND97 Burn of ankle or foot
D ND99 Acute skin injury due to skin contact with corrosive substance
D ND9Y Burns of external body surface, other specified site
D ND9Z Burns of external body surface, unspecified site
C Burns of eye or internal organs
D NE00 Burn of eye or ocular adnexa
D NE01 Burn of respiratory tract
D NE02 Burn of other internal organs
D NE0Z Burns of unspecified internal organ
C Burns of multiple or unspecified body regions
D NE10 Burns of multiple body regions
D NE11 Burn of unspecified body region
C NE2Z Burns, unspecified
B Frostbite
C NE40 Superficial frostbite
C NE41 Frostbite with tissue necrosis
C NE42 Frostbite involving multiple body regions
C NE4Z Frostbite, unspecified
B Harmful effects of substances
C NE60 Harmful effects of drugs, medicaments or biological substances, not elsewhere classified
C NE61 Harmful effects of or exposure to noxious substances, chiefly nonmedicinal as to source, not elsewhere classified
C NE6Z Harmful effects of unspecified substance
B Injury or harm arising from surgical or medical care, not elsewhere classified
C NE80 Injury or harm arising following infusion, transfusion or therapeutic injection, not elsewhere classified
C NE81 Injury or harm arising from a procedure, not elsewhere classified
C NE82 Dysfunction or complication of pacemaker, pacemaker lead or implantable cardioverter defibrillator, not elsewhere classified
C NE83 Injury or harm arising from other device, implant or graft, not elsewhere classified
C NE84 Failure or rejection of transplanted organs or tissues
D H00083 Allograft rejection
C NE85 Complications peculiar to reattachment or amputation
C NE86 Malignant hyperthermia due to anaesthesia
C NE87 Failed or difficult intubation
C NE88 Drug toxicity associated with harm in surgical or medical care, not elsewhere classified
C NE89 Awareness under general anaesthesia
C NE8Y Other specified injury or harm arising from surgical or medical care, not elsewhere classified
C NE8Z Injury or harm arising from surgical or medical care, not elsewhere classified, unspecified
B Other or unspecified effects of external causes
C NF00 Effects of radiation, not elsewhere classified
C NF01 Effects of heat
C NF02 Hypothermia
C NF03 Other effects of reduced temperature
D H01643 Chilblains
C NF04 Effects of air pressure or water pressure
C NF05 Asphyxiation
C NF06 Effects of strenuous physical exercise
C NF07 Effects of other deprivation
C NF08 Effects of certain specified external causes
C NF09 Adverse effects, not elsewhere classified
C NF0A Certain early complications of trauma, not elsewhere classified
C NF0Y Other specified effects of external causes
C NF0Z Unspecified effects of external causes
B NF2Y Other specified injury, poisoning or certain other consequences of external causes
B NF2Z Unspecified injury, poisoning or certain other consequences of external causes
#
A25 Codes for special purposes
B International provisional assignment of new diseases of uncertain aetiology and emergency use
C RA01 COVID-19
D H02398 COVID-19
C RA02 Post COVID-19 condition
C RA03 Multisystem inflammatory syndrome associated with COVID-19
B National provisional assignment of new diseases of uncertain aetiology
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#
#[ DISEASE | BRITE | KEGG2 | KEGG ]
#Last updated: April 23, 2024
#
ICD-11 by World Health Organization
#
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