ORTHOLOGY: K00544
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Entry
K00544 KO
Symbol
BHMT
Name
betaine-homocysteine S-methyltransferase [EC:
2.1.1.5
]
Pathway
map00260
Glycine, serine and threonine metabolism
map00270
Cysteine and methionine metabolism
map01100
Metabolic pathways
map01110
Biosynthesis of secondary metabolites
Module
M00974
Betaine metabolism, animals, betaine => glycine
Reaction
R02821
trimethylaminoacetate:L-homosysteine S-methyltransferase
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09105 Amino acid metabolism
00260 Glycine, serine and threonine metabolism
K00544 BHMT; betaine-homocysteine S-methyltransferase
00270 Cysteine and methionine metabolism
K00544 BHMT; betaine-homocysteine S-methyltransferase
Enzymes [BR:
ko01000
]
2. Transferases
2.1 Transferring one-carbon groups
2.1.1 Methyltransferases
2.1.1.5 betaine---homocysteine S-methyltransferase
K00544 BHMT; betaine-homocysteine S-methyltransferase
BRITE hierarchy
Other DBs
GO:
0047150
Genes
HSA:
635
(BHMT)
PTR:
461786
(BHMT)
PPS:
100985336
(BHMT)
GGO:
101138811
(BHMT)
PON:
100174207
(BHMT)
NLE:
100588814
(BHMT)
HMH:
116471070
(BHMT)
MCC:
714363
(BHMT)
MCF:
102117049
(BHMT)
MTHB:
126957590
MNI:
105475095
(BHMT)
CSAB:
103223581
(BHMT)
CATY:
105599167
(BHMT)
PANU:
101022670
(BHMT)
TGE:
112626272
(BHMT)
MLEU:
105548271
(BHMT)
RRO:
104662970
(BHMT)
RBB:
108528900
(BHMT)
TFN:
117065310
(BHMT)
PTEH:
111544428
(BHMT)
CANG:
105524090
(BHMT)
CJC:
100393375
(BHMT)
SBQ:
101049322
(BHMT)
CIMI:
108303778
(BHMT)
CSYR:
103250081
(BHMT)
MMUR:
105872623
(BHMT)
LCAT:
123648430
(BHMT)
PCOQ:
105826595
(BHMT)
OGA:
100945871
(BHMT)
MMU:
12116
(Bhmt)
MCAL:
110307549
(Bhmt)
MPAH:
110328978
(Bhmt)
RNO:
81508
(Bhmt)
MCOC:
116083552
(Bhmt)
ANU:
117700497
(Bhmt)
117717310
MUN:
110539650
CGE:
100754488
(Bhmt)
MAUA:
101832592
(Bhmt)
PROB:
127221074
(Bhmt)
PLEU:
114694686
(Bhmt)
MORG:
121455833
(Bhmt)
MFOT:
126508497
AAMP:
119810203
(Bhmt)
NGI:
103750287
(Bhmt)
HGL:
101723121
(Bhmt)
CPOC:
100724631
(Bhmt)
CCAN:
109675223
(Bhmt)
DORD:
105985348
(Bhmt)
DSP:
122117199
(Bhmt)
PLOP:
125339895
NCAR:
124986895
MMMA:
107152310
(Bhmt)
OCU:
100339955
OPI:
101519034
TUP:
102489167
(BHMT)
GVR:
103597321
(BHMT)
CFA:
479171
(BHMT)
CLUD:
112653426
(BHMT)
VVP:
112919588
(BHMT)
VLG:
121489537
(BHMT)
NPO:
129521084
(BHMT)
AML:
100465664
(BHMT)
UMR:
103681460
(BHMT)
UAH:
113255170
(BHMT)
UAR:
123791536
(BHMT)
ELK:
111148342
LLV:
125100501
MPUF:
101682838
MNP:
132028758
(BHMT)
MLK:
131832393
(BHMT)
NVS:
122901114
(BHMT)
ORO:
101373012
(BHMT)
EJU:
114217614
(BHMT)
ZCA:
113929554
(BHMT)
MLX:
118017139
(BHMT)
NSU:
110589329
(BHMT)
LWW:
102732753
(BHMT)
FCA:
101085179
(BHMT)
PYU:
121014017
(BHMT)
PCOO:
112860987
PBG:
122490207
PVIV:
125161206
LRUF:
124504614
PTG:
102955687
(BHMT)
PPAD:
109274945
(BHMT)
PUC:
125934939
AJU:
106974816
HHV:
120242011
(BHMT)
BTA:
497025
(BHMT)
BOM:
102286920
(BHMT)
BIU:
109564665
(BHMT)
BBUB:
102394345
BBIS:
104984714
(BHMT)
CHX:
102175297
OAS:
101113853
(BHMT)
BTAX:
128054421
ODA:
120852576
(BHMT)
CCAD:
122443008
(BHMT)
MBEZ:
129563603
SSC:
397371
(BHMT)
CFR:
102523171
(BHMT)
CBAI:
105064349
(BHMT)
CDK:
105084827
(BHMT)
VPC:
102525828
(BHMT)
BACU:
103000437
(BHMT)
BMUS:
118892398
(BHMT)
LVE:
103081575
(BHMT)
OOR:
101282223
(BHMT)
DLE:
111184957
(BHMT)
PCAD:
102991634
PSIU:
116750387
(BHMT)
NASI:
112406757
(BHMT)
ECB:
100073265
EPZ:
103548663
(BHMT)
EAI:
106841179
(BHMT)
MYB:
102252728
(BHMT)
MYD:
102775016
(BHMT)
MMYO:
118656687
(BHMT)
MLF:
102425902
(BHMT)
PKL:
118703445
(BHMT)
EFUS:
103305221
(BHMT)
MNA:
107535044
DRO:
112307473
(BHMT)
SHON:
118977292
(BHMT)
AJM:
119035984
(BHMT)
PDIC:
114510404
(BHMT)
PHAS:
123824717
(BHMT)
MMF:
118641671
(BHMT)
PPAM:
129074639
(BHMT)
HAI:
109381916
(BHMT)
RFQ:
117025006
(BHMT)
PALE:
102887754
(BHMT)
PGIG:
120612469
(BHMT)
PVP:
105304644
(BHMT)
RAY:
107497234
(BHMT)
MJV:
108387740
(BHMT)
TOD:
119260224
(BHMT)
SARA:
101541457
(BHMT)
SETR:
126001877
(BHMT)
LAV:
100672133
(BHMT)
TMU:
101354749
ETF:
101642241
(BHMT)
DNM:
101442098
MDO:
100032615
(BHMT)
GAS:
123236818
SHR:
100927569
(BHMT)
AFZ:
127558468
PCW:
110216636
OAA:
100088080
GGA:
416371
(BHMT)
PCOC:
116239911
MGP:
100541641
CJO:
107305933
TPAI:
128074393
LMUT:
125687327
NMEL:
110389382
APLA:
101802407
ACYG:
106042084
CATA:
118251473
AFUL:
116500626
TGU:
100221623
LSR:
110470994
SCAN:
103819545
PMOA:
120502442
OTC:
121341255
PRUF:
121355361
GFR:
102044419
(BHMT)
FAB:
101813460
(BHMT)
OMA:
130265578
PHI:
102112767
PMAJ:
107216432
CCAE:
111941401
CCW:
104695711
CBRC:
103622046
ETL:
114056915
ZAB:
102071668
ACHL:
103810908
SVG:
106856212
MMEA:
130572275
HRT:
120765162
FPG:
101910450
(BHMT)
FCH:
102048321
CLV:
102097034
EGZ:
104124900
NNI:
104011959
104017633
PCRI:
104037008
PLET:
104615204
EHS:
104509696
PCAO:
104052704
ACUN:
113489762
TALA:
104357116
PADL:
103919765
AFOR:
103899795
ACHC:
115336616
HALD:
104311516
HLE:
104841296
AGEN:
126035668
GCL:
127027354
127028691
CCRI:
104169315
CSTI:
104559023
CMAC:
104481766
MUI:
104540707
BREG:
104634490
FGA:
104077850
GSTE:
104262804
LDI:
104348421
MNB:
103767887
OHA:
104330961
NNT:
104411470
SHAB:
115601220
DPUB:
104309462
PGUU:
104458762
ACAR:
104518556
CPEA:
104395693
AVIT:
104268516
CVF:
104285791
RTD:
128902458
CUCA:
104064002
TEO:
104380260
BRHI:
104497298
AAM:
106490831
106499347
AROW:
112967357
NPD:
112945144
TGT:
104581206
DNE:
112987027
SCAM:
104152993
ASN:
102378363
AMJ:
102561209
(BHMT)
CPOO:
109307998
GGN:
109297738
PSS:
102445649
CMY:
102947612
CCAY:
125636505
DCC:
119855822
CPIC:
101937801
TST:
117878734
CABI:
116823758
MRV:
120408209
ACS:
100558455
ASAO:
132767046
PVT:
110073962
(BHMT)
SUND:
121923668
PBI:
103049200
PMUR:
107287879
CTIG:
120312302
TSR:
106544491
PGUT:
117679272
APRI:
131192943
PTEX:
113447452
NSS:
113413944
113419350
VKO:
123031562
PMUA:
114606168
PRAF:
128423192
ZVI:
118076698
(BHMT)
HCG:
128344708
GJA:
107117367
STOW:
125436280
EMC:
129334292
XLA:
495275
(bhmt.L)
XTR:
496651
(bhmt)
NPR:
108799975
RTEM:
120929341
BBUF:
120992415
BGAR:
122924738
MUO:
115463048
GSH:
117353538
DRE:
322228
(bhmt)
SRX:
107717756
107724714
(bhmt)
SANH:
107679462
SGH:
107574103
CCAR:
109046108
CAUA:
113080755
113097702
CGIB:
127942096
127986306
PTET:
122341028
(bhmt)
LROH:
127162125
(bhmt)
OMC:
131528427
(bhmt)
PPRM:
120461919
(bhmt)
RKG:
130088056
(bhmt)
MAMB:
125252262
(bhmt)
CIDE:
127504046
MASI:
127430858
TROS:
130550720
(bhmt)
TDW:
130407734
(bhmt)
MANU:
129423064
(bhmt)
IPU:
108279028
(bhmt)
IFU:
128622897
(bhmt)
PHYP:
113535813
SMEO:
124397867
(bhmt)
TFD:
113646449
(bhmt)
TVC:
132860088
(bhmt)
TRN:
134330404
(bhmt)
AMEX:
103034807
CMAO:
118820406
(bhmt)
EEE:
113573779
CHAR:
105901160
105901214
105902436
(bhmt)
105910603
TRU:
101061373
101062063
TFS:
130517451
(bhmt)
130526444
TNG:
GSTEN00030962G001
LCO:
104921205
104921289
104930138
104930139
104936284
NCC:
104943386
104943387
104948669
104948670
104966862
TBEN:
117472348
117475958
117476489
(bhmt)
CGOB:
115013331
115013368
115013615
115016357
PGEO:
117452088
117455756
(bhmt)
GACU:
117536708
117560599
117560604
117561495
EMAC:
134868888
(bhmt)
134873351
134873820
134874286
ELY:
117251874
117251875
117252237
117252925
117252926
117269200
EFO:
125890425
125890426
125890449
125890450
125906136
PLEP:
121944080
121944246
121944247
121944389
SLUC:
116054167
116054168
116056791
116062994
(bhmt)
ECRA:
117945057
117945058
117945219
117959558
(bhmt)
ESP:
116689207
116689257
PFLV:
114555694
114555876
114555939
114570759
GAT:
120830956
120830957
120831287
120832005
(bhmt)
PPUG:
119224706
119224707
119225361
119225362
119226903
AFB:
129100666
129100667
129100923
129100924
129102188
CLUM:
117735983
117736261
117736815
117736816
117740696
117740910
(bhmt)
PSWI:
130196706
130197168
130197169
130205406
(bhmt)
MSAM:
119891844
119914971
(bhmt)
SCHU:
122865754
122876422
122876937
122876938
CUD:
121509995
121510073
121510074
121510092
121525687
(bhmt)
ALAT:
119018856
119018903
119018904
119019260
119019508
119030143
MZE:
101464577
101482601
112435685
ONL:
100704302
100705166
100705436
OAU:
116315584
116328388
116328389
OLA:
101157623
101175580
OML:
112148056
112162826
(bhmt)
CSAI:
133450647
133450648
133454611
(bhmt)
XMA:
102218191
102225771
102226035
XCO:
114149906
114154707
114154708
XHE:
116724267
116730429
116730431
PRET:
103470080
103470081
103473309
PFOR:
103135835
103141748
PLAI:
106937104
106956825
PMEI:
106916212
106923054
GAF:
122819377
(bhmt)
122827328
122827332
PPRL:
129365809
129374187
(bhmt)
CVG:
107092421
107092484
107093785
CTUL:
119788268
(bhmt)
119798561
119798562
GMU:
124873094
(bhmt)
124877131
NFU:
107374849
107394162
KMR:
108233717
108233718
108251296
(bhmt)
ALIM:
106513660
106532974
NWH:
119413898
AOCE:
111564721
111564722
111570352
111581621
111581625
MCEP:
124996948
(bhmT)
125012487
125012488
125012755
125012756
CSEM:
103390007
103397629
POV:
109625962
109637078
109637079
109638087
SSEN:
122758689
(bhmt)
122769031
122769454
HHIP:
117767260
117768517
117768519
117771585
(bhmt)
HSP:
118098097
118114836
118114895
118114896
PPLT:
128424855
128437929
128438014
128438016
SMAU:
118301462
(bhmt)
118313322
118314207
118314208
LCF:
108878770
108882050
108882056
108895445
(bhmt)
SDU:
111229230
111237735
111237759
111239026
SLAL:
111651687
111651689
111660294
111666825
XGL:
120805803
120806477
HCQ:
109517690
109527101
SSCV:
125979297
125994694
SBIA:
133499786
133515234
PEE:
133399939
133413362
(bhmt)
PTAO:
133475179
133489844
(bhmt)
BPEC:
110156680
110156723
110157444
110172084
110172085
MALB:
109953000
109956508
BSPL:
114862603
114867454
(bhmt)
SJO:
128364714
128364715
128364815
128365203
128380740
SASA:
100194600
(bhmt)
106568115
STRU:
115159735
115203928
OTW:
112220278
(bhmt)
112230819
OMY:
110509664
110523446
(bhmt)
OGO:
124007416
124049093
ONE:
115101012
115121040
OKI:
109868318
109874056
OKE:
118371634
118385459
SALP:
111961763
111963903
SNH:
120021263
120025679
CCLU:
121541555
121582649
ELS:
105015174
SFM:
108925116
108925117
(bhmt)
PKI:
111849814
(bhmt)
111849880
AANG:
118213304
118213305
(bhmt)
118237452
LOC:
102689652
PSPA:
121305143
121313674
ARUT:
117403613
117974146
PSEX:
120532416
(bhmt)
LCM:
102351553
(BHMT)
CMK:
103177766
(bhmt)
RTP:
109930797
(bhmt)
CPLA:
122558390
(bhmt)
HOC:
132822390
(bhmt)
LERI:
129694867
129714267
PMRN:
116942187
LRJ:
133343910
133343913
BFO:
118403599
118403625
118403740
118403835
118408941
118409375
118412861
118419165
118419166
118420119
118422786
118423158
118423159
BBEL:
109462372
109463244
109464847
109467561
109472834
109474178
109474209
109474210
109476287
109481064
CIN:
100180493
100181849
100182838
113474336
SCLV:
120326246
120327870
120328505
120328506
120328890
SPU:
100891161
105438577
105447246
115918144
115918913
115928328
115929946
575553
579857
580174
582813
588895
589758
752628
LPIC:
129258483
129258484
129258534
129259077
129259157
129259605
129262595
129264145
129265678
APLC:
110974267
110984631
110984637
110984652
110984655
110984668
110984669
110984679
110986934
110987105
110988857
110990180
AJC:
117103427
117116060
SKO:
100371248
100372758
100372908
100374951
100376137
100376292
100376443
100376597
100378429
100378580
100378727
102807376
SGRE:
126354127
IEL:
124154290
PVM:
113817434
113819630
PJA:
122245301
122247003
122258389
122266441
PCHN:
125033259
125033278
125035210
125035256
PMOO:
119577942
119583518
119583532
HAME:
121878891
121878895
PCLA:
123771683
CQD:
128696652
PTRU:
123504391
123504392
123504421
123512443
ESN:
126997661
126997662
127008696
MNZ:
135208776
135208777
135213177
HAZT:
108678493
EAF:
111700817
111700974
111708867
LSM:
121129618
PPOI:
119090929
119094136
119096867
ISC:
8023777
DSV:
119442634
RSAN:
119387357
119387358
RMP:
119188312
CSCU:
111619880
PTEP:
107451377
ABRU:
129961808
UDV:
129225264
SDM:
118188532
118195838
LPOL:
106462891
106462894
106462895
LGI:
LOTGIDRAFT_183387
LOTGIDRAFT_217867
LOTGIDRAFT_230320
LOTGIDRAFT_233748
PVUL:
126809610
126811534
126812388
126812389
130010354
PCAN:
112572659
HRF:
124129484
124137148
124138282
124138283
124138284
124140307
124140311
124140312
124146516
124146517
124146524
HRJ:
124262605
124262606
124262607
124262608
124262609
124269213
124269214
124280593
124289090
124291430
124291446
CRG:
105318322
105339804
CVN:
111108276
111109969
CANU:
128159878
128184450
OED:
125674091
125674093
125676585
125677062
MYI:
110455538
110456381
110456382
110456384
110456469
110458153
110464929
110464943
110467328
PMAX:
117326857
117326858
117326859
117327192
117327193
117327194
117327227
117328542
117330294
117331264
117331595
MMER:
123527072
123528071
123536698
123546866
123546873
123548659
123548660
123550078
123551339
123551349
RPHI:
132734918
132738754
132738770
132746720
132747125
132749131
132749132
DPOL:
127841289
127850279
OBI:
106875610
106880067
OSN:
115222737
115222981
115223003
LAK:
106156503
106166038
106166449
106167822
106171079
106171080
106171100
106178981
106179201
NVE:
5519847
EPA:
110231416
110238130
110238131
110238132
110240957
110240959
110240960
110242935
110246242
ATEN:
116294619
116295943
116297504
116297506
116297515
116301137
ADF:
107340042
107342964
AMIL:
114950037
114953867
114960594
114974172
PDAM:
113672660
113673312
113674473
113682319
113686957
SPIS:
111324403
111336507
111338100
111344161
DGT:
114518175
114533873
114540583
XEN:
124453110
124455543
HMG:
100206048
HSY:
130640717
130640969
130641098
130645044
130649193
TAD:
TRIADDRAFT_63716
TRIADDRAFT_63717
AQU:
100638323
100639967
100640174
100640299
105315720
ACAN:
ACA1_155280
PSKY:
A6B44_09920
FPH:
Fphi_0698
FPT:
BZ13_1329
FPI:
BF30_905
FPM:
LA56_1471
FPX:
KU46_649
FPZ:
LA55_102
FPJ:
LA02_579
FRT:
F7308_0118
FRF:
LO80_06845
FHA:
CDV26_01030
FRX:
F7310_00640
FRC:
KX01_643
KX01_645
FAD:
CDH04_09075
FMI:
F0R74_09025
F0R74_09035
FSR:
KQR59_00590
FRL:
FIP56_00595
SPIU:
SPICUR_03835
SROS:
BBH56_03220
CSA:
Csal_0065
CCAG:
SR908_07635
HHAO:
QWG60_02820
SUTR:
L0B52_00870
OCD:
FHY55_16660
PLCG:
RVY76_00055
THW:
BMG03_09465
TEC:
AKL02_008645
PUB:
SAR11_1173
(bhmT)
APC:
HIMB59_00001060
HIMB59_00005120
HIMB59_00005130
APM:
HIMB5_00004530
DRT:
Dret_2255
DALK:
DSCA_49870
BSHI:
LGQ02_01385
OIH:
OB0691
HHD:
HBHAL_1691
HMN:
HM131_17460
HLI:
HLI_07355
HNZ:
P9989_03155
VIR:
X953_04635
VHL:
BME96_03820
VIG:
BKP57_05720
VIL:
CFK37_04880
VNE:
CFK40_05435
VPN:
A21D_02277
VPT:
KBP50_17210
VIK:
KFZ58_07585
LAO:
AOX59_16950
SJE:
AAV35_009460
POF:
GS400_01695
PCHU:
QNI29_12900
BBEV:
BBEV_2151
(yitJ-1)
BSE:
Bsel_2622
PHJ:
LC071_01415
SHV:
AAT16_06155
PMAR:
B0X71_09835
SPAE:
E2C16_15420
ERZ:
ER308_05595
PSAI:
C3B54_11833
BRX:
BH708_15645
BRV:
CFK39_10470
BRZ:
CFK38_00255
BSAU:
DWV08_16395
HMM:
R3I40_01245
SERJ:
SGUI_2075
BLY:
A2T55_13075
BLIN:
BLSMQ_2928
BCAU:
I6G59_17580
BSPO:
L1F31_13415
DCO:
SAMEA4475696_1438
(metH_1)
KBS:
EPA93_23460
TTR:
Tter_2133
MICA:
P0L94_16250
FSI:
Flexsi_0945
» show all
Taxonomy
UniProt
Reference
PMID:
8798461
Authors
Garrow TA
Title
Purification, kinetic properties, and cDNA cloning of mammalian betaine-homocysteine methyltransferase.
Journal
J Biol Chem 271:22831-8 (1996)
DOI:
10.1074/jbc.271.37.22831
Sequence
[hsa:
635
] [ssc:
397371
]
LinkDB
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DBGET
integrated database retrieval system