ORTHOLOGY: K00905
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Entry
K00905 KO
Symbol
BCKDK
Name
[3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase [EC:
2.7.11.4
]
Disease
H02136
Branched-chain ketoacid dehydrogenase kinase deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09181 Protein families: metabolism
01001 Protein kinases
K00905 BCKDK; [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase
Enzymes [BR:
ko01000
]
2. Transferases
2.7 Transferring phosphorus-containing groups
2.7.11 Protein-serine/threonine kinases
2.7.11.4 [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase
K00905 BCKDK; [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase
Protein kinases [BR:
ko01001
]
Serine/threonine kinases: Other
PDHK family [OT]
K00905 BCKDK; [3-methyl-2-oxobutanoate dehydrogenase (acetyl-transferring)] kinase
BRITE hierarchy
Other DBs
GO:
0047323
Genes
HSA:
10295
(BCKDK)
PTR:
741960
(BCKDK)
PPS:
100988171
(BCKDK)
PON:
100435349
(BCKDK)
NLE:
100592408
(BCKDK)
HMH:
116471186
(BCKDK)
MCC:
712985
(BCKDK)
MCF:
102135926
(BCKDK)
MTHB:
126944216
MNI:
105482954
(BCKDK)
CSAB:
103231287
(BCKDK)
CATY:
105599511
(BCKDK)
PANU:
101027030
(BCKDK)
TGE:
112614202
(BCKDK)
MLEU:
105541464
(BCKDK)
RRO:
104661569
(BCKDK)
RBB:
108529119
(BCKDK)
TFN:
117087687
(BCKDK)
PTEH:
111525669
(BCKDK)
CANG:
105505704
(BCKDK)
CJC:
100386931
(BCKDK)
SBQ:
101039806
(BCKDK)
CIMI:
108293885
(BCKDK)
CSYR:
103264391
(BCKDK)
MMUR:
105871047
(BCKDK)
LCAT:
123632697
(BCKDK)
PCOQ:
105823160
(BCKDK)
OGA:
100947900
(BCKDK)
MMU:
12041
(Bckdk)
MCAL:
110297841
(Bckdk)
MPAH:
110321236
(Bckdk)
RNO:
29603
(Bckdk)
MCOC:
116103042
(Bckdk)
ANU:
117697241
(Bckdk)
117702413
MUN:
110564541
(Bckdk)
CGE:
100755998
(Bckdk)
MAUA:
101822893
(Bckdk)
PROB:
127217058
127228407
(Bckdk)
PLEU:
114704397
(Bckdk)
MORG:
121457571
(Bckdk)
MFOT:
126496299
126515868
AAMP:
119815638
(Bckdk)
NGI:
103726326
(Bckdk)
HGL:
101715390
(Bckdk)
CPOC:
100717874
(Bckdk)
CCAN:
109682760
(Bckdk)
DORD:
105982094
(Bckdk)
DSP:
122096193
(Bckdk)
PLOP:
125340380
(Bckdk)
NCAR:
124970051
MMMA:
107146975
(Bckdk)
OCU:
100341990
OPI:
101520752
(BCKDK)
TUP:
102488075
(BCKDK)
GVR:
103610041
(BCKDK)
CFA:
479776
(BCKDK)
CLUD:
112640132
(BCKDK)
VVP:
112929264
(BCKDK)
VLG:
121488356
(BCKDK)
NPO:
129519631
(BCKDK)
AML:
100476243
(BCKDK)
UMR:
103657884
(BCKDK)
UAH:
113267717
(BCKDK)
UAR:
123784676
(BCKDK)
ELK:
111162250
LLV:
125090575
MPUF:
101675298
(BCKDK)
MNP:
132026685
(BCKDK)
MLK:
131819642
(BCKDK)
NVS:
122895620
(BCKDK)
ORO:
101379705
(BCKDK)
EJU:
114214545
(BCKDK)
ZCA:
113933674
(BCKDK)
MLX:
117999566
(BCKDK)
NSU:
110589941
(BCKDK)
LWW:
102726562
(BCKDK)
FCA:
101089414
(BCKDK)
PYU:
121022182
(BCKDK)
PCOO:
112856709
(BCKDK)
PBG:
122471418
(BCKDK)
PVIV:
125154855
(BCKDK)
LRUF:
124517968
PTG:
102964750
(BCKDK)
PPAD:
109259022
(BCKDK)
PUC:
125928113
AJU:
106979116
HHV:
120242260
(BCKDK)
BTA:
505005
(BCKDK)
BOM:
102272790
(BCKDK)
BIU:
109578528
(BCKDK)
BBUB:
102404806
(BCKDK)
BBIS:
104986680
(BCKDK)
CHX:
102178232
(BCKDK)
OAS:
101104290
(BCKDK)
BTAX:
128068171
(BCKDK)
ODA:
120877678
(BCKDK)
CCAD:
122432927
(BCKDK)
MBEZ:
129545561
(BCKDK)
SSC:
100522544
(BCKDK)
CFR:
102514896
(BCKDK)
CBAI:
105082778
(BCKDK)
CDK:
105102713
(BCKDK)
VPC:
102531026
(BCKDK)
BACU:
103002138
(BCKDK)
BMUS:
118880604
(BCKDK)
LVE:
103076626
(BCKDK)
OOR:
101285430
(BCKDK)
DLE:
111182112
(BCKDK)
PCAD:
102984751
(BCKDK)
PSIU:
116740163
(BCKDK)
NASI:
112399308
(BCKDK)
ECB:
100063321
(BCKDK)
EPZ:
103547243
(BCKDK)
EAI:
106831884
(BCKDK)
MYB:
102256163
(BCKDK)
MYD:
102771109
(BCKDK)
MMYO:
118656742
(BCKDK)
MLF:
102435805
(BCKDK)
PKL:
118704940
(BCKDK)
EFUS:
103296236
(BCKDK)
MNA:
107540820
(BCKDK)
DRO:
112304677
(BCKDK)
AJM:
119041166
(BCKDK)
PDIC:
114503149
(BCKDK)
PHAS:
123825479
(BCKDK)
MMF:
118642782
(BCKDK)
PPAM:
129078009
(BCKDK)
HAI:
109374188
(BCKDK)
RFQ:
117019669
(BCKDK)
PALE:
102887175
(BCKDK)
PGIG:
120620059
(BCKDK)
PVP:
105304509
(BCKDK)
RAY:
107503982
(BCKDK)
MJV:
118966794
(BCKDK)
TOD:
119241708
(BCKDK)
SARA:
101549573
(BCKDK)
SETR:
126030903
(BCKDK)
LAV:
100663738
(BCKDK)
TMU:
101356582
ETF:
101661633
(BCKDK)
DNM:
101447993
(BCKDK)
MDO:
100013633
(BCKDK)
GAS:
123231143
(BCKDK)
SHR:
100930326
(BCKDK)
AFZ:
127562729
PCW:
110223122
(BCKDK)
OAA:
100080324
(BCKDK)
NMEL:
110391739
(BCKDK)
TGU:
115497487
(BCKDK)
LSR:
110483485
PMOA:
120508515
(BCKDK)
FAB:
101807123
(BCKDK)
OMA:
130266970
(BCKDK)
PHI:
102106406
(BCKDK)
PMAJ:
107199235
(BCKDK)
CCAE:
111922266
111943911
ZLE:
135460770
(BCKDK)
SVG:
106864428
(BCKDK)
FPG:
101920590
(BCKDK)
CLV:
106146054
(BCKDK)
AFOR:
103903856
(BCKDK)
ACHC:
115338556
(BCKDK)
GCL:
127027938
RTD:
128903534
(BCKDK)
ASN:
102385742
(BCKDK)
AMJ:
102557785
(BCKDK)
PSS:
102450847
(BCKDK)
CMY:
102940861
(BCKDK)
CCAY:
125638102
(BCKDK)
DCC:
119857007
(BCKDK)
CPIC:
101952608
(BCKDK)
TST:
117876269
(BCKDK)
CABI:
116815528
(BCKDK)
MRV:
120403409
120403410
ACS:
100555810
(bckdk)
ASAO:
132777752
(BCKDK)
PVT:
110086395
(BCKDK)
SUND:
121933323
(BCKDK)
PBI:
103051605
(BCKDK)
PMUR:
107294318
(BCKDK)
107299945
CTIG:
120302257
(BCKDK)
TSR:
106545492
(BCKDK)
PGUT:
117666825
(BCKDK)
APRI:
131197220
(BCKDK)
PTEX:
113449982
(BCKDK)
NSS:
113422497
(BCKDK)
PMUA:
114582840
114582841
(BCKDK)
PRAF:
128399695
(BCKDK)
ZVI:
118094672
(BCKDK)
HCG:
128328741
(BCKDK)
GJA:
107106646
(BCKDK)
STOW:
125444549
(BCKDK)
EMC:
129340531
(BCKDK)
XLA:
108703947
(bckdk.L)
432076
(bckdk.S)
XTR:
100380070
(bckdk)
NPR:
108803576
(BCKDK)
RTEM:
120943005
(BCKDK)
BBUF:
121009053
(BCKDK)
BGAR:
122945338
(BCKDK)
MUO:
115474420
115475067
GSH:
117360751
(BCKDK)
DRE:
282677
(bckdk)
SRX:
107710731
(bckdk)
107712146
SANH:
107681895
107685622
SGH:
107587720
107595470
CCAR:
109045589
(bckdk)
CAUA:
113049749
113081119
CGIB:
127958012
127995824
PTET:
122345211
(bckdk)
LROH:
127165097
(bckdk)
OMC:
131540694
(bckdk)
PPRM:
120472055
(bckdk)
RKG:
130082457
(bckdk)
MAMB:
125267713
(bckdk)
CIDE:
127512319
MASI:
127421397
127434948
TROS:
130564639
(bckdk)
TDW:
130418846
(bckdk)
MANU:
129440909
(bckdk)
IPU:
108260303
IFU:
128603499
(bckdk)
PHYP:
113531644
(bckdk)
SMEO:
124378977
(bckdk)
TFD:
113663375
(bckdk)
TVC:
132840685
(bckdk)
TRN:
134303318
(bckdk)
AMEX:
103026403
(bckdk)
CMAO:
118814330
(bckdk)
EEE:
113573709
(bckdk)
CHAR:
105895352
(bckdk)
TRU:
101071747
(bckdk)
TFS:
130538065
(bckdk)
TNG:
GSTEN00019477G001
LCO:
104921106
(bckdk)
TBEN:
117490299
(bckdk)
CGOB:
115018640
(bckdk)
PGEO:
117458359
(bckdk)
GACU:
117562232
(bckdk)
EMAC:
134871629
(bckdk)
ELY:
117268193
(bckdk)
EFO:
125898969
(bckdk)
PLEP:
121952255
(bckdk)
SLUC:
116055879
(bckdk)
ECRA:
117954975
(bckdk)
ESP:
116700204
(bckdk)
PFLV:
114566983
(bckdk)
GAT:
120822932
(bckdk)
PPUG:
119215485
(bckdk)
AFB:
129113366
(bckdk)
CLUM:
117743082
(bckdk)
PSWI:
130211500
(bckdk)
MSAM:
119895373
(bckdk)
SCHU:
122887982
(bckdk)
CUD:
121518713
(bckdk)
ALAT:
119031148
(bckdk)
MZE:
101470802
(bckdk)
ONL:
100693463
(bckdk)
OAU:
116326363
(bckdk)
OLA:
101172677
(bckdk)
OML:
112142877
(bckdk)
CSAI:
133459947
(bckdk)
XMA:
102232910
(bckdk)
XCO:
114152515
(bckdk)
XHE:
116728235
(bckdk)
PRET:
103476315
(bckdk)
PFOR:
103145532
(bckdk)
PLAI:
106946269
(bckdk)
PMEI:
106915550
(bckdk)
GAF:
122844723
(bckdk)
PPRL:
129370582
(bckdk)
CVG:
107081858
(bckdk)
CTUL:
119786817
(bckdk)
GMU:
124876421
(bckdk)
NFU:
107387216
(bckdk)
KMR:
108238069
(bckdk)
ALIM:
106525416
(bckdk)
NWH:
119419902
(bckdk)
AOCE:
111586755
(bckdk)
MCEP:
125021037
(bckdk)
CSEM:
103395393
(bckdk)
POV:
109635794
(bckdk)
SSEN:
122779765
(bckdk)
HHIP:
117773929
(bckdk)
HSP:
118121921
(bckdk)
PPLT:
128456602
(bckdk)
SMAU:
118301536
(bckdk)
LCF:
108893638
SDU:
111217087
(bckdk)
SLAL:
111651631
(bckdk)
XGL:
120802328
(bckdk)
HCQ:
109517958
(bckdk)
SSCV:
125982520
SBIA:
133491343
(bckdk)
PEE:
133416090
(bckdk)
PTAO:
133467755
(bckdk)
BPEC:
110166962
(bckdk)
MALB:
109959266
(bckdk)
BSPL:
114869989
(bckdk)
SJO:
128371012
(bckdk)
SASA:
106567669
(BCKD)
106603456
STRU:
115148785
115154249
OTW:
112228513
(bckdk)
112257931
OMY:
110533575
(bckdk)
110537551
OGO:
123999522
124011317
(bckdk)
ONE:
115105474
115135971
OKI:
109872983
109892803
OKE:
118390022
(bckdk)
118391098
SALP:
111950264
111980924
SNH:
120030810
120057014
(bckdk)
CCLU:
121550854
121579377
(bckdk)
ELS:
105011092
(bckdk)
SFM:
108928236
(bckdk)
PKI:
111847878
(bckdk)
AANG:
118209553
118235075
(bckdk)
LOC:
102682703
102698785
PSPA:
121305157
121308469
(bckdk)
ARUT:
117398293
117418356
117429291
(bckdk)
PSEX:
120531318
(bckdk)
120536704
LCM:
102360605
(BCKDK)
CMK:
103180529
(bckdk)
RTP:
109918994
(bckdk)
109924425
CPLA:
122542053
122564137
(bckdk)
HOC:
132808882
132830442
(bckdk)
LERI:
129710722
(bckdk)
PMRN:
116937490
116958441
(BCKDK)
BFO:
118425510
BBEL:
109465957
SCLV:
120341705
SPU:
574737
LPIC:
129254732
APLC:
110976612
AJC:
117121942
SKO:
100369777
FCD:
110862028
DPX:
DAPPUDRAFT_308613
DMK:
116933693
123474709
DPZ:
124327589
PVM:
113825010
PJA:
122257442
PCHN:
125031495
HAME:
121867985
PCLA:
123772092
PTRU:
123498494
ESN:
126999725
MNZ:
135211355
HAZT:
108678411
EAF:
111699483
LSM:
121127391
TCF:
131886090
PPOI:
119098442
ISC:
8028544
DSV:
119445285
RSAN:
119391051
RMP:
119168205
TUT:
107368956
DPTE:
113789621
DFR:
124498909
CSCU:
111620430
PTEP:
107444190
ABRU:
129972337
UDV:
129220028
SDM:
118188450
LPOL:
106458320
106471357
106473246
PMEO:
129589030
HRO:
HELRODRAFT_193864
HELRODRAFT_66850
LGI:
LOTGIDRAFT_116873
PVUL:
126825569
PCAN:
112561778
BGT:
106075238
GAE:
121367979
HRF:
124132068
HRJ:
124254155
CRG:
105328662
CVN:
111136048
CANU:
128189604
MYI:
110455574
PMAX:
117333050
MCAF:
127712146
MMER:
123533898
RPHI:
132742896
DPOL:
127842804
OBI:
106879645
OSN:
115222452
LAK:
106155712
OVI:
T265_03130
NVE:
5509294
EPA:
110252284
ATEN:
116290344
ADF:
107358500
AMIL:
114958723
PDAM:
113684461
SPIS:
111345051
DGT:
114523680
114523987
XEN:
124435713
HMG:
100214984
HSY:
130623859
TAD:
TRIADDRAFT_52704
CCP:
CHC_T00006845001
OPA:
HPODL_03307
RSX:
RhiXN_01526
MBR:
MONBRDRAFT_15226
MONBRDRAFT_5845
SRE:
PTSG_08628
TGO:
TGME49_318560
SMIN:
v1.2.008918.t1
(symbB.v1.2.008918.t1)
v1.2.010686.t1
(symbB.v1.2.010686.t1)
v1.2.010686.t2
(symbB.v1.2.010686.t2)
v1.2.012337.t1
(symbB.v1.2.012337.t1)
» show all
Taxonomy
UniProt
Reference
PMID:
1377677
Authors
Popov KM, Zhao Y, Shimomura Y, Kuntz MJ, Harris RA
Title
Branched-chain alpha-ketoacid dehydrogenase kinase. Molecular cloning, expression, and sequence similarity with histidine protein kinases.
Journal
J Biol Chem 267:13127-30 (1992)
DOI:
10.1016/S0021-9258(18)42179-5
Sequence
[rno:
29603
]
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DBGET
integrated database retrieval system