ORTHOLOGY: K17680
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Entry
K17680 KO
Symbol
PEO1
Name
twinkle protein [EC:
5.6.2.3
]
Pathway
map05017
Spinocerebellar ataxia
Disease
H00469
Mitochondrial DNA depletion syndrome
H01118
Progressive external ophthalmoplegia
H02095
Perrault syndrome
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09160 Human Diseases
09164 Neurodegenerative disease
05017 Spinocerebellar ataxia
K17680 PEO1; twinkle protein
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K17680 PEO1; twinkle protein
Enzymes [BR:
ko01000
]
5. Isomerases
5.6 Isomerases altering macromolecular conformation
5.6.2 Enzymes altering nucleic acid conformation
5.6.2.3 DNA 5'-3' helicase
K17680 PEO1; twinkle protein
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial DNA transcription, translation, and replication factors
Mitochondrial DNA replication factors
Mitochondrial DNA maintenance factors
K17680 PEO1; twinkle protein
BRITE hierarchy
Other DBs
GO:
0043139
Genes
HSA:
56652
(TWNK)
PTR:
745279
(TWNK)
PPS:
100972543
(TWNK)
GGO:
101144386
(TWNK)
PON:
100431671
(TWNK)
NLE:
100607282
(TWNK)
HMH:
116484927
(TWNK)
MCC:
710958
(TWNK)
MCF:
102131591
(TWNK)
MTHB:
126963068
MNI:
105478383
(TWNK)
CSAB:
103216394
(TWNK)
CATY:
105581847
PANU:
101006096
(TWNK)
TGE:
112632194
(TWNK)
MLEU:
105537757
RRO:
104656483
(TWNK)
RBB:
108515144
(CUNH10orf2)
TFN:
117068325
(TWNK)
PTEH:
111538814
(TWNK)
CANG:
105507134
CJC:
100387060
(TWNK)
118142804
SBQ:
101037759
CIMI:
108306351
(TWNK)
CSYR:
103251585
(TWNK)
MMUR:
105873807
(TWNK)
LCAT:
123650119
(TWNK)
PCOQ:
105824317
OGA:
100945245
(TWNK)
MMU:
226153
(Twnk)
MCAL:
110285355
(Twnk)
MPAH:
110325674
(Twnk)
RNO:
309441
(Twnk)
MCOC:
116103908
(Twnk)
ANU:
117693398
(Twnk)
MUN:
110556111
(Twnk)
CGE:
100756896
(Twnk)
MAUA:
101833798
(Twnk)
PROB:
127233265
(Twnk)
PLEU:
114708118
(Twnk)
MORG:
121454602
(Twnk)
MFOT:
126504387
AAMP:
119814694
(Twnk)
NGI:
103743991
(Twnk)
HGL:
101719932
(Twnk)
CPOC:
100733250
(Twnk)
CCAN:
109695267
(Twnk)
DORD:
105986714
DSP:
122115901
(Twnk)
PLOP:
125346145
(Twnk)
NCAR:
124984713
MMMA:
107149810
(Twnk)
OCU:
100349273
(TWNK)
OPI:
101528855
(TWNK)
TUP:
102483088
(TWNK)
GVR:
103603369
CFA:
486845
(TWNK)
CLUD:
112672208
(TWNK)
VVP:
112914968
(TWNK)
VLG:
121480602
(TWNK)
NPO:
129493936
(TWNK)
AML:
100470161
(TWNK)
UMR:
103678288
(TWNK)
UAH:
113251842
(TWNK)
UAR:
123795875
(TWNK)
ELK:
111145384
LLV:
125085261
MPUF:
101674783
MNP:
132016709
(TWNK)
MLK:
131828534
(TWNK)
NVS:
122901027
(TWNK)
ORO:
101369820
EJU:
114205424
(TWNK)
ZCA:
113923381
(TWNK)
MLX:
118025073
(TWNK)
NSU:
110589672
(TWNK)
LWW:
102736307
(TWNK)
FCA:
101093964
(TWNK)
PYU:
121037120
(TWNK)
PCOO:
112854790
(TWNK)
PBG:
122493150
(TWNK)
PVIV:
125147665
(TWNK)
LRUF:
124507071
PTG:
102957034
(TWNK)
PPAD:
109272779
(TWNK)
PUC:
125933425
AJU:
106966876
(TWNK)
HHV:
120243220
(TWNK)
BTA:
538467
(TWNK)
BOM:
102282967
(TWNK)
BIU:
109579131
(TWNK)
BBUB:
102408935
(TWNK)
BBIS:
105002704
CHX:
102183657
(C26H10orf2)
OAS:
101123251
(TWNK)
BTAX:
128067752
(TWNK)
ODA:
120873678
(TWNK)
CCAD:
122446026
(TWNK)
MBEZ:
129555437
(TWNK)
SSC:
100625408
(TWNK)
CFR:
102508767
(TWNK)
CBAI:
105081735
CDK:
105084329
(TWNK)
VPC:
102530222
(TWNK)
BACU:
103006521
(TWNK)
BMUS:
118882511
(TWNK)
LVE:
103089678
OOR:
101284488
(TWNK)
DLE:
111172383
(TWNK)
PCAD:
102996981
(TWNK)
PSIU:
116741655
(TWNK)
NASI:
112393064
(TWNK)
ECB:
100070286
(TWNK)
EPZ:
103560252
(TWNK)
EAI:
106828845
(TWNK)
MYB:
102254481
(TWNK)
MYD:
102756256
(TWNK)
MMYO:
118669839
(TWNK)
MLF:
102430362
(TWNK)
PKL:
118719421
(TWNK)
EFUS:
103288486
(TWNK)
MNA:
107542659
DRO:
112300384
(TWNK)
SHON:
118999506
(TWNK)
AJM:
119059650
(TWNK)
PDIC:
114497287
(TWNK)
PHAS:
123828705
(TWNK)
MMF:
118632787
(TWNK)
PPAM:
129077123
(TWNK)
HAI:
109379641
(TWNK)
RFQ:
117035808
(TWNK)
PALE:
102897253
(TWNK)
PGIG:
120609185
(TWNK)
PVP:
105304633
(TWNK)
RAY:
107497794
MJV:
108409574
(TWNK)
TOD:
119233658
(TWNK)
SARA:
101559433
SETR:
126033829
(TWNK)
LAV:
104845803
(TWNK)
TMU:
101344344
ETF:
101647080
(TWNK)
DNM:
101444092
(TWNK)
MDO:
100029801
(TWNK)
GAS:
123236235
(TWNK)
SHR:
100931263
(TWNK)
AFZ:
127551483
PCW:
110194450
(TWNK)
OAA:
100081173
100681837
114817231
GGA:
425626
(TWNK)
PCOC:
116231688
(TWNK)
MGP:
100538480
(TWNK)
CJO:
107316026
(TWNK)
TPAI:
128077712
(TWNK)
LMUT:
125693207
(TWNK)
NMEL:
110400264
(TWNK)
APLA:
119717375
(TWNK)
ACYG:
106029314
(TWNK)
CATA:
118248605
(TWNK)
AFUL:
116491136
(TWNK)
TGU:
100231468
(TWNK)
LSR:
110473584
(TWNK)
SCAN:
103814143
(TWNK)
PMOA:
120501979
(TWNK)
OTC:
121341774
(TWNK)
PRUF:
121350227
(TWNK)
GFR:
102038483
(TWNK)
FAB:
101814355
(TWNK)
OMA:
130254744
(TWNK)
PHI:
102102487
PMAJ:
107207151
(TWNK)
CCAE:
111930945
(TWNK)
CCW:
104697884
(TWNK)
CBRC:
103624661
(CUNH10orf2)
ETL:
114070409
(TWNK)
ZAB:
102062638
(TWNK)
ZLE:
135449309
(TWNK)
ACHL:
103805977
SVG:
106857605
MMEA:
130581669
(TWNK)
HRT:
120756181
(TWNK)
FPG:
101923766
(TWNK)
FCH:
102055021
(TWNK)
CLV:
102085450
(TWNK)
EGZ:
104125633
NNI:
104013505
PCRI:
104033343
PLET:
104622096
EHS:
104505207
PCAO:
104047695
ACUN:
113481606
(TWNK)
TALA:
104366299
(TWNK)
PADL:
103916308
AFOR:
103897891
(TWNK)
ACHC:
115348151
(TWNK)
HALD:
104323800
HLE:
104830111
AGEN:
126042894
GCL:
127017571
CCRI:
104157059
CSTI:
104553628
MUI:
104548152
BREG:
104643575
FGA:
104078920
GSTE:
104256595
LDI:
104350972
MNB:
103769612
OHA:
104335825
NNT:
104410072
SHAB:
115607994
(TWNK)
DPUB:
104307165
PGUU:
104460667
CPEA:
104390951
AVIT:
104275635
CVF:
104294639
RTD:
128911489
(TWNK)
CUCA:
104059806
TEO:
104377880
AAM:
106494686
(TWNK)
AROW:
112967881
(TWNK)
NPD:
112957107
(TWNK)
DNE:
112984804
(TWNK)
SCAM:
104138122
ASN:
102370952
(TWNK)
AMJ:
106737961
(TWNK)
GGN:
109287183
(TWNK)
PSS:
102445911
(TWNK)
CMY:
102939228
(TWNK)
CCAY:
125640126
(TWNK)
DCC:
119859287
(TWNK)
CPIC:
101943408
(TWNK)
CABI:
116833954
(TWNK)
MRV:
120408880
(TWNK)
ACS:
100551924
(twnk)
ASAO:
132770892
(TWNK)
PVT:
110077612
(TWNK)
SUND:
121925457
(TWNK)
PBI:
103053121
(TWNK)
CTIG:
120316296
(TWNK)
TSR:
106547610
PGUT:
117678640
(TWNK)
APRI:
131201111
(TWNK)
PTEX:
113439057
(TWNK)
NSS:
113412378
(TWNK)
VKO:
123027011
(TWNK)
PMUA:
114597541
(TWNK)
PRAF:
128414302
(TWNK)
ZVI:
118093849
(TWNK)
HCG:
128351296
(TWNK)
GJA:
107109676
(TWNK)
STOW:
125438015
(TWNK)
EMC:
129332908
(TWNK)
XLA:
414487
(twnk.L)
XTR:
100491229
(twnk)
NPR:
108784545
(CUNH10orf2)
RTEM:
120947002
(TWNK)
BBUF:
120988926
(TWNK)
BGAR:
122933451
(TWNK)
MUO:
115471098
(TWNK)
GSH:
117359464
(TWNK)
DRE:
100330448
(twnk)
SRX:
107722219
107755431
SANH:
107684073
107690904
SGH:
107565785
107581591
CCAR:
109101684
CAUA:
113064161
113111633
CGIB:
127969504
128025413
PTET:
122355074
(twnk)
LROH:
127174442
(twnk)
OMC:
131551441
(twnk)
PPRM:
120474656
(twnk)
RKG:
130105413
(twnk)
MAMB:
125255573
(twnk)
CIDE:
127523778
MASI:
127423044
127426923
TROS:
130569211
(twnk)
TDW:
130438616
(twnk)
MANU:
129420396
(twnk)
IPU:
108273940
(twnk)
IFU:
128616513
(twnk)
PHYP:
113527049
(twnk)
SMEO:
124388842
(twnk)
TFD:
113638887
(twnk)
TVC:
132837762
(twnk)
TRN:
134321887
(twnk)
AMEX:
103026372
(twnk)
CMAO:
118809383
(twnk)
EEE:
113577642
(twnk)
CHAR:
105894050
(twnk)
105911559
TRU:
101065637
(twnk)
TFS:
130524582
(twnk)
TNG:
GSTEN00026957G001
LCO:
104928476
(twnk)
NCC:
104950658
TBEN:
117473360
(twnk)
CGOB:
115024245
(twnk)
PGEO:
117465229
(twnk)
GACU:
117547342
(twnk)
EMAC:
134870384
(twnk)
ELY:
117246823
(twnk)
EFO:
125880847
(twnk)
PLEP:
121959315
(twnk)
SLUC:
116061255
(twnk)
ECRA:
117937356
(twnk)
ESP:
116670955
(twnk)
PFLV:
114547795
(twnk)
GAT:
120819272
(twnk)
PPUG:
119212903
(twnk)
AFB:
129091399
(twnk)
CLUM:
117748680
(twnk)
PSWI:
130203574
(twnk)
MSAM:
119915497
(twnk)
SCHU:
122867514
(twnk)
CUD:
121527851
(twnk)
ALAT:
119009352
(twnk)
MZE:
101483101
(twnk)
ONL:
100692913
(twnk)
OAU:
116336324
(twnk)
OLA:
101170228
(twnk)
OML:
112154664
(twnk)
CSAI:
133418845
(twnk)
XMA:
102218585
(twnk)
XCO:
114152382
(twnk)
XHE:
116727714
(twnk)
PRET:
103481674
(clg19h10orf2)
PFOR:
103151625
PLAI:
106939043
PMEI:
106907463
GAF:
122822932
(twnk)
PPRL:
129368002
(twnk)
CVG:
107092744
CTUL:
119791105
(twnk)
GMU:
124874612
(twnk)
NFU:
107387660
(csgr12h10orf2)
KMR:
108246987
(twnk)
ALIM:
106535522
NWH:
119423808
(twnk)
AOCE:
111582456
(twnk)
MCEP:
125021944
(twnK)
CSEM:
103381557
(twnk)
POV:
109644376
(twnk)
SSEN:
122758846
(twnk)
HHIP:
117752460
(twnk)
HSP:
118100918
(twnk)
PPLT:
128426489
(twnk)
SMAU:
118287948
(twnk)
LCF:
108894827
SDU:
111220257
(twnk)
SLAL:
111656128
(twnk)
XGL:
120793926
(twnk)
HCQ:
109512963
(twnk)
SSCV:
125990871
SBIA:
133495430
(twnk)
PEE:
133418066
(twnk)
PTAO:
133469253
(twnk)
BPEC:
110154341
(twnk)
MALB:
109969586
(twnk)
BSPL:
114845568
(twnk)
SJO:
128381856
(twnk)
SASA:
106579274
STRU:
115159085
OTW:
112223632
(twnk)
OMY:
110491537
(twnk)
OGO:
124048301
(twnk)
ONE:
115106510
(twnk)
OKI:
109865436
OKE:
118366455
(twnk)
SALP:
111977728
SNH:
120046225
(twnk)
CCLU:
121541474
(twnk)
ELS:
109614573
(twnk)
SFM:
108924862
(twnk)
PKI:
111848388
(twnk)
AANG:
118217598
(twnk)
LOC:
102683723
(clg5h10orf2)
PSPA:
121321621
121325695
ARUT:
117415463
(twnk)
PSEX:
120542779
(twnk)
LCM:
102355158
(TWNK)
CMK:
103172197
(twnk)
RTP:
109937130
(twnk)
CPLA:
122561347
(twnk)
HOC:
132826377
(twnk)
LERI:
129704101
(twnk)
PMRN:
116940519
(TWNK)
LRJ:
133343374
(TWNK)
BFO:
118406640
BBEL:
109463399
SCLV:
120330142
SPU:
581516
LPIC:
129268159
129268166
APLC:
110978490
AJC:
117100109
SKO:
100377192
DME:
Dmel_CG5924
(mtDNA-helicase)
DER:
6542762
DSE:
6611865
DSI:
Dsimw501_GD22331
(Dsim_GD22331)
DYA:
Dyak_GE10270
DAN:
6498047
DSR:
110183444
DPO:
4817443
DPE:
6588671
DMN:
108162964
DWI:
6641531
DGR:
6562330
DMO:
Dmoj_GI24377
DAZ:
108611286
DNV:
115562945
DHE:
111603598
DVI:
6629093
CCAT:
101454261
BOD:
106617688
BDR:
105222265
RZE:
108376657
AOQ:
129248426
TDA:
119690034
MDE:
101895609
SCAC:
106083524
LCQ:
111681717
LSQ:
119606729
GFS:
119633940
ECOE:
129946685
CLON:
129614986
HIS:
119657052
ACOZ:
120958245
AARA:
120900960
AMER:
121600518
ASTE:
118505308
AFUN:
125771388
AMOU:
128309784
AALI:
118464740
AAG:
110680936
5577487
AALB:
109413116
ASUA:
134224232
CQU:
CpipJ_CPIJ017385
CpipJ_CPIJ019938
CPII:
120414911
CNS:
116345862
BCOO:
119066091
AME:
100578653
ACER:
107997955
ALAB:
122710813
ADR:
102671128
AFLR:
100865665
BIM:
100743399
BBIF:
117207670
BVK:
117236158
BVAN:
117153487
BTER:
100647146
BAFF:
126922284
BPYO:
122569457
BPAS:
132916737
CCAL:
108626542
OBB:
114878136
OLG:
117603682
MGEN:
117222064
NMEA:
116430444
CGIG:
122395299
SOC:
105195942
MPHA:
105834519
AEC:
105145762
ACEP:
105624185
PBAR:
105428656
VEM:
105567311
HST:
105189075
DQU:
106750911
CFO:
105258070
FEX:
115232752
115232859
LHU:
105671160
PGC:
109855947
OBO:
105277367
PCF:
106789096
PFUC:
122519132
VPS:
122631735
VCRB:
124426554
VVE:
124952206
NVI:
100120404
CSOL:
105362447
TPRE:
106651547
LHT:
122497812
LBD:
127282043
MDL:
103577331
CGLO:
123266833
FAS:
105274030
DAM:
107048493
AGIF:
122857072
CINS:
118066605
VCAN:
122417064
CCIN:
107273524
DSM:
124404415
NPT:
124213326
NFB:
124174730
NLO:
107222281
NVG:
124296891
AROA:
105692394
TCA:
658926
DPA:
109539397
SOY:
115875495
AGRG:
126739906
ATD:
109602308
CSET:
123306277
AGB:
108915658
LDC:
111505913
DVV:
114336008
NVL:
108562398
PPYR:
116173234
116181904
OTU:
111415155
BMOR:
101738164
MSEX:
115445539
DPL:
KGM_204279
BANY:
112058434
MJU:
123864773
NIQ:
126776252
VCD:
124542411
MCIX:
123663745
PMAC:
106712430
PPOT:
106110986
PXU:
106117334
PRAP:
111001188
PBX:
123707409
PNAP:
125056215
ZCE:
119830451
CCRC:
123705676
LSIN:
126971104
AAGE:
121729918
HAW:
110370502
HZE:
124645168
TNL:
113492786
SLIU:
111358045
OFU:
114355681
ATRA:
106136995
GMW:
113522641
PXY:
105380271
105392425
PGW:
126382027
LGLY:
125240535
CFEL:
113376600
113378354
CCRN:
123294636
API:
100161261
DNX:
107161889
AGS:
114121463
RMD:
113547763
ACOO:
126834409
DVT:
126905556
BTAB:
109035711
DCI:
103514043
CLEC:
106662005
HHAL:
106690318
NLU:
111053073
HVI:
124357502
MQU:
128994685
128995418
PHU:
Phum_PHUM149580
FOC:
113210471
TPAL:
117653338
ZNE:
110840022
CSEC:
111864621
SGRE:
126267951
126315253
IEL:
124158634
FCD:
110846294
DPX:
DAPPUDRAFT_314156
DMK:
116918756
DPZ:
124312922
PVM:
113815512
PJA:
122257448
PCHN:
125036730
PMOO:
119592466
HAME:
121876882
PCLA:
123767903
CQD:
128686489
PTRU:
123515586
ESN:
126984456
127010104
MNZ:
135223721
HAZT:
108680115
EAF:
111697155
LSM:
121126419
TCF:
131888523
PPOI:
119108268
119108269
DSV:
119450485
RSAN:
119383529
RMP:
119170580
VDE:
111251244
VJA:
111259989
TUT:
107364333
DPTE:
113790981
DFR:
124496115
CSCU:
111621724
PTEP:
107441552
ABRU:
129985226
UDV:
129224966
SDM:
118195011
LPOL:
106470580
PMEO:
129583998
CEL:
CELE_F46G11.1
(twnk-1)
CBR:
CBG_14751
CRQ:
GCK72_024473
NAI:
NECAME_16417
BMY:
BM_BM4162
(Bm4162)
LOA:
LOAG_05495
TSP:
Tsp_04337
Tsp_12020
HRO:
HELRODRAFT_189902
LGI:
LOTGIDRAFT_135083
PVUL:
126832150
PCAN:
112562839
BGT:
106062384
GAE:
121390797
HRF:
124141715
HRJ:
124259069
CRG:
105327113
MYI:
110463114
PMAX:
117333366
MMER:
123535436
RPHI:
132717533
DPOL:
127871412
MAEA:
128230230
OBI:
106882273
OSN:
115219134
LJP:
135476580
LAK:
106156672
106171970
SMM:
Smp_146360
Smp_177240
OVI:
T265_11962
EGL:
EGR_08368
LLON:
135486327
NVE:
5515150
EPA:
110241423
ATEN:
116298730
ADF:
107332069
AMIL:
114973520
PDAM:
113667640
SPIS:
111321923
DGT:
114533221
XEN:
124455497
HMG:
100209293
HSY:
130644599
RES:
135695730
TAD:
TRIADDRAFT_18685
AQU:
100636025
ATH:
AT1G30680
ALY:
9329701
CRB:
17897459
CSAT:
104741673
104757455
104777099
EUS:
EUTSA_v10006950mg
BRP:
103840315
BNA:
106367250
106406957
BOE:
106343104
RSZ:
108854908
THJ:
104798583
CPAP:
110821872
CIT:
102625113
102625402
CIC:
CICLE_v10014667mg
CICLE_v10015609mg
PVY:
116121640
MINC:
123219231
TCC:
18595141
18595142
GRA:
105768799
105768800
GHI:
107906337
107958509
GAB:
108452942
HSYR:
120131303
120196299
DZI:
111275401
111278848
EGR:
104441222
104441581
GMX:
100779625
100804637
100814805
GSJ:
114388458
114425001
114425484
PVU:
PHAVU_006G124200g
PHAVU_006G124400g
VRA:
106774429
106774529
VAR:
108342359
108343475
VUN:
114187006
114189068
VUM:
124849078
124849083
CCAJ:
109811460
109811483
APRC:
113863410
113867336
MTR:
11418712
25486321
25486330
TPRA:
123894426
123897192
123899664
CAM:
101503034
101510295
PSAT:
127074839
127074859
VVO:
131595337
131599813
LJA:
Lj6g3v1618200.1
(Lj6g3v1618200.1)
Lj6g3v1618290.1
(Lj6g3v1618290.1)
Lj6g3v1618290.2
(Lj6g3v1618290.2)
ADU:
107482351
107483217
107483268
AIP:
107638325
107638948
AHF:
112740854
112741522
112795575
112795576
112796226
112796235
LANG:
109329465
109329468
109345526
PCIN:
129285930
129297687
129305269
129305836
QSA:
O6P43_013201
O6P43_030228
O6P43_032228
FVE:
101310787
101311081
RCN:
112165993
112168017
PPER:
18778606
18780488
PMUM:
103325299
103325302
PAVI:
110765014
110765018
PDUL:
117623789
117624316
MDM:
103446089
103454461
MSYL:
126587445
126620877
PXB:
103945072
103952332
ZJU:
107418353
MNT:
21408640
21409586
CSAV:
115697729
115701383
CSV:
101213010
101219062
101219541
CMO:
103488704
103488713
BHJ:
120082741
120082994
MCHA:
111012535
111012634
CMAX:
111490430
111495250
CMOS:
111434017
111457136
CPEP:
111783068
111801532
RCU:
8265479
8265542
JCU:
105636782
105636783
HBR:
110631726
110655771
110657047
MESC:
110600112
110622074
POP:
7480391
7490760
PEU:
105135908
105135909
PALZ:
118029435
118029640
JRE:
108985682
108996330
CILL:
122277146
122303305
CAVE:
132172252
132182329
132183209
QSU:
111996138
112035030
QLO:
115982424
115992722
TWL:
119981102
120006711
VVI:
100247126
100247384
100257655
100263216
VRI:
117906864
117923593
117923779
117923920
SLY:
101263081
101264268
SPEN:
107011899
107012051
SOT:
102591920
102601660
SSTN:
125848856
125849156
SDUL:
129872087
129873760
CANN:
107858471
107859068
LBB:
132622606
132631544
NTA:
107763222
107819042
107823224
107826455
NSY:
104219496
104229060
NTO:
104089091
104094759
NAU:
109208551
109212527
INI:
109153115
ITR:
116027386
SIND:
105175814
105175815
OEU:
111368690
111401845
EGT:
105948822
105948900
SSPL:
121768142
121769533
121771952
121771953
121773510
121777849
SMIL:
131026370
131026375
131026389
SHIS:
125188697
125203836
125204065
APAN:
127247482
127247484
127249514
HAN:
110876258
110876276
110890574
ECAD:
122582036
122583972
LSV:
111893508
111893536
CCAV:
112519298
112520330
DCR:
108201219
108206456
108209936
CSIN:
114299937
RVL:
131312984
131312987
AEW:
130755909
BVG:
104882973
SOE:
110804797
CQI:
110702912
110724188
ATRI:
130815371
MOF:
131160413
NNU:
104587875
MING:
122059651
TSS:
122650131
PSOM:
113280798
113289978
113298190
OSA:
4341808
DOSA:
Os06t0671700-01
(Os06g0671700)
OBR:
102708903
OGL:
127777535
BDI:
100846256
ATS:
109752291
TDC:
119331418
119337357
119339284
TAES:
123149113
123157297
123165625
123165627
LPER:
127312052
127312055
LRD:
124663899
124700488
124701092
SBI:
8061599
ZMA:
103629647
SITA:
101767722
SVS:
117853743
PVIR:
120671634
120704191
PHAI:
112890819
PDA:
103719626
103720546
EGU:
105049153
105059833
MUS:
103971459
103999510
103999574
ZOF:
121988537
121988539
121997416
121997419
122000738
122005025
DCT:
110095717
110102885
110109794
PEQ:
110028816
110038414
AOF:
109844596
MSIN:
131248984
NCOL:
116267790
ATR:
18443031
SMO:
SELMODRAFT_164801
SELMODRAFT_171959
PPP:
112289739
VCN:
VOLCADRAFT_88130
MNG:
MNEG_16042
CSL:
COCSUDRAFT_13389
CVR:
CHLNCDRAFT_31176
APRO:
F751_0794
OLU:
OSTLU_94562
OTA:
OT_ostta06g03480
BPG:
Bathy05g03920
MIS:
MICPUN_83947
MPP:
MICPUCDRAFT_21196
(JGI:MicpuC2_21196)
CME:
CYME_CMT452C
GSL:
Gasu_04190
CCP:
CHC_T00004107001
DDI:
DDB_G0288209
DPP:
DICPUDRAFT_97936
DFA:
DFA_00827
ACAN:
ACA1_164120
TET:
TTHERM_00691710
PTM:
GSPATT00002365001
GSPATT00006831001
GSPATT00011504001
PTI:
PHATRDRAFT_605
FCY:
FRACYDRAFT_181837
TPS:
THAPSDRAFT_35968
THAPSDRAFT_bd1983
PIF:
PITG_12166
PSOJ:
PHYSODRAFT_479432
SPAR:
SPRG_16173
GTT:
GUITHDRAFT_98228
NGR:
NAEGRDRAFT_31486
ELX:
CDCO157_1142K
ECG:
E2348C_0676
EOC:
CE10_1034
SEI:
SPC_1284
SEC:
SCH_0341
SEW:
SeSA_A0621
SFL:
SF0682
SFX:
S0718
SFV:
SFV_2689
SFE:
SFxv_0753
SFN:
SFy_0929
SFS:
SFyv_0966
CSJ:
CSK29544_00020
CMJ:
AFK66_021200
AFK66_021985
KPR:
KPR_4251
KOK:
KONIH1_12630
CAF:
AL524_11960
KLE:
AO703_05705
LEE:
DVA44_13400
DVA44_19305
PVJ:
LMA04_00535
EBC:
C2U52_16990
PANP:
PSNIH2_13500
PER:
LAC65_11140
XNE:
XNC1_3413
XNM:
XNC2_3287
XBU:
HGO23_04070
PSI:
S70_04610
PVC:
G3341_06435
ANS:
ArsFIN_04640
(dnaG_1)
ArsFIN_17880
(dnaG_3)
AET:
LDL57_11850
LDL57_16625
AAPC:
QG404_01240
VCI:
O3Y_07210
VVM:
VVMO6_01592
VVMO6_03554
PAG:
PLES_25231
PNC:
NCGM2_2906
PAEL:
T223_12865
PAEU:
BN889_06759
PCQ:
PcP3B5_46440
PPU:
PP_2270
PHOM:
KJF94_16090
ACUM:
C9E88_016625
LPP:
lpp2117
LLG:
44548918_02696
LIB:
E4T55_02015
LADL:
NCTC12735_00446
LANT:
TUM19329_01570
TUM19329_01690
METL:
U737_19055
MISZ:
MishRS11D_02840
NOC:
Noc_0053
NWR:
E3U44_01870
SCOM:
PYG29_00490
RPF:
Rpic12D_3447
CNAN:
A2G96_17760
BTE:
BTH_I0913
BTQ:
BTQ_932
BTD:
BTI_1093
BTHE:
BTN_1925
BTHL:
BG87_2983
BOK:
DM82_4346
BMK:
DM80_3054
BDL:
AK34_714
BPSL:
WS57_25620
WS57_28160
BARI:
NLX30_18170
BGO:
BM43_489
PARB:
CJU94_19575
PGP:
CUJ91_04700
PACS:
FAZ98_31380
FAZ98_31875
TCAR:
U0034_16880
BBH:
BN112_0045
BN112_1311
BN112_4839
BBR:
BB2209
BB3510
BBX:
BBS798_3342
BTRM:
SAMEA390648703089
ASEL:
RAS12_11980
RHY:
RD110_08005
DAC:
Daci_1933
DTS:
BI380_14240
DLA:
I6G47_16435
VAA:
AX767_00400
VBO:
CKY39_19680
VAM:
C4F17_07130
CODO:
LAD35_06830
LAD35_15170
OTD:
J1M35_15905
STHM:
IS481_11990
PBH:
AAW51_2092
HAR:
HEAR3034
CARE:
LT85_1008
OVB:
NB640_12340
QAU:
KI612_02095
AMIH:
CO731_05113
ANJ:
AMD1_4989
PMOB:
HG718_00455
ECAA:
J3R84_13060
RLE:
RL3945
RHL:
LPU83_0589
NGG:
RG540_CH13710
BEL:
BE61_51350
BBAN:
J4G43_045850
J4G43_047080
BPAH:
QA639_21100
BRAZ:
LRP30_13450
RPX:
Rpdx1_2982
NHA:
Nham_3347
BHE:
BH14520
BHN:
PRJBM_01420
BHS:
BM1374165_01495
BQU:
BQ11500
BQR:
RM11_1056
BBK:
BARBAKC583_0187
BTR:
BT_2129
BTX:
BM1374166_01911
BGR:
Bgr_17450
BCD:
BARCL_1203
BAUS:
BAnh1_11120
BVN:
BVwin_12980
BANC:
PU02_0281
BART:
BJB15x_010590
BARA:
BA1379B_010720
BARW:
BWD162_013000
BARR:
Bra60_011840
BARO:
B11Cv2_011380
BARJ:
BJB63x_010440
BEZ:
NCTC12898_01319
BARN:
D1092_07145
BKY:
D1093_09470
BALS:
HWV54_02980
BTAY:
LAJ60_05100
AZC:
AZC_3598
MOC:
BB934_43910
MLD:
U0023_13110
MSL:
Msil_2768
BDM:
EQG53_05565
SAER:
NEF64_14180
SNOS:
K8P63_06925
SJP:
SJA_C1-09960
SHYD:
CJD35_13625
SPHJ:
BSL82_03510
BSL82_03880
BSL82_09610
AFLV:
QQW98_08330
KDP:
N5W20_05485
APB:
SAR116_0393
GBZ:
JZM60_09545
JZM60_12735
FPLA:
A4U99_14585
OVA:
OBV_19840
DED:
DHBDCA_p1808
DEC:
DCF50_p1819
BHV:
BLHYD_25690
(radA_2)
CLE:
Clole_0947
CEW:
EKH84_07240
CSPO:
QNI18_00520
CMIU:
B1H56_14335
COW:
Calow_1650
CKI:
Calkr_1541
CLC:
Calla_0929
CKN:
Calkro_0781
CCHA:
ELD05_04020
MHW:
ACT01_06865
RUFI:
K0V07_13500
ROO:
G5S37_20050
ALUS:
STSP2_03301
VBC:
C5Q97_18985
FVA:
FV113G1_23740
FUL:
C4N20_00255
STR:
Sterm_3911
BTH:
BT_1172
BTHO:
Btheta7330_02745
BXY:
BXY_07590
BOA:
Bovatus_00487
(dnaG_1)
BCEL:
BcellWH2_00988
BcellWH2_05226
BCAE:
A4V03_07155
BHF:
C3V43_02670
BIS:
DXK01_001585
DXK01_015245
DXK01_020685
BUN:
Bun01g_29530
BEG:
INE88_03379
BSTE:
K6V31_00750
BFE:
K6V30_17820
BFC:
BacF7301_16885
BSAL:
K6V25_14445
BFIN:
BFINE_40340
BVU:
BVU_3918
BDO:
EL88_04370
EL88_13215
BDH:
GV66_20860
PORP:
J4862_06000
PII:
NF347_08905
BVIR:
I6J59_16380
PHER:
prwr041_03420
prwr041_04100
prwr041_19920
prwr041_20410
prwr041_25910
PRU:
PRU_2774
ALD:
GFH31_06915
AIT:
AI2BBH_10340
AIU:
NQ491_04140
SOQ:
LQ777_06415
HBN:
GUY19_11855
RSR:
T7867_11070
FOR:
FORMB_17130
VG:
13405734
(B619_gp61)
14183015
(F850_gp55)
24657153
(ACQ51_gp45)
26519683
(SEN22_43)
3342479
(61)
6159366
(P)
7353068
(52)
8250800
(47)
» show all
Taxonomy
Virus taxonomy
UniProt
Reference
PMID:
12975372
Authors
Korhonen JA, Gaspari M, Falkenberg M
Title
TWINKLE Has 5' -> 3' DNA helicase activity and is specifically stimulated by mitochondrial single-stranded DNA-binding protein.
Journal
J Biol Chem 278:48627-32 (2003)
DOI:
10.1074/jbc.M306981200
Sequence
[hsa:
56652
]
Reference
PMID:
11431692
Authors
Spelbrink JN, Li FY, Tiranti V, Nikali K, Yuan QP, Tariq M, Wanrooij S, Garrido N, Comi G, Morandi L, Santoro L, Toscano A, Fabrizi GM, Somer H, Croxen R, Beeson D, Poulton J, Suomalainen A, Jacobs HT, Zeviani M, Larsson C
Title
Human mitochondrial DNA deletions associated with mutations in the gene encoding Twinkle, a phage T7 gene 4-like protein localized in mitochondria.
Journal
Nat Genet 28:223-31 (2001)
DOI:
10.1038/90058
Sequence
[hsa:
56652
]
LinkDB
All DBs
DBGET
integrated database retrieval system