KEGG   Bos indicus (zebu cattle): 109572632
Entry
109572632         CDS       T04792                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
biu  Bos indicus (zebu cattle)
Pathway
biu00280  Valine, leucine and isoleucine degradation
biu00640  Propanoate metabolism
biu00785  Lipoic acid metabolism
biu01100  Metabolic pathways
biu01210  2-Oxocarboxylic acid metabolism
Module
biu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:biu00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    109572632 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    109572632 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    109572632 (BCKDHA)
Enzymes [BR:biu01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     109572632 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 109572632
NCBI-ProteinID: XP_019835140
UniProt: A0A6P5DC14
LinkDB
Position
18:50228424..50247707
AA seq 449 aa
MAMAVAVAVARVWRPSRGLGRTGLPLLRLLGARGLARSHPHRWQQQQHFSSLDDKPQFPG
ASAEFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMD
RILYESQRQGRISFYMTNYGEEGTHVGSAAALDDTDLVFGQYREAGVLMYRDYPLELFMA
QCYGNVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANXVVICYF
GEGAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSI
RVDGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDK
QDHPISRLRHHLQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPNPSLIFSDVYQEM
PAQLRKQQESLARHLQTYGEHYPLDHFEK
NT seq 1350 nt   +upstreamnt  +downstreamnt
atggcgatggcggtggcggttgcggtggccagggtttggagaccaagtcgaggcttggga
cggacgggcctcccgctcctgcggctgcttggggctcgtgggctggctagatctcacccc
cacaggtggcagcaacagcagcacttctcgtccctggatgacaagccgcagttcccaggg
gcctcagcggagttcatagacaagctcgaattcatccagcccaatgtcatctctgggatc
cccatctaccgggtcatggaccggcagggccagatcatcaaccccagcgaggatccccac
ctgccccaggagaaggtgctcaaattctacaagagcatgaccctgctcaacaccatggac
cgcatcctctatgaatcccagaggcagggccgcatatccttctacatgaccaactatggc
gaagaggggacacacgtggggagcgcagcagccctggacgacacagacctggtgtttggc
cagtaccgggaggcaggtgtgctcatgtaccgggactacccgttggagctgttcatggcc
cagtgctacggcaacgtgagcgacctgggcaaggggcgccagatgcccgtccactacggc
tgcagggagcgccacttcgtcaccatctcytctccactggccacgcagatcccccaggcg
gtcggggcggcctacgcggccaagagggccaacgctaacrgggtggtcatctgttacttt
ggagagggggcggccagtgagggggacgcccacgccggcttcaacttcgccgccaccctc
gagtgccccatcatcttcttctgtcggaacaacggctacgccatctccacgcccacctcg
gagcagtaccgcggggacggcatagcggctcgaggccccgggtacggcatcctgtccatc
cgcgtggacggcaatgatgtgtttgccgtgtacaacgccaccaaggaggcccggcggcgg
gccgtggcggagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccac
agcaccagtgacgacagctcggcgtaccgctcagtggacgaggtcaactactgggacaag
caggaccaccccatctcccggctgcggcatcacctgcagagccgcggctggtgggacgac
gagcaggagaaggcctggaggaagcagtcccgcaagaaggtaatggaggcctttgagcag
gctgagcggaagctgaagcccaaccccagcttgatcttctcggacgtgtatcaggagatg
cctgcccagctccgcaagcagcaggagtctctggcacgtcacctccagacctatggtgaa
cactacccgctggaccacttcgagaagtga

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