Equus caballus (horse): 100068678
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Entry
100068678 CDS
T01058
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X4
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
ecb
Equus caballus (horse)
Pathway
ecb00280
Valine, leucine and isoleucine degradation
ecb00640
Propanoate metabolism
ecb00785
Lipoic acid metabolism
ecb01100
Metabolic pathways
ecb01210
2-Oxocarboxylic acid metabolism
Module
ecb_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
ecb00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100068678 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100068678 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100068678 (BCKDHA)
Enzymes [BR:
ecb01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100068678 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
100068678
NCBI-ProteinID:
XP_001500344
Ensembl:
ENSECAG00000012246
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All DBs
Position
10:12066726..12084522
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AA seq
445 aa
AA seq
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MAVVTAAARVLGSSRGLGQDGLLLLRRLGVRGLAISHPQRQQQRFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPNLPQEKVLKFYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NVSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSRGWWDDEQEKDWRKQSRKKVMEAFEQAERKPKPNFSLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLDHFEK
NT seq
1338 nt
NT seq
+upstream
nt +downstream
nt
atggcggtggtgacagctgcggcgagagtcctgggatcaagtagaggcctgggccaggat
ggcctactgctcttgcggcggcttggggttcgggggctggctatatctcacccccagagg
cagcagcagcgcttctcgtccttggatgacaagccccagttcccaggggcctcagcggag
tttatagacaagctagagttcatccagcctaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggaccccaatctgccccaggag
aaggtgctcaagttctacaagagcatgacactgctcaacaccatggaccgcatcctctac
gagtcccagcggcagggccggatctccttctacatgaccaactatggcgaggaggggaca
cacgtggggagtgcagcagccctggacaacacggacctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgggactaccccctggaactgttcatggcccagtgctacggc
aacgtgagtgacctgggcaaggggcgccagatgcccgtccactatggctgcaaggagcgc
cactttgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcggcc
tacgcggccaagcgggccaatgccaacagggtcgtcatctgttactttggtgagggggcg
gccagtgagggagatgcccacgccggcttcaacttcgccgccaccctcgagtgccccatc
atcttcttctgccggaacaacggctatgccatctccacacccacttctgagcagtaccgc
ggggatggcatcgcggctcgaggccccgggtatggcatcatgtcaatccgcgtggacggc
aatgatgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgtgccgtggcagag
aaccagcccttcctcattgaggccatgacctacaggatcgggcaccatagcaccagtgac
gatagctcagcgtaccgctctgtggacgaggtcaattactgggacaagcaggaccacccc
atctcgcggctgaggcactacctgcagagccgtggctggtgggatgatgagcaggagaag
gactggaggaagcagtctcgtaagaaggtgatggaggcctttgagcaggctgagcggaag
ccgaagcccaacttcagcctgctcttctcagatgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtccctggcccgtcacctccagacctatggcgagcactaccccctg
gaccacttcgagaagtga
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