KEGG   Homo sapiens (human): 10845
Entry
10845             CDS       T01001                                 
Symbol
CLPX, EPP2
Name
(RefSeq) caseinolytic mitochondrial matrix peptidase chaperone subunit X
  KO
K03544  ATP-dependent Clp protease ATP-binding subunit ClpX
Organism
hsa  Homo sapiens (human)
Disease
H00201  Erythropoietic porphyria
H01763  Porphyria
Brite
KEGG Orthology (KO) [BR:hsa00001]
 09180 Brite Hierarchies
  09182 Protein families: genetic information processing
   03110 Chaperones and folding catalysts [BR:hsa03110]
    10845 (CLPX)
Chaperones and folding catalysts [BR:hsa03110]
 Heat shock proteins
  HSP100
   10845 (CLPX)
SSDB
Motif
Pfam: AAA_2 AAA ClpB_D2-small AAA_5 Sigma54_activat AAA_7 Mg_chelatase Sigma54_activ_2 AAA_22 AAA_14 AAA_16 IstB_IS21 RuvB_N T2SSE NACHT TsaE MCM nSTAND3 DEAD AAA_18 ABC_tran ResIII AAA_24 AAA_29 TIP49 PduV-EutP
Other DBs
NCBI-GeneID: 10845
NCBI-ProteinID: NP_006651
OMIM: 615611
HGNC: 2088
Ensembl: ENSG00000166855
UniProt: O76031
LinkDB
Position
15:complement(65148219..65185342)
AA seq 633 aa
MPSCGACTCGAAAVRLITSSLASAQRGISGGRIHMSVLGRLGTFETQILQRAPLRSFTET
PAYFASKDGISKDGSGDGNKKSASEGSSKKSGSGNSGKGGNQLRCPKCGDLCTHVETFVS
STRFVKCEKCHHFFVVLSEADSKKSIIKEPESAAEAVKLAFQQKPPPPPKKIYNYLDKYV
VGQSFAKKVLSVAVYNHYKRIYNNIPANLRQQAEVEKQTSLTPRELEIRRREDEYRFTKL
LQIAGISPHGNALGASMQQQVNQQIPQEKRGGEVLDSSHDDIKLEKSNILLLGPTGSGKT
LLAQTLAKCLDVPFAICDCTTLTQAGYVGEDIESVIAKLLQDANYNVEKAQQGIVFLDEV
DKIGSVPGIHQLRDVGGEGVQQGLLKLLEGTIVNVPEKNSRKLRGETVQVDTTNILFVAS
GAFNGLDRIISRRKNEKYLGFGTPSNLGKGRRAAAAADLANRSGESNTHQDIEEKDRLLR
HVEARDLIEFGMIPEFVGRLPVVVPLHSLDEKTLVQILTEPRNAVIPQYQALFSMDKCEL
NVTEDALKAIARLALERKTGARGLRSIMEKLLLEPMFEVPNSDIVCVEVDKEVVEGKKEP
GYIRAPTKESSEEEYDSGVEEEGWPRQADAANS
NT seq 1902 nt   +upstreamnt  +downstreamnt
atgcccagctgcggtgcttgtacttgcggcgcggcggccgtccggctcatcacctcctca
ctcgcctccgcgcagagaggtatttctggtggtcgcattcatatgtcagttttaggaagg
cttgggacatttgaaactcagattctgcaaagagctcctcttagatcctttacagaaaca
ccagcatactttgcctcaaaagatgggataagtaaagatggttctggagatggaaataag
aaatcagcaagtgagggaagtagtaagaaatcaggctctgggaattctgggaaaggtgga
aaccagctgcgctgtcctaaatgtggcgacttgtgcacacatgtagagacctttgtatca
tccacccgttttgtcaagtgtgaaaagtgtcatcatttttttgttgtgctatctgaagca
gactcaaagaaaagcataattaaagaacctgaatcagcagcagaagctgtaaaattggca
ttccaacagaaaccaccacctccccctaagaagatttataactacctcgacaagtatgtt
gttggccagtcatttgctaagaaggtgctttcagttgctgtgtacaatcattataagaga
atatataataatatcccagctaatctgagacagcaagcagaggttgagaagcagacatca
ttaacaccaagagagttagaaataagaagacgggaggatgagtacagatttacaaaattg
cttcagattgctggaattagcccacatggtaatgctttaggagcatcaatgcagcaacag
gtaaatcaacaaatacctcaggaaaaacgaggaggtgaagtattggattcttctcatgat
gacataaaacttgaaaaaagtaatattttgctgcttggaccaactgggtcaggtaaaact
ctgctggcacaaaccctagctaaatgccttgatgtcccttttgctatctgtgactgtaca
actttgactcaggctggatatgtaggcgaagatattgaatctgtgattgcaaaactactc
caagatgccaattataatgtggaaaaagcacaacaaggaattgtctttctggatgaagta
gataagattggcagtgtgccaggcattcatcaattacgggatgtaggtggagaaggcgtt
cagcaaggcttattaaaactactagaaggcacaatagtcaatgttccagaaaagaattcc
cgaaagctccgtggagaaacagttcaagttgatacaacaaacatcctgtttgtggcatct
ggtgctttcaatggtttagacagaatcatcagcaggaggaaaaatgaaaagtatcttgga
tttggaacaccatctaatctgggaaaaggcagaagggctgcagctgctgcagaccttgct
aatcgaagtggggaatcgaatactcaccaagacattgaagaaaaagatcggttattgcgt
catgtggaagccagagatctgattgagtttggcatgattcctgagtttgtgggacggttg
cctgtggtggttccattgcatagcctagatgagaaaacacttgtacaaatattaactgag
ccacgaaatgctgttattcctcagtaccaggccttattcagcatggataagtgtgaactg
aatgttactgaggatgctttgaaagctatagccagattggcactagaacgaaaaacaggt
gcacgaggccttcggtccataatggaaaagctgttactagaaccaatgtttgaagtccct
aattctgatatcgtatgtgtggaggttgacaaagaagtagtagaaggaaaaaaggaacca
ggatacatccgggctccaacaaaagaatcctctgaagaggagtatgactctggagttgaa
gaagaaggatggccccgccaagcagatgctgcaaacagctaa

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