Homo sapiens (human): 411
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Entry
411 CDS
T01001
Symbol
ARSB, ASB, G4S, MPS6
Name
(RefSeq) arylsulfatase B
KO
K01135
arylsulfatase B [EC:
3.1.6.12
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00531
Glycosaminoglycan degradation
hsa01100
Metabolic pathways
hsa04142
Lysosome
Module
hsa_M00076
Dermatan sulfate degradation
hsa_M00077
Chondroitin sulfate degradation
Network
nt06012
Glycosaminoglycan degradation
Element
N00610
Dermatan sulfate degradation
Disease
H00131
Mucopolysaccharidosis type VI
H00421
Mucopolysaccharidosis
Drug target
Galsulfase:
D06565
<JP/US>
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09107 Glycan biosynthesis and metabolism
00531 Glycosaminoglycan degradation
411 (ARSB)
09140 Cellular Processes
09141 Transport and catabolism
04142 Lysosome
411 (ARSB)
Enzymes [BR:
hsa01000
]
3. Hydrolases
3.1 Acting on ester bonds
3.1.6 Sulfuric-ester hydrolases
3.1.6.12 N-acetylgalactosamine-4-sulfatase
411 (ARSB)
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Ortholog
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Gene cluster
GFIT
Motif
Pfam:
Sulfatase
Phosphodiest
Sulfatase_C
Motif
Other DBs
NCBI-GeneID:
411
NCBI-ProteinID:
NP_000037
OMIM:
611542
HGNC:
714
Ensembl:
ENSG00000113273
UniProt:
P15848
Structure
PDB
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All DBs
Position
5:complement(78777209..78985958)
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AA seq
533 aa
AA seq
DB search
MGPRGAASLPRGPGPRRLLLPVVLPLLLLLLLAPPGSGAGASRPPHLVFLLADDLGWNDV
GFHGSRIRTPHLDALAAGGVLLDNYYTQPLCTPSRSQLLTGRYQIRTGLQHQIIWPCQPS
CVPLDEKLLPQLLKEAGYTTHMVGKWHLGMYRKECLPTRRGFDTYFGYLLGSEDYYSHER
CTLIDALNVTRCALDFRDGEEVATGYKNMYSTNIFTKRAIALITNHPPEKPLFLYLALQS
VHEPLQVPEEYLKPYDFIQDKNRHHYAGMVSLMDEAVGNVTAALKSSGLWNNTVFIFSTD
NGGQTLAGGNNWPLRGRKWSLWEGGVRGVGFVASPLLKQKGVKNRELIHISDWLPTLVKL
ARGHTNGTKPLDGFDVWKTISEGSPSPRIELLHNIDPNFVDSSPCPRNSMAPAKDDSSLP
EYSAFNTSVHAAIRHGNWKLLTGYPGCGYWFPPPSQYNVSEIPSSDPPTKTLWLFDIDRD
PEERHDLSREYPHIVTKLLSRLQFYHKHSVPVYFPAQDPRCDPKATGVWGPWM
NT seq
1602 nt
NT seq
+upstream
nt +downstream
nt
atgggtccgcgcggcgcggcgagcttgccccgaggccccggacctcggcggctgctcctc
cccgtcgtcctcccgctgctgctgctgctgttgttggcgccgccgggctcgggcgccggg
gccagccggccgccccacctggtcttcttgctggcagacgacctaggctggaacgacgtc
ggcttccacggctcccgcatccgcacgccgcacctggacgcgctggcggccggcggggtg
ctcctggacaactactacacgcagccgctgtgcacgccgtcgcggagccagctgctcact
ggccgctaccagatccgtacaggtttacagcaccaaataatctggccctgtcagcccagc
tgtgttcctctggatgaaaaactcctgccccagctcctaaaagaagcaggttatactacc
catatggtcggaaaatggcacctgggaatgtaccggaaagaatgccttccaacccgccga
ggatttgatacctactttggatatctcctgggtagtgaagattattattcccatgaacgc
tgtacattaattgacgctctgaatgtcacacgatgtgctcttgattttcgagatggcgaa
gaagttgcaacaggatataaaaatatgtattcaacaaacatattcaccaaaagggctata
gccctcataactaaccatccaccagagaagcctctgtttctctaccttgctctccagtct
gtgcatgagccccttcaggtccctgaggaatacttgaagccatatgactttatccaagac
aagaacaggcatcactatgcaggaatggtgtcccttatggatgaagcagtaggaaatgtc
actgcagctttaaaaagcagtgggctctggaacaacacggtgttcatcttttctacagat
aacggagggcagactttggcagggggtaataactggccccttcgaggaagaaaatggagc
ctgtgggaaggaggcgtccgaggggtgggctttgtggcaagccccttgctgaagcagaag
ggcgtgaagaaccgggagctcatccacatctctgactggctgccaacactcgtgaagctg
gccaggggacacaccaatggcacaaagcctctggatggcttcgacgtgtggaaaaccatc
agtgaaggaagcccatcccccagaattgagctgctgcataatattgacccgaacttcgtg
gactcttcaccgtgtcccaggaacagcatggctccagcaaaggatgactcttctcttcca
gaatattcagcctttaacacatctgtccatgctgcaattagacatggaaattggaaactc
ctcacgggctacccaggctgtggttactggttccctccaccgtctcaatacaatgtttct
gagataccctcatcagacccaccaaccaagaccctctggctctttgatattgatcgggac
cctgaagaaagacatgacctgtccagagaatatcctcacatcgtcacaaagctcctgtcc
cgcctacagttctaccataaacactcagtccccgtgtacttccctgcacaggacccccgc
tgtgatcccaaggccactggggtgtggggcccttggatgtag
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