Mus musculus (house mouse): 18597
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Entry
18597 CDS
T01002
Symbol
Pdha1, Pdha-1
Name
(RefSeq) pyruvate dehydrogenase E1 alpha 1
KO
K00161
pyruvate dehydrogenase E1 component subunit alpha [EC:
1.2.4.1
]
Organism
mmu
Mus musculus (house mouse)
Pathway
mmu00010
Glycolysis / Gluconeogenesis
mmu00020
Citrate cycle (TCA cycle)
mmu00620
Pyruvate metabolism
mmu00785
Lipoic acid metabolism
mmu01100
Metabolic pathways
mmu01200
Carbon metabolism
mmu01210
2-Oxocarboxylic acid metabolism
mmu04066
HIF-1 signaling pathway
mmu04922
Glucagon signaling pathway
mmu05230
Central carbon metabolism in cancer
mmu05415
Diabetic cardiomyopathy
Module
mmu_M00307
Pyruvate oxidation, pyruvate => acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
mmu00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00010 Glycolysis / Gluconeogenesis
18597 (Pdha1)
00020 Citrate cycle (TCA cycle)
18597 (Pdha1)
00620 Pyruvate metabolism
18597 (Pdha1)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
18597 (Pdha1)
09130 Environmental Information Processing
09132 Signal transduction
04066 HIF-1 signaling pathway
18597 (Pdha1)
09150 Organismal Systems
09152 Endocrine system
04922 Glucagon signaling pathway
18597 (Pdha1)
09160 Human Diseases
09161 Cancer: overview
05230 Central carbon metabolism in cancer
18597 (Pdha1)
09166 Cardiovascular disease
05415 Diabetic cardiomyopathy
18597 (Pdha1)
Enzymes [BR:
mmu01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.1 pyruvate dehydrogenase (acetyl-transferring)
18597 (Pdha1)
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GFIT
Motif
Pfam:
E1_dh
DXP_synthase_N
TPP_enzyme_C
Motif
Other DBs
NCBI-GeneID:
18597
NCBI-ProteinID:
NP_032836
MGI:
97532
Ensembl:
ENSMUSG00000031299
UniProt:
P35486
Q3UFJ3
LinkDB
All DBs
Position
X:complement(158905215..158921426)
Genome browser
AA seq
390 aa
AA seq
DB search
MRKMLAAVSRVLAGSAQKPASRVLVASRNFANDATFEIKKCDLHRLEEGPPVTTVLTRED
GLKYYRMMQTVRRMELKADQLYKQKIIRGFCHLCDGQEACCVGLEAGINPTDHLITAYRA
HGFTFTRGLPVRAILAELTGRRGGCAKGKGGSMHMYAKNFYGGNGIVGAQVPLGAGIALA
CKYNGKDEVCLTLYGDGAANQGQIFEAYNMAALWKLPCIFICENNRYGMGTSVERAAAST
DYYKRGDFIPGLRVDGMDILCVREATKFAAAYCRSGKGPILMELQTYRYHGHSMSDPGVS
YRTREEIQEVRSKSDPIMLLKDRMVNSNLASVEELKEIDVEVRKEIEDAAQFATADPEPP
LEELGYHIYSSDPPFEVRGANQWIKFKSVS
NT seq
1173 nt
NT seq
+upstream
nt +downstream
nt
atgaggaagatgcttgccgctgtatcccgcgtgttggcaggctctgcgcagaagccggca
agccgagtgctggttgcttcccgtaattttgcaaatgatgctacatttgagattaagaaa
tgtgaccttcatcggctagaagagggccccccagtcaccacagtgctcaccagagaggat
gggctcaagtactacaggatgatgcagactgtgcgccggatggagctaaaggcggatcag
ctgtataagcagaaaatcattcgtggtttctgtcacttgtgtgatggtcaggaagcctgc
tgcgtgggcctggaggctggcataaaccctacggaccacctcatcactgcctatcgagca
catggcttcaccttcactcggggcctgcctgtgcgagcaattcttgcagagctaacagga
cgaagaggaggttgtgctaaagggaaaggcgggtcaatgcacatgtacgccaagaacttc
tatggaggcaacggcatcgttggagctcaggtgcccctgggagcaggaattgccctggcc
tgcaagtacaatggaaaagatgaggtctgtttgacattatacggcgatggtgctgctaat
cagggtcagatctttgaagcttacaatatggcagcactgtggaaattaccttgcattttt
atctgtgagaacaaccgctatggcatggggacgtctgttgagagagcagcagccagcacg
gactactacaaaagaggagattttattcctggactcagggtagatggaatggatatcttg
tgcgtccgagaggcaacaaagtttgcggctgcctattgcaggtctggtaaggggcccatc
ctgatggagctccagacttaccgctaccatggacacagcatgagtgaccctggagtaagc
taccgcactcgagaagaaatccaggaagtaagaagtaagagtgaccctattatgcttctc
aaggatagaatggtgaacagcaatcttgcaagtgttgaagaattaaaggagattgatgtg
gaagtgaggaaagaaatcgaggatgctgcccagtttgccacggctgatcctgagcccccg
ttggaggaactaggctatcacatctacagcagtgatcctccctttgaagtgcgtggtgcc
aaccagtggatcaagtttaagtcagtcagttaa
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