Homo sapiens (human): 37
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Entry
37 CDS
T01001
Symbol
ACADVL, ACAD6, LCACD, VLCAD
Name
(RefSeq) acyl-CoA dehydrogenase very long chain
KO
K09479
very long chain acyl-CoA dehydrogenase [EC:
1.3.8.9
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00071
Fatty acid degradation
hsa01100
Metabolic pathways
hsa01212
Fatty acid metabolism
hsa04936
Alcoholic liver disease
Module
hsa_M00087
beta-Oxidation
Network
nt06020
beta-Oxidation in mitochondria
Element
N00804
beta-Oxidation
Disease
H00392
VLCAD deficiency
H00525
Disorders of mitochondrial fatty-acid oxidation
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09103 Lipid metabolism
00071 Fatty acid degradation
37 (ACADVL)
09160 Human Diseases
09167 Endocrine and metabolic disease
04936 Alcoholic liver disease
37 (ACADVL)
Enzymes [BR:
hsa01000
]
1. Oxidoreductases
1.3 Acting on the CH-CH group of donors
1.3.8 With a flavin as acceptor
1.3.8.9 very-long-chain acyl-CoA dehydrogenase
37 (ACADVL)
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Ortholog
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Gene cluster
GFIT
Motif
Pfam:
Acyl-CoA_dh_1
ACAD9-ACADV_C
Acyl-CoA_dh_M
Acyl-CoA_dh_N
Acyl-CoA_dh_2
Acyl-CoA-dh_C
Motif
Other DBs
NCBI-GeneID:
37
NCBI-ProteinID:
NP_000009
OMIM:
609575
HGNC:
92
Ensembl:
ENSG00000072778
UniProt:
P49748
Structure
PDB
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All DBs
Position
17:7217125..7225266
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AA seq
655 aa
AA seq
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MQAARMAASLGRQLLRLGGGSSRLTALLGQPRPGPARRPYAGGAAQLALDKSDSHPSDAL
TRKKPAKAESKSFAVGMFKGQLTTDQVFPYPSVLNEEQTQFLKELVEPVSRFFEEVNDPA
KNDALEMVEETTWQGLKELGAFGLQVPSELGGVGLCNTQYARLVEIVGMHDLGVGITLGA
HQSIGFKGILLFGTKAQKEKYLPKLASGETVAAFCLTEPSSGSDAASIRTSAVPSPCGKY
YTLNGSKLWISNGGLADIFTVFAKTPVTDPATGAVKEKITAFVVERGFGGITHGPPEKKM
GIKASNTAEVFFDGVRVPSENVLGEVGSGFKVAMHILNNGRFGMAAALAGTMRGIIAKAV
DHATNRTQFGEKIHNFGLIQEKLARMVMLQYVTESMAYMVSANMDQGATDFQIEAAISKI
FGSEAAWKVTDECIQIMGGMGFMKEPGVERVLRDLRIFRIFEGTNDILRLFVALQGCMDK
GKELSGLGSALKNPFGNAGLLLGEAGKQLRRRAGLGSGLSLSGLVHPELSRSGELAVRAL
EQFATVVEAKLIKHKKGIVNEQFLLQRLADGAIDLYAMVVVLSRASRSLSEGHPTAQHEK
MLCDTWCIEAAARIREGMAALQSDPWQQELYRNFKSISKALVERGGVVTSNPLGF
NT seq
1968 nt
NT seq
+upstream
nt +downstream
nt
atgcaggcggctcggatggccgcgagcttggggcggcagctgctgaggctcgggggcgga
agctcgcggctcacggcgctcctggggcagccccggcccggccctgcccggcggccctat
gccgggggtgccgctcagctggctctggacaagtcagattcccacccctctgacgctctg
accaggaaaaaaccggccaaggcggaatctaagtcctttgctgtgggaatgttcaaaggc
cagctcaccacagatcaggtgttcccatacccgtccgtgctcaacgaagagcagacacag
tttcttaaagagctggtggagcctgtgtcccgtttcttcgaggaagtgaacgatcccgcc
aagaatgacgctctggagatggtggaggagaccacttggcagggcctcaaggagctgggg
gcctttggtctgcaagtgcccagtgagctgggtggtgtgggcctttgcaacacccagtac
gcccgtttggtggagatcgtgggcatgcatgaccttggcgtgggcattaccctgggggcc
catcagagcatcggtttcaaaggcatcctgctctttggcacaaaggcccagaaagaaaaa
tacctccccaagctggcatctggggagactgtggccgctttctgtctaaccgagccctca
agcgggtcagatgcagcctccatccgaacctctgctgtgcccagcccctgtggaaaatac
tataccctcaatggaagcaagctttggatcagtaatgggggcctagcagacatcttcacg
gtctttgccaagacaccagttacagatccagccacaggagccgtgaaggagaagatcaca
gcttttgtggtggagaggggcttcgggggcattacccatgggccccctgagaagaagatg
ggcatcaaggcttcaaacacagcagaggtgttctttgatggagtacgggtgccatcggag
aacgtgctgggtgaggttgggagtggcttcaaggttgccatgcacatcctcaacaatgga
aggtttggcatggctgcggccctggcaggtaccatgagaggcatcattgctaaggcggta
gatcatgccactaatcgtacccagtttggggagaaaattcacaactttgggctgatccag
gagaagctggcacggatggttatgctgcagtatgtaactgagtccatggcttacatggtg
agtgctaacatggaccagggagccacggacttccagatagaggccgccatcagcaaaatc
tttggctcggaggcagcctggaaggtgacagatgaatgcatccaaatcatggggggtatg
ggcttcatgaaggaacctggagtagagcgtgtgctccgagatcttcgcatcttccggatc
tttgaggggacaaatgacattcttcggctgtttgtggctctgcagggctgtatggacaaa
ggaaaggagctctctgggcttggcagtgctctaaagaatccctttgggaatgctggcctc
ctgctaggagaggcaggcaaacagctgaggcggcgggcagggctgggcagcggcctgagt
ctcagcggacttgtccacccggagttgagtcggagtggcgagctggcagtacgggctctg
gagcagtttgccactgtggtggaggccaagctgataaaacacaagaaggggattgtcaat
gaacagtttctgctgcagcggctggcagacggggccatcgacctctatgccatggtggtg
gttctctcgagggcctcaagatccctgagtgagggccaccccacggcccagcatgagaaa
atgctctgtgacacctggtgtatcgaggctgcagctcggatccgagagggcatggccgcc
ctgcagtctgacccctggcagcaagagctctaccgcaacttcaaaagcatctccaaggcc
ttggtggagcggggtggtgtggtcaccagcaacccacttggcttctga
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